leucine and Hyperammonemia

leucine has been researched along with Hyperammonemia in 9 studies

Research

Studies (9)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's5 (55.56)29.6817
2010's3 (33.33)24.3611
2020's1 (11.11)2.80

Authors

AuthorsStudies
Li, Y; Liu, XF; Lu, JJ; Qiang, JW; Yang, XY1
Allard, P; Alvarez, F; Gauthier, N; Kratz, L; Lépine, F; Mamer, OA; Mitchell, GA; Moser, AB; Robitaille, Y; Sweetman, L; Wang, SP; Wu, JW1
Dasarathy, S; Davuluri, G; Guan, BJ; Hatzoglou, M; Krokowski, D; Kumar, A; Singh, D; Thapaliya, S1
Kelly, A; Stanley, CA1
Ball, RO; Elango, R; Pencharz, PB1
Murata, K; Ohie, T; Taketani, T; Toriumi, Y; Uchiyama, A; Yamaguchi, S1
Allen, A; Collins, HW; Doliba, NM; Kwagh, J; Li, C; Matschinsky, FM; Najafi, H; Qin, W; Smith, TJ; Stanley, CA1
Ferry, RJ; Grimberg, A; Kelly, A; Koo-McCoy, S; Ng, D; Stanley, CA; Thornton, PS1
Aral, B; Benelli, C; De Lonlay, P; Dionisi-Vici, C; Fouque, F; Ganguly, A; Heinrichs, C; Kamoun, P; Rabier, D; Robert, JJ; Saudubray, JM; Stanley, C; Touati, G1

Other Studies

9 other study(ies) available for leucine and Hyperammonemia

ArticleYear
The interaction of ammonia and manganese in abnormal metabolism of minimal hepatic encephalopathy: A comparison metabolomics study.
    PloS one, 2023, Volume: 18, Issue:8

    Topics: Alanine; Ammonia; Animals; Arginine; Brain; Citrulline; gamma-Aminobutyric Acid; Glutamic Acid; Glutamine; Hepatic Encephalopathy; Hyperammonemia; Inositol; Isoleucine; Lactic Acid; Leucine; Manganese; Metabolomics; Rats; Rats, Sprague-Dawley; Taurine

2023
A liver-specific defect of Acyl-CoA degradation produces hyperammonemia, hypoglycemia and a distinct hepatic Acyl-CoA pattern.
    PloS one, 2013, Volume: 8, Issue:7

    Topics: Acetyl Coenzyme A; Acyl Coenzyme A; Animals; Carbon Dioxide; Gene Knockout Techniques; Gene Order; Gene Targeting; Genes, Lethal; Gluconeogenesis; Hepatocytes; Humans; Hyperammonemia; Hypoglycemia; Lethargy; Leucine; Liver; Metabolic Networks and Pathways; Metabolome; Mice; Mice, Knockout; Mitochondria; Models, Biological; Peroxisomes; Phenotype; Pyruvic Acid

2013
Metabolic adaptation of skeletal muscle to hyperammonemia drives the beneficial effects of l-leucine in cirrhosis.
    Journal of hepatology, 2016, Volume: 65, Issue:5

    Topics: Animals; Humans; Hyperammonemia; Leucine; Liver Cirrhosis; Muscle, Skeletal; Phosphorylation; Rats; Sarcopenia

2016
Neurological aspects in hyperinsulinism-hyperammonaemia syndrome.
    Developmental medicine and child neurology, 2008, Volume: 50, Issue:12

    Topics: Brain Damage, Chronic; Child; Dietary Proteins; Enzyme Activation; Glucose Transporter Type 1; Glutamate Dehydrogenase; Guanosine Triphosphate; Humans; Hyperammonemia; Hyperinsulinism; Hypoglycemia; Leucine; Liver; Mutation, Missense; Neurologic Examination; Pancreas

2008
Determination of the tolerable upper intake level of leucine in adult men.
    The Journal of nutrition, 2012, Volume: 142, Issue:12

    Topics: Adult; Animals; Humans; Hyperammonemia; Leucine; Male; Nutritional Requirements; Oxidation-Reduction

2012
A case of hyperinsulinism/hyperammonaemia syndrome: usefulness of the oral protein tolerance for the evaluation of treatment.
    European journal of pediatrics, 2005, Volume: 164, Issue:3

    Topics: Child; Exons; Female; Glutamate Dehydrogenase; Humans; Hyperammonemia; Hyperinsulinism; Hypoglycemia; Leucine; Mutation; Syndrome

2005
Green tea polyphenols modulate insulin secretion by inhibiting glutamate dehydrogenase.
    The Journal of biological chemistry, 2006, Apr-14, Volume: 281, Issue:15

    Topics: Adenosine Diphosphate; Adenosine Triphosphate; Animals; Cattle; Dose-Response Relationship, Drug; Enzyme Inhibitors; Flavonoids; Glutamate Dehydrogenase; Guanosine Triphosphate; Hyperammonemia; Insulin; Insulin Secretion; Insulin-Secreting Cells; Islets of Langerhans; Kinetics; Leucine; Male; Models, Biological; Models, Chemical; Models, Molecular; Oxygen Consumption; Perfusion; Phenols; Polyphenols; Protein Conformation; Rats; Rats, Wistar; Tea; Time Factors

2006
Acute insulin responses to leucine in children with the hyperinsulinism/hyperammonemia syndrome.
    The Journal of clinical endocrinology and metabolism, 2001, Volume: 86, Issue:8

    Topics: Adolescent; Adult; Amino Acid Substitution; Ammonia; Blood Glucose; Child; Child, Preschool; Diazoxide; Female; Glutamate Dehydrogenase; Humans; Hyperammonemia; Hyperinsulinism; Infant; Insulin; Insulin Secretion; Leucine; Male; Point Mutation; Syndrome

2001
Hyperinsulinism and hyperammonemia syndrome: report of twelve unrelated patients.
    Pediatric research, 2001, Volume: 50, Issue:3

    Topics: Adolescent; Blood Glucose; Child; Child, Preschool; Diet; Female; Glutamate Dehydrogenase; Guanosine Triphosphate; Humans; Hyperammonemia; Hyperinsulinism; Infant; Infant, Newborn; Leucine; Lymphocytes; Male; Syndrome

2001