leucine and Fasting Hypoglycemia

leucine has been researched along with Fasting Hypoglycemia in 229 studies

Research

Studies (229)

TimeframeStudies, this research(%)All Research%
pre-1990207 (90.39)18.7374
1990's6 (2.62)18.2507
2000's11 (4.80)29.6817
2010's4 (1.75)24.3611
2020's1 (0.44)2.80

Authors

AuthorsStudies
Al-Sari, NH; Legido-Quigley, C; Mattila, IM; Pedersen, J; Pedersen-Bjergaard, U; Sejling, AS; She, R1
Allard, P; Alvarez, F; Gauthier, N; Kratz, L; Lépine, F; Mamer, OA; Mitchell, GA; Moser, AB; Robitaille, Y; Sweetman, L; Wang, SP; Wu, JW1
Battezzati, A; Benedini, S; DeTaddeo, F; Luzi, L; Maffi, P; Secchi, A; Sereni, LP1
Kelly, A; Stanley, CA1
Hollinger, EF; Holterman, MJ; Kim, AW; Lee, DD1
Acquaviva, C; Caruba, C; Giudicelli, H; Khalfi, A; Moreigne, M; Pierron, S; Rolland, MO; Touati, G1
Haberstich, P; Kindler, CH; Schürch, M1
Akcay, T; Chadefaux, B; Eaton, S; Ellard, S; Flanagan, SE; Heslegrave, AJ; Hussain, K; Kapoor, RR; Simsek, E1
BUTTERFIELD, WJ; WHICHELOW, MJ; WOOLF, LI; WRIGHT, PH1
FLANAGAN, GC; RYAN, WG; SCHWARTZ, TB1
AUERBACH, VH; DIGEORGE, AM; MABRY, CC4
GILLET, P; LOEB, H; VAN WIEN, H1
COTTE, J; HERMIER, M; JEUNE, M; MARTIN, J1
COCHRANE, W1
GRUMBACH, MM; KAPLAN, SL1
CHAPTAL, J; DOSSA, D; GUILLAUMOT, R; JEAN, R; MOREL, G1
BALASH, WR; BONESSI, JV; DANOWSKI, TS; MOSES, C1
GENTZ, J; LEHMANN, O; ZETTERSTROM, R1
GOMEZ, MR; GOTHAM, JE; MEYER, JS1
GOODELL, RA; STOBO, EA1
HARTMANN, W; SCHREIER, K1
LUCAS, C; REAVEN, G2
BARTTER, FC; HADDAD, HM; PRONOVE, P; ROBERTS, WC1
BOWYER, A; HANASHIRO, P; SCHWARTZ, TB1
ZILOCCHI, C1
GOLDNER, MG; WEISENFELD, S1
BRUUN, I1
BONESSI, JV; DANOWSKI, TS; MOSES, C1
DEKABAN, A; FIELD, JB; STEVENS, H1
CONN, JW; FAJANS, SS; FLOYD, JC; KNOPF, RF4
BRADHAM, R; BUSE, J; BUSE, MG; MARSHALL, JN; OBERMAN, H1
FRAWLEY, TF; PENSUWAN, S; YERRY, R; ZACHAREWICZ, F1
GERSHBERG, H; NADLER, HL; NEUMANN, LL1
Kirtley, WR; Mcarthur, LG; Waife, SO1
BOSHELL, BR; KIRSCHENFELD, JJ; SOTERES, PS1
BUTTERFIELD, WJ; JARRETT, RJ1
METZ, R; PIRANI, C; ROSENTHAL, IM1
CARNEVALI, R; POLI, E; RAINERI, P1
COLES, HM1
ARREAZA VAZ, R; GOMEZ MALARET, S; MACHADO, L1
BAENS, GS; CORNBLATH, M; KLEIN, RI; WYBREGT, SH1
SCHOLTZ, DA1
BIELIK, E; GALIK, L; HRNCIAR, J; HRNCIAROVA, M1
BUSE, J; BUSE, MG; KRECH, LH; MCMASTER, J1
FIELD, JB2
AKIYAMA, Y; ISHIGAMI, R; KWATA, T; NATORI, H; OHMOTO, J; OKADA, H; SHIOTANI, S; YOSHIDA, A1
GOSCINSKA, Z; GUMINSKA, M; HALIKOWSKI, B1
DRASH, A; WOLFF, F1
DEVRIM, S; SASMAZ, O1
KUZUYA, T; NYDICK, M; SAMOLS, E; WILLIAMS, RH1
CHAPTAL, J; GUILLAUMOT, R; JEAN, R; MOREL, G1
ROTH, H; SEGAL, S1
EYMONTT, MJ; GWINUP, G; HAMWI, GJ; KRUGER, FA; MAYNARD, DE1
GINSBERG, DM1
GRIESE, GG; WENZEL, FJ1
WOLFF, G3
CLARKE, DW; EHRLICH, R; EVANS, J; FORBATH, N; VOLPE, R1
FAJANS, SS1
CREUTZFELDT, W; FRERICHS, H1
GREENBERG, RE; REAVEN, G1
GREENSTEIN, NM; LEVY, W; NIV, M1
LUNDBAEK, K1
Ganguly, A; Katz, LE; MacMullen, C; Magge, SN; Shyng, SL; Stanley, CA; Steinkrauss, L1
Murata, K; Ohie, T; Taketani, T; Toriumi, Y; Uchiyama, A; Yamaguchi, S1
Avogaro, A; Boyle, PJ; Cobelli, C; Lubow, JM; Mandeville, KA; Piñón, IG; Toffolo, G; Treeson, DM1
Bodamer, OA; Hussein, K; Langhans, CD; Leonard, JV; Mayatepek, E; Morris, AA; Rating, D1
Hoe, FM; Simmons, RA; Stanley, CA; Steinkrauss, L; Thornton, PS; Wanner, LA1
Fourtner, SH; Kelly, A; Stanley, CA1
Donnell, GN; Koch, R; Lieberman, E; Shaw, KN1
Kenny, FM; Preeyasombat, C1
Robinson, A; Snyder, R1
Correia, JP; DeMoura, MC; Madeira, F1
Palm, D; Welling, P1
Dekaban, A; Moore, W1
Gościńska, Z1
Bain, HW; Ehrlich, R; Martin, J1
Colin, AA; Guttman, H; Hochberg, Z; Spindel, A1
Bradvica, C; Golden, MP; Graham, MJ; Santiago, J; Sargeant, DT; White, NH; Zuniga, O1
Böhles, H1
Kogut, MD; Roe, TF1
Schreier, K1
de Geeter, B; Kurtz, F; Maertens, P; Messer, J; Raber, A; Willard, D1
Donati, MA; Filippi, L; Novembre, E; Zammarchi, E1
Carver, TD; Fennessey, PV; Hay, WW; Pike, AW; Quick, AA; Teng, CC1
Hosaka, T; Oka, Y1
Battezzati, A; Benedini, S; Fattorini, A; Luzi, L; Piceni Sereni, L1
Berry, GT; Ciafre, M; Fukao, T; Gibson, J; Kondo, N; Mazur, A; Mitchell, GA; Palmieri, MJ1
Berger, H1
Araki, N; Harano, Y; Hoshi, M; Kohama, M; Sakamoto, A1
Klöppel, G; Seifert, G1
Förster, H1
Senior, B; Wolfsdorf, JI1
Duff, JH; Groves, AC; Woolf, LI1
Glassman, MS; MacGillivray, MH; Schultz, RM1
Duran, M; Heymans, H; Ketel, A; Ketting, D; Schutgens, RB; Veder, HA; Wadman, SK1
Baker, L; Stanley, CA1
Alberti, KG; Marks, V1
Dallmeier, M; Okoh, O1
Grüttner, R; Held, KR; Plettner, C; Singh, S; Sternowsky, HJ2
Reich, H; Schünke, W1
Horváth, M; Mestyán, J; Schultz, K; Soltész, G1
Ruderman, NB1
Couropmitree, C; Freinkel, N; Hahnel, R; Horwitz, DL; Metzger, B; Nagel, TC; Rubenstein, AH1
Aarskog, D; Fluge, G; Stoa, KF1
Krämer, K; Sailer, FX1
Horwitz, DL; Kuzuya, H; Rubenstein, AH; Sandler, R1
Förster, VH1
Lücking, T1
Abumrad, NN; Eltayeb, K; Hourani, H; Lacy, B1
Abumrad, NN; Hourani, H; May, ME; Morris, JA; Williams, P1
Beaudoing, A; Boujet, C; Halimi, S; Joannard, A; Pradines, S1
Barrett, E; Fagin, KD; Jacob, R; Plewe, G; Sherwin, RS1
Abumrad, NN; Buckspan, R; Devlin, JT; Horton, ES; Hoxworth, B1
Hähnel, R; Wysocki, SJ1
Hansen, E; Jacobsen, BB1
Yoshinaga, T1
Bicknell, J; Crome, L1
Brillanti, F; Geminiani, GD; Gozzetti, G; Zampa, GA1
Miles, LE1
Otawara, S; Otsuka, Y; Takahata, Y1
Drash, A; Schultz, R1
Lundbaek, K; Lyngsoe, J; Madsen, B; Orskov, H; Yde, H1
Greenwood, FC; Howorth, PJ; Marks, V; Samols, E1
Grumbach, MM; Kaplan, SL; Schotland, MG1
Antony, GJ; Underwood, LE; Van Wyk, JJ1
Hung, W; Migeon, CJ1
Frawley, TF; Pensuwan, S1
Steiner, DF1
Etheridge, JE1
Conn, JW; Fajans, SS; Floyd, JC; Harrison, TS; Knopf, RF; Thiffault, CA1
Sleisenger, MH; Walsh, JH1
Marks, V; Samols, E1
Dorner, M; Fontaine, R; Haarscher, A; Hasselmann, JL; Levy-Silagy, J; Schneegans, E1
Bryson, GH; Hume, DM; Williams, C1
Blaskovics, M; Donnell, GN; Kogut, MD1
Williams, C1
Caquet, R1
Pi-Sunyer, FX; Van Itallie, TB; Zintel, HA1
Ito, T; Kikuchi, T; Kumagaya, M; Matsuo, N; Tsuchiya, H1
Hidaka, J; Yoshinaga, T1
Brooten, P; Felig, P; Landsberg, L; Sachs, FL1
Joss, E; Rossi, E; Zuppinger, K1
Brauman, H; Corvilain, J; Telerman-Toppet, N1
Grinvalsky, HT; Remigio, PA1
Parmentier, J; Rubay, J1
Schwartz, JF; Zwiren, GT1
Gorden, P; Roth, J; Sherman, B1
Marks, V1
Levey, GS; Mintz, DH; Schmidt, WM1
Corredor, DG; Danowski, TS; Dhawer, VP; Gonzalez, AR; Jung, Y; Khurana, RC; Klayton, R; Sieracki, JC1
Baker, L; Balsam, MJ; Bishop, HC; Hummeler, K; Kaye, R; Yakovac, WC1
Birchard, E; Cameron, GS; Cole, FM; Tuttle, RJ; Wright, AD1
Alsever, RN; Stjernholm, MR1
Lefebvre, P; Luyckx, A1
Ishihara, Y; Kuroda, A; Sato, N; Tajima, Y; Wada, Y1
Grögler, F; Lucke, C; Mitzkat, HJ1
Chaussain, JL; Georges, P; Job, JC; Olive, G1
Perrone, L1
Shapiro, JR; Sotoudeh, F1
Antony, GJ; Underwood, LE; Van den Brande, JL; Van Wyk, JJ; Voina, SJ1
Hirata, Y1
Altenähr, E; Freytag, G; Klöppel, G; Reichel, W; Willig, R1
Manchester, KL1
Kovac, T1
Colle, E; Schiff, D; Stern, L; Wells, D1
Danowski, TS; Khurana, RC; Klayton, R; Nolan, S; Stephan, T1
Káldor, A; Nékám, K; Pogátsa, G1
Kershnar, AK; Madrigal, LS; Roe, TF; Weitzman, JJ1
Menchini, GF; Meozzi, A1
Duprey, J; Lubetzki, J1
Christensen, NJ1
Hansson, O; Tuvemo, T; Westphal, O1
Thorell, JI; Victorin, LH1
Bannert, N; Fischer, HU; Schütze, I1
Conn, FW; Fajans, SS; Floyd, JC; Knopf, RF1
Isshiki, G; Ogawa, S; Okuno, G; Ueda, T; Yoshinaga, T1
Baker, RJ1
Costamaillere, L1
Brendel, K; Bressler, R; Corredor, C1
Nakajima, I; Ogawa, S; Okumura, Y; Yoshinaga, T1
Misugi, K; Misugi, N; Smith, B; Sotos, J1
Wüstenberg, PW1
Bower, BD; Rayner, PH; Stimmler, L1
Carson, NA1
Fraser, TR; Hartog, M; Lowy, C; Tevaarwerk, G1
Hagberg, B; Hambraeus, L; Westphal, O1
Felig, P; Hendler, R; Kim, YJ; Lynch, V1
Conn, JW; Fajans, SS; Floyd, JC; Knopf, RF; Pek, S; Weissman, P1
Christensen, HN; Tager, HS1
Barbieri, D; Marcondes, E; Quarentei, G; Setian, N1
Berger, S; Green, OC1
Courtecuisse, V; Desbuquois, B; Royer, P1
Danks, DM1
Bachmann, KD1
Brown, RE; Young, RB1
Davis, JM; Himwich, WA; Pederson, VC1
Sidrak, GH; West, ME1
Andreani, D; Fallucca, F; Javicoli, M; Tamburrano, G1
Ambs, E; Brunnberg, J; Gekle, D1
Albeaux-Fernet, M1
Federspil, G; Frezzato, S; Macrì, C; Muggeo, M; Tiengo, A; Trisotto, A; Vianello, A1
Grant, DB1
Chiumello, G; Drash, A; Kenny, FM1
Nabben, FA1
Abe, M; Sano, T; Yaginuma, M1
Ehrlich, RM; Martin, JM1
Teller, W1
Baker, L; Koblenzer, PJ1
Chaptal, J; Guillaumot, R; Jean, R1
Leonards, R; Nader, P1
Maruyama, H1
Friend, JA; Hales, CN1
Colwell, AR1
Gershberg, H; Javier, Z1
Buckler, JM; Grant, DB; Piesowicz, AT1
Hartmann, AF; Stokes, JM; Wohltmann, HJ1
Goodman, AD; Kassoff, A; Mereu, TR1

