Compounds > leucine

leucine and Encephalopathy, Subacute Spongiform, Gerstmann-Straussler Type

leucine has been researched along with Encephalopathy, Subacute Spongiform, Gerstmann-Straussler Type in 7 studies

Research

Studies (7)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's4 (57.14)18.2507
2000's2 (28.57)29.6817
2010's1 (14.29)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Ciano, C; Di Fede, G; Fancellu, R; Mariotti, C; Nanetti, L; Pareyson, D; Politi, LS; Salsano, E; Scaioli, V; Tagliavini, F1
Doh-ura, K; Furuta, A; Iwaki, T; Morisada, Y; Nakashima, S; Sasaki, K; Tateishi, J1
Hope, J; Manson, JC; Melton, DW; Moore, RC; Redhead, NJ; Selfridge, J1
Hayashi, Y; Kitamoto, N; Kitamoto, T; Kutomi, T; Muramoto, T; Sano, C; Tanaka, T; Yutani, C1
Hsiao, K; Prusiner, SB1
DeArmond, SJ; Foster, D; Groth, D; Hsiao, K; Prusiner, SB; Scott, M; Serban, H1
DeArmond, SJ; Foster, D; Groth, DF; Hsiao, KK; Prusiner, SB; Scott, M1

Reviews

1 review(s) available for leucine and Encephalopathy, Subacute Spongiform, Gerstmann-Straussler Type

ArticleYear
Molecular genetics and transgenic model of Gertsmann-Sträussler-Scheinker disease.
    Alzheimer disease and associated disorders, 1991,Fall, Volume: 5, Issue:3

    Topics: Alzheimer Disease; Amyloid beta-Peptides; Animals; Brain; Codon; Genetic Markers; Gerstmann-Straussler-Scheinker Disease; Humans; Leucine; Mice; Mice, Transgenic; Models, Genetic; Prions; Proline; PrPSc Proteins

1991

Other Studies

6 other study(ies) available for leucine and Encephalopathy, Subacute Spongiform, Gerstmann-Straussler Type

ArticleYear
Lower limb areflexia without central and peripheral conduction abnormalities is highly suggestive of Gerstmann-Sträussler-Scheinker disease Pro102Leu.
    Journal of the neurological sciences, 2011, Mar-15, Volume: 302, Issue:1-2

    Topics: Adult; Brain; Electroencephalography; Electrophysiological Phenomena; Evoked Potentials, Motor; Evoked Potentials, Somatosensory; Family; Female; Gerstmann-Straussler-Scheinker Disease; Humans; Italy; Leucine; Lower Extremity; Magnetic Resonance Imaging; Male; Middle Aged; Neural Conduction; Neurologic Examination; Prions; Proline; Reflex, Abnormal

2011
Neuropathological features of a case with schizophrenia and prion protein gene P102L mutation before onset of Gerstmann-Sträussler-Scheinker disease.
    Acta neuropathologica, 2003, Volume: 106, Issue:1

    Topics: Amyloid beta-Peptides; Astrocytes; Brain; Family Health; Female; Gerstmann-Straussler-Scheinker Disease; Glial Fibrillary Acidic Protein; Humans; Immunohistochemistry; Inclusion Bodies; Leucine; Microscopy, Electron; Middle Aged; Mutation; Organ Size; Pedigree; Prions; Proline; S100 Proteins; Schizophrenia; Staining and Labeling; Ubiquitin

2003
Double replacement gene targeting for the production of a series of mouse strains with different prion protein gene alterations.
    Bio/technology (Nature Publishing Company), 1995, Volume: 13, Issue:9

    Topics: Alleles; Animals; Cell Line; Codon; Embryo, Mammalian; Gene Targeting; Genetic Vectors; Gerstmann-Straussler-Scheinker Disease; Humans; Leucine; Mice; Mice, Knockout; Mutagenesis, Site-Directed; Polymerase Chain Reaction; Prions; Proline; Protein Engineering; Stem Cells

1995
Analyses of Gerstmann-Straussler syndrome with 102Leu219Lys using monoclonal antibodies that specifically detect human prion protein with 219Glu.
    Neuroscience letters, 2000, Jul-21, Volume: 288, Issue:3

    Topics: Amino Acid Substitution; Animals; Antibodies, Monoclonal; Epitope Mapping; Gerstmann-Straussler-Scheinker Disease; Glutamic Acid; Humans; Immunohistochemistry; Leucine; Lysine; Mice; Mice, Inbred BALB C; Polymorphism, Genetic; Prions

2000
Spontaneous neurodegeneration in transgenic mice with prion protein codon 101 proline----leucine substitution.
    Annals of the New York Academy of Sciences, 1991, Volume: 640

    Topics: Amino Acid Sequence; Animals; Brain; Codon; Gene Expression; Gerstmann-Straussler-Scheinker Disease; Leucine; Mice; Mice, Inbred C57BL; Mice, Transgenic; Molecular Sequence Data; Prions; Proline; PrPSc Proteins

1991
Spontaneous neurodegeneration in transgenic mice with mutant prion protein.
    Science (New York, N.Y.), 1990, Dec-14, Volume: 250, Issue:4987

    Topics: Amino Acid Sequence; Animals; Base Sequence; Brain; Brain Diseases; Codon; Disease Models, Animal; DNA; Endopeptidase K; Gerstmann-Straussler-Scheinker Disease; Leucine; Mice; Mice, Transgenic; Molecular Sequence Data; Mutation; Nucleic Acid Hybridization; Pedigree; Prions; PrPSc Proteins; Serine Endopeptidases; Transfection; Vacuoles; Viral Proteins

1990