leucine has been researched along with Compensatory Hyperinsulinemia in 86 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 41 (47.67) | 18.7374 |
1990's | 19 (22.09) | 18.2507 |
2000's | 16 (18.60) | 29.6817 |
2010's | 9 (10.47) | 24.3611 |
2020's | 1 (1.16) | 2.80 |
Authors | Studies |
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Du, JL; Lei, PP; Li, YH; Liu, K; Long, W; Ma, L; Qu, PF; Tang, X; Wang, YB; Wei, SJ; Xi, YM | 1 |
Klein, S; Mittendorfer, B; Okunade, AL; Porter, L; Ramaswamy, R; Reeds, DN; Smith, GI; van Vliet, S; Yoshino, J | 1 |
Chevalier, S; Gougeon, R; Labonte, CC; Marliss, EB; Morais, JA | 1 |
Kelly, A; Stanley, CA | 1 |
Crowley, VE; DeLong, C; Hand, E; Hatunic, M; Nolan, JJ; Stapleton, M | 1 |
Baiocchi, MR; Coracina, A; Kiwanuka, E; Millioni, R; Puricelli, L; Semplicini, A; Tessari, P; Vettore, M; Zaramella, M | 1 |
Atherton, P; Jaffery, H; Mittendorfer, B; Mohammed, BS; Rankin, D; Reeds, DN; Rennie, MJ; Smith, GI | 1 |
Castillo, L; Coss-Bu, J; Joosten, KF; Schierbeek, H; van Goudoever, JB; Verbruggen, SC | 1 |
Braun, S; Demmelmair, H; Hartl, WH; Jauch, KW; Koletzko, B; Kuppinger, D; Rittler, P; Vogeser, M | 1 |
Byrne, BJ; Cade, WT; Crowley, JR; Maisenbacher, M; O'Connor, R; Peterson, LR; Reeds, DN; Spencer, CT; Waggoner, AD | 1 |
Akcay, T; Chadefaux, B; Eaton, S; Ellard, S; Flanagan, SE; Heslegrave, AJ; Hussain, K; Kapoor, RR; Simsek, E | 1 |
Asmann, Y; Barazzoni, R; Coenen-Schimke, JM; Nair, KS; Robinson, MM; Short, KR | 1 |
Deger, SM; Egbert, P; Ellis, CD; Hung, AM; Ikizler, TA; Sha, F; Siew, ED; Sundell, MB | 1 |
Bôle-Feysot, C; Cailleux, AF; Claeyssens, S; Coëffier, M; Déchelotte, P; Donnadieu, N; Guérin, C; Lavoinne, A; Lecleire, S; Maurer, B | 1 |
GRUMBACH, MM; KAPLAN, SL | 1 |
GOLDNER, MG; WEISENFELD, S | 1 |
BOUMAN, PR | 1 |
CARNEVALI, R; POLI, E; RAINERI, P | 1 |
GRANN, V; MAHLER, RJ; PURDY, R | 1 |
BIELIK, E; GALIK, L; HRNCIAR, J; HRNCIAROVA, M | 1 |
BECKER, FO; CLARK, J; SCHWARTZ, TB | 1 |
CONN, JW; FAJANS, SS; FLOYD, JC; KNOPF, RF | 1 |
Agus, MS; Jaksic, T; Javid, PJ; Ryan, DP | 1 |
Murata, K; Ohie, T; Taketani, T; Toriumi, Y; Uchiyama, A; Yamaguchi, S | 1 |
Aalinkeel, R; Hill, DJ; Mitrani, P; Pandya, JD; Patel, MS; Song, F; Srinivasan, M; Strutt, B | 1 |
Chevalier, S; Gougeon, R; Lamarche, M; Marliss, EB; Morais, JA | 1 |
Hoe, FM; Simmons, RA; Stanley, CA; Steinkrauss, L; Thornton, PS; Wanner, LA | 1 |
Collins, HW; Daikhin, Y; Hsu, BY; Kelly, A; Kwagh, J; Lazarow, A; Li, C; MacMullen, C; Matschinsky, FM; Matter, A; Najafi, H; Nissim, I; Petty, TJ; Stanley, CA; Yudkoff, M | 1 |
Brown, LD; Hay, WW | 1 |
Chevalier, S; Gougeon, R; Marliss, EB; Morais, JA; Pereira, S | 1 |
Donnell, GN; Koch, R; Lieberman, E; Shaw, KN | 1 |
Besch, W; Wilke, B | 1 |
Bradvica, C; Golden, MP; Graham, MJ; Santiago, J; Sargeant, DT; White, NH; Zuniga, O | 1 |
de Geeter, B; Kurtz, F; Maertens, P; Messer, J; Raber, A; Willard, D | 1 |
Bayle, G; Berry, C; Bonnet, Y; Champredon, C; Charrier, S; Grizard, J; Obled, C; Prugnaud, J; Tauveron, I; Thiéblot, P | 1 |