Reviews

29 review(s) available for leucine and Fasting Hypoglycemia

ArticleYear
[Anaesthesia in patients with maple syrup urine disease. Case report and perioperative anaesthetic management].
    Der Anaesthesist, 2010, Volume: 59, Issue:10

    Topics: Adult; Anesthesia; Humans; Hypoglycemia; Leucine; Male; Maple Syrup Urine Disease; Nervous System Diseases; Perioperative Care

2010
[CONGENITAL DISORDERS OF CARBOHYDRATE METABOLISM].
    Polskie Archiwum Medycyny Wewnetrznej, 1963, Volume: 33

    Topics: Carbohydrate Metabolism; Diabetes Mellitus; Fructose; Galactosemias; Glucosephosphate Dehydrogenase Deficiency; Glucosephosphates; Glycogen Storage Disease; Humans; Hypoglycemia; Leucine; Metabolic Diseases; Pentoses; Urine

1963
[HYPERINSULINISM. DIAGNOSTIC AND THERAPEUTIC ASPECTS].
    Lekarska veda v zahranici, 1964, Mar-20, Volume: 37

    Topics: Diagnosis, Differential; Electrodiagnosis; Electroencephalography; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Pancreas; Sleep Wake Disorders; Surgical Procedures, Operative; Tolbutamide

1964
HYPOGLYCEMIA ASSOCIATED WITH EXTRAPANCREATIC NEOPLASMS, WITH A NOTE ON OTHER UNUSUAL FORMS OF HYPOGLYCEMIA.
    Advances in internal medicine, 1964, Volume: 12

    Topics: Adrenogenital Syndrome; Carcinoma, Hepatocellular; Drug Therapy; Glycogen Storage Disease Type I; Humans; Hypoglycemia; Leucine; Liver Glycogen; Liver Neoplasms; Mesenchymoma; Neoplasms; Retroperitoneal Neoplasms; Thoracic Neoplasms; Tolbutamide

1964
[HYPOGLYCEMIA. 3].
    Medizinische Monatsschrift, 1965, Volume: 19

    Topics: Ethanol; Humans; Hypoglycemia; Insulin; Leucine; Salicylates

1965
LEUCINE-INDUCED HYPOGLYCEMIA.
    The New England journal of medicine, 1965, Jun-10, Volume: 272

    Topics: Adenoma, Islet Cell; Amino Acid Metabolism, Inborn Errors; Diagnosis; Humans; Hypoglycemia; Insulin; Leucine; Metabolism; Pancreatic Neoplasms

1965
[HYPOGLYCEMIA CAUSED BY LEUCINE].
    Deutsche medizinische Wochenschrift (1946), 1965, May-21, Volume: 90

    Topics: Hypoglycemia; Leucine; Pancreatic Diseases; Toxicology

1965
[The diagnosis of hypoglycemia in childhood (author's transl)].
    Klinische Padiatrie, 1980, Volume: 192, Issue:4

    Topics: Adolescent; Age Factors; Alanine; Child; Child, Preschool; Deoxyglucose; Glucagon; Glucose Tolerance Test; Hepatomegaly; Humans; Hypoglycemia; Infant; Infant, Newborn; Leucine; Time Factors; Tolbutamide

1980
[Tolbutamide, glucagon, leucine and arginine tolerance test].
    Nihon rinsho. Japanese journal of clinical medicine, 1997, Volume: 55 Suppl 2

    Topics: Arginine; Diabetes Mellitus; Glucagon; Humans; Hypoglycemia; Insulin; Insulin Secretion; Islets of Langerhans; Leucine; Pancreatic Function Tests; Tolbutamide

1997
[Diffuse nesidioblastic island hyperplasia in the juvenile hypoglycemia syndrome].
    Deutsche medizinische Wochenschrift (1946), 1975, Sep-19, Volume: 100, Issue:38

    Topics: Adenoma, Islet Cell; Child; Child, Preschool; Humans; Hyperplasia; Hypoglycemia; Infant; Infant, Newborn; Islets of Langerhans; Leucine; Pancreatic Neoplasms; Syndrome

1975
Hyperinsulinism in infants and children: diagnosis and therapy.
    Advances in pediatrics, 1976, Volume: 23

    Topics: Adult; Blood Glucose; Child; Child, Preschool; Diazoxide; Fatty Acids, Nonesterified; Humans; Hydroxybutyrates; Hyperinsulinism; Hypoglycemia; Infant; Infant, Newborn; Insulin; Leucine; Male; Pancreatectomy; Proinsulin

1976
Selected tests of carbohydrate metabolism.
    Clinics in endocrinology and metabolism, 1976, Volume: 5, Issue:3

    Topics: Adolescent; Adult; Blood Glucose; Carbohydrate Metabolism; Child; Clinical Laboratory Techniques; Diazoxide; Fasting; Female; Fructose; Galactose; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Inulin; Lactose; Leucine; Male; Middle Aged; Proinsulin; Time Factors; Tolbutamide

1976
Muscle amino acid metabolism and gluconeogenesis.
    Annual review of medicine, 1975, Volume: 26

    Topics: Adaptation, Physiological; Alanine; Amino Acids; Aminoacylation; Animals; Fasting; Forearm; Gluconeogenesis; Glucose; Glutamine; Homeostasis; Humans; Hyperglycemia; Hypoglycemia; Kidney Failure, Chronic; Leucine; Muscle Proteins; Muscles; Nitrogen; Pericardium; Rats; Starvation

1975
Hypoglycemia. Definition, clinical presentations, classification, and laboratory tests.
    Endocrinology and metabolism clinics of North America, 1989, Volume: 18, Issue:1

    Topics: Blood Glucose; Calcium; Fever; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Hypothermia; Insulin; Leucine; Nervous System Diseases; Tolbutamide

1989
[Hypoglycemia. 3].
    Medizinische Monatsschrift, 1970, Volume: 24, Issue:7

    Topics: Animals; Arginine; Biguanides; Diazoxide; Dicumarol; Drug Synergism; Ethanol; Glucagon; Glucocorticoids; Glucose; Guinea Pigs; Humans; Hypoglycemia; Hypoglycemic Agents; Leucine; Mice; Rabbits; Rats; Sympatholytics; Tolbutamide; Xylitol

1970
Hypoglycemia: tolbutamide and leucine tests in insulinoma.
    The Medical clinics of North America, 1968, Volume: 52, Issue:2

    Topics: Adenoma, Islet Cell; Blood Glucose; Fasting; Female; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Insulin Secretion; Leucine; Male; Middle Aged; Pancreatic Neoplasms; Tolbutamide

1968
Hypoglycemia and the central nervous system.
    Pediatric clinics of North America, 1967, Volume: 14, Issue:4

    Topics: Adrenocorticotropic Hormone; Anticonvulsants; Brain; Child, Preschool; Diazoxide; Diet Therapy; Epinephrine; Fasting; Glucagon; Glucose; Glucose Tolerance Test; Humans; Hypoglycemia; Hypoxia; Infant; Infant, Newborn; Infant, Newborn, Diseases; Insulin; Leucine; Oxygen Consumption; Seizures; Tolbutamide; Zinc

1967
Functioning tumors of the pancreas.
    Medical times, 1968, Volume: 96, Issue:9

    Topics: Adenoma, Islet Cell; Diarrhea; Digestive System; Fasting; Gastrins; Glucagon; Glucose; Glucose Tolerance Test; Humans; Hypoglycemia; Hypokalemia; Leucine; Pancreatic Neoplasms; Tolbutamide; Zollinger-Ellison Syndrome

1968
Progress report. Diagnosis of insulinoma.
    Gut, 1971, Volume: 12, Issue:10

    Topics: Adenoma, Islet Cell; Angiography; Blood Glucose; Child; Child, Preschool; Diagnosis, Differential; Ethanol; Fasting; Glucagon; Glucose Tolerance Test; Hormones, Ectopic; Humans; Hypoglycemia; Infant; Infant, Newborn; Injections, Intravenous; Insulin; Leucine; Pancreatic Neoplasms; Parathyroid Neoplasms; Pituitary Neoplasms; Tolbutamide

1971
[Insulinoma].
    Nihon rinsho. Japanese journal of clinical medicine, 1973, Volume: 31, Issue:3

    Topics: Adenoma, Islet Cell; Adolescent; Adult; Aged; Angiography; Child; Diagnosis, Differential; Diagnostic Techniques, Surgical; Female; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Male; Middle Aged; Pancreatic Neoplasms; Proinsulin; Tolbutamide

1973
[Hypoglycemia].
    Nihon rinsho. Japanese journal of clinical medicine, 1972, Volume: 30, Issue:11

    Topics: Blood Glucose; Ethanol; Fasting; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Iatrogenic Disease; Insulin; Insulin Antibodies; Leucine; Tolbutamide

1972
Biochemistry of hypogylcin.
    FEBS letters, 1974, Mar-23, Volume: 40, Issue:0

    Topics: Alanine; Amino Acyl-tRNA Synthetases; Animals; Carbon Radioisotopes; Crystallization; Cyclopropanes; Fatty Acids; Female; Fetus; Humans; Hypoglycemia; Jamaica; Leucine; Liver; Organ Specificity; Plants; Pregnancy; Rats; Species Specificity; Toxins, Biological; Vomiting

1974
Effect of amino acids and proteins on insulin secretion in man.
    Recent progress in hormone research, 1967, Volume: 23

    Topics: Amino Acids; Arginine; Humans; Hypoglycemia; Insulin; Insulin Secretion; Leucine; Proteins

1967
[Hypoglycemia. 3].
    Medizinische Monatsschrift, 1968, Volume: 22, Issue:3

    Topics: Biguanides; Cyclophosphamide; Diet, Diabetic; Ethanol; Glucagon; Humans; Hypoglycemia; Hypoglycemic Agents; Insulin; Leucine; Plant Poisoning; Sulfonamides; Sympathomimetics; Tolbutamide

1968
Newer considerations in the diagnosis and management of fasting hypoglycemia.
    The Surgical clinics of North America, 1969, Volume: 49, Issue:1

    Topics: Adult; Blood Glucose; Catecholamines; Celiac Artery; Child, Preschool; Fasting; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Leucine; Liver Function Tests; Radiography; Radioisotopes; Radionuclide Imaging; Selenium; Tolbutamide

1969
[Spontaneous hypoglycemias].
    Revista medica de Chile, 1969, Volume: 97, Issue:4

    Topics: Ethanol; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Leucine; Tolbutamide

1969
Hypoglycin and hypoglycin-like compounds.
    Pharmacological reviews, 1969, Volume: 21, Issue:2

    Topics: Amino Acids; Animals; Blood Glucose; Carnitine; Chemical Phenomena; Chemistry; Cholesterol; Coenzyme A; Columbidae; Cyclohexanes; Fatty Acids; Fruit; Gluconeogenesis; Glucose; Glycolysis; Hypoglycemia; Hypoglycemic Agents; In Vitro Techniques; Leucine; Mice; Propionates; Rabbits; Rats; Toxins, Biological; Transferases; Vomiting

1969
[The hypoglycemia syndrome].
    Zeitschrift fur die gesamte innere Medizin und ihre Grenzgebiete, 1970, Jun-01, Volume: 25, Issue:11

    Topics: Alloxan; Angiography; Antibiotics, Antineoplastic; Blood Glucose; Diagnosis, Differential; Diazoxide; Diet Therapy; Epinephrine; Gastrointestinal Diseases; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Metabolic Diseases; Neoplasms; Pancreatic Neoplasms; Prednisone; Tolbutamide

1970
[Leucine-sensitive hypoglycemias].
    Rein et foie, maladies de la nutrition; actualites, 1966, Volume: 9

    Topics: Child; Female; Humans; Hypoglycemia; Infant; Leucine; Male

1966

Trials

1 trial(s) available for leucine and Fasting Hypoglycemia

ArticleYear
Decreased branched-chain amino acids and elevated fatty acids during antecedent hypoglycemia in type 1 diabetes.
    BMJ open diabetes research & care, 2023, Volume: 11, Issue:3

