lignoceric acid has been researched along with Adrenoleukodystrophy in 34 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 11 (32.35) | 18.7374 |
| 1990's | 13 (38.24) | 18.2507 |
| 2000's | 5 (14.71) | 29.6817 |
| 2010's | 5 (14.71) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Aloisi, AM; Blasevich, M; Fessas, D; Haman, N; Paroni, R; Petroni, A | 1 |
| Ben Youssef, IT; Feki, M; Kaabachi, N; Kraoua, I; Nasrallah, F; Omar, S; Sanhaji, H; Zidi, W | 1 |
| Imanaka, T; Kawaguchi, K; Matsumoto, S; Matsuya, Y; Minato, D; Morita, M; Okazaki, A; Shimozawa, N; Tomita, K; Watanabe, S | 1 |
| Brown, A; Ingram, G; Jardine, P; Robertson, NP; Scolding, NJ; Steward, CG; Wilkins, A | 1 |
| de Visser, M; Dijkgraaf, MG; Engelen, M; Hijzen, M; Kemp, S; Ofman, R; Poll-The, BT; van der Wardt, LA; van Geel, BM; Wanders, RJ | 1 |
| Aiello, C; Bizzarri, C; Cappa, M; Di Biase, A; Giannone, G | 1 |
| Blasevich, M; Petroni, A; Uziel, G | 1 |
| Kemp, S; Kulik, W; Mooyer, PA; Valianpour, F; Wanders, RJ | 1 |
| Avigan, J; Chemke, J; Rizzo, WB; Schulman, JD | 1 |
| Goldfischer, S; Moser, AE; Moser, HW; Singh, I | 1 |
| Aubourg, P; Contreras, M; Mandel, JL; Mosser, J; Singh, I | 1 |
| Kremser, K; Lazo, O; Singh, I | 1 |
| Dhaunsi, GS; Lazo, O; Ozand, P; Pahan, K; Singh, I | 1 |
| Aveldaño, MI; Donnari, D | 1 |
| Burdette, DE; Fink, JK; Kremser, K; Pahan, K; Singh, I; Stanley, W | 1 |
| Inoue, K; Kondo, N; Orii, T; Shimozawa, N; Suzuki, Y; Tomatsu, S; Yajima, S | 1 |
| Khan, M; Pahan, K; Singh, I | 1 |
| Chahal, A; Khan, M; Sandhir, R; Singh, I | 1 |
| Blasevich, M; Cavarretta, I; Galli, C; Magnaghi, V; Melcangi, RC; Papini, N; Petroni, A | 1 |
| Berger, J; Dvoráková, L; Hrebícek, M; Hujová, J; Kmoch, S; Storkánová, G; Unterrainer, G; Zeman, J | 1 |
| Contreras, M; Dhaunsi, GS; Lazo, O; Singh, I | 1 |
| Masuno, M; Okamoto, H; Orii, T; Shimozawa, N; Suzuki, Y; Yajima, S | 1 |
| Brückwilder, ML; Hashimoto, T; Monnens, LA; Reubsaet, FA; Trijbels, JM; Veerkamp, JH | 1 |
| Poulos, A; Singh, H; Street, JM | 1 |
| Contreras, M; Lazo, O; Singh, AK; Singh, I; Stanley, W; Weise, M; Yoshida, Y | 1 |
| Derwas, N; Paton, B; Poulos, A; Sharp, P; Singh, H | 1 |
| Derwas, N; Poulos, A; Singh, H | 1 |
| Heikoop, J; Poll-Thé, BT; Saudubray, JM; Schram, AW; Schutgens, RB; Tager, JM; van den Bosch, H; van Roermund, CW; van Wijland, MJ; Wanders, RJ | 1 |
| Bhushan, A; Contreras, M; Lazo, O; Singh, I; Stanley, W | 1 |
| Schutgens, RB; Tager, JM; van den Bosch, H; van Roermund, CW; Wanders, RJ | 1 |
| Contreras, M; Hashmi, M; Irazu, C; Lazo, O; Singh, I; Stanley, W | 1 |
| Griffin, J; Moser, AB; Moser, HW; Sacktor, NC | 1 |
| Kodama, S; Nishio, H; Ohno, M; Onaga, A; Saeki, Y; Shimada, M; Tanaka, K; Yamano, T | 1 |
| Ariga, T; Miyatake, T; Sano-Kawamura, T; Tsuji, S | 1 |
1 trial(s) available for lignoceric acid and Adrenoleukodystrophy
| Article | Year |
|---|---|
Lovastatin in X-linked adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Cholesterol, LDL; Cross-Over Studies; Double-Blind Method; Fatty Acids; Humans; Hydroxymethylglutaryl-CoA Reductase Inhibitors; Lovastatin; Pilot Projects | 2010 |
33 other study(ies) available for lignoceric acid and Adrenoleukodystrophy
| Article | Year |
|---|---|
Thermogenic flux induced by lignoceric acid in peroxisomes isolated from HepG2 cells and from X-adrenoleukodystrophy and control fibroblasts.