Ang, BC; Halliday, D; Powell-Tuck, J | 1 |
Battezzati, A; Bianchi, E; Di Carlo, V; Luzi, L; Perseghin, G; Pozza, G; Terruzzi, I | 1 |
Biolo, G; Declan Fleming, RY; Wolfe, RR | 1 |
DeFronzo, RA; Luzi, L; Petrides, AS | 1 |
Beaufrere, B; Campbell, PJ; Gerich, JE; Gottesman, IS; Haymond, MW; Heiling, VJ; Tsalikian, E | 1 |
Battezzati, A; Bianchi, E; Ferrari, G; La Rocca, E; Luzi, L; Perseghin, G; Secchi, A; Spotti, D; Terruzzi, I; Vergani, S | 1 |
Brennan, MF; Heslin, MJ; Newman, E; Pisters, PW; Wolf, RF | 3 |
Donati, MA; Filippi, L; Novembre, E; Zammarchi, E | 1 |
Bolli, GB; Brunetti, P; Cruciani, G; De Feo, P; Lucidi, P; Monacchia, F; Reboldi, G; Volpi, E | 1 |
Beckett, PR; Copeland, KC; Davis, TA; Hardin, DS; Nguyen, HV; Wray-Cahen, D | 1 |
Bedford, D; Caslake, M; Malmström, R; Packard, CJ; Shepherd, J; Stewart, P; Taskinen, MR; Yki-Järvinen, H | 1 |
Bernard, C; Berthault, MF; Ktorza, A; Magnan, C; Pénicaud, L; Portha, B; Pralong, WF; Saulnier, C; Thibault, C | 1 |
Bayle, G; Benoit, P; Berry, C; Capitan, P; Champredon, C; Dejax, C; Fabricio, A; Grizard, J; Prugnaud, J; Rochon, C; Tauveron, I; Thieblot, P | 1 |
Ferry, RJ; Grimberg, A; Kelly, A; Koo-McCoy, S; Ng, D; Stanley, CA; Thornton, PS | 1 |
Aral, B; Benelli, C; De Lonlay, P; Dionisi-Vici, C; Fouque, F; Ganguly, A; Heinrichs, C; Kamoun, P; Rabier, D; Robert, JJ; Saudubray, JM; Stanley, C; Touati, G | 1 |
Bilz, S; Bloesch, D; Keller, U; Laager, R; Turkalj, I | 1 |
Berger, H | 1 |
Förster, H | 1 |
Hudson, AJ; Tevaarwerk, GJ | 1 |
Baker, L; Stanley, CA | 1 |
Reich, H; Schünke, W | 1 |
Eaton, RP; Schade, S | 1 |
Couropmitree, C; Freinkel, N; Hahnel, R; Horwitz, DL; Metzger, B; Nagel, TC; Rubenstein, AH | 1 |
Krämer, K; Sailer, FX | 1 |
Horwitz, DL; Kuzuya, H; Rubenstein, AH; Sandler, R | 1 |
Boyle, DW; Denne, SC; Liechty, EA; Liu, YM; Moorehead, H | 1 |
Amatruda, JM; Barnard, RR; Statt, M; Welle, S | 1 |
Caballero, B; Wurtman, RJ | 1 |
Bennet, WM; Connacher, AA; Jung, RT; Rennie, MJ; Scrimgeour, CM | 1 |
Biolo, G; Crepaldi, G; Fantin, G; Inchiostro, S; Iori, E; Marescotti, MC; Tessari, P; Tiengo, A; Trevisan, R | 1 |
Gates, RJ; Hunt, MI; Lazarus, NR | 1 |
Miles, LE | 1 |
Lundbaek, K; Lyngsoe, J; Madsen, B; Orskov, H; Yde, H | 1 |
Frawley, TF; Pensuwan, S | 1 |
Glöckner, E; Knoke, M; Markert, J; Reding, R | 1 |
Conn, JW; Fajans, SS; Floyd, JC; Harrison, TS; Knopf, RF; Thiffault, CA | 1 |
Marks, V; Samols, E | 1 |
Grinvalsky, HT; Remigio, PA | 1 |
Ishihara, Y; Kuroda, A; Sato, N; Tajima, Y; Wada, Y | 1 |
Altenähr, E; Freytag, G; Klöppel, G; Reichel, W; Willig, R | 1 |
Colle, E; Schiff, D; Stern, L; Wells, D | 1 |
Forsham, PH; Grodsky, GM; Johnson, S; Karam, JH; Levin, SR | 1 |
Duprey, J; Lubetzki, J | 1 |
Barbosa, J; Goetz, F; Kennedy, W; Nuttall, FQ | 1 |
Bannert, N; Fischer, HU; Schütze, I | 1 |
Wüstenberg, PW | 1 |
Barbieri, D; Marcondes, E; Quarentei, G; Setian, N | 1 |
Federspil, G; Frezzato, S; Macrì, C; Muggeo, M; Tiengo, A; Trisotto, A; Vianello, A | 1 |