    Topics: Amino Acids; Amino Acids, Branched-Chain; Blood Glucose; Diabetes Mellitus, Type 1; Fatty Acids; Humans; Hypoglycemia; Hypoglycemic Agents; Insulin; Isoleucine; Leucine

2023

Other Studies

199 other study(ies) available for leucine and Fasting Hypoglycemia

ArticleYear
A liver-specific defect of Acyl-CoA degradation produces hyperammonemia, hypoglycemia and a distinct hepatic Acyl-CoA pattern.
    PloS one, 2013, Volume: 8, Issue:7

    Topics: Acetyl Coenzyme A; Acyl Coenzyme A; Animals; Carbon Dioxide; Gene Knockout Techniques; Gene Order; Gene Targeting; Genes, Lethal; Gluconeogenesis; Hepatocytes; Humans; Hyperammonemia; Hypoglycemia; Lethargy; Leucine; Liver; Metabolic Networks and Pathways; Metabolome; Mice; Mice, Knockout; Mitochondria; Models, Biological; Peroxisomes; Phenotype; Pyruvic Acid

2013
Protein and glutamine kinetics during counter-regulatory failure in type 1 diabetes.
    Nutrition, metabolism, and cardiovascular diseases : NMCD, 2009, Volume: 19, Issue:5

    Topics: Adult; Blood Glucose; Case-Control Studies; Diabetes Mellitus, Type 1; Epinephrine; Female; Glucagon; Gluconeogenesis; Glucose; Glucose Clamp Technique; Glutamine; Humans; Hypoglycemia; Insulin; Leucine; Male; Metabolic Clearance Rate

2009
Neurological aspects in hyperinsulinism-hyperammonaemia syndrome.
    Developmental medicine and child neurology, 2008, Volume: 50, Issue:12

    Topics: Brain Damage, Chronic; Child; Dietary Proteins; Enzyme Activation; Glucose Transporter Type 1; Glutamate Dehydrogenase; Guanosine Triphosphate; Humans; Hyperammonemia; Hyperinsulinism; Hypoglycemia; Leucine; Liver; Mutation, Missense; Neurologic Examination; Pancreas

2008
Persistent hypoglycemia in a child with a gastrocolic fistula--an unexpected presentation of leucine-sensitive hypoglycemia.
    Journal of pediatric surgery, 2009, Volume: 44, Issue:4

    Topics: Blood Glucose; Child; Chronic Disease; Colonic Diseases; Fluoroscopy; Follow-Up Studies; Gastric Fistula; Humans; Hypersensitivity; Hypoglycemia; Incidental Findings; Intestinal Fistula; Leucine; Male; Risk Assessment; Severity of Illness Index

2009
[Late onset 3-HMG-CoA lyase deficiency: a rare but treatable disorder].
    Archives de pediatrie : organe officiel de la Societe francaise de pediatrie, 2010, Volume: 17, Issue:1

    Topics: Alleles; Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Chromosome Aberrations; Combined Modality Therapy; Diet, Protein-Restricted; DNA Mutational Analysis; Exons; Genes, Recessive; Humans; Hypoglycemia; Leucine; Male; Meglutol; Oxo-Acid-Lyases; Polymerase Chain Reaction; Rare Diseases; Sequence Analysis, DNA

2010
Leucine-sensitive hyperinsulinaemic hypoglycaemia in patients with loss of function mutations in 3-Hydroxyacyl-CoA Dehydrogenase.
    Orphanet journal of rare diseases, 2012, May-14, Volume: 7

    Topics: 3-Hydroxyacyl CoA Dehydrogenases; Child; Child, Preschool; Female; Glutamate Dehydrogenase; Humans; Hyperinsulinism; Hypoglycemia; Immunoprecipitation; Infant; Insulin; Leucine; Male; Mutation

2012
Hypoglycaemic response to leucine in a leucine-sensitive man.
    Nature, 1960, Oct-01, Volume: 188

    Topics: Humans; Hypoglycemia; Hypoglycemic Agents; Leucine; Male

1960
Studies on patients with islet-cell tumor, including the phenomenon of leucine-induced accentuation of hypoglycemia.
    The Journal of clinical endocrinology and metabolism, 1961, Volume: 21

    Topics: Adenoma, Islet Cell; Blood Glucose; Humans; Hypoglycemia; Leucine; Pancreatic Neoplasms

1961
Elevated serum insulin associated with leucine-induced hypoglycaemia.
    Nature, 1960, Dec-17, Volume: 188

    Topics: Humans; Hypoglycemia; Insulin; Insulins; Leucine

1960
[Study of a case of hypoglycemia caused by reaction to leucine].
    Acta paediatrica Belgica, 1960, Volume: 14

    Topics: Child; Humans; Hypersensitivity; Hypoglycemia; Immune System Diseases; Infant; Leucine; Pancreatic Diseases

1960
Leucine-induced hypoglycemia. I. Clinical observations and diagnostic considerations.
    The Journal of pediatrics, 1960, Volume: 57

    Topics: Child; Humans; Hypoglycemia; Infant; Leucine

1960
Leucine-induced hypoglycemia. II. Studies concerning other amino acids and leucine metabolites.
    The Journal of pediatrics, 1960, Volume: 57

    Topics: Amino Acids; Antifibrinolytic Agents; Child; Humans; Hypoglycemia; Infant; Leucine

1960
[Functional hypoglycemia sensitive to L-leucine. Apropos of a case].
    Pediatrie, 1961, Volume: 16

    Topics: Child; Humans; Hypoglycemia; Infant; Leucine; Pancreatic Diseases

1961
Idiopathic infantile hypoglycemia and leucine sensitivity.
    Metabolism: clinical and experimental, 1960, Volume: 9

    Topics: Child; Humans; Hypoglycemia; Infant; Leucine; Pancreatic Diseases

1960
Amino acid and alpha-keto acid-induced hyperinsulinism in the leucine-sensitive type of infantile and childhood hypoglycemia.
    The Journal of pediatrics, 1960, Volume: 57

    Topics: Amino Acids; Child; Humans; Hyperinsulinism; Hypoglycemia; Infant; Keto Acids; Leucine; Seizures

1960
[Clinical and biological study of an infant affected with recurrent hypoglycemia caused by sensitivity to leucine].
    Archives francaises de pediatrie, 1961, Volume: 18

    Topics: Child; Humans; Hypoglycemia; Infant; Leucine; Pancreatic Diseases

1961
Leucine prolongation of tolbutamide-induced hypoglycemia.
    Metabolism: clinical and experimental, 1962, Volume: 11

    Topics: Humans; Hypoglycemia; Hypoglycemic Agents; Leucine; Pancreatic Diseases; Phosphates; Potassium; Tolbutamide

1962
Studies on leucin-induced hypoglycemia.
    Acta paediatrica, 1962, Volume: 51

    Topics: Brain; Brain Diseases; Child; Humans; Hypoglycemia; Infant; Leucine; Metabolic Diseases; Pancreatic Diseases

1962
Effect of sodium glutamate on leucine-induced hypoglycemia: clinical and electroencephalographic study.
    Pediatrics, 1961, Volume: 28

    Topics: Child; Electroencephalography; Glutamates; Humans; Hypoglycemia; Infant; Leucine; Seizures; Sodium Glutamate

1961
Leucine-sensitive hypoglycaemia: case report and family study.
    The Medical journal of Australia, 1961, Dec-30, Volume: 48(2)

    Topics: Child; Humans; Hypoglycemia; Infant; Leucine; Research

1961
[Leucine-sensitive hypoglycemia].
    Monatsschrift fur Kinderheilkunde, 1961, Volume: 109

    Topics: Humans; Hypoglycemia; Leucine; Pancreatic Diseases

1961
Chlorpropamide-induced leucine hypoglycemia.
    The Journal of clinical investigation, 1963, Volume: 42

    Topics: Chlorpropamide; Humans; Hypoglycemia; Leucine; Pancreatic Diseases

1963
Leucine-induced hypoglycemia.
    The New England journal of medicine, 1962, Nov-22, Volume: 267

    Topics: Humans; Hypoglycemia; Leucine

1962
The phenomenon of leucine sensitivity.
    The Medical clinics of North America, 1963, Volume: 47

    Topics: Humans; Hypoglycemia; Leucine

1963
[A case of hypoglycemia sensitive to leucine].
    Minerva pediatrica, 1963, Feb-11, Volume: 15

    Topics: Humans; Hypoglycemia; Leucine

1963
Hyperinsulinemia in 1-leucine-sensitive hypoglycemia in an adult.
    The American journal of medicine, 1961, Volume: 31

    Topics: Adenoma, Islet Cell; Adult; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Medical Records; Pancreatic Neoplasms

1961
[Leucine hypersensitivity with hypoglycemia and epilepsy. A case in a 3-year-old boy].
    Ugeskrift for laeger, 1963, Jan-11, Volume: 125

    Topics: Epilepsy; Humans; Hypersensitivity; Hypoglycemia; Intellectual Disability; Leucine; Male

1963
Acute tolbutamide and leucine effects in diabetes mellitus.
    Metabolism: clinical and experimental, 1962, Volume: 11

    Topics: Diabetes Mellitus; Hyperglycemia; Hypoglycemia; Leucine; Pancreatic Diseases; Phosphates; Potassium; Tolbutamide

1962
Familial idiopathic hypoglycemia: neurological complications.
    Archives of neurology, 1962, Volume: 7

    Topics: Alanine; Galactose; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Leucine; Nervous System Diseases; Neurologic Manifestations

1962
Comparison of experimentally induced and naturally occurring sensitivity to leucine hypoglycemia.
    The Journal of clinical endocrinology and metabolism, 1963, Volume: 23

    Topics: Chlorpropamide; Hypoglycemia; Insulin; Leucine; Pancreatic Diseases

1963
LEUCINE-INDUCED HYPOGLYCEMIA. III. THE BLOOD GLUCOSE DEPRESSANT ACTION OF LEUCINE IN NORMAL INDIVIDUALS.
    The Journal of pediatrics, 1963, Volume: 63

    Topics: Blood Glucose; Child; Humans; Hypoglycemia; Leucine; Toxicology

1963
FUNCTIONING PANCREATIC ISLET CELL ADENOMA. WITH LEUCINE-INDUCED HYPOGLYCEMIA.
    Archives of internal medicine, 1963, Volume: 112

    Topics: Adenoma, Islet Cell; Fasting; Humans; Hypoglycemia; Insulin; Leucine; Pancreatic Neoplasms; Pathology; Surgical Procedures, Operative; Tolbutamide; Toxicology

1963
STUDIES ON THE MECHANISM OF LEUCINE-INDUCED HYPOGLYCEMIA.
    Metabolism: clinical and experimental, 1963, Volume: 12

    Topics: Carbohydrate Metabolism; Diaphragm; Fasting; Glucagon; Glycogen; Hypoglycemia; Insulin; Islets of Langerhans; Leucine; Liver Glycogen; Muscles; Pharmacology; Rats; Research; Tolbutamide

1963
HYPOGLYCEMIA, GROWTH RETARDATION, AND PROBABLE ISOLATED GROWTH HORMONE DEFICIENCY IN A 1-YEAR-OLD CHILD.
    The Journal of pediatrics, 1963, Volume: 63

    Topics: Carbohydrate Metabolism; Child; Deficiency Diseases; Dwarfism, Pituitary; Growth; Growth Hormone; Human Growth Hormone; Humans; Hypoglycemia; Infant; Leucine; Tolbutamide

1963
EFFECTS OF LARGE DOSES OF L-LEUCINE IN ANIMALS AND MAN.
    The American journal of clinical nutrition, 1963, Volume: 13

    Topics: Blood Chemical Analysis; Blood Glucose; Dogs; Hypoglycemia; Leucine; Nitrogen; Pharmacology; Rats; Research

1963
EXTRAPANCREATIC INSULIN-SECRETING TUMOR.
    The New England journal of medicine, 1964, Feb-13, Volume: 270

    Topics: Fibrosarcoma; Geriatrics; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Leucine; Pathology; Retroperitoneal Neoplasms; Surgical Procedures, Operative; Tolbutamide

1964
EVIDENCE THAT INSULIN RELEASE IS THE MECHANISM FOR EXPERIMENTALLY INDUCED LEUCINE HYPOGLYCEMIA IN MAN.
    The Journal of clinical investigation, 1963, Volume: 42

    Topics: Hypoglycemia; Insulin; Leucine; Pancreatic Diseases; Pharmacology; Physiology

1963
LEUCINE-INDUCED HYPOGLYCAEMIA AND ORAL HYPOGLYCAEMIC DRUGS.
    British medical journal, 1964, Apr-04, Volume: 1, Issue:5387

    Topics: Autoradiography; Carbon Isotopes; Chromatography; Diaphragm; Hypoglycemia; Hypoglycemic Agents; Insulin; Leucine; Pharmacology; Phenformin; Proteins; Rats; Research; Tolbutamide

1964
CONGENITAL LEUCINE-SENSITIVE HYPOGLYCEMIA. ASSOCIATION WITH HYPERPLASIA OF BETA CELLS OF THE ISLETS OF LANGERHANS.
    American journal of diseases of children (1960), 1964, Volume: 107