Topics: Adrenoleukodystrophy; Cell Line, Tumor; Fatty Acids; Fibroblasts; Hep G2 Cells; Humans; Lipid Metabolism; Oxidation-Reduction; Peroxisomes; Thermogenesis | 2019 |
X-linked Adrenoleukodystrophy, The Tunisian Experience.
Topics: Adolescent; Adrenoleukodystrophy; Adult; Child; Child, Preschool; Chromatography, Gas; Family Health; Fatty Acids; Female; Humans; Male; Middle Aged; Pattern Recognition, Automated; Phenotype; Reproducibility of Results; Retrospective Studies; Tunisia | 2015 |
A novel method for determining peroxisomal fatty acid β-oxidation.
Topics: Adrenoleukodystrophy; Carnitine Acyltransferases; Cells, Cultured; Fatty Acids; Fibroblasts; Humans; Lauric Acids; Lipid Metabolism, Inborn Errors; Mitochondria; Oxidation-Reduction; Peroxisomal Disorders; Peroxisomes; Pyrenes; Skin; Zellweger Syndrome | 2016 |
Very long chain fatty acid levels in patients diagnosed with multiple sclerosis.
Topics: Adrenoleukodystrophy; Adult; Biomarkers; Fatty Acids; Female; Genotype; Humans; Male; Middle Aged; Multiple Sclerosis; Multiple Sclerosis, Chronic Progressive; Pedigree; Phenotype | 2009 |
Is subclinical adrenal failure in adrenoleukodystrophy/adrenomyeloneuropathy reversible?
Topics: Adrenal Glands; Adrenal Insufficiency; Adrenocorticotropic Hormone; Adrenoleukodystrophy; Adult; Dietary Fats; Drug Combinations; Erucic Acids; Fatty Acids; Humans; Hydrocortisone; Triolein | 2011 |
Effects of the testosterone metabolite dihydrotestosterone and 5 alpha-androstan-3 alpha,17 beta-diol on very long chain fatty acid metabolism in X-adrenoleukodystrophic fibroblasts.
Topics: Adrenoleukodystrophy; Androstane-3,17-diol; Cells, Cultured; Child; Cholesterol Esters; Dihydrotestosterone; Fatty Acids; Fibroblasts; Humans; Lipid Metabolism; Oxidation-Reduction; Peroxisomes; Skin | 2003 |
Method for measurement of peroxisomal very-long-chain fatty acid beta-oxidation in human skin fibroblasts using stable-isotope-labeled tetracosanoic acid.
Topics: Adrenoleukodystrophy; Deuterium; Fatty Acids; Feasibility Studies; Fibroblasts; Humans; Isotope Labeling; Oxidation-Reduction; Peroxisomes; Skin; Spectrometry, Mass, Electrospray Ionization | 2004 |
Adrenoleukodystrophy: very long-chain fatty acid metabolism in fibroblasts.
Topics: Adrenoleukodystrophy; Cells, Cultured; Culture Media; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Humans; Palmitates | 1984 |
Lignoceric acid is oxidized in the peroxisome: implications for the Zellweger cerebro-hepato-renal syndrome and adrenoleukodystrophy.
Topics: Abnormalities, Multiple; Adrenoleukodystrophy; Animals; Brain Diseases; Catalase; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Humans; Kidney Diseases; Liver; Liver Diseases; Male; Microbodies; Mitochondria, Liver; Oxidation-Reduction; Rats; Rats, Inbred Strains; Sex Chromosome Aberrations; Syndrome; Urate Oxidase | 1984 |
The protein coded by the X-adrenoleukodystrophy gene is a peroxisomal integral membrane protein.
Topics: Adrenoleukodystrophy; Antibodies, Monoclonal; Blotting, Western; Cell Fractionation; Cells, Cultured; Centrifugation, Isopycnic; Coenzyme A Ligases; Fatty Acids; Fibroblasts; Genetic Linkage; Humans; Intracellular Membranes; Membrane Proteins; Microbodies; Oxidation-Reduction; X Chromosome | 1994 |
Purification of peroxisomes and subcellular distribution of enzyme activities for activation and oxidation of very-long-chain fatty acids in rat brain.
Topics: Adrenoleukodystrophy; Animals; Antibodies; Brain Chemistry; Coenzyme A Ligases; Fatty Acids; Liver; Microbodies; Mitochondria; Palmitic Acid; Palmitic Acids; Rats; Repressor Proteins; Saccharomyces cerevisiae Proteins; Subcellular Fractions; Zellweger Syndrome | 1993 |
Phytanic acid alpha-oxidation. Differential subcellular localization in rat and human tissues and its inhibition by nycodenz.