Conn, JW; Fajans, SS; Floyd, JC; Knopf, RF; Rull, J | 1 |
6 review(s) available for leucine and Compensatory Hyperinsulinemia
Article | Year |
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[POSSIBILITIES AND LIMITATIONS IN THE DETERMINATION OF INSULIN IN BLOOD IN THE DIAGNOSIS OF HYPERINSULINISM].
Topics: Adenoma, Islet Cell; Blood; Diagnosis; Humans; Hyperglycemia; Hyperinsulinism; Insulin; Leucine; Pancreatic Neoplasms; Tolbutamide | 1963 |
[HYPERINSULINISM. DIAGNOSTIC AND THERAPEUTIC ASPECTS].
Topics: Diagnosis, Differential; Electrodiagnosis; Electroencephalography; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Pancreas; Sleep Wake Disorders; Surgical Procedures, Operative; Tolbutamide | 1964 |
Hyperinsulinism in infants and children: diagnosis and therapy.
Topics: Adult; Blood Glucose; Child; Child, Preschool; Diazoxide; Fatty Acids, Nonesterified; Humans; Hydroxybutyrates; Hyperinsulinism; Hypoglycemia; Infant; Infant, Newborn; Insulin; Leucine; Male; Pancreatectomy; Proinsulin | 1976 |
Hypoglycemia: tolbutamide and leucine tests in insulinoma.
Topics: Adenoma, Islet Cell; Blood Glucose; Fasting; Female; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Insulin Secretion; Leucine; Male; Middle Aged; Pancreatic Neoplasms; Tolbutamide | 1968 |
[Insulinoma].
Topics: Adenoma, Islet Cell; Adolescent; Adult; Aged; Angiography; Child; Diagnosis, Differential; Diagnostic Techniques, Surgical; Female; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Male; Middle Aged; Pancreatic Neoplasms; Proinsulin; Tolbutamide | 1973 |
[The hypoglycemia syndrome].
Topics: Alloxan; Angiography; Antibiotics, Antineoplastic; Blood Glucose; Diagnosis, Differential; Diazoxide; Diet Therapy; Epinephrine; Gastrointestinal Diseases; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Metabolic Diseases; Neoplasms; Pancreatic Neoplasms; Prednisone; Tolbutamide | 1970 |
10 trial(s) available for leucine and Compensatory Hyperinsulinemia
Article | Year |
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No major sex differences in muscle protein synthesis rates in the postabsorptive state and during hyperinsulinemia-hyperaminoacidemia in middle-aged adults.
Topics: Adult; Blood Glucose; Body Composition; Female; Glucose Clamp Technique; Humans; Hyperinsulinism; Infusions, Intravenous; Insulin; Kinetics; Leucine; Male; Muscle Proteins; Muscle, Skeletal; Phenylalanine; Phosphorylation; Protein Kinases; Proto-Oncogene Proteins c-akt; Ribosomal Protein S6 Kinases, 70-kDa; RNA; Sex Factors; Signal Transduction; TOR Serine-Threonine Kinases | 2009 |
Albumin synthesis rates in post-surgical infants and septic adolescents; influence of amino acids, energy, and insulin.
Topics: Adolescent; Albumins; Amino Acids; Blood Glucose; Critical Illness; Cross-Over Studies; Female; Glucose; Homeostasis; Humans; Hyperinsulinism; Infant; Insulin; Insulin Resistance; Intensive Care Units, Pediatric; Leucine