    Topics: Humans; Hyperplasia; Hypertrophy; Hypoglycemia; Infant; Insulin-Secreting Cells; Islands; Islets of Langerhans; Isoleucine; Leucine; Pancreatic Diseases

1964
[HYPOGLYCEMIC REACTION TO LEUCINE, VALINE AND PHENYLALANINE IN A CASE OF DIFFUSE HYPERPLASIA OF THE BETA CELLS].
    Folia endocrinologica, 1963, Volume: 16

    Topics: Glucose Tolerance Test; Humans; Hyperinsulinism; Hyperplasia; Hypoglycemia; Hypoglycemic Agents; Insulin-Secreting Cells; Islands; Islets of Langerhans; Leucine; Pathology; Pharmacology; Phenylalanine; Tolbutamide; Valine

1963
LEUCINE-SENSITIVE HYPOGLYCEMIA.
    Proceedings of the Royal Society of Medicine, 1964, Volume: 57

    Topics: Glucose Tolerance Test; Humans; Hypoglycemia; Infant; Leucine; Metabolism; Methylprednisolone; Seizures; Tolbutamide

1964
[CONSIDERATIONS ON 2 CASES OF IDIOPATHIC LEUCINE SENSITIVE HYPOGLYCEMIA].
    Archivos de pediatria del Uruguay, 1964, Volume: 35

    Topics: Diet; Diet Therapy; Glucose; Humans; Hypoglycemia; Infant; Isoleucine; Leucine; Pancreatic Diseases

1964
SYMPTOMATIC NEONATAL HYPOGLYCEMIA. STUDIES OF CARBOHYDRATE METABOLISM IN THE NEWBORN INFANT. VIII.
    Pediatrics, 1964, Volume: 33

    Topics: Adolescent; Black People; Blood Chemical Analysis; Carbohydrate Metabolism; Central Nervous System Diseases; Child; Diseases in Twins; Epinephrine; Female; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Infant; Infant, Newborn; Infant, Newborn, Diseases; Infant, Premature, Diseases; Leucine; Liver Glycogen; Neurologic Manifestations; Polycythemia; Pre-Eclampsia; Pregnancy; Tolbutamide

1964
SPONTANEOUS HYPOGLYCEMIA: DIAGNOSTIC CONSIDERATIONS AND MANAGEMENT.
    Arizona medicine, 1964, Volume: 21

    Topics: Adenoma, Islet Cell; Diabetes Mellitus; Diagnosis, Differential; Humans; Hypoglycemia; Leucine; Malingering; Neoplasm Metastasis; Pancreatic Neoplasms; Surgical Procedures, Operative; Tolbutamide

1964
THE EFFECT OF TRIS (HYDROXYMETHYL) AMINOMETHANE ON GLUCOSE UTILIZATION OF SKELETAL MUSCLE.
    Metabolism: clinical and experimental, 1964, Volume: 13

    Topics: Acidosis; Animals; Carbohydrate Metabolism; Carbon Isotopes; Dogs; Glucose; Hypoglycemia; Insulin; Lactates; Leucine; Metabolism; Methylamines; Muscle, Skeletal; Muscles; Propylene Glycols; Proteins; Rabbits; Rats; Research; Tromethamine

1964
CLINICAL AND BIOCHEMICAL STUDIES IN PATIENTS WITH FUNCTIONING ISLET CELL TUMORS.
    The American journal of medicine, 1964, Volume: 36

    Topics: Adenoma, Islet Cell; Amino Acids; Biochemical Phenomena; Biochemistry; Biomedical Research; Carbohydrate Metabolism; Glucose; Glucose Tolerance Test; Glutarates; Humans; Hypoglycemia; Insulin; Isoleucine; Leucine; Liver Neoplasms; Neoplasm Metastasis; Pancreatic Neoplasms; Research; Valine

1964
[STUDIES ON ORAL TOLBUTAMIDE TEST].
    Naika hokan. Japanese archives of internal medicine, 1964, Volume: 11

    Topics: Blood Glucose; Carbutamide; Cystine; Diabetes Mellitus; Diagnosis; Gastric Juice; Hypoglycemia; Leucine; Liver Cirrhosis; Nephritis; Pancreatic Diseases; Pharmacology; Tolbutamide

1964
[EFFECT OF LEUCINE ON GLYCEMIA IN DIABETES IN CHILDREN].
    Pediatria polska, 1964, Volume: 39

    Topics: Adolescent; Blood Glucose; Child; Diabetes Mellitus; Diabetes Mellitus, Type 1; Epinephrine; Humans; Hypoglycemia; Leucine; Pharmacology; Phenylketonurias

1964
DRUG THERAPY IN LEUCINE-SENSITIVE HYPOGLYCEMIA.
    Metabolism: clinical and experimental, 1964, Volume: 13

    Topics: Antihypertensive Agents; Benzothiadiazines; Child; Diazoxide; Dietary Carbohydrates; Dietary Proteins; Drug Therapy; Fasting; Humans; Hypoglycemia; Leucine; Pancreatic Diseases; Pharmacology

1964
PLASMA INSULIN IN ORGANIC HYPERINSULINISM: COMPARATIVE EFFECTS OF TOLBUTAMIDE, LEUCINE AND GLUCOSE.
    The Journal of clinical endocrinology and metabolism, 1964, Volume: 24

    Topics: Adenoma, Islet Cell; Blood; Blood Chemical Analysis; Blood Glucose; Glucagon; Glucose; Humans; Hyperglycemia; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Pancreatic Neoplasms; Pharmacology; Surgical Procedures, Operative; Tolbutamide

1964
[EXPERIMENTAL STUDIES ON THE MECHANISM OF L-LEUCINE HYPOGLYCEMIA. (CROSS-CIRCULATION ASSAYS IN DOGS)].
    Turk Tip Cemiyeti mecmuasi, 1964, Volume: 30

    Topics: Biological Assay; Dogs; Hypoglycemia; Leucine; Pancreatic Diseases; Research

1964
A DIFFICULT DIAGNOSTIC PROBLEM IN SPONTANEOUS HYPOGLYCEMIA. REACTIVE HYPOGLYCEMIA IN MILD DIABETES MELLITUS.
    Annals of internal medicine, 1964, Volume: 61

    Topics: Blood Glucose; Diabetes Mellitus; Diagnosis, Differential; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Leucine

1964
A COMPARISON OF LEUCINE- AND ACETOACETATE-INDUCED HYPOGLYCEMIA IN MAN.
    The Journal of clinical investigation, 1964, Volume: 43

    Topics: Acetoacetates; Biomedical Research; Chlorpropamide; Drug Synergism; Hypoglycemia; Insulin; Leucine; Metabolism; Pancreatic Diseases; Pharmacology; Toxicology; Valerian

1964
[CONTRIBUTION TO THE BIOLOGICAL STUDY OF RECURRENT HYPOGLYCEMIA CAUSED BY SENSITIVITY TO LEUCINE. RESEARCH ON THE QUANTITATIVE LEUCINE-INSULIN RELATION].
    La Medecine infantile, 1964, Volume: 71

    Topics: Adolescent; Amino Acids; Blood Chemical Analysis; Child; Humans; Hypoglycemia; Insulin; Leucine; Pancreatic Diseases; Physiology; Potassium; Research

1964
THE DIETARY MANAGEMENT OF LEUCINE-SENSITIVE HYPOGLYCEMIA, WITH REPORT OF A CASE.
    Pediatrics, 1964, Volume: 34

    Topics: Diet; Diet Therapy; Dietary Proteins; Drug Therapy; Humans; Hypoglycemia; Infant; Infant, Newborn; Leucine; Neurologic Manifestations; Prednisone

1964
CUSHING'S SYNDROME WITH HYPOGLYCEMIA CAUSED BY ADRENOCORTICAL CARCINOMA.
    The Journal of clinical endocrinology and metabolism, 1965, Volume: 25

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Gland Neoplasms; Adrenocortical Carcinoma; Aldosterone; Anabolic Agents; Androsterone; Cushing Syndrome; Dexamethasone; Etiocholanolone; Humans; Hydrocortisone; Hypoglycemia; Leucine; Manganese; Pathology; Steroids; Tolbutamide; Urine

1965
LEUCINE-SENSITIVE HYPOGLYCEMIA TREATED WITH LONG-ACTING EPINEPHRINE.
    Pediatrics, 1965, Volume: 35

    Topics: Amino Acid Metabolism, Inborn Errors; Delayed-Action Preparations; Drug Therapy; Epinephrine; Humans; Hypoglycemia; Infant; Injections; Injections, Subcutaneous; Leucine

1965
EVIDENCE FAVORING THE SARCOMATOUS ORIGIN OF AN INSULIN-LIKE SUBSTANCE IN A CASE OF FIBROSARCOMA WITH HYPOGLYCEMIA.
    The American journal of medicine, 1965, Volume: 38

    Topics: Blood Glucose; Calcium Isotopes; Chemical Phenomena; Chemistry; Epinephrine; Fibrosarcoma; Glucagon; Glucose Tolerance Test; Growth Hormone; Human Growth Hormone; Humans; Hypoglycemia; Insulin; Leucine; Liver Neoplasms; Pathology; Prolactin; Radioisotopes; Radionuclide Imaging; Tolbutamide

1965
EXPERIMENTAL LEUCINE-INDUCED HYPOGLYCEMIA IN MICE.
    Metabolism: clinical and experimental, 1965, Volume: 14

    Topics: Carbohydrate Metabolism; Carbon Isotopes; Clinical Enzyme Tests; Fructose-Bisphosphatase; Glucose; Glucose-6-Phosphatase; Glycerol; Glycine; Hypoglycemia; Insulin; Insulin, Long-Acting; Leucine; Lipid Metabolism; Liver; Mice; Pyruvates; Research; Toxicology

1965
Leucine sensitive hypoglycemia. The value of milk free diet.
    The Jewish Memorial Hospital bulletin, 1962, Volume: 6-7

    Topics: Child; Diet; Humans; Hypoglycemia; Infant; Leucine; Milk; Nutrition Assessment; Nutritional Status; Pancreatic Diseases; Seizures

1962
[Leucine hypersensitivity with hypoglycemia. A case in a 2-year-old child].
    Ugeskrift for laeger, 1962, Feb-16, Volume: 124

    Topics: Child; Humans; Hypersensitivity; Hypoglycemia; Infant; Leucine

1962
The use of insulin in the production of L-leucine-induced hypoglycemia in normal dogs.
    The Journal of clinical investigation, 1962, Volume: 41

    Topics: Animals; Dogs; Hypoglycemia; Insulin; Leucine; Pancreatic Diseases

1962
Familial leucine-sensitive hypoglycemia of infancy due to a dominant mutation of the beta-cell sulfonylurea receptor.
    The Journal of clinical endocrinology and metabolism, 2004, Volume: 89, Issue:9

    Topics: Child, Preschool; Congenital Hyperinsulinism; Humans; Hypoglycemia; Islets of Langerhans; Leucine; Male; Multidrug Resistance-Associated Proteins; Mutation

2004
A case of hyperinsulinism/hyperammonaemia syndrome: usefulness of the oral protein tolerance for the evaluation of treatment.
    European journal of pediatrics, 2005, Volume: 164, Issue:3

    Topics: Child; Exons; Female; Glutamate Dehydrogenase; Humans; Hyperammonemia; Hyperinsulinism; Hypoglycemia; Leucine; Mutation; Syndrome

2005
Brain oxygen utilization is unchanged by hypoglycemia in normal humans: lactate, alanine, and leucine uptake are not sufficient to offset energy deficit.
    American journal of physiology. Endocrinology and metabolism, 2006, Volume: 290, Issue:1

    Topics: Adult; Alanine; Blood Glucose; Brain; Cerebrovascular Circulation; Energy Metabolism; Female; Glucose; Glucose Clamp Technique; Humans; Hypoglycemia; Lactic Acid; Leucine; Male; Oxygen

2006
Glucose and leucine kinetics in idiopathic ketotic hypoglycaemia.
    Archives of disease in childhood, 2006, Volume: 91, Issue:6

    Topics: Alanine; Amino Acids, Branched-Chain; Basal Metabolism; Calorimetry, Indirect; Carnitine; Case-Control Studies; Child; Child, Preschool; Fasting; Female; Glucose; Humans; Hypoglycemia; Infant; Insulin; Ketosis; Leucine; Male

2006
Clinical features and insulin regulation in infants with a syndrome of prolonged neonatal hyperinsulinism.
    The Journal of pediatrics, 2006, Volume: 148, Issue:2

    Topics: Antihypertensive Agents; Calcium; Case-Control Studies; Diazoxide; Enteral Nutrition; Fasting; Female; Glucose; Humans; Hyperinsulinism; Hypoglycemia; Hypoglycemic Agents; Infant; Infant, Newborn; Infusions, Intravenous; Insulin; Insulin Secretion; Leucine; Male; Prospective Studies; Risk Factors; Sweetening Agents; Tolbutamide

2006
Protein-sensitive hypoglycemia without leucine sensitivity in hyperinsulinism caused by K(ATP) channel mutations.
    The Journal of pediatrics, 2006, Volume: 149, Issue:1