Topics: Adrenoleukodystrophy; Animals; Cell Fractionation; Cells, Cultured; Centrifugation, Density Gradient; Chlorides; Chondrodysplasia Punctata; Epoxy Compounds; Fatty Acids; Ferric Compounds; Fibroblasts; Humans; Hypoglycemic Agents; Iohexol; Kinetics; Liver; Microbodies; Mitochondria; Organelles; Oxidation-Reduction; Palmitic Acid; Palmitic Acids; Phytanic Acid; Rats; Rats, Sprague-Dawley; Skin; Subcellular Fractions; Zellweger Syndrome | 1993 |
Plasma phospholipid fatty acids in X-linked adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Child; Fatty Acids; Fatty Acids, Unsaturated; Genetic Linkage; Humans; Linoleic Acid; Linoleic Acids; Male; Oleic Acid; Oleic Acids; Phospholipids; Sphingomyelins; X Chromosome | 1996 |
Late-onset generalized disorder of peroxisomes.
Topics: Adrenoleukodystrophy; Adult; Catalase; Fatty Acids; Genetic Linkage; Humans; Male; Microbodies; Oxidation-Reduction; Palmitic Acid; Palmitic Acids; X Chromosome; Zellweger Syndrome | 1996 |
Carrier identification of X-linked adrenoleukodystrophy by measurement of very long chain fatty acids and lignoceric acid oxidation.
Topics: Adrenoleukodystrophy; Cells, Cultured; Fatty Acids; Female; Fibroblasts; Heterozygote; Humans; Male; Oxidation-Reduction; Sphingomyelins; X Chromosome | 1996 |
Lovastatin and sodium phenylacetate normalize the levels of very long chain fatty acids in skin fibroblasts of X- adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Cells, Cultured; Drug Synergism; Fatty Acids; Fibroblasts; Gene Deletion; Humans; Intracellular Fluid; Lovastatin; Mevalonic Acid; Oxidation-Reduction; Phenylacetates; Skin; X Chromosome | 1998 |
Localization of nervonic acid beta-oxidation in human and rodent peroxisomes: impaired oxidation in Zellweger syndrome and X-linked adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Animals; Cell Line; Coenzyme A Ligases; Fatty Acids; Fatty Acids, Monounsaturated; Fibroblasts; Genetic Linkage; Humans; Microbodies; Neuroglia; Oxidation-Reduction; Rats; Rats, Sprague-Dawley; Repressor Proteins; Saccharomyces cerevisiae Proteins; X Chromosome; Zellweger Syndrome | 1998 |
Testosterone metabolites in patients reduce the levels of very long chain fatty acids accumulated in X-adrenoleukodystrophic fibroblasts.
Topics: Adrenoleukodystrophy; Child; Dihydrotestosterone; Fatty Acids; Fibroblasts; Humans; Skin; Testosterone | 2000 |
Eight novel ABCD1 gene mutations and three polymorphisms in patients with X-linked adrenoleukodystrophy: The first polymorphism causing an amino acid exchange.
Topics: 5' Untranslated Regions; Adolescent; Adrenoleukodystrophy; Adult; Alleles; Amino Acid Motifs; ATP Binding Cassette Transporter, Subfamily D, Member 1; ATP-Binding Cassette Transporters; Child; Conserved Sequence; Czech Republic; DNA Mutational Analysis; Exons; Fatty Acids; Female; Genetic Linkage; Humans; Male; Membrane Proteins; Molecular Sequence Data; Mutation, Missense; Oxidation-Reduction; Palmitic Acid; Phenotype; Polymorphism, Genetic; Polymorphism, Single Nucleotide; Slovakia; X Chromosome | 2001 |
Transport of fatty acids into human and rat peroxisomes. Differential transport of palmitic and lignoceric acids and its implication to X-adrenoleukodystrophy.
Topics: Acyl Coenzyme A; Adrenoleukodystrophy; Animals; Biological Transport; Cells, Cultured; Fatty Acids; Fibroblasts; Humans; Liver; Microbodies; Oxidation-Reduction; Palmitic Acids; Palmitoyl Coenzyme A; Rats; Rats, Inbred Strains; Skin | 1992 |
Transformation and characterization of mutant human fibroblasts defective in peroxisome assembly.
Topics: Acyltransferases; Adrenoleukodystrophy; Cell Line, Transformed; Dihydroxyacetone Phosphate; Fatty Acids; Fibroblasts; Humans; Microbodies; Mutation; Transformation, Genetic; Zellweger Syndrome | 1992 |
Immunochemical and biochemical studies of fatty acid oxidation in fibroblasts of Zellweger and X-linked adrenoleukodystrophy patients.
