leucine and Diseases, Metabolic

leucine has been researched along with Diseases, Metabolic in 28 studies

Research

Studies (28)

TimeframeStudies, this research(%)All Research%
pre-199018 (64.29)18.7374
1990's0 (0.00)18.2507
2000's2 (7.14)29.6817
2010's4 (14.29)24.3611
2020's4 (14.29)2.80

Authors

AuthorsStudies
Eminoğlu, FT; Kahveci, F; Kendirli, T; Köse, E; Kraja, E; Okulu, E; Öncül, Ü1
Capparelli, R; Cuomo, P; Iannelli, A; Iannelli, D1
Berska, J; Bugajska, J; Gotfryd-Bugajska, K; Pasternak, A; Sztefko, K; Szura, M1
de Ligt, M; Hesselink, MKC; Hoeks, J; Phielix, E; Schrauwen, P; Vanweert, F1
Holeček, M1
He, T; Ma, X; Nie, C; Zhang, G; Zhang, W1
Chace, DH; De Jesús, VR; Hannon, WH; Lim, TH; Mei, JV1
Area, E; Artuch, R; Cormand, B; Drakaki, K; Garcia-Cazorla, A; Giannakopoulos, A; Kanavakis, E; Orfanou, I; Ormazabal, A; Pons, R; Ribasés, M; Serrano, M; Toma, C; Youroukos, S1
MACKENZIE, DY; WOOLF, LI1
DANCIS, J; LEVITZ, M; MILLER, S; WESTALL, RG1
CROME, L; DUTTON, G; ROSS, CF1
DENT, CE; WESTALL, RG1
PATRICK, AD1
TASHIAN, RE1
GENTZ, J; LEHMANN, O; ZETTERSTROM, R1
DANCIS, J; HUTZLER, J; JANSEN, V; LEVITZ, M1
RIEDER, RF; WEATHERALL, DJ1
HOLT, LE; NORTON, PM; ROITMAN, E; SNYDERMAN, SE1
Ficicioglu, C; Payan, I1
Darmaun, D; Dumon, H; Humbert, B; Le Bacquer, O; Nguyen, P1
Fischer, JE; Freund, HR; Ryan, JA1
Lutz, P1
Blum, KU1
Menchini, GF; Meozzi, A1
Wüstenberg, PW1
Hagge, W; Irtel von Brenndorff, A1

Reviews

5 review(s) available for leucine and Diseases, Metabolic

ArticleYear
Role of Branched-Chain Amino Acid Metabolism in Type 2 Diabetes, Obesity, Cardiovascular Disease and Non-Alcoholic Fatty Liver Disease.
    International journal of molecular sciences, 2022, Apr-13, Volume: 23, Issue:8

    Topics: Amino Acids, Branched-Chain; Animals; Cardiovascular Diseases; Diabetes Mellitus, Type 2; Humans; Leucine; Mammals; Metabolic Diseases; Non-alcoholic Fatty Liver Disease; Obesity

2022
The role of skeletal muscle in the pathogenesis of altered concentrations of branched-chain amino acids (valine, leucine, and isoleucine) in liver cirrhosis, diabetes, and other diseases.
    Physiological research, 2021, 07-12, Volume: 70, Issue:3

    Topics: Amino Acids, Branched-Chain; Animals; Diabetes Mellitus; Humans; Isoleucine; Leucine; Liver Cirrhosis; Metabolic Diseases; Muscle, Skeletal; Valine

2021
Branched Chain Amino Acids: Beyond Nutrition Metabolism.
    International journal of molecular sciences, 2018, Mar-23, Volume: 19, Issue:4

    Topics: Amino Acids, Branched-Chain; Animals; Diabetes Mellitus, Type 2; Humans; Insulin Resistance; Isoleucine; Leucine; Metabolic Diseases; Signal Transduction; Valine

2018
[CONGENITAL DISORDERS OF CARBOHYDRATE METABOLISM].
    Polskie Archiwum Medycyny Wewnetrznej, 1963, Volume: 33

    Topics: Carbohydrate Metabolism; Diabetes Mellitus; Fructose; Galactosemias; Glucosephosphate Dehydrogenase Deficiency; Glucosephosphates; Glycogen Storage Disease; Humans; Hypoglycemia; Leucine; Metabolic Diseases; Pentoses; Urine

1963
[The hypoglycemia syndrome].
    Zeitschrift fur die gesamte innere Medizin und ihre Grenzgebiete, 1970, Jun-01, Volume: 25, Issue:11

    Topics: Alloxan; Angiography; Antibiotics, Antineoplastic; Blood Glucose; Diagnosis, Differential; Diazoxide; Diet Therapy; Epinephrine; Gastrointestinal Diseases; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Metabolic Diseases; Neoplasms; Pancreatic Neoplasms; Prednisone; Tolbutamide

1970

Other Studies

23 other study(ies) available for leucine and Diseases, Metabolic

ArticleYear
Characteristics of continuous venovenous hemodiafiltration in the acute treatment of inherited metabolic disorders.
    Pediatric nephrology (Berlin, Germany), 2022, Volume: 37, Issue:6

    Topics: Aged; Ammonia; Child; Continuous Renal Replacement Therapy; Hemodiafiltration; Humans; Hypotension; Infant; Infant, Newborn; Leucine; Maple Syrup Urine Disease; Metabolic Diseases; Metabolism, Inborn Errors; Renal Dialysis

2022
Characteristics of amino acid profiles and incretin hormones in patients with gallstone disease: a pilot study.
    Polish archives of internal medicine, 2019, 12-23, Volume: 129, Issue:12

    Topics: Adult; Aged; Cholecystolithiasis; Diabetes Mellitus, Type 2; Female; Humans; Incretins; Isoleucine; Leucine; Lysine; Male; Metabolic Diseases; Middle Aged; Pilot Projects; Valine

2019
Elevated Plasma Branched-Chain Amino Acid Levels Correlate With Type 2 Diabetes-Related Metabolic Disturbances.
    The Journal of clinical endocrinology and metabolism, 2021, 03-25, Volume: 106, Issue:4

    Topics: Adult; Aged; Amino Acids, Branched-Chain; Case-Control Studies; Diabetes Complications; Diabetes Mellitus, Type 2; Female; Humans; Insulin Resistance; Leucine; Male; Metabolic Diseases; Middle Aged; Mitochondria; Oxidation-Reduction

2021
Comparison of amino acids and acylcarnitines assay methods used in newborn screening assays by tandem mass spectrometry.
    Clinica chimica acta; international journal of clinical chemistry, 2010, May-02, Volume: 411, Issue:9-10

    Topics: Amino Acids; Butanols; Carnitine; Humans; Infant, Newborn; Leucine; Metabolic Diseases; Methionine; Neonatal Screening; Palmitoylcarnitine; Phenylalanine; Quality Control; Tandem Mass Spectrometry

2010
Tyrosine hydroxylase deficiency in three Greek patients with a common ancestral mutation.
    Movement disorders : official journal of the Movement Disorder Society, 2010, Jun-15, Volume: 25, Issue:8

    Topics: Child, Preschool; Dihydroxyphenylalanine; DNA Mutational Analysis; Greece; Homovanillic Acid; Humans; Hydroxyindoleacetic Acid; Leucine; Metabolic Diseases; Methoxyhydroxyphenylglycol; Mutation; Proline; Tyrosine; Tyrosine 3-Monooxygenase; Young Adult

2010
Maple syrup urine disease; an inborn error of the metabolism of valine, leucine, and isoleucine associated with gross mental deficiency.
    British medical journal, 1959, Jan-10, Volume: 1, Issue:5114

    Topics: Biochemical Phenomena; Child; Humans; Infant; Intellectual Disability; Isoleucine; Leucine; Maple Syrup Urine Disease; Metabolic Diseases; Valine

1959
Maple syrup urine disease.
    British medical journal, 1959, Jan-10, Volume: 1, Issue:5114

    Topics: Biochemical Phenomena; Child; Humans; Infant; Intellectual Disability; Leucine; Maple Syrup Urine Disease; Metabolic Diseases

1959
Maple syrup urine disease.
    The Journal of pathology and bacteriology, 1961, Volume: 81

    Topics: Biochemical Phenomena; Body Fluids; Humans; Leucine; Maple Syrup Urine Disease; Metabolic Diseases; Urine; Valine

1961
Studies in maple syrup urine disease.
    Archives of disease in childhood, 1961, Volume: 36

    Topics: Child; Humans; Infant; Leucine; Maple Syrup Urine Disease; Metabolic Diseases; Valine

1961
Maple syrup urine disease.
    Archives of disease in childhood, 1961, Volume: 36

    Topics: Child; Humans; Infant; Leucine; Maple Syrup Urine Disease; Metabolic Diseases; Valine

1961
Inhibition of brain glutamic acid decarboxylase by phenylalanine, valine, and leucine derivatives: a suggestion concerning the etiology of the neurological defect in phenylketonuria and branched-chain ketonuria.
    Metabolism: clinical and experimental, 1961, Volume: 10

    Topics: Amino Acids; Brain; Glutamate Decarboxylase; Humans; Intellectual Disability; Ketosis; Leucine; Lyases; Maple Syrup Urine Disease; Metabolic Diseases; Phenylalanine; Phenylketonurias; Valine

1961
Studies on leucin-induced hypoglycemia.
    Acta paediatrica, 1962, Volume: 51

    Topics: Brain; Brain Diseases; Child; Humans; Hypoglycemia; Infant; Leucine; Metabolic Diseases; Pancreatic Diseases

1962
THE METABOLISM OF LEUCINE IN TISSUE CULTURE OF SKIN FIBROBLASTS OF MAPLE-SYRUP-URINE DISEASE.
    Biochimica et biophysica acta, 1963, Nov-08, Volume: 77

    Topics: Acer; Carbon Isotopes; Carboxy-Lyases; Clinical Enzyme Tests; Connective Tissue; Fibroblasts; Humans; Leucine; Maple Syrup Urine Disease; Metabolic Diseases; Proteins; Skin; Tissue Culture Techniques

1963
STUDIES ON HEMOGLOBIN BIOSYNTHESIS: ASYNCHRONOUS SYNTHESIS OF HEMOGLOBIN A AND HEMOGLOBIN A2 BY ERYTHROCYTE PRECURSORS.
    The Journal of clinical investigation, 1965, Volume: 44

    Topics: Anemia; Anemia, Hemolytic; Anemia, Hypochromic; Anemia, Pernicious; Anemia, Sickle Cell; Blood Protein Electrophoresis; Bone Marrow; Chromatography; Folic Acid; Folic Acid Deficiency; Hemoglobin A2; Hemoglobin, Sickle; Hemoglobins; Hemoglobins, Abnormal; Humans; Iron; Iron Isotopes; Leucine; Metabolic Diseases; Primary Myelofibrosis; Proteins; Pyruvate Kinase; Reticulocytes; Spherocytosis, Hereditary; Thalassemia; Vitamin B Deficiency

1965
[Maple syrup urine disease].
    Actualidad pediatrica; revista de bibliografia internacional, 1961, Volume: 19

    Topics: Biochemical Phenomena; Body Fluids; Humans; Leucine; Maple Syrup Urine Disease; Metabolic Diseases; Valine

1961
A new finding in maple-syrup-urine disease.
    Lancet (London, England), 1962, Jan-06, Volume: 1, Issue:7219

    Topics: Acer; Child; Humans; Infant; Intellectual Disability; Leucine; Maple Syrup Urine Disease; Metabolic Diseases; Methionine

1962
3-Methylcrotonyl-CoA carboxylase deficiency: metabolic decompensation in a noncompliant child detected through newborn screening.
    Pediatrics, 2006, Volume: 118, Issue:6

    Topics: Amino Acid Metabolism, Inborn Errors; Carbon-Carbon Ligases; Female; Humans; Infant; Infant, Newborn; Leucine; Metabolic Diseases; Neonatal Screening; Treatment Refusal

2006
Protein restriction and dexamethasone as a model of protein hypercatabolism in dogs: effect of glutamine on leucine turnover.
    Metabolism: clinical and experimental, 2001, Volume: 50, Issue:3

    Topics: Animals; Dexamethasone; Dietary Proteins; Dogs; Glucocorticoids; Glutamine; Injections, Intravenous; Kinetics; Leucine; Metabolic Diseases; Oxidation-Reduction

2001
Amino acid derangements in patients with sepsis: treatment with branched chain amino acid rich infusions.
    Annals of surgery, 1978, Volume: 188, Issue:3

    Topics: Amino Acids; Blood Glucose; Glucagon; Humans; Insulin; Isoleucine; Leucine; Metabolic Diseases; Parenteral Nutrition; Regression Analysis; Sepsis; Valine

1978
[Diagnostic methods for the detection of amino acid metabolism disorders].
    Monatsschrift fur Kinderheilkunde, 1973, Volume: 121, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Bacillus subtilis; Blood Protein Electrophoresis; Chemistry, Clinical; Chromatography; Clinical Enzyme Tests; Colorimetry; Fluorometry; Histidine; Humans; Leucine; Mass Screening; Metabolic Diseases; Methionine; Methods; Microbial Sensitivity Tests; Organization and Administration; Phenylalanine; Phenylketonurias; Tyrosine

1973
[Blood cells as indicators of metabolic disorders].
    Zeitschrift fur klinische Chemie und klinische Biochemie, 1967, Volume: 5, Issue:5

    Topics: Acidosis; Adrenal Insufficiency; Alcoholism; Alkalosis; Diabetes Mellitus; Down Syndrome; Electrolytes; Erythrocytes; Galactosemias; Glucosephosphate Dehydrogenase; Glycogen Storage Disease; Humans; Hyperaldosteronism; Hypertension; Hyperthyroidism; Kidney Failure, Chronic; Leucine; Leukocytes; Maple Syrup Urine Disease; Metabolic Diseases; Muscular Dystrophies; Paralyses, Familial Periodic; Potassium; Sodium; Vitamin B Deficiency

1967
[On a case of spontaneous hypoglycemia in a nursing infant].
    Folia endocrinologica, 1973, Volume: 26, Issue:5

    Topics: Female; Food Hypersensitivity; Humans; Hypoglycemia; Infant; Infant, Newborn; Infant, Newborn, Diseases; Leucine; Metabolic Diseases

1973
[Experiences with a new amino acid analyzer for a rapid analysis].
    Monatsschrift fur Kinderheilkunde, 1970, Volume: 118, Issue:6

    Topics: Amino Acids; Autoanalysis; Homocystine; Homocystinuria; Humans; Infant, Newborn; Infant, Premature, Diseases; Isoleucine; Leucine; Maple Syrup Urine Disease; Metabolic Diseases; Methionine; Phenylalanine; Phenylketonurias; Tyrosine; Valine

1970