    Topics: Adenosine Triphosphate; Administration, Oral; Adolescent; Adult; ATP-Binding Cassette Transporters; Blood Glucose; Case-Control Studies; Child; Child, Preschool; Congenital Hyperinsulinism; Female; Glutamate Dehydrogenase; Humans; Hypoglycemia; Infant; Infant, Newborn; Insulin; Leucine; Male; Mutation; Potassium Channels; Potassium Channels, Inwardly Rectifying; Proteins; Receptors, Drug; Sulfonylurea Receptors

2006
Hypoglycemia in maple syrup urine disease.
    American journal of diseases of children (1960), 1967, Volume: 113, Issue:1

    Topics: Animals; Caseins; Female; Gluconeogenesis; Glucose; Glucose Tolerance Test; Glycogen; Humans; Hyperinsulinism; Hypoglycemia; In Vitro Techniques; Infant; Leucine; Male; Maple Syrup Urine Disease; Rats

1967
Cortisol production rate. VI. Hypoglycemia in the neonatal and postneonatal period, and in association with dwarfism.
    The Journal of pediatrics, 1967, Volume: 70, Issue:1

    Topics: 17-Ketosteroids; Birth Weight; Child; Child, Preschool; Dwarfism; Epinephrine; Female; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Infant; Infant, Newborn; Insulin; Leucine; Male; Pituitary Function Tests; Tolbutamide

1967
Leucine-induced hypoglycemia.
    American journal of diseases of children (1960), 1967, Volume: 113, Issue:5

    Topics: Diet Therapy; Dietary Carbohydrates; Female; Humans; Hypoglycemia; Infant; Intellectual Disability; Leucine; Male

1967
Clinical alcohol hypoglycemia.
    Annals of internal medicine, 1967, Volume: 66, Issue:5

    Topics: Aged; Alcoholic Intoxication; Alcoholism; Blood Glucose; Ethanol; Fasting; Female; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Injections, Intravenous; Leucine; Male; Tolbutamide

1967
[Leucine sensitive hypoglycemia].
    Monatsschrift fur Kinderheilkunde, 1967, Volume: 115, Issue:1

    Topics: Diet Therapy; Epinephrine; Female; Glucocorticoids; Glutamates; Humans; Hypoglycemia; Infant, Newborn; Leucine; Prednisone

1967
Neurological complications of idiopathic hypoglycemia in children.
    Acta neurologica Scandinavica, 1967, Volume: 43, Issue:1

    Topics: Cerebral Cortex; Child; Child, Preschool; Diet Therapy; Female; Glucose Tolerance Test; Humans; Hypoglycemia; Infant; Leucine; Male; Nerve Degeneration; Neuroglia; Seizures

1967
[Effect of leucine on glycemia in childhood diabetes].
    Folia medica Cracoviensia, 1967, Volume: 9, Issue:1

    Topics: Adolescent; Child; Diabetes Mellitus, Type 1; Humans; Hypoglycemia; Leucine

1967
Comment on management of hypoglycemia.
    The Journal of pediatrics, 1967, Volume: 71, Issue:4

    Topics: Diazoxide; Humans; Hypoglycemia; Leucine; Pancreatectomy

1967
Leucine-induced hypoglycemia in a family: effect of diphenylhydantoin, oxprenolol, and diazoxide.
    Hormone research, 1984, Volume: 20, Issue:4

    Topics: Adult; Child; Child, Preschool; Diazoxide; Female; Genes, Dominant; Humans; Hypoglycemia; Infant; Leucine; Male; Oxprenolol; Pedigree; Phenytoin

1984
Persistent leucine sensitivity following partial pancreatectomy and diazoxide treatment. Therapeutic response.
    American journal of diseases of children (1960), 1983, Volume: 137, Issue:4

    Topics: Child, Preschool; Diazoxide; Female; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Pancreatectomy; Pancreatic Diseases; Seizures

1983
Idiopathic leucine-sensitive hypoglycemia syndrome: insulin and glucagon responses and effects of diazoxide.
    Pediatric research, 1982, Volume: 16, Issue:1

    Topics: Arginine; Blood Glucose; Child; Child, Preschool; Diazoxide; Female; Glucagon; Humans; Hypoglycemia; Insulin; Leucine; Male

1982
[Modern possibilities in the early diagnosis of congenital metabolic diseases].
    Die Medizinische Welt, 1982, Apr-02, Volume: 33, Issue:13

    Topics: Female; Humans; Hypercholesterolemia; Hyperlipoproteinemia Type IV; Hypoglycemia; Infant, Newborn; Leucine; Metabolism, Inborn Errors; Phenylketonurias; Pregnancy; Prenatal Diagnosis

1982
[Long-term diazoxide therapy in recurrent leucine-sensitive hypoglycemia (author's transl)].
    Annales de pediatrie, 1980, Volume: 27, Issue:10

    Topics: Child, Preschool; Diazoxide; Female; Growth; Humans; Hyperinsulinism; Hypoglycemia; Infant; Infant, Newborn; Leucine

1980
Biochemical evaluation of a patient with a familial form of leucine-sensitive hypoglycemia and concomitant hyperammonemia.
    Metabolism: clinical and experimental, 1996, Volume: 45, Issue:8

    Topics: Adult; Ammonia; Drug Resistance; Female; Glutamates; Humans; Hyperinsulinism; Hypoglycemia; Infant; Leucine; Male

1996
Leucine metabolism in chronically hypoglycemic hypoinsulinemic growth-restricted fetal sheep.
    The American journal of physiology, 1997, Volume: 272, Issue:1 Pt 1

    Topics: Animals; Blood Glucose; Body Weight; Carbon Isotopes; Chronic Disease; Female; Fetal Blood; Fetal Growth Retardation; Fetus; Hypoglycemia; Insulin; Keto Acids; Leucine; Organ Size; Oxygen; Placenta; Pregnancy; Sheep

1997
Effect of hypoglycemia on amino acid and protein metabolism in healthy humans.
    Diabetes, 2000, Volume: 49, Issue:9

    Topics: Adult; Blood Glucose; C-Peptide; Carbon Isotopes; Fatty Acids, Nonesterified; Female; Glucose Clamp Technique; Glutamine; Humans; Hypoglycemia; Insulin; Insulin Secretion; Kinetics; Leucine; Male; Nitrogen Isotopes; Proteins; Reference Values; Sodium Bicarbonate

2000
Neonatal hypoglycaemia in severe succinyl-CoA: 3-oxoacid CoA-transferase deficiency.
    Journal of inherited metabolic disease, 2001, Volume: 24, Issue:5

    Topics: Attention Deficit Disorder with Hyperactivity; Blood Glucose; Brain; Child; Coenzyme A-Transferases; Glucose; Humans; Hypoglycemia; Immunoblotting; Infant, Newborn; Infusions, Intravenous; Insulin; Ketone Bodies; Leucine; Metabolism, Inborn Errors; Tomography, X-Ray Computed

2001
Hypoglycemia: a perspective.
    Postgraduate medicine, 1975, Volume: 57, Issue:2

    Topics: Adenoma, Islet Cell; Citric Acid Cycle; Diabetes Complications; Diazoxide; Female; Glucose; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Liver; Liver Diseases; Middle Aged; Muscles; Pancreatic Neoplasms; Streptozocin; Tolbutamide

1975
Qualitative abnormality of insulin secretion in a case with insulinoma.
    Endocrinologia japonica, 1975, Volume: 22, Issue:2

    Topics: Adenoma; Adenoma, Islet Cell; Blood Glucose; Female; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Insulin Secretion; Leucine; Microscopy, Electron; Middle Aged; Pancreatic Neoplasms

1975
[Hypoglycemia. 3. Hypoglycemias caused by defined metabolic defects; hormonal regulation of blood glucose concentration and its disorders].
    Fortschritte der Medizin, 1976, Feb-12, Volume: 94, Issue:5

    Topics: Fructose-1,6-Diphosphatase Deficiency; Galactose; Gluconeogenesis; Glucosephosphate Dehydrogenase Deficiency; Glycogen; Glycogen Storage Disease; Glycoside Hydrolases; Humans; Hyperinsulinism; Hypoglycemia; Hypothyroidism; Insulin; Lactates; Leucine; Parathyroid Hormone; Phosphorylases; Pyruvate Carboxylase Deficiency Disease

1976
The diagnosis of insulinoma in a child in the absence of fasting hyperinsulinemia.
    Pediatrics, 1979, Volume: 64, Issue:4

    Topics: Adenoma, Islet Cell; Blood Glucose; Child; Fasting; Female; Glucose; Glycogen; Humans; Hypoglycemia; Insulin; Insulin Secretion; Ketone Bodies; Leucine; Pancreatic Neoplasms

1979
Amino acid metabolism in dogs with E. coli bacteremic shock.
    Surgery, 1979, Volume: 85, Issue:2

    Topics: Alanine; Amino Acids; Animals; Blood Gas Analysis; Blood Pressure; Blood Urea Nitrogen; Dogs; Escherichia coli Infections; Glucagon; Glycine; Hypoglycemia; Isoleucine; Lactates; Leucine; Muscles; Shock, Septic; Valine

1979
Gonadal dysgenesis and leucine-sensitive hypoglycemia.
    The Journal of pediatrics, 1979, Volume: 94, Issue:6

    Topics: Female; Humans; Hypoglycemia; Infant; Leucine; Turner Syndrome

1979
Lethal hypoglycemia in a child with a deficiency of 3-hydroxy-3-methylglutarylcoenzyme A lyase.
    The Journal of pediatrics, 1979, Volume: 94, Issue:1

    Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Glutarates; Humans; Hypoglycemia; Infant; Leucine; Liver; Male; Oxo-Acid-Lyases

1979
[Leucine-sensitive hypoglycemia and its diet therapy].
    MMW, Munchener medizinische Wochenschrift, 1976, Nov-12, Volume: 118, Issue:46

    Topics: Amino Acid Metabolism, Inborn Errors; Child; Diagnostic Errors; Female; Humans; Hypoglycemia; Leucine; Spasms, Infantile

1976
[Ketotic hypoglycemia in intermittent branch-chain ketoaciduria. Enzymatic and gas chromatographic studies].
    Monatsschrift fur Kinderheilkunde, 1976, Volume: 124, Issue:5

    Topics: Child; Chromatography, Gas; Female; Fibroblasts; Humans; Hypoglycemia; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Valine

1976
[Leucine-sensitive hypoglycaemia and its treatment with diazoxide (author's transl)].
    Monatsschrift fur Kinderheilkunde, 1976, Volume: 129, Issue:9

    Topics: Amino Acid Metabolism, Inborn Errors; Blood Glucose; Diazoxide; Dietary Proteins; Female; Humans; Hyperinsulinism; Hypoglycemia; Infant; Insulin; Leucine; Prognosis; Seizures

1976
The metabolic effects of glucagon infusion in normoglycaemic and hypoglycaemic small-for-gestational-age infants. II. Changes in plasma amino acids.
    Acta paediatrica Academiae Scientiarum Hungaricae, 1976, Volume: 17, Issue:3

    Topics: Alanine; Amino Acids; Aspartic Acid; Blood Glucose; Citrulline; Glucagon; Gluconeogenesis; Glycine; Humans; Hypoglycemia; Infant, Low Birth Weight; Infant, Newborn; Infant, Small for Gestational Age; Infusions, Parenteral; Isoleucine; Leucine; Liver; Proline; Valine

1976
Plasma C-peptide and diagnosis of factitious hyperinsulinism. Study of an insulin-dependent diabetic patient with "spontaneous" hypoglycemia.
    Annals of internal medicine, 1975, Volume: 82, Issue:2

    Topics: Diabetes Mellitus; Diagnosis, Differential; Glucagon; Glucose; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Iodine Radioisotopes; Leucine; Male; Middle Aged; Peptides; Radioimmunoassay; Substance-Related Disorders; Tolbutamide

1975
Endocrinological aspects at follow-up studies in neonatal hypoglycaemia.
    Acta paediatrica Scandinavica, 1975, Volume: 64, Issue:2

    Topics: Blood Glucose; Child, Preschool; Fatty Acids, Nonesterified; Follow-Up Studies; Glucose Tolerance Test; Growth Hormone; Humans; Hydrocortisone; Hypoglycemia; Infant, Newborn; Infant, Newborn, Diseases; Insulin; Leucine; Stimulation, Chemical; Tolbutamide

1975
[Diagnosis of organic hyperinsulinism].
    Anasthesiologische und intensivmedizinische Praxis, 1975, Volume: 10, Issue:1

    Topics: Diagnosis, Differential; Diazoxide; Fasting; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Radiography; Radionuclide Imaging; Tolbutamide

1975
Hypoglycemia and endogenous hyperinsulinism complicating diabetes mellitus. Application of the C-peptide assay to diagnosis and therapy.
    The American journal of medicine, 1975, Volume: 59, Issue:5

    Topics: Blood Glucose; Diabetes Complications; Diabetes Mellitus; Growth Hormone; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Male; Middle Aged; Pancreatectomy; Peptides; Tolbutamide

1975
[Hypoglycemia. Series 2: symptoms, diagnosis].
    Fortschritte der Medizin, 1976, Feb-05, Volume: 94, Issue:4

    Topics: Adult; Blood Glucose; Catecholamines; Fatigue; Female; Glucagon; Glucose Tolerance Test; Headache; Humans; Hunger; Hypoglycemia; Infant; Infant, Newborn; Insulin; Keto Acids; Leucine; Neurologic Manifestations; Pregnancy; Tolbutamide

1976
[Intermittent branched--chain ketoacidurie in ketotic hypoglycemia: investigations to localize the biochemical defect (author's transl)].
    Monatsschrift fur Kinderheilkunde, 1976, Volume: 124, Issue:2

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child; Female; Fibroblasts; Humans; Hypoglycemia; Intellectual Disability; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Valine

1976
[Leucine sensitive hypoglycemia. Follow-up studies under treatment with diazoxide (author's transl)].
    European journal of pediatrics, 1976, Mar-08, Volume: 121, Issue:4

    Topics: Blood Glucose; Diazoxide; Dietary Proteins; Drug Hypersensitivity; Epilepsy; Female; Humans; Hypertrichosis; Hypoglycemia; Infant; Infant, Newborn; Insulin; Intellectual Disability; Leucine; Male

1976
The role of the central nervous system in modulating glucose and protein metabolism during insulin-induced hypoglycemia.
    Brain research, 1992, Aug-07, Volume: 587, Issue:2

    Topics: Animals; Blood Glucose; Carotid Arteries; Central Nervous System; Dogs; Female; Glucose; Hindlimb; Hypoglycemia; Infusions, Intravenous; Insulin; Leucine; Liver; Male; Proteins; Vertebral Artery

1992
Effect of insulin-induced hypoglycemia on protein metabolism in vivo.
    The American journal of physiology, 1990, Volume: 259, Issue:3 Pt 1

    Topics: Amino Acids; Animals; Blood Glucose; Carbon Dioxide; Catecholamines; Digestive System; Dogs; Female; Hydrocortisone; Hypoglycemia; Insulin; Kinetics; Leucine; Liver; Male; Proteins; Splanchnic Circulation

1990
[Familial form of hypoglycemia due to leucine hypersensitivity].
    Pediatrie, 1990, Volume: 45, Issue:9

    Topics: Adult; Drug Hypersensitivity; Female; Humans; Hypoglycemia; Infant; Insulin; Leucine; Male

1990
Acute effects of insulin-like growth factor I on glucose and amino acid metabolism in the awake fasted rat. Comparison with insulin.
    The Journal of clinical investigation, 1989, Volume: 83, Issue:5

    Topics: Amino Acids; Animals; Blood Glucose; Fasting; Humans; Hypoglycemia; Infusions, Intravenous; Insulin; Insulin-Like Growth Factor I; Kinetics; Leucine; Male; Rats; Rats, Inbred Strains; Recombinant Proteins; Somatomedins

1989
Extrapancreatic effects of L-leucine infusion in leucine-sensitive and control subjects.
    Metabolism: clinical and experimental, 1987, Volume: 36, Issue:7

    Topics: Adolescent; Adult; Fasting; Female; Glucose; Humans; Hypoglycemia; Insulin; Kinetics; Leucine; Male; Middle Aged; Muscles; Somatostatin

1987
3-Hydroxy-3-methylglutaryl-coenzyme a lyase deficiency: a review.
    Journal of inherited metabolic disease, 1986, Volume: 9, Issue:3

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child; Dietary Carbohydrates; Dietary Proteins; Female; Genes, Recessive; Humans; Hypoglycemia; Leucine; Male; Oxo-Acid-Lyases

1986
[Familial leucine sensitive hypoglycemia].
    Ugeskrift for laeger, 1985, Apr-08, Volume: 147, Issue:15

    Topics: Adult; Child; Female; Food Hypersensitivity; Humans; Hypoglycemia; Insulin; Leucine; Male; Middle Aged

1985
[A morphological study on the mechanism of insulin-release, using sulfonylurea, l-leucine, and alpha-ketocarboxylic acids].
    Nihon Naibunpi Gakkai zasshi, 1968, Oct-20, Volume: 44, Issue:7

    Topics: Animals; Blood Glucose; Butyrates; Chlorpropamide; Diabetes Mellitus; Diazoxide; Ferredoxins; Histocytochemistry; Humans; Hypoglycemia; Hypoglycemic Agents; In Vitro Techniques; Insulin; Insulin Secretion; Islets of Langerhans; Keto Acids; Leucine; Methods; Rats; Staining and Labeling; Sulfur Isotopes; Time Factors; Zinc

1968
A case of leucine-induced hypoglycaemia.
    Journal of neurology, neurosurgery, and psychiatry, 1969, Volume: 32, Issue:5

    Topics: Autopsy; Child, Preschool; Developmental Disabilities; Fasting; Gliosis; Glucagon; Glucose; Glucose Tolerance Test; Humans; Hypoglycemia; Infant; Intellectual Disability; Leucine; Male; Methylprednisolone; Occipital Lobe; Seizures; Temporal Lobe

1969
[Pancreatic insulinomas sensitive to 1-leucine: glycometabolic findings in two cases before and after surgical removal].
    Giornale di clinica medica, 1965, Volume: 46, Issue:8

    Topics: Adenoma, Islet Cell; Adult; Humans; Hypoglycemia; In Vitro Techniques; Leucine; Male; Middle Aged

1965
Biochemical studies in a patient with hyperinsulinism.
    The New Zealand medical journal, 1966, Volume: 65, Issue:406

    Topics: Adenoma, Islet Cell; Adult; Female; Glucagon; Glucose Tolerance Test; Humans; Hydrocortisone; Hyperinsulinism; Hypoglycemia; Leucine; Pancreatic Neoplasms; Tolbutamide

1966
[Case of leucine-sensitive hypoglycemia treated by pancreatectomy].
    Nihon Shonika Gakkai zasshi. Acta paediatrica Japonica, 1966, Volume: 70, Issue:2

    Topics: Adenoma, Islet Cell; Child; Electroencephalography; Humans; Hypoglycemia; Leucine; Male; Pancreatectomy

1966
Islet cell adenoma in childhood: report of a case.
    Pediatrics, 1967, Volume: 39, Issue:1

    Topics: Adenoma; Adenoma, Islet Cell; Catecholamines; Child; Electroencephalography; Epinephrine; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Intelligence Tests; Leucine; Male; Tolbutamide

1967
The diagnosis of insuloma.
    Acta medica Scandinavica, 1967, Volume: 181, Issue:3

    Topics: Adenoma, Islet Cell; Adult; Aged; Diagnosis, Differential; Fasting; Female; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Male; Middle Aged; Radiography; Tolbutamide

1967
Plasma growth hormone levels in spontaneous hypoglycemia.
    The Journal of clinical endocrinology and metabolism, 1967, Volume: 27, Issue:4

    Topics: Adenoma, Islet Cell; Adrenal Gland Diseases; Adult; Aged; Carcinoma; Cholangitis; Deficiency Diseases; Fasting; Female; Fluorometry; Glucose; Glucose Tolerance Test; Growth Hormone; Humans; Hydrocortisone; Hypoglycemia; Immunoassay; Insulin; Leucine; Lung Neoplasms; Male; Middle Aged; Pancreatitis; Sertoli-Leydig Cell Tumor; Stomach Neoplasms; Tolbutamide

1967
The tolbutamide tolerance texxt in the evaluation of childhood hypoglycemia.
    Pediatrics, 1967, Volume: 39, Issue:6

    Topics: Acidosis; Adenoma, Islet Cell; Child; Child, Preschool; Diagnosis, Differential; Humans; Hypoglycemia; Infant; Leucine; Tolbutamide

1967
Studies in hypoglycemia of infancy and childhood. Diagnosis and treatment.
    American journal of diseases of children (1960), 1967, Volume: 114, Issue:4

    Topics: Adenoma, Acidophil; Adolescent; Blood Glucose; Child; Child, Preschool; Diet Therapy; Epinephrine; Female; Glucagon; Glucocorticoids; Glucose Tolerance Test; Humans; Hypoglycemia; Hypopituitarism; Infant; Insulin; Leucine; Male; Pancreatectomy; Tolbutamide

1967
Hypoglycemia in a two-year-old boy with adrenocorticotropic hormone (ACTH) deficiency (probably isolated) and adrenal medullary unresponsiveness to insulin-induced hypoglycemia.
    The Journal of clinical endocrinology and metabolism, 1968, Volume: 28, Issue:2

    Topics: Adrenal Insufficiency; Adrenal Medulla; Adrenocorticotropic Hormone; Blood Glucose; Catecholamines; Child, Preschool; Epinephrine; Glucose Tolerance Test; Humans; Hypoglycemia; Hypopituitarism; Insulin Coma; Leucine; Male; Norepinephrine; Pituitary-Adrenal Function Tests; Tolbutamide; Transferases

1968
Evidence for a precursor in the biosynthesis of insulin.
    Transactions of the New York Academy of Sciences, 1967, Volume: 30, Issue:1

    Topics: Adenoma, Islet Cell; Amino Acid Sequence; Animals; Chromatography, Gel; Humans; Hypoglycemia; In Vitro Techniques; Insulin; Leucine; Phenylalanine; Rats; Tritium

1967
Further studies on diazoxide suppression of insulin release from abnormal and normal islet tissue in man.
    Annals of the New York Academy of Sciences, 1968, Apr-11, Volume: 150, Issue:2

    Topics: Adenoma, Islet Cell; Arginine; Blood Glucose; Catecholamines; Depression, Chemical; Diazoxide; Female; Glucagon; Glucose; Humans; Hyperglycemia; Hyperinsulinism; Hypoglycemia; Insulin; Insulin Secretion; Islets of Langerhans; Leucine; Male; Tolbutamide; Trichlormethiazide

1968
Glucagon test for insulinoma: a chemical study in 25 cases.
    Journal of clinical pathology, 1968, Volume: 21, Issue:3

    Topics: Adenoma, Islet Cell; Adult; Blood Glucose; Diagnosis, Differential; Female; Glucagon; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Male; Middle Aged; Tolbutamide

1968
[Apropos of a case of severe hypoglycemia. Present possibilities of diagnosis and treatment].
    Annales de pediatrie, 1968, Oct-02, Volume: 15, Issue:10

    Topics: Adenoma, Islet Cell; Blood Glucose; Diagnosis, Differential; Diazoxide; Glucocorticoids; Glucose; Glucose Tolerance Test; Humans; Hypoglycemia; Infant; Insulin; Leucine; Male; Pancreatectomy; Tolbutamide

1968
Islet cell tumors and hypoglycemia.
    Annals of surgery, 1969, Volume: 169, Issue:5

    Topics: Adenoma, Islet Cell; Adolescent; Adult; Aged; Child; Fasting; Female; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Infant; Infant, Newborn; Insulin; Insulin Secretion; Leucine; Male; Middle Aged; Radiography; Tolbutamide

1969
Idiopathic hypoglycemia: a study of twenty-six children.
    The Journal of pediatrics, 1969, Volume: 74, Issue:6

    Topics: Adrenocorticotropic Hormone; Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Diabetes Mellitus; Diet Therapy; Electroencephalography; Female; Glucose Tolerance Test; Humans; Hypoglycemia; Infant; Infant, Newborn; Infant, Newborn, Diseases; Insulin; Insulin Secretion; Intellectual Disability; Leucine; Liver Glycogen; Male; Neurologic Manifestations; Pancreatectomy; Prednisone; Pregnancy; Tolbutamide

1969
Islet cell tumors of the pancreas.
    Virginia medical monthly, 1969, Volume: 96, Issue:3

    Topics: Adenoma, Islet Cell; Aged; Fasting; Female; Humans; Hypoglycemia; Insulin; Leucine; Male; Middle Aged; Pancreatic Neoplasms; Tolbutamide

1969
[Alcoholic hypoglycemia in adults].
    La semaine des hopitaux : organe fonde par l'Association d'enseignement medical des hopitaux de Paris, 1968, Nov-14, Volume: 44, Issue:47

    Topics: Adult; Alcoholism; Diet; Glucagon; Glucose Tolerance Test; Hepatic Encephalopathy; Humans; Hypoglycemia; Insulin; Leucine; NAD; Socioeconomic Factors; Tolbutamide

1968
Insulin stimulatory tests in a patient with islet cell adenoma.
    American journal of surgery, 1969, Volume: 118, Issue:1

    Topics: Adenoma, Islet Cell; Aged; Antigen-Antibody Reactions; Blood Glucose; Fasting; Female; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Insulin Antibodies; Insulin Secretion; Leucine; Methods; Tolbutamide

1969
[Case of ketotic hypoglycemia].
    Nihon Shonika Gakkai zasshi. Acta paediatrica Japonica, 1969, Mar-01, Volume: 73, Issue:3

    Topics: Acidosis; Adrenocorticotropic Hormone; Blood Glucose; Child, Preschool; Female; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Leucine

1969
On the mechanism of sensitivity to leucine in the case of "leucine sensitive hypoglycemia". (I).
    Endokrinologie, 1969, Volume: 54, Issue:1

    Topics: Adenoma, Islet Cell; Blood Glucose; Butyrates; Caproates; Child, Preschool; Female; Histocytochemistry; Humans; Hypoglycemia; Insulin; Islets of Langerhans; Keto Acids; Leucine; Male; Middle Aged; Zinc

1969
Medical grand rounds at Yale-New Haven Hospital. Diagnosis and management of hypoglycemia.
    Connecticut medicine, 1970, Volume: 34, Issue:3

    Topics: Adenoma, Islet Cell; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Leucine; Pancreatic Neoplasms; Tolbutamide

1970
[Hypoglycemias in childhood].
    Monatsschrift fur Kinderheilkunde, 1969, Volume: 117, Issue:4

    Topics: Adenoma; Adenoma, Islet Cell; Adrenal Insufficiency; Child; Child, Preschool; Female; Humans; Hypoglycemia; Leucine

1969
[Apropos of 2 cases of insulinoma. Note on the effect of hypoglycemic effect of leucine].
    Acta clinica Belgica, 1969, Volume: 24, Issue:2

    Topics: Adenoma, Islet Cell; Aortography; Female; Humans; Hyperglycemia; Hypoglycemia; Leucine; Middle Aged; Pancreas; Pancreatic Neoplasms

1969
Islet cell tumor with hypoglycemia.
    American family physician, 1971, Volume: 3, Issue:3

    Topics: Adenoma, Islet Cell; Adolescent; Adult; Female; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Middle Aged; Pancreatectomy; Pancreatic Neoplasms; Radioimmunoassay; Tolbutamide

1971
[2 cases of Langerhans adenoma].
    Acta chirurgica Belgica, 1969, Volume: 68, Issue:4

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adenoma, Islet Cell; Adult; Aged; Angiography; Celiac Artery; Female; Gastrointestinal Hemorrhage; Glucagon; Humans; Hypoglycemia; Insulin; Intracranial Arteriosclerosis; Leucine; Mesenteric Arteries; Obesity; Pancreatectomy; Pancreatic Neoplasms; Pregnancy; Pregnancy Complications; Prognosis; Tolbutamide

1969
Islet cell adenomatosis and adenoma in an infant.
    The Journal of pediatrics, 1971, Volume: 79, Issue:2

    Topics: Adenoma, Islet Cell; Adrenocorticotropic Hormone; Diazoxide; Glucose; Humans; Hypoglycemia; Infant, Newborn; Infant, Newborn, Diseases; Intellectual Disability; Leucine; Male; Pancreatectomy; Pancreatic Neoplasms; Prednisone; Tolbutamide

1971
Proinsulin-like component of circulating insulin in the basal state and in patients and hamsters with islet cell tumors.
    The Journal of clinical investigation, 1971, Volume: 50, Issue:10

    Topics: Acromegaly; Adenoma, Islet Cell; Adolescent; Adult; Animals; Child; Chromatography, Gel; Cricetinae; Cushing Syndrome; Diazoxide; Disease Models, Animal; Female; Glucagon; Glucose Tolerance Test; Half-Life; Humans; Hypoglycemia; Hypokalemia; Insulin; Iodine Isotopes; Leucine; Male; Middle Aged; Myotonic Dystrophy; Neoplasms, Experimental; Obesity; Proinsulin; Radioimmunoassay; Stimulation, Chemical; Tolbutamide

1971
Activation of adenyl cyclase in a pancreatic islet cell adenoma by glucagon and tolbutamide.
    Metabolism: clinical and experimental, 1972, Volume: 21, Issue:2

    Topics: Adenoma, Islet Cell; Adenosine Triphosphate; Adenylyl Cyclases; Administration, Oral; Arginine; Blood Glucose; Cyclic AMP; Enzyme Activation; Fasting; Fluorides; Glucagon; Glucose; Humans; Hypoglycemia; In Vitro Techniques; Injections, Intravenous; Insulin; Insulin Secretion; Leucine; Male; Middle Aged; Phosphorus Isotopes; Tolbutamide

1972
Insulin and glucose patterns in control subjects and in proved insulinoma.
    The American journal of the medical sciences, 1971, Volume: 262, Issue:2

    Topics: Adenoma, Islet Cell; Adult; Aged; Blood Glucose; Child; False Negative Reactions; Fasting; Female; Glucagon; Humans; Hypoglycemia; Insulin; Leucine; Male; Middle Aged; Pancreatic Neoplasms; Time Factors; Tolbutamide

1971
Beta cell adenoma in a child with hypoglycemia controlled with diazoxide.
    The Journal of pediatrics, 1972, Volume: 80, Issue:5

    Topics: Adenoma, Islet Cell; Blood Glucose; Child, Preschool; Diazoxide; Female; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Leucine; Microscopy, Electron; Pancreatectomy; Pancreatic Neoplasms; Splenectomy; Tolbutamide

1972
Insulinoma diagnosed by insulin immunoassay and angiography.
    Journal of pediatric surgery, 1972, Volume: 7, Issue:6

    Topics: Adenoma, Islet Cell; Angiography; Blood Glucose; Child; Humans; Hypoglycemia; Immunoassay; Insulin; Leucine; Male; Pancreatic Neoplasms; Proinsulin; Tolbutamide

1972
Current concepts in diagnosis of insulinoma.
    Rocky Mountain medical journal, 1974, Volume: 71, Issue:4

    Topics: Adenoma, Islet Cell; Blood Glucose; Fasting; Glucagon; Humans; Hypoglycemia; Insulin; Leucine; Proinsulin; Tolbutamide

1974
[Exploration of hypoglycemia].
    Revue medicale de Liege, 1974, Apr-15, Volume: 29, Issue:8

    Topics: Adenoma, Islet Cell; Arginine; Blood Glucose; Diazoxide; Diet; Fasting; Glucagon; Hormones, Ectopic; Humans; Hypoglycemia; Insulin; Insulin Secretion; Leucine; Medical History Taking; Pancreatic Neoplasms; Physical Examination; Time Factors; Tolbutamide

1974
[Atypical case of insulinoma (author's transl)].
    Medizinische Klinik, 1974, Sep-06, Volume: 69, Issue:36

    Topics: Adenoma, Islet Cell; Angiography; Blood Glucose; Fasting; Female; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Leucine; Middle Aged; Pancreatic Neoplasms; Tolbutamide; Ultrasonography

1974
Glycemic response to 24-hour fast in normal children and children with ketotic hypoglycemia: II. Hormonal and metabolic changes.
    The Journal of pediatrics, 1974, Volume: 85, Issue:6

    Topics: Acidosis; Alanine; Amino Acids; Autoanalysis; Blood Glucose; Child; Child, Preschool; Fasting; Fatty Acids, Nonesterified; Female; Glucagon; Growth Hormone; Hormones; Humans; Hydrocortisone; Hypoglycemia; Insulin; Isoleucine; Ketones; Ketosis; Leucine; Male; Valine

1974
[Diet therapy of some inborn errors of metabolism].
    La Pediatria, 1974, Sep-30, Volume: 82, Issue:2

    Topics: Age Factors; Amino Acid Metabolism, Inborn Errors; Celiac Disease; Child; Child, Preschool; Histidine; Humans; Hypoglycemia; Infant; Infant Nutritional Physiological Phenomena; Infant, Newborn; Lactose Intolerance; Leucine; Maple Syrup Urine Disease; Metabolism, Inborn Errors; Methionine; Phenylketonurias; Proteins; Tyrosine

1974
The diagnostic evaluation of the patient with hypoglycemic symptoms.
    The Medical annals of the District of Columbia, 1972, Volume: 41, Issue:1

    Topics: Adrenal Glands; Diagnosis, Differential; Fasting; Glucose Tolerance Test; Humans; Hyperventilation; Hypoglycemia; Hypotension; Leucine; Pheochromocytoma; Radiography; Sella Turcica; Thyroid Gland; Tolbutamide

1972
Islet cell function and glucose homeostasis in hypopituitary dwarfism: synergism between growth hormone and cortisone.
    The Journal of pediatrics, 1973, Volume: 82, Issue:1

    Topics: Blood Glucose; Child; Cortisone; Drug Synergism; Dwarfism, Pituitary; Female; Glucose; Glucose Tolerance Test; Growth Hormone; Homeostasis; Humans; Hypoglycemia; Insulin; Islets of Langerhans; Leucine; Male; Pregnancy; Tolbutamide

1973
Morphometric and ultrastructural studies in an infant with leucine-sensitive hypoglycemia, hyperinsulinism and islet hyperplasia.
    Diabetologia, 1974, Volume: 10, Issue:3

    Topics: Biopsy; Blood Glucose; Female; Histocytochemistry; Humans; Hyperinsulinism; Hypertrophy; Hypoglycemia; Infant, Newborn; Infant, Newborn, Diseases; Insulin; Islets of Langerhans; Leucine; Microscopy, Electron; Pancreas

1974
[Better accomplishment of a leucine test].
    Wiener Zeitschrift fur innere Medizin und ihre Grenzgebiete, 1972, Volume: 53, Issue:10

    Topics: Adolescent; Adult; Aged; Blood Glucose; Female; Humans; Hypoglycemia; Leucine; Male; Methods; Middle Aged; Suspensions

1972
Metabolic aspects of the Beckwith-Wiedemann syndrome.
    The Journal of pediatrics, 1973, Volume: 82, Issue:2

    Topics: Abnormalities, Multiple; Adrenal Gland Diseases; Blood Glucose; Child, Preschool; Diazoxide; Epinephrine; Glucagon; Glucose; Glucose Tolerance Test; Growth Hormone; Hernia, Umbilical; Humans; Hydrocortisone; Hyperinsulinism; Hypoglycemia; Infant, Newborn; Infant, Newborn, Diseases; Insulin; Kidney Diseases; Leucine; Male; Tolbutamide; Tongue; Umbilicus

1973
Glucose, tolbutamide and leucine tolerances in hypoglycemia.
    Postgraduate medicine, 1973, Volume: 53, Issue:4

    Topics: Administration, Oral; Blood Glucose; Diabetes Complications; Diabetes Mellitus; Glucose Tolerance Test; Humans; Hypoglycemia; Injections, Intravenous; Insulin; Leucine; Time Factors; Tolbutamide

1973
Effect of leucine on carbohydrate metabolism of the liver.
    Hormone and metabolic research = Hormon- und Stoffwechselforschung = Hormones et metabolisme, 1973, Volume: 5, Issue:1

    Topics: Alanine; Amino Acids; Animals; Blood Glucose; Carbohydrate Metabolism; Chlorpropamide; Drug Synergism; Female; Glucose; Glycine; Hypoglycemia; Insulin; Leucine; Liver; Liver Glycogen; Perfusion; Rats

1973
Beckwith's syndrome with extreme organ hyperplasia.
    Pediatrics, 1973, Volume: 52, Issue:3

    Topics: 17-Ketosteroids; Abdominal Neoplasms; Abnormalities, Multiple; Adrenal Gland Diseases; Adrenal Glands; Antigens; Blood Glucose; Female; Hernia, Umbilical; Humans; Hyperplasia; Hypoglycemia; Infant, Newborn; Insulin; Kidney Diseases; Leucine; Pancreas; Pancreatectomy; Time Factors; Tongue; Umbilicus

1973
[On a case of spontaneous hypoglycemia in a nursing infant].
    Folia endocrinologica, 1973, Volume: 26, Issue:5

    Topics: Female; Food Hypersensitivity; Humans; Hypoglycemia; Infant; Infant, Newborn; Infant, Newborn, Diseases; Leucine; Metabolic Diseases

1973
[Hypoglycemia].
    Actualites de physiologie pathologique, 1973, Volume: 4

    Topics: Child; Dietary Carbohydrates; Epinephrine; Gastrointestinal Hormones; Glucagon; Gluconeogenesis; Glucose; Humans; Hyperglycemia; Hyperinsulinism; Hypoglycemia; Hypoglycemic Agents; Insulin; Intestinal Absorption; Leucine; Liver Glycogen; Pancreatic Neoplasms; Thyroid Hormones; Tolbutamide

1973
Hypoadrenalinemia during insulin hypoglycemia in children with ketotic hypoglycemia.
    The Journal of clinical endocrinology and metabolism, 1974, Volume: 38, Issue:1

    Topics: Adult; Blood Glucose; Child; Child, Preschool; Epinephrine; Female; Humans; Hypoglycemia; Insulin; Leucine; Male; Norepinephrine

1974
[Diazoxide as therapy for idiopathic hypoglycemia in children (author's transl)].
    Monatsschrift fur Kinderheilkunde, 1974, Volume: 122, Issue:1

    Topics: Catecholamines; Child; Child, Preschool; Cyanosis; Diazoxide; Diet Therapy; Fasting; Female; Fever; Humans; Hypoglycemia; Infant; Infant, Newborn; Insulin; Intellectual Disability; Isoleucine; Leucine; Male; Microcephaly; Pregnancy; Seizures; Valine

1974
Plasma insulin and blood glucose during long-term treatment with diazoxide for infant hypoglycemia.
    Acta paediatrica Scandinavica, 1974, Volume: 63, Issue:2

    Topics: Acidosis; Blood Glucose; Child, Preschool; Diazoxide; Follow-Up Studies; Glucose; Glucose Tolerance Test; Humans; Hypertrichosis; Hypoglycemia; Infant; Infant, Newborn; Insulin; Intellectual Disability; Leucine; Stimulation, Chemical; Time Factors

1974
[Childhood hypoglycemia with convulsions].
    Zeitschrift fur arztliche Fortbildung, 1974, Volume: 68, Issue:1

    Topics: Blood Glucose; Child, Preschool; Electroencephalography; Epinephrine; Fasting; Female; Glucagon; Humans; Hyperinsulinism; Hypoglycemia; Infant; Insulin; Leucine; Male; Prednisone; Seizures; Spasms, Infantile; Time Factors

1974
A-cell deficiency and B-cell hyperplasia of Langerhans' islet as a cause of leucine sensitive hypoglycemia.
    Endokrinologie, 1968, Volume: 53, Issue:3

    Topics: Blood Glucose; Diazoxide; Epinephrine; Glucose Tolerance Test; Humans; Hyperplasia; Hypoglycemia; Infant; Insulin; Islets of Langerhans; Leucine; Male; Pancreatectomy; Pancreatic Diseases; Seizures; Tolbutamide

1968
On the mechanism of sensitivity to leucine in the case of "leucine sensitive hypoglycemia". II. The hypoglycemic affect of alpha-ketobutyric acid in the case of "leucine sensitive hypoglycemia".
    Endokrinologie, 1969, Volume: 54, Issue:3

    Topics: Animals; Blood Glucose; Butyrates; Chlorpropamide; Diabetes Mellitus; Hypoglycemia; Insulin; Insulin Secretion; Islets of Langerhans; Keto Acids; Leucine; Male; Rats

1969
The pancreatic islet of infants with severe hypoglycemia.
    Archives of pathology, 1970, Volume: 89, Issue:3

    Topics: Blood Glucose; Epinephrine; Fasting; Fatty Acids, Nonesterified; Female; Glucagon; Glucose; Glucose Tolerance Test; Growth Hormone; Humans; Hyperplasia; Hypertrophy; Hypoglycemia; Infant; Infant, Newborn; Insulin; Islets of Langerhans; Leucine; Microscopy, Electron; Radioimmunoassay; Time Factors; Tolbutamide

1970
Leucine-sensitive hypoglycaemia treated with diazoxide.
    Archives of disease in childhood, 1967, Volume: 42, Issue:224

    Topics: Blood Glucose; Diazoxide; Female; Humans; Hypoglycemia; Infant; Infant, Newborn; Leucine; Male

1967
Chemical pathology of amino acid diseases.
    Acta neurologica et psychiatrica Belgica, 1968, Volume: 68, Issue:4

    Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Chemical Phenomena; Chemistry; Child; Child, Preschool; Female; Homocystine; Humans; Hypoglycemia; Infant; Intellectual Disability; Leucine; Male; Maple Syrup Urine Disease; Methionine; Pyridoxine; Valine

1968
Leucine-sensitive hypoglycaemia.
    Proceedings of the Royal Society of Medicine, 1970, Volume: 63, Issue:4

    Topics: Adolescent; Diazoxide; Diet Therapy; Epilepsy, Tonic-Clonic; Female; Humans; Hypoglycemia; Leucine

1970
Ketotic hypoglycaemia associated with transient branched-chain aminoacidemia.
    Acta paediatrica Scandinavica, 1972, Volume: 61, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Birth Weight; Blood Glucose; Child; Child, Preschool; Creatinine; Diet Therapy; Female; Growth Hormone; Humans; Hypoglycemia; Isoleucine; Keto Acids; Leucine; Male; Maple Syrup Urine Disease; Pre-Eclampsia; Pregnancy; Valine

1972
Amino acid metabolism during starvation in human pregnancy.
    The Journal of clinical investigation, 1972, Volume: 51, Issue:5

    Topics: Adolescent; Adult; Alanine; Amino Acids; Aminobutyrates; Amniotic Fluid; Blood Glucose; Female; Food Deprivation; Gluconeogenesis; Glycine; Humans; Hypoglycemia; Isoleucine; Leucine; Pregnancy; Serine; Starvation; Threonine; Time Factors; Valine

1972
Amino acids and insulin release in vivo.
    Israel journal of medical sciences, 1972, Volume: 8, Issue:3

    Topics: Amino Acids; Animals; Arginine; Blood Glucose; Chlorpropamide; Cycloheptanes; Diabetes Mellitus; Dietary Proteins; Dogs; Glucagon; Glucose; Heptoses; Humans; Hypoglycemia; Insulin; Leucine; Pancreas; Piperidines; Time Factors

1972
Hypoglycemic action of 2-aminonorbornane-2-carboxylic acid in the rat.
    Biochemical and biophysical research communications, 1971, Jul-02, Volume: 44, Issue:1

    Topics: Amino Acids; Amino Acids, Cyclic; Animals; Binding Sites; Blood Glucose; Drug Synergism; Hypoglycemia; Insulin; Insulin Secretion; Kinetics; Leucine; Male; Rats; Stereoisomerism; Structure-Activity Relationship; Terpenes; Tolbutamide

1971
[Hypoglycemia induced by leucine. Study of a case].
    Revista do Hospital das Clinicas, 1971, Volume: 26, Issue:5

    Topics: Child, Preschool; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Male

1971
The clinical use of diazoxide in leucine-sensitive hypoglycemia.
    Annals of the New York Academy of Sciences, 1968, Apr-11, Volume: 150, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Diazoxide; Female; Humans; Hyperglycemia; Hypertrichosis; Hypoglycemia; Infant; Infant, Newborn; Insulin; Insulin Secretion; Leucine; Male

1968
Childhood hypoglycaemia, as a sequel of erythroblastosis foetalis.
    Acta paediatrica Scandinavica, 1969, Volume: 58, Issue:4

    Topics: Child, Preschool; Erythroblastosis, Fetal; Female; Glucose Tolerance Test; Growth Hormone; Humans; Hypoglycemia; Infant; Insulin; Leucine; Pregnancy

1969
[Hypoglycemias of the newborn].
    Monatsschrift fur Kinderheilkunde, 1969, Volume: 117, Issue:4

    Topics: Female; Glycogen; Humans; Hypoglycemia; Infant, Newborn; Infant, Newborn, Diseases; Leucine; Lipid Metabolism; Maternal-Fetal Exchange; Pregnancy

1969
A possible role for the exocrine pancreas in the pathogenesis of neonatal leucine-sensitive hypoglycemia.
    The American journal of digestive diseases, 1970, Volume: 15, Issue:1

    Topics: Diazoxide; Exocrine Glands; Humans; Hypoglycemia; Infant, Newborn; Infant, Newborn, Diseases; Leucine; Male; Pancreas

1970
Hypoglycemia and developmental changes in free amino acids of rat brain.
    Journal of applied physiology, 1970, Volume: 29, Issue:2

    Topics: Age Factors; Alanine; Amino Acids; Aminobutyrates; Animals; Brain; Glutamates; Glycine; Hypoglycemia; Insulin; Isoleucine; Leucine; Rats; Taurine

1970
Some biological observations on hypoglycin-A in the presence of leucine.
    The West Indian medical journal, 1970, Volume: 19, Issue:1

    Topics: Amino Acids; Animals; Antineoplastic Agents; Blood Glucose; Drug Synergism; Female; Fruit; Hypoglycemia; Leucine; Plant Extracts; Plants; Rats

1970
[Diagnostic tests in hypoglycemic syndromes].
    Folia endocrinologica, 1970, Volume: 23, Issue:2

    Topics: Blood Glucose; Diagnosis, Differential; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Leucine; Tolbutamide

1970
[Cerebral convulsion as symptom in spontaneous hypoglycemia in childhood].
    Medizinische Klinik, 1971, Jun-23, Volume: 66, Issue:30

    Topics: Acetone; Adrenal Cortex Hormones; Blood Glucose; Child, Preschool; Diagnosis, Differential; Diet Therapy; Dietary Fats; Electroencephalography; Epinephrine; Female; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Infant; Insulin; Leucine; Male; Prognosis; Seizures; Tolbutamide

1971
[Management of functional hypoglycemia in the adult].
    Folia clinica internacional, 1967, Volume: 17, Issue:10

    Topics: Adult; Fructose; Galactosemias; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Leucine; Tolbutamide

1967
[Functional exploration of insulin secretion in sponteaneous hypoglycemia].
    Acta isotopica, 1967, Dec-15, Volume: 7, Issue:1

    Topics: Adenoma; Arginine; Glucagon; Glucose; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Insulin Secretion; Leucine; Pancreas; Pancreatic Neoplasms; Tolbutamide

1967
Serum-insulin changes following administration of L-leucine to children.
    Archives of disease in childhood, 1968, Volume: 43, Issue:227

    Topics: Blood Glucose; Child; Child, Preschool; Diet Therapy; Fasting; Female; Humans; Hypoglycemia; Infant; Insulin; Intellectual Disability; Leucine; Male

1968
Tolbutamide tolerance test and plasma-insulin response in hypoglycemia.
    The Journal of pediatrics, 1968, Volume: 72, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Blood Glucose; Child; Diagnosis, Differential; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Leucine; Tolbutamide

1968
[Transient hypoglycemia with leucine hypersensitivity not based on increased insulin production. Treatment with zinc glucagon].
    Maandschrift voor kindergeneeskunde, 1968, Volume: 36, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Glucagon; Humans; Hypersensitivity; Hypoglycemia; Infant; Insulin; Leucine; Male; Zinc

1968
[Hypoglycemic syndrome].
    Saishin igaku. Modern medicine, 1968, Volume: 23, Issue:4

    Topics: Diabetes Complications; Ethanol; Female; Humans; Hypoglycemia; Insulin; Leucine; Middle Aged; Ribose

1968
Diazoxide in the management of hypoglycemia in infancy and childhood.
    American journal of diseases of children (1960), 1969, Volume: 117, Issue:4

    Topics: Blood Glucose; Child; Child, Preschool; Diazoxide; Female; Glucose; Glucose Tolerance Test; Growth Hormone; Humans; Hypoglycemia; Infant; Insulin; Insulin Secretion; Leucine; Male; Tolbutamide

1969
[Idiopathic hypoglycemia in the child].
    Deutsche medizinische Wochenschrift (1946), 1969, Mar-28, Volume: 94, Issue:13

    Topics: Age Factors; Child; Child, Preschool; Epinephrine; Fatty Acids, Nonesterified; Female; Glucagon; Glucose Tolerance Test; Growth Hormone; Humans; Hypoglycemia; Infant; Infant, Newborn; Insulin; Leucine; Male; Tolbutamide

1969
Hypertichosis lanuginosa acquisita.
    Archives of dermatology, 1969, Volume: 99, Issue:6

    Topics: Diazoxide; Humans; Hypertrichosis; Hypoglycemia; Infant; Leucine; Male; Pancreatectomy; Seizures

1969
[Recurrent hypoglycemia caused by sensitivity to leucine].
    La Revue du praticien, 1965, May-11, Volume: 15, Issue:14

    Topics: Female; Humans; Hypoglycemia; Infant; Infant Nutrition Disorders; Leucine; Male

1965
Varicella and hypoglycemia with recovery: case report.
    American journal of diseases of children (1960), 1965, Volume: 110, Issue:6

    Topics: Blood Chemical Analysis; Chickenpox; Child, Preschool; Female; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Leucine; Prednisone

1965
[Hypoglycemia and central nervous disorders].
    Shinkei kenkyu no shimpo. Advances in neurological sciences, 1965, Volume: 9, Issue:2

    Topics: Brain Diseases; Humans; Hypoglycemia; Infant; Infant, Newborn; Leucine

1965
Spontaneous hypoglycaemia and sarcoma. A case report.
    Acta endocrinologica, 1965, Volume: 50, Issue:2

    Topics: Blood; Fibrosarcoma; Glucagon; Glucose Tolerance Test; Granulosa Cell Tumor; Humans; Hypoglycemia; Insulin; Leucine; Male; Middle Aged; Tolbutamide

1965
Hypoglycemia due to intrapancreatic infusion of leucine.
    Diabetes, 1966, Volume: 15, Issue:8

    Topics: Animals; Dogs; Hypoglycemia; Insulin; Leucine; Liver; Pancreas; Tolbutamide

1966
Leucine-sensitive hypoglycemia. Treatment with zinc glucagon and corticosteroids.
    The American journal of medicine, 1966, Volume: 41, Issue:4

    Topics: Diazoxide; Diet; Female; Glucagon; Humans; Hypoglycemia; Leucine; Middle Aged; Prednisone

1966
Effect of treatment with diazoxide and chlorothiazide on a child with leucine-sensitive hypoglycaemia.
    British medical journal, 1966, Dec-17, Volume: 2, Issue:5528

    Topics: Child, Preschool; Chlorothiazide; Diazoxide; Female; Glucose Tolerance Test; Humans; Hypoglycemia; Leucine

1966
Pancreatectomy for refractory hypoglycemia in children.
    Archives of surgery (Chicago, Ill. : 1960), 1966, Volume: 93, Issue:1

    Topics: Child; Child, Preschool; Epinephrine; Galactose; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Infant; Insulin; Leucine; Male; Nervous System Diseases; Pancreas; Pancreatectomy

1966
Diazoxide in the treatment of infantile hypoglycemia.
    The New England journal of medicine, 1966, Dec-29, Volume: 275, Issue:26

    Topics: Autoanalysis; Diazoxide; Drug Hypersensitivity; Female; Glucose Tolerance Test; Hirsutism; Humans; Hypoglycemia; Infant; Insulin; Intellectual Disability; Leucine

1966