Topics: Acetyl-CoA C-Acyltransferase; Acyl-CoA Oxidase; Adrenoleukodystrophy; Fatty Acids; Fibroblasts; Humans; Immunoblotting; Microbodies; Oxidation-Reduction; Oxidoreductases; Palmitic Acid; Palmitic Acids; X Chromosome; Zellweger Syndrome | 1991 |
Metabolism of saturated and polyunsaturated very-long-chain fatty acids in fibroblasts from patients with defects in peroxisomal beta-oxidation.
Topics: Adrenoleukodystrophy; Carbon Dioxide; Carbon Radioisotopes; Cells, Cultured; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fatty Acids, Monounsaturated; Fatty Acids, Unsaturated; Fibroblasts; Glutamates; Humans; Lipid Metabolism; Microbodies; Oxidation-Reduction; Skin | 1990 |
Cellular oxidation of lignoceric acid is regulated by the subcellular localization of lignoceroyl-CoA ligases.
Topics: Adrenoleukodystrophy; Cell Fractionation; Cell Line; Coenzyme A Ligases; Diffuse Cerebral Sclerosis of Schilder; Endoplasmic Reticulum; Fatty Acids; Fibroblasts; Genetic Linkage; Histocytochemistry; Humans; Microbodies; Microscopy, Electron; Mitochondria; Oxidation-Reduction; Palmitic Acid; Palmitic Acids; Repressor Proteins; Saccharomyces cerevisiae Proteins; X Chromosome; Zellweger Syndrome | 1990 |
Accumulation and defective beta-oxidation of very long chain fatty acids in Zellweger's syndrome, adrenoleukodystrophy and Refsum's disease variants.
Topics: Adrenoleukodystrophy; Carbon Dioxide; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Genetic Diseases, Inborn; Humans; Microbodies; Oxidation-Reduction; Refsum Disease; Syndrome | 1986 |
Beta-oxidation of very-long-chain fatty acids and their coenzyme A derivatives by human skin fibroblasts.
Topics: Abnormalities, Multiple; Acyl Coenzyme A; Adenosine Triphosphate; Adrenoleukodystrophy; Cell Line; Fatty Acids; Fibroblasts; Humans; Kinetics; Magnesium; NAD; Oxidation-Reduction; Refsum Disease; Skin; X Chromosome | 1987 |
Peroxisomal very long-chain fatty acid beta-oxidation in human skin fibroblasts: activity in Zellweger syndrome and other peroxisomal disorders.
Topics: Adrenoleukodystrophy; Adult; Brain Diseases; Cells, Cultured; Fatty Acids; Female; Fibroblasts; Humans; Kidney Diseases; Lipid Metabolism, Inborn Errors; Liver Diseases; Microbodies; Oxidation-Reduction; Refsum Disease; Skin; Syndrome | 1987 |
Adrenoleukodystrophy: impaired oxidation of fatty acids due to peroxisomal lignoceroyl-CoA ligase deficiency.
Topics: Adrenoleukodystrophy; Animals; Coenzyme A Ligases; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Humans; Liver; Microbodies; Palmitic Acid; Palmitic Acids; Rats; Skin | 1989 |
Impaired ability of peroxisomes to activate very-long-chain fatty acids in X-linked adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Humans; Male; Microbodies | 1988 |
Peroxisomal lignoceroyl-CoA ligase deficiency in childhood adrenoleukodystrophy and adrenomyeloneuropathy.
Topics: Adrenoleukodystrophy; Cell Fractionation; Cell Line; Coenzyme A Ligases; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Genetic Linkage; Humans; Microbodies; Microsomes; Mitochondria; Oxidation-Reduction; Palmitic Acids; Palmitoyl Coenzyme A; Skin; X Chromosome | 1988 |
Effects of subperineurial injections of very-long-chain and medium-chain fatty acids into rat sciatic nerve.
Topics: Adrenoleukodystrophy; Animals; Cholesterol Esters; Diffuse Cerebral Sclerosis of Schilder; Disease Models, Animal; Fatty Acids; Lipids; Male; Palmitic Acid; Palmitic Acids; Peripheral Nerves; Rats; Rats, Inbred Strains | 1986 |
Electronmicroscopic study on biopsied rectal mucosa in adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Child; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Humans; Male; Microscopy, Electron; Mucous Membrane; Rectum | 1987 |
Metabolism of [17,18-3H2]hexacosanoic acid and [15,16-3H2]lignoceric acid in cultured skin fibroblasts from patients with adrenoleukodystrophy (ALD) and adrenomyeloneuropathy (AMN).
Topics: Adrenoleukodystrophy; Cells, Cultured; Centrifugation, Density Gradient; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Humans; Skin; Solubility | 1985 |