leucine and Compensatory Hyperinsulinemia

leucine has been researched along with Compensatory Hyperinsulinemia in 86 studies

Research

Studies (86)

TimeframeStudies, this research(%)All Research%
pre-199041 (47.67)18.7374
1990's19 (22.09)18.2507
2000's16 (18.60)29.6817
2010's9 (10.47)24.3611
2020's1 (1.16)2.80

Authors

AuthorsStudies
Du, JL; Lei, PP; Li, YH; Liu, K; Long, W; Ma, L; Qu, PF; Tang, X; Wang, YB; Wei, SJ; Xi, YM1
Klein, S; Mittendorfer, B; Okunade, AL; Porter, L; Ramaswamy, R; Reeds, DN; Smith, GI; van Vliet, S; Yoshino, J1
Chevalier, S; Gougeon, R; Labonte, CC; Marliss, EB; Morais, JA1
Kelly, A; Stanley, CA1
Crowley, VE; DeLong, C; Hand, E; Hatunic, M; Nolan, JJ; Stapleton, M1
Baiocchi, MR; Coracina, A; Kiwanuka, E; Millioni, R; Puricelli, L; Semplicini, A; Tessari, P; Vettore, M; Zaramella, M1
Atherton, P; Jaffery, H; Mittendorfer, B; Mohammed, BS; Rankin, D; Reeds, DN; Rennie, MJ; Smith, GI1
Castillo, L; Coss-Bu, J; Joosten, KF; Schierbeek, H; van Goudoever, JB; Verbruggen, SC1
Braun, S; Demmelmair, H; Hartl, WH; Jauch, KW; Koletzko, B; Kuppinger, D; Rittler, P; Vogeser, M1
Byrne, BJ; Cade, WT; Crowley, JR; Maisenbacher, M; O'Connor, R; Peterson, LR; Reeds, DN; Spencer, CT; Waggoner, AD1
Akcay, T; Chadefaux, B; Eaton, S; Ellard, S; Flanagan, SE; Heslegrave, AJ; Hussain, K; Kapoor, RR; Simsek, E1
Asmann, Y; Barazzoni, R; Coenen-Schimke, JM; Nair, KS; Robinson, MM; Short, KR1
Deger, SM; Egbert, P; Ellis, CD; Hung, AM; Ikizler, TA; Sha, F; Siew, ED; Sundell, MB1
Bôle-Feysot, C; Cailleux, AF; Claeyssens, S; Coëffier, M; Déchelotte, P; Donnadieu, N; Guérin, C; Lavoinne, A; Lecleire, S; Maurer, B1
GRUMBACH, MM; KAPLAN, SL1
GOLDNER, MG; WEISENFELD, S1
BOUMAN, PR1
CARNEVALI, R; POLI, E; RAINERI, P1
GRANN, V; MAHLER, RJ; PURDY, R1
BIELIK, E; GALIK, L; HRNCIAR, J; HRNCIAROVA, M1
BECKER, FO; CLARK, J; SCHWARTZ, TB1
CONN, JW; FAJANS, SS; FLOYD, JC; KNOPF, RF1
Agus, MS; Jaksic, T; Javid, PJ; Ryan, DP1
Murata, K; Ohie, T; Taketani, T; Toriumi, Y; Uchiyama, A; Yamaguchi, S1
Aalinkeel, R; Hill, DJ; Mitrani, P; Pandya, JD; Patel, MS; Song, F; Srinivasan, M; Strutt, B1
Chevalier, S; Gougeon, R; Lamarche, M; Marliss, EB; Morais, JA1
Hoe, FM; Simmons, RA; Stanley, CA; Steinkrauss, L; Thornton, PS; Wanner, LA1
Collins, HW; Daikhin, Y; Hsu, BY; Kelly, A; Kwagh, J; Lazarow, A; Li, C; MacMullen, C; Matschinsky, FM; Matter, A; Najafi, H; Nissim, I; Petty, TJ; Stanley, CA; Yudkoff, M1
Brown, LD; Hay, WW1
Chevalier, S; Gougeon, R; Marliss, EB; Morais, JA; Pereira, S1
Donnell, GN; Koch, R; Lieberman, E; Shaw, KN1
Besch, W; Wilke, B1
Bradvica, C; Golden, MP; Graham, MJ; Santiago, J; Sargeant, DT; White, NH; Zuniga, O1
de Geeter, B; Kurtz, F; Maertens, P; Messer, J; Raber, A; Willard, D1
Bayle, G; Berry, C; Bonnet, Y; Champredon, C; Charrier, S; Grizard, J; Obled, C; Prugnaud, J; Tauveron, I; Thiéblot, P1
Ang, BC; Halliday, D; Powell-Tuck, J1
Battezzati, A; Bianchi, E; Di Carlo, V; Luzi, L; Perseghin, G; Pozza, G; Terruzzi, I1
Biolo, G; Declan Fleming, RY; Wolfe, RR1
DeFronzo, RA; Luzi, L; Petrides, AS1
Beaufrere, B; Campbell, PJ; Gerich, JE; Gottesman, IS; Haymond, MW; Heiling, VJ; Tsalikian, E1
Battezzati, A; Bianchi, E; Ferrari, G; La Rocca, E; Luzi, L; Perseghin, G; Secchi, A; Spotti, D; Terruzzi, I; Vergani, S1
Brennan, MF; Heslin, MJ; Newman, E; Pisters, PW; Wolf, RF3
Donati, MA; Filippi, L; Novembre, E; Zammarchi, E1
Bolli, GB; Brunetti, P; Cruciani, G; De Feo, P; Lucidi, P; Monacchia, F; Reboldi, G; Volpi, E1
Beckett, PR; Copeland, KC; Davis, TA; Hardin, DS; Nguyen, HV; Wray-Cahen, D1
Bedford, D; Caslake, M; Malmström, R; Packard, CJ; Shepherd, J; Stewart, P; Taskinen, MR; Yki-Järvinen, H1
Bernard, C; Berthault, MF; Ktorza, A; Magnan, C; Pénicaud, L; Portha, B; Pralong, WF; Saulnier, C; Thibault, C1
Bayle, G; Benoit, P; Berry, C; Capitan, P; Champredon, C; Dejax, C; Fabricio, A; Grizard, J; Prugnaud, J; Rochon, C; Tauveron, I; Thieblot, P1
Ferry, RJ; Grimberg, A; Kelly, A; Koo-McCoy, S; Ng, D; Stanley, CA; Thornton, PS1
Aral, B; Benelli, C; De Lonlay, P; Dionisi-Vici, C; Fouque, F; Ganguly, A; Heinrichs, C; Kamoun, P; Rabier, D; Robert, JJ; Saudubray, JM; Stanley, C; Touati, G1
Bilz, S; Bloesch, D; Keller, U; Laager, R; Turkalj, I1
Berger, H1
Förster, H1
Hudson, AJ; Tevaarwerk, GJ1
Baker, L; Stanley, CA1
Reich, H; Schünke, W1
Eaton, RP; Schade, S1
Couropmitree, C; Freinkel, N; Hahnel, R; Horwitz, DL; Metzger, B; Nagel, TC; Rubenstein, AH1
Krämer, K; Sailer, FX1
Horwitz, DL; Kuzuya, H; Rubenstein, AH; Sandler, R1
Boyle, DW; Denne, SC; Liechty, EA; Liu, YM; Moorehead, H1
Amatruda, JM; Barnard, RR; Statt, M; Welle, S1
Caballero, B; Wurtman, RJ1
Bennet, WM; Connacher, AA; Jung, RT; Rennie, MJ; Scrimgeour, CM1
Biolo, G; Crepaldi, G; Fantin, G; Inchiostro, S; Iori, E; Marescotti, MC; Tessari, P; Tiengo, A; Trevisan, R1
Gates, RJ; Hunt, MI; Lazarus, NR1
Miles, LE1
Lundbaek, K; Lyngsoe, J; Madsen, B; Orskov, H; Yde, H1
Frawley, TF; Pensuwan, S1
Glöckner, E; Knoke, M; Markert, J; Reding, R1
Conn, JW; Fajans, SS; Floyd, JC; Harrison, TS; Knopf, RF; Thiffault, CA1
Marks, V; Samols, E1
Grinvalsky, HT; Remigio, PA1
Ishihara, Y; Kuroda, A; Sato, N; Tajima, Y; Wada, Y1
Altenähr, E; Freytag, G; Klöppel, G; Reichel, W; Willig, R1
Colle, E; Schiff, D; Stern, L; Wells, D1
Forsham, PH; Grodsky, GM; Johnson, S; Karam, JH; Levin, SR1
Duprey, J; Lubetzki, J1
Barbosa, J; Goetz, F; Kennedy, W; Nuttall, FQ1
Bannert, N; Fischer, HU; Schütze, I1
Wüstenberg, PW1
Barbieri, D; Marcondes, E; Quarentei, G; Setian, N1
Federspil, G; Frezzato, S; Macrì, C; Muggeo, M; Tiengo, A; Trisotto, A; Vianello, A1
Conn, JW; Fajans, SS; Floyd, JC; Knopf, RF; Rull, J1

Reviews

6 review(s) available for leucine and Compensatory Hyperinsulinemia

ArticleYear
[POSSIBILITIES AND LIMITATIONS IN THE DETERMINATION OF INSULIN IN BLOOD IN THE DIAGNOSIS OF HYPERINSULINISM].
    Maandschrift voor kindergeneeskunde, 1963, Volume: 31

    Topics: Adenoma, Islet Cell; Blood; Diagnosis; Humans; Hyperglycemia; Hyperinsulinism; Insulin; Leucine; Pancreatic Neoplasms; Tolbutamide

1963
[HYPERINSULINISM. DIAGNOSTIC AND THERAPEUTIC ASPECTS].
    Lekarska veda v zahranici, 1964, Mar-20, Volume: 37

    Topics: Diagnosis, Differential; Electrodiagnosis; Electroencephalography; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Pancreas; Sleep Wake Disorders; Surgical Procedures, Operative; Tolbutamide

1964
Hyperinsulinism in infants and children: diagnosis and therapy.
    Advances in pediatrics, 1976, Volume: 23

    Topics: Adult; Blood Glucose; Child; Child, Preschool; Diazoxide; Fatty Acids, Nonesterified; Humans; Hydroxybutyrates; Hyperinsulinism; Hypoglycemia; Infant; Infant, Newborn; Insulin; Leucine; Male; Pancreatectomy; Proinsulin

1976
Hypoglycemia: tolbutamide and leucine tests in insulinoma.
    The Medical clinics of North America, 1968, Volume: 52, Issue:2

    Topics: Adenoma, Islet Cell; Blood Glucose; Fasting; Female; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Insulin Secretion; Leucine; Male; Middle Aged; Pancreatic Neoplasms; Tolbutamide

1968
[Insulinoma].
    Nihon rinsho. Japanese journal of clinical medicine, 1973, Volume: 31, Issue:3

    Topics: Adenoma, Islet Cell; Adolescent; Adult; Aged; Angiography; Child; Diagnosis, Differential; Diagnostic Techniques, Surgical; Female; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Male; Middle Aged; Pancreatic Neoplasms; Proinsulin; Tolbutamide

1973
[The hypoglycemia syndrome].
    Zeitschrift fur die gesamte innere Medizin und ihre Grenzgebiete, 1970, Jun-01, Volume: 25, Issue:11

    Topics: Alloxan; Angiography; Antibiotics, Antineoplastic; Blood Glucose; Diagnosis, Differential; Diazoxide; Diet Therapy; Epinephrine; Gastrointestinal Diseases; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Metabolic Diseases; Neoplasms; Pancreatic Neoplasms; Prednisone; Tolbutamide

1970

Trials

10 trial(s) available for leucine and Compensatory Hyperinsulinemia

ArticleYear
No major sex differences in muscle protein synthesis rates in the postabsorptive state and during hyperinsulinemia-hyperaminoacidemia in middle-aged adults.
    Journal of applied physiology (Bethesda, Md. : 1985), 2009, Volume: 107, Issue:4

    Topics: Adult; Blood Glucose; Body Composition; Female; Glucose Clamp Technique; Humans; Hyperinsulinism; Infusions, Intravenous; Insulin; Kinetics; Leucine; Male; Muscle Proteins; Muscle, Skeletal; Phenylalanine; Phosphorylation; Protein Kinases; Proto-Oncogene Proteins c-akt; Ribosomal Protein S6 Kinases, 70-kDa; RNA; Sex Factors; Signal Transduction; TOR Serine-Threonine Kinases

2009
Albumin synthesis rates in post-surgical infants and septic adolescents; influence of amino acids, energy, and insulin.
    Clinical nutrition (Edinburgh, Scotland), 2011, Volume: 30, Issue:4

    Topics: Adolescent; Albumins; Amino Acids; Blood Glucose; Critical Illness; Cross-Over Studies; Female; Glucose; Homeostasis; Humans; Hyperinsulinism; Infant; Insulin; Insulin Resistance; Intensive Care Units, Pediatric; Leucine; Male; Parenteral Nutrition, Total; Sepsis

2011
Albumin synthesis rates are not responsive to hyperglycemic hyperinsulinemia in postoperative patients.
    JPEN. Journal of parenteral and enteral nutrition, 2011, Volume: 35, Issue:3

    Topics: Abdomen; Aged; Carbon Isotopes; Case-Control Studies; Glucose; Humans; Hyperglycemia; Hyperinsulinism; Insulin; Leucine; Middle Aged; Postoperative Complications; Serum Albumin

2011
Insulin fails to enhance mTOR phosphorylation, mitochondrial protein synthesis, and ATP production in human skeletal muscle without amino acid replacement.
    American journal of physiology. Endocrinology and metabolism, 2012, Nov-01, Volume: 303, Issue:9

    Topics: Adenosine Triphosphate; Adult; Amino Acids; Carbon Isotopes; Female; Gene Expression Regulation; Humans; Hyperinsulinism; Infusions, Intravenous; Insulin; Insulin, Regular, Human; Leucine; Male; Mitochondria, Muscle; Mitochondrial Proteins; Muscle, Skeletal; Phosphorylation; Protein Processing, Post-Translational; Proto-Oncogene Proteins c-akt; RNA, Messenger; TOR Serine-Threonine Kinases; Young Adult

2012
Enteral delivery of proteins stimulates protein synthesis in human duodenal mucosa in the fed state through a mammalian target of rapamycin-independent pathway.
    The American journal of clinical nutrition, 2013, Volume: 97, Issue:2

    Topics: Adult; Carbon Isotopes; Deuterium; Dietary Proteins; Duodenum; Enteral Nutrition; Extracellular Signal-Regulated MAP Kinases; Glutamine; Humans; Hyperinsulinism; Intestinal Mucosa; Leucine; Male; Phenylalanine; Phosphatidylinositol 3-Kinase; Phosphorylation; Postprandial Period; Protein Biosynthesis; Protein Processing, Post-Translational; TOR Serine-Threonine Kinases; Up-Regulation; Young Adult

2013
Intravenous insulin decreases protein breakdown in infants on extracorporeal membrane oxygenation.
    Journal of pediatric surgery, 2004, Volume: 39, Issue:6

    Topics: Blood Glucose; Cohort Studies; Cross-Over Studies; Extracorporeal Membrane Oxygenation; Female; Glucose; Humans; Hyperinsulinism; Infant; Infant, Newborn; Infant, Newborn, Diseases; Infusions, Intravenous; Insulin; Leucine; Male; Parenteral Nutrition, Total; Pilot Projects; Prospective Studies; Proteins; Treatment Outcome

2004
The influence of sex on the protein anabolic response to insulin.
    Metabolism: clinical and experimental, 2005, Volume: 54, Issue:11

    Topics: Adult; Carbon Isotopes; Dietary Proteins; Energy Metabolism; Female; Glucose; Humans; Hyperinsulinism; Hypoglycemic Agents; Insulin; Leucine; Male; Sex Characteristics; Tritium

2005
Whole-body protein turnover in response to hyperinsulinemia in humans postabsorptively with [15N]glycine as tracer.
    The American journal of clinical nutrition, 1995, Volume: 61, Issue:5

    Topics: Adult; Ammonia; Blood Glucose; Carbon Isotopes; Cross-Over Studies; Female; Glucose Clamp Technique; Glycine; Humans; Hyperinsulinism; Insulin; Leucine; Male; Nitrogen Isotopes; Nutritional Status; Proteins; Urea

1995
Physiologic hyperinsulinemia stimulates protein synthesis and enhances transport of selected amino acids in human skeletal muscle.
    The Journal of clinical investigation, 1995, Volume: 95, Issue:2

    Topics: Adult; Alanine; Amino Acids; Biological Transport; Femoral Vein; Humans; Hyperinsulinism; Insulin; Kinetics; Leucine; Lysine; Male; Mathematics; Models, Biological; Muscle, Skeletal; Phenylalanine; Protein Biosynthesis; Reference Values

1995
Effects of medium- and long-chain fatty acids on whole body leucine and glucose kinetics in man.
    Metabolism: clinical and experimental, 2002, Volume: 51, Issue:6

    Topics: Adult; C-Peptide; Carbon Isotopes; Fatty Acids; Fatty Acids, Nonesterified; Glucagon; Glucose; Glucose Clamp Technique; Humans; Hyperinsulinism; Infusions, Intravenous; Insulin; Keto Acids; Lactic Acid; Leucine; Liver; Male; Oxidation-Reduction; Proteins; Reference Values; Triglycerides

2002

Other Studies

70 other study(ies) available for leucine and Compensatory Hyperinsulinemia

ArticleYear
Functional analysis of HADH c.99C>G shows that the variant causes the proliferation of pancreatic islets and leu-sensitive hyperinsulinaemia.
    Journal of genetics, 2022, Volume: 101

    Topics: 3-Hydroxyacyl-CoA Dehydrogenase; Animals; Blood Glucose; Carboxymethylcellulose Sodium; Cell Proliferation; Glucagon; Glucose; Hyperinsulinism; Insulin; Islets of Langerhans; Leucine; Rats; Sodium

2022
The muscle anabolic effect of protein ingestion during a hyperinsulinaemic euglycaemic clamp in middle-aged women is not caused by leucine alone.
    The Journal of physiology, 2018, Volume: 596, Issue:19

    Topics: Anabolic Agents; Eating; Female; Glucose; Glucose Clamp Technique; Humans; Hyperinsulinism; Insulin; Leucine; Middle Aged; Muscle Proteins; Signal Transduction; TOR Serine-Threonine Kinases

2018
Effect of 10% dietary protein intake on whole body protein kinetics in type 2 diabetic adults.
    Clinical nutrition (Edinburgh, Scotland), 2015, Volume: 34, Issue:6

    Topics: Amino Acids; Blood Glucose; Body Mass Index; Body Weight; Diabetes Mellitus, Type 2; Diet, Protein-Restricted; Dietary Proteins; Energy Intake; Female; Glucose Clamp Technique; Humans; Hyperinsulinism; Insulin; Insulin Resistance; Leucine; Male; Mental Recall; Middle Aged; Obesity; Sex Factors; Waist Circumference

2015
Neurological aspects in hyperinsulinism-hyperammonaemia syndrome.
    Developmental medicine and child neurology, 2008, Volume: 50, Issue:12

    Topics: Brain Damage, Chronic; Child; Dietary Proteins; Enzyme Activation; Glucose Transporter Type 1; Glutamate Dehydrogenase; Guanosine Triphosphate; Humans; Hyperammonemia; Hyperinsulinism; Hypoglycemia; Leucine; Liver; Mutation, Missense; Neurologic Examination; Pancreas

2008
The Leu262Val polymorphism of presenilin associated rhomboid like protein (PARL) is associated with earlier onset of type 2 diabetes and increased urinary microalbumin creatinine ratio in an Irish case-control population.
    Diabetes research and clinical practice, 2009, Volume: 83, Issue:3

    Topics: Age of Onset; Albuminuria; Amino Acid Substitution; Animals; Case-Control Studies; Creatinine; Diabetes Mellitus, Type 2; Diabetic Angiopathies; Diabetic Nephropathies; Disease Models, Animal; Genetic Variation; Gerbillinae; Humans; Hyperinsulinism; Ireland; Leucine; Metalloproteases; Mitochondrial Proteins; Polymorphism, Single Nucleotide; Reference Values; Valine

2009
Fibrinogen kinetics and protein turnover in hypertension: Effects of insulin.
    Nutrition, metabolism, and cardiovascular diseases : NMCD, 2009, Volume: 19, Issue:11

    Topics: Adult; Biomarkers; Blood Glucose; Case-Control Studies; Deuterium; Fibrinogen; Glucose; Glucose Clamp Technique; Humans; Hyperinsulinism; Hypertension; Indicator Dilution Techniques; Infusions, Intravenous; Insulin; Kinetics; Leucine; Male; Middle Aged; Peptide Hydrolases; Up-Regulation

2009
Substrate metabolism during basal and hyperinsulinemic conditions in adolescents and young-adults with Barth syndrome.
    Journal of inherited metabolic disease, 2013, Volume: 36, Issue:1

    Topics: Adolescent; Adult; Barth Syndrome; Blood Glucose; Body Composition; Echocardiography; Fatty Acids; Glucose; Humans; Hyperinsulinism; Insulin; Leucine; Lipid Metabolism; Lipolysis; Male; Mitochondria; Oxidation-Reduction; Young Adult

2013
Leucine-sensitive hyperinsulinaemic hypoglycaemia in patients with loss of function mutations in 3-Hydroxyacyl-CoA Dehydrogenase.
    Orphanet journal of rare diseases, 2012, May-14, Volume: 7

    Topics: 3-Hydroxyacyl CoA Dehydrogenases; Child; Child, Preschool; Female; Glutamate Dehydrogenase; Humans; Hyperinsulinism; Hypoglycemia; Immunoprecipitation; Infant; Insulin; Leucine; Male; Mutation

2012
Insulin resistance and protein metabolism in chronic hemodialysis patients.
    Journal of renal nutrition : the official journal of the Council on Renal Nutrition of the National Kidney Foundation, 2013, Volume: 23, Issue:3

    Topics: Adult; Aged; Amino Acids; Black or African American; Blood Glucose; Body Composition; Chromatography, High Pressure Liquid; Cross-Sectional Studies; Dose-Response Relationship, Drug; Female; Glucose Clamp Technique; Humans; Hyperinsulinism; Insulin; Insulin Resistance; Leucine; Male; Middle Aged; Proteins; Renal Dialysis; Sarcopenia; Sensitivity and Specificity

2013
Amino acid and alpha-keto acid-induced hyperinsulinism in the leucine-sensitive type of infantile and childhood hypoglycemia.
    The Journal of pediatrics, 1960, Volume: 57

    Topics: Amino Acids; Child; Humans; Hyperinsulinism; Hypoglycemia; Infant; Keto Acids; Leucine; Seizures

1960
Hyperinsulinemia in 1-leucine-sensitive hypoglycemia in an adult.
    The American journal of medicine, 1961, Volume: 31

    Topics: Adenoma, Islet Cell; Adult; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Medical Records; Pancreatic Neoplasms

1961
[HYPOGLYCEMIC REACTION TO LEUCINE, VALINE AND PHENYLALANINE IN A CASE OF DIFFUSE HYPERPLASIA OF THE BETA CELLS].
    Folia endocrinologica, 1963, Volume: 16

    Topics: Glucose Tolerance Test; Humans; Hyperinsulinism; Hyperplasia; Hypoglycemia; Hypoglycemic Agents; Insulin-Secreting Cells; Islands; Islets of Langerhans; Leucine; Pathology; Pharmacology; Phenylalanine; Tolbutamide; Valine

1963
FUNCTIONING ISLET CELL ADENOMA.
    JAMA, 1964, Jun-01, Volume: 188

    Topics: Adenoma, Islet Cell; Cerebrovascular Disorders; Diagnosis, Differential; Geriatrics; Humans; Hyperinsulinism; Leucine; Pancreatic Neoplasms; Tolbutamide

1964
L-LEUCINE SENSITIVITY AND GLUCOSE TOLERANCE IN NORMAL SUBJECTS.
    The Journal of clinical endocrinology and metabolism, 1964, Volume: 24

    Topics: Blood Glucose; Carbohydrate Metabolism; Diabetes Mellitus; Diagnosis; Glucose Tolerance Test; Humans; Hyperinsulinism; Leucine

1964
PLASMA INSULIN IN ORGANIC HYPERINSULINISM: COMPARATIVE EFFECTS OF TOLBUTAMIDE, LEUCINE AND GLUCOSE.
    The Journal of clinical endocrinology and metabolism, 1964, Volume: 24

    Topics: Adenoma, Islet Cell; Blood; Blood Chemical Analysis; Blood Glucose; Glucagon; Glucose; Humans; Hyperglycemia; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Pancreatic Neoplasms; Pharmacology; Surgical Procedures, Operative; Tolbutamide

1964
A case of hyperinsulinism/hyperammonaemia syndrome: usefulness of the oral protein tolerance for the evaluation of treatment.
    European journal of pediatrics, 2005, Volume: 164, Issue:3

    Topics: Child; Exons; Female; Glutamate Dehydrogenase; Humans; Hyperammonemia; Hyperinsulinism; Hypoglycemia; Leucine; Mutation; Syndrome

2005
Maternal hyperinsulinemia predisposes rat fetuses for hyperinsulinemia, and adult-onset obesity and maternal mild food restriction reverses this phenotype.
    American journal of physiology. Endocrinology and metabolism, 2006, Volume: 290, Issue:1

    Topics: Animals; Animals, Newborn; Arginine; Basic Helix-Loop-Helix Transcription Factors; Blood Glucose; Body Weight; Diet; Dietary Carbohydrates; Female; Fetus; Gene Expression; Glucose; Hepatocyte Nuclear Factor 3-beta; Homeodomain Proteins; Hyperinsulinism; Insulin; Islets of Langerhans; Leucine; Lipids; Male; Obesity; Pregnancy; Prenatal Exposure Delayed Effects; Proinsulin; Protein Precursors; Rats; Rats, Sprague-Dawley; RNA, Messenger; Trans-Activators

2006
Clinical features and insulin regulation in infants with a syndrome of prolonged neonatal hyperinsulinism.
    The Journal of pediatrics, 2006, Volume: 148, Issue:2

    Topics: Antihypertensive Agents; Calcium; Case-Control Studies; Diazoxide; Enteral Nutrition; Fasting; Female; Glucose; Humans; Hyperinsulinism; Hypoglycemia; Hypoglycemic Agents; Infant; Infant, Newborn; Infusions, Intravenous; Insulin; Insulin Secretion; Leucine; Male; Prospective Studies; Risk Factors; Sweetening Agents; Tolbutamide

2006
Effects of a GTP-insensitive mutation of glutamate dehydrogenase on insulin secretion in transgenic mice.
    The Journal of biological chemistry, 2006, Jun-02, Volume: 281, Issue:22

    Topics: Adenosine Diphosphate; Adenosine Triphosphate; Animals; Calcium Signaling; Glucose; Glutamate Dehydrogenase; Glutamine; Guanosine Triphosphate; Humans; Hyperinsulinism; In Vitro Techniques; Insulin; Insulin Secretion; Islets of Langerhans; Kinetics; Leucine; Mice; Mice, Inbred C57BL; Mice, Transgenic; Models, Biological; Mutation; Recombinant Proteins

2006
Effect of hyperinsulinemia on amino acid utilization and oxidation independent of glucose metabolism in the ovine fetus.
    American journal of physiology. Endocrinology and metabolism, 2006, Volume: 291, Issue:6

    Topics: Algorithms; Amino Acids; Amino Acids, Branched-Chain; Animals; Blood Gas Analysis; Blood Glucose; Female; Fetus; Glucose; Hyperinsulinism; Insulin; Kinetics; Lactic Acid; Leucine; Oxidation-Reduction; Pregnancy; Sheep

2006
Insulin resistance of protein metabolism in type 2 diabetes.
    Diabetes, 2008, Volume: 57, Issue:1

    Topics: Adult; Amino Acids; Blood Chemical Analysis; Body Mass Index; Diabetes Mellitus, Type 2; Female; Follicular Phase; Glucose Clamp Technique; Humans; Hyperinsulinism; Insulin; Insulin Resistance; Leucine; Male; Middle Aged; Proteins; Reference Values

2008
Hypoglycemia in maple syrup urine disease.
    American journal of diseases of children (1960), 1967, Volume: 113, Issue:1

    Topics: Animals; Caseins; Female; Gluconeogenesis; Glucose; Glucose Tolerance Test; Glycogen; Humans; Hyperinsulinism; Hypoglycemia; In Vitro Techniques; Infant; Leucine; Male; Maple Syrup Urine Disease; Rats

1967
Characterization of beta-cell specific function of isolated pancreatic islets from hyperglycemic C57BL/KsJ-db/db mice.
    Acta biologica et medica Germanica, 1982, Volume: 41, Issue:12

    Topics: Animals; Blood Glucose; Cells, Cultured; Hyperglycemia; Hyperinsulinism; Insulin; Islets of Langerhans; Leucine; Male; Mice; Mice, Inbred C57BL; Mice, Inbred Strains; Proinsulin; Protein Precursors

1982
Persistent leucine sensitivity following partial pancreatectomy and diazoxide treatment. Therapeutic response.
    American journal of diseases of children (1960), 1983, Volume: 137, Issue:4

    Topics: Child, Preschool; Diazoxide; Female; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Pancreatectomy; Pancreatic Diseases; Seizures

1983
[Long-term diazoxide therapy in recurrent leucine-sensitive hypoglycemia (author's transl)].
    Annales de pediatrie, 1980, Volume: 27, Issue:10

    Topics: Child, Preschool; Diazoxide; Female; Growth; Humans; Hyperinsulinism; Hypoglycemia; Infant; Infant, Newborn; Leucine

1980
Response of leucine metabolism to hyperinsulinemia under amino acid replacement in experimental hyperthyroidism.
    The American journal of physiology, 1995, Volume: 269, Issue:3 Pt 1

    Topics: Adult; Amino Acids; Blood Glucose; Carbon Dioxide; Humans; Hyperinsulinism; Hyperthyroidism; Insulin; Keto Acids; Kinetics; Leucine; Male; Reference Values; Respiration

1995
Defective insulin action on protein and glucose metabolism during chronic hyperinsulinemia in subjects with benign insulinoma.
    Diabetes, 1995, Volume: 44, Issue:7

    Topics: Adult; Blood Glucose; Carbon Radioisotopes; Chronic Disease; Glucose; Glucose Clamp Technique; Humans; Hyperinsulinism; Insulin; Insulinoma; Keto Acids; Leucine; Liver; Middle Aged; Pancreatic Neoplasms; Proteins; Radioisotope Dilution Technique; Reference Values; Tritium

1995
Time-dependent regulation by insulin of leucine metabolism in young healthy adults.
    The American journal of physiology, 1994, Volume: 267, Issue:3 Pt 1

    Topics: Adolescent; Adult; Amino Acids; Blood Glucose; Calorimetry, Indirect; Female; Glucagon; Humans; Hyperinsulinism; Insulin; Keto Acids; Leucine; Male; Osmolar Concentration; Oxidation-Reduction; Reference Values; Time Factors

1994
Differential effects of hyperglycemia and hyperinsulinemia on leucine rate of appearance in normal humans.
    The Journal of clinical endocrinology and metabolism, 1993, Volume: 76, Issue:1

    Topics: Adult; Blood Glucose; Female; Glucagon; Glucose Clamp Technique; Humans; Hyperglycemia; Hyperinsulinism; Insulin; Insulin Infusion Systems; Leucine; Male; Middle Aged; Reference Values; Somatostatin

1993
Combined pancreas and kidney transplantation normalizes protein metabolism in insulin-dependent diabetic-uremic patients.
    The Journal of clinical investigation, 1994, Volume: 93, Issue:5

    Topics: Adult; Blood Glucose; Diabetes Mellitus, Type 1; Female; Hemoglobins; Hormones; Humans; Hyperinsulinism; Immunosuppression Therapy; Keto Acids; Kidney Failure, Chronic; Kidney Transplantation; Leucine; Male; Nitrogen; Oxidation-Reduction; Pancreas Transplantation; Proteins; Uremia; Uveitis, Posterior

1994
The effect of systemic hyperinsulinemia with concomitant amino acid infusion on skeletal muscle protein turnover in the human forearm.
    Metabolism: clinical and experimental, 1994, Volume: 43, Issue:1

    Topics: Adult; Aged; Amino Acids; Amino Acids, Branched-Chain; Blood Glucose; Carbon Radioisotopes; Chromatography, High Pressure Liquid; Female; Forearm; Glucagon; Humans; Hyperinsulinism; Insulin; Leucine; Male; Middle Aged; Muscle Proteins; Muscles; Phenylalanine; Time Factors; Tritium

1994
Biochemical evaluation of a patient with a familial form of leucine-sensitive hypoglycemia and concomitant hyperammonemia.
    Metabolism: clinical and experimental, 1996, Volume: 45, Issue:8

    Topics: Adult; Ammonia; Drug Resistance; Female; Glutamates; Humans; Hyperinsulinism; Hypoglycemia; Infant; Leucine; Male

1996
Contribution of amino acids and insulin to protein anabolism during meal absorption.
    Diabetes, 1996, Volume: 45, Issue:9

    Topics: Administration, Oral; Adult; Amino Acids; Antithrombin III; Blood Glucose; C-Peptide; Carbon Radioisotopes; Eating; Fatty Acids, Nonesterified; Female; Fibrinogen; Glucagon; Glucose; Humans; Hyperinsulinism; Immunoglobulin G; Insulin; Intestinal Absorption; Keto Acids; Kinetics; Leucine; Lipid Metabolism; Lipids; Male; Protein Biosynthesis; Proteins; Radioisotope Dilution Technique; Serum Albumin

1996
Spectrophometric assay for measuring branched-chain amino acid concentrations: application for measuring the sensitivity of protein metabolism to insulin.
    Analytical biochemistry, 1996, Aug-15, Volume: 240, Issue:1

    Topics: Amino Acid Oxidoreductases; Amino Acids, Branched-Chain; Blood Proteins; Chromatography, High Pressure Liquid; Enzyme Stability; Humans; Hyperinsulinism; Insulin; Isoleucine; Kinetics; Leucine; Leucine Dehydrogenase; NAD; Spectrophotometry; Valine

1996
Defective regulation of triglyceride metabolism by insulin in the liver in NIDDM.
    Diabetologia, 1997, Volume: 40, Issue:4

    Topics: Apolipoproteins B; Cholesterol; Cholesterol, HDL; Deuterium; Diabetes Mellitus, Type 2; Fatty Acids, Nonesterified; Glucose Clamp Technique; Humans; Hyperglycemia; Hyperinsulinism; Infusions, Intravenous; Insulin; Leucine; Lipoproteins, VLDL; Liver; Male; Middle Aged; Models, Biological; Radioisotope Dilution Technique; Reference Values; Triglycerides

1997
Pancreatic beta-cell regeneration after 48-h glucose infusion in mildly diabetic rats is not correlated with functional improvement.
    Diabetes, 1998, Volume: 47, Issue:7

    Topics: Animals; Arginine; Blood Glucose; Diabetes Mellitus, Experimental; Glucose; Hyperglycemia; Hyperinsulinism; Immunoenzyme Techniques; In Vitro Techniques; Insulin; Insulin Secretion; Islets of Langerhans; Leucine; Male; Rats; Rats, Wistar; Regeneration

1998
Response of leucine metabolism to hyperinsulinemia in hypothyroid patients before and after thyroxine replacement.
    The Journal of clinical endocrinology and metabolism, 2000, Volume: 85, Issue:2

    Topics: Adult; Amino Acids; Blood Glucose; Carbon Dioxide; Humans; Hyperinsulinism; Hypothyroidism; Insulin; Keto Acids; Leucine; Middle Aged; Respiration

2000
Acute insulin responses to leucine in children with the hyperinsulinism/hyperammonemia syndrome.
    The Journal of clinical endocrinology and metabolism, 2001, Volume: 86, Issue:8

    Topics: Adolescent; Adult; Amino Acid Substitution; Ammonia; Blood Glucose; Child; Child, Preschool; Diazoxide; Female; Glutamate Dehydrogenase; Humans; Hyperammonemia; Hyperinsulinism; Infant; Insulin; Insulin Secretion; Leucine; Male; Point Mutation; Syndrome

2001
Hyperinsulinism and hyperammonemia syndrome: report of twelve unrelated patients.
    Pediatric research, 2001, Volume: 50, Issue:3

    Topics: Adolescent; Blood Glucose; Child; Child, Preschool; Diet; Female; Glutamate Dehydrogenase; Guanosine Triphosphate; Humans; Hyperammonemia; Hyperinsulinism; Infant; Infant, Newborn; Leucine; Lymphocytes; Male; Syndrome

2001
Hypoglycemia: a perspective.
    Postgraduate medicine, 1975, Volume: 57, Issue:2

    Topics: Adenoma, Islet Cell; Citric Acid Cycle; Diabetes Complications; Diazoxide; Female; Glucose; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Liver; Liver Diseases; Middle Aged; Muscles; Pancreatic Neoplasms; Streptozocin; Tolbutamide

1975
[Hypoglycemia. 3. Hypoglycemias caused by defined metabolic defects; hormonal regulation of blood glucose concentration and its disorders].
    Fortschritte der Medizin, 1976, Feb-12, Volume: 94, Issue:5

    Topics: Fructose-1,6-Diphosphatase Deficiency; Galactose; Gluconeogenesis; Glucosephosphate Dehydrogenase Deficiency; Glycogen; Glycogen Storage Disease; Glycoside Hydrolases; Humans; Hyperinsulinism; Hypoglycemia; Hypothyroidism; Insulin; Lactates; Leucine; Parathyroid Hormone; Phosphorylases; Pyruvate Carboxylase Deficiency Disease

1976
Carbohydrate metabolism and insulin resistance in myotonia dystrophica.
    The Journal of clinical endocrinology and metabolism, 1977, Volume: 44, Issue:3

    Topics: Adult; Aged; Arginine; Blood Glucose; Carbohydrate Metabolism; Diabetes Mellitus; Female; Fructose; Galactose; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Insulin; Insulin Resistance; Insulin Secretion; Islets of Langerhans; Leucine; Male; Middle Aged; Myotonic Dystrophy; Sorbitol; Tolbutamide; Xylose

1977
[Leucine-sensitive hypoglycaemia and its treatment with diazoxide (author's transl)].
    Monatsschrift fur Kinderheilkunde, 1976, Volume: 129, Issue:9

    Topics: Amino Acid Metabolism, Inborn Errors; Blood Glucose; Diazoxide; Dietary Proteins; Female; Humans; Hyperinsulinism; Hypoglycemia; Infant; Insulin; Leucine; Prognosis; Seizures

1976
Insulin secretion by perfused islets from the obese Zucker rat.
    Proceedings of the Society for Experimental Biology and Medicine. Society for Experimental Biology and Medicine (New York, N.Y.), 1975, Volume: 149, Issue:2

    Topics: Animals; Glucose; Hyperinsulinism; In Vitro Techniques; Insulin; Insulin Secretion; Islets of Langerhans; Leucine; Male; Obesity; Perfusion; Rats; Stimulation, Chemical

1975
Plasma C-peptide and diagnosis of factitious hyperinsulinism. Study of an insulin-dependent diabetic patient with "spontaneous" hypoglycemia.
    Annals of internal medicine, 1975, Volume: 82, Issue:2

    Topics: Diabetes Mellitus; Diagnosis, Differential; Glucagon; Glucose; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Iodine Radioisotopes; Leucine; Male; Middle Aged; Peptides; Radioimmunoassay; Substance-Related Disorders; Tolbutamide

1975
[Diagnosis of organic hyperinsulinism].
    Anasthesiologische und intensivmedizinische Praxis, 1975, Volume: 10, Issue:1

    Topics: Diagnosis, Differential; Diazoxide; Fasting; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Radiography; Radionuclide Imaging; Tolbutamide

1975
Hypoglycemia and endogenous hyperinsulinism complicating diabetes mellitus. Application of the C-peptide assay to diagnosis and therapy.
    The American journal of medicine, 1975, Volume: 59, Issue:5

    Topics: Blood Glucose; Diabetes Complications; Diabetes Mellitus; Growth Hormone; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Male; Middle Aged; Pancreatectomy; Peptides; Tolbutamide

1975
Effect of hyperinsulinemia on whole body and skeletal muscle leucine carbon kinetics in humans.
    The American journal of physiology, 1992, Volume: 262, Issue:6 Pt 1

    Topics: Amino Acids; Bicarbonates; Carbon Radioisotopes; Female; Humans; Hyperinsulinism; Insulin; Kinetics; Leucine; Male; Middle Aged; Models, Biological; Muscles; Radioisotope Dilution Technique; Sodium; Sodium Bicarbonate

1992
Effect of hyperinsulinemia on ovine fetal leucine kinetics during prolonged maternal fasting.
    The American journal of physiology, 1992, Volume: 263, Issue:4 Pt 1

    Topics: Animals; Carbon; Fasting; Female; Fetus; Hyperinsulinism; Kinetics; Leucine; Maternal-Fetal Exchange; Nitrogen; Pregnancy; Pregnancy, Animal; Sheep; Time Factors

1992
Increased protein turnover in obese women.
    Metabolism: clinical and experimental, 1992, Volume: 41, Issue:9

    Topics: Abdomen; Adult; Body Mass Index; Body Weight; Female; Glucose Tolerance Test; Hip; Humans; Hyperglycemia; Hyperinsulinism; Insulin; Insulin Resistance; Leucine; Magnetic Resonance Imaging; Middle Aged; Obesity; Proteins

1992
Effect of systemic hyperinsulinemia in cancer patients.
    Cancer research, 1992, Jul-15, Volume: 52, Issue:14

    Topics: Body Weight; Female; Gastrointestinal Neoplasms; Glucose; Humans; Hyperinsulinism; Leucine; Lung Neoplasms; Male; Middle Aged; Proteins

1992
Differential effects of insulin resistance on leucine and glucose kinetics in obesity.
    Metabolism: clinical and experimental, 1991, Volume: 40, Issue:1

    Topics: Adult; Amino Acids, Branched-Chain; Blood Glucose; Carbon Isotopes; Female; Glucose; Humans; Hyperinsulinism; Insulin Resistance; Kinetics; Leucine; Obesity

1991
Euglycemic hyperinsulinemia augments amino acid uptake by human leg tissues during hyperaminoacidemia.
    The American journal of physiology, 1990, Volume: 259, Issue:2 Pt 1

    Topics: Adult; Amino Acids; Bicarbonates; Carbon Isotopes; Female; Glucose; Glucose Clamp Technique; Humans; Hyperinsulinism; Insulin; Kinetics; Leucine; Male; Muscles; Nitrogen Isotopes; Phenylalanine; Sodium; Sodium Bicarbonate

1990
Differential effects of hyperinsulinemia and hyperaminoacidemia on leucine-carbon metabolism in vivo. Evidence for distinct mechanisms in regulation of net amino acid deposition.
    The Journal of clinical investigation, 1987, Volume: 79, Issue:4

    Topics: Amino Acids; Blood Glucose; Carbon; Female; Glucagon; Humans; Hyperinsulinism; Insulin; Keto Acids; Kinetics; Leucine; Male

1987
Further studies on the amelioration of the characteristics of New Zealand Obese (NZO) mice following implantation of islets of Langerhans.
    Diabetologia, 1974, Volume: 10, Issue:5

    Topics: Animals; Blood Glucose; Body Weight; Cytological Techniques; Diffusion; Hyperglycemia; Hyperinsulinism; Insulin; Islets of Langerhans; Islets of Langerhans Transplantation; Leucine; Male; Mice; Mice, Inbred Strains; Micropore Filters; Obesity; Peritoneal Cavity; Proinsulin; Streptozocin; Time Factors; Transplantation, Homologous; Tritium

1974
Biochemical studies in a patient with hyperinsulinism.
    The New Zealand medical journal, 1966, Volume: 65, Issue:406

    Topics: Adenoma, Islet Cell; Adult; Female; Glucagon; Glucose Tolerance Test; Humans; Hydrocortisone; Hyperinsulinism; Hypoglycemia; Leucine; Pancreatic Neoplasms; Tolbutamide

1966
The diagnosis of insuloma.
    Acta medica Scandinavica, 1967, Volume: 181, Issue:3

    Topics: Adenoma, Islet Cell; Adult; Aged; Diagnosis, Differential; Fasting; Female; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Male; Middle Aged; Radiography; Tolbutamide

1967
[Current methods of study and morphologic findings in B-cell adenoma of the pancreas].
    Zentralblatt fur Chirurgie, 1967, Volume: 92, Issue:26a Pt 1

    Topics: Adenoma, Islet Cell; Adolescent; Blood Glucose; Diagnosis, Differential; Female; Glucose Tolerance Test; Humans; Hyperinsulinism; Leucine; Microscopy, Electron; Pancreas; Pancreatic Neoplasms; Tolbutamide

1967
Further studies on diazoxide suppression of insulin release from abnormal and normal islet tissue in man.
    Annals of the New York Academy of Sciences, 1968, Apr-11, Volume: 150, Issue:2

    Topics: Adenoma, Islet Cell; Arginine; Blood Glucose; Catecholamines; Depression, Chemical; Diazoxide; Female; Glucagon; Glucose; Humans; Hyperglycemia; Hyperinsulinism; Hypoglycemia; Insulin; Insulin Secretion; Islets of Langerhans; Leucine; Male; Tolbutamide; Trichlormethiazide

1968
Glucagon test for insulinoma: a chemical study in 25 cases.
    Journal of clinical pathology, 1968, Volume: 21, Issue:3

    Topics: Adenoma, Islet Cell; Adult; Blood Glucose; Diagnosis, Differential; Female; Glucagon; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Male; Middle Aged; Tolbutamide

1968
Islet cell tumor with hypoglycemia.
    American family physician, 1971, Volume: 3, Issue:3

    Topics: Adenoma, Islet Cell; Adolescent; Adult; Female; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Middle Aged; Pancreatectomy; Pancreatic Neoplasms; Radioimmunoassay; Tolbutamide

1971
Morphometric and ultrastructural studies in an infant with leucine-sensitive hypoglycemia, hyperinsulinism and islet hyperplasia.
    Diabetologia, 1974, Volume: 10, Issue:3

    Topics: Biopsy; Blood Glucose; Female; Histocytochemistry; Humans; Hyperinsulinism; Hypertrophy; Hypoglycemia; Infant, Newborn; Infant, Newborn, Diseases; Insulin; Islets of Langerhans; Leucine; Microscopy, Electron; Pancreas

1974
Metabolic aspects of the Beckwith-Wiedemann syndrome.
    The Journal of pediatrics, 1973, Volume: 82, Issue:2

    Topics: Abnormalities, Multiple; Adrenal Gland Diseases; Blood Glucose; Child, Preschool; Diazoxide; Epinephrine; Glucagon; Glucose; Glucose Tolerance Test; Growth Hormone; Hernia, Umbilical; Humans; Hydrocortisone; Hyperinsulinism; Hypoglycemia; Infant, Newborn; Infant, Newborn, Diseases; Insulin; Kidney Diseases; Leucine; Male; Tolbutamide; Tongue; Umbilicus

1973
Hyperinsulin response to oral leucine in obesity and acromegaly.
    The Journal of clinical endocrinology and metabolism, 1973, Volume: 37, Issue:3

    Topics: Acromegaly; Blood Glucose; Fatty Acids, Nonesterified; Glucose Tolerance Test; Growth Hormone; Humans; Hyperinsulinism; Insulin; Leucine; Male; Obesity

1973
[Hypoglycemia].
    Actualites de physiologie pathologique, 1973, Volume: 4

    Topics: Child; Dietary Carbohydrates; Epinephrine; Gastrointestinal Hormones; Glucagon; Gluconeogenesis; Glucose; Humans; Hyperglycemia; Hyperinsulinism; Hypoglycemia; Hypoglycemic Agents; Insulin; Intestinal Absorption; Leucine; Liver Glycogen; Pancreatic Neoplasms; Thyroid Hormones; Tolbutamide

1973
Plasma insulin in patients with myotonic dystrophy and their relatives.
    Medicine, 1974, Volume: 53, Issue:4

    Topics: Adolescent; Adult; Aged; Amino Acids; Antigens; Arginine; Child; Child, Preschool; Electromyography; Female; Glucagon; Glucose Tolerance Test; Heterozygote; Humans; Hyperinsulinism; Insulin; Leucine; Male; Middle Aged; Muscles; Myotonic Dystrophy; Tolbutamide

1974
[Childhood hypoglycemia with convulsions].
    Zeitschrift fur arztliche Fortbildung, 1974, Volume: 68, Issue:1

    Topics: Blood Glucose; Child, Preschool; Electroencephalography; Epinephrine; Fasting; Female; Glucagon; Humans; Hyperinsulinism; Hypoglycemia; Infant; Insulin; Leucine; Male; Prednisone; Seizures; Spasms, Infantile; Time Factors

1974
[Hypoglycemia induced by leucine. Study of a case].
    Revista do Hospital das Clinicas, 1971, Volume: 26, Issue:5

    Topics: Child, Preschool; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Male

1971
[Functional exploration of insulin secretion in sponteaneous hypoglycemia].
    Acta isotopica, 1967, Dec-15, Volume: 7, Issue:1

    Topics: Adenoma; Arginine; Glucagon; Glucose; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Insulin Secretion; Leucine; Pancreas; Pancreatic Neoplasms; Tolbutamide

1967
Stimulation of insulin secretion by amino acids.
    The Journal of clinical investigation, 1966, Volume: 45, Issue:9

    Topics: Adult; Amino Acids; Arginine; Blood Glucose; Fatty Acids; Female; Histidine; Humans; Hyperinsulinism; Insulin; Isoleucine; Leucine; Lysine; Male; Methionine; Phenylalanine; Threonine; Tryptophan; Valine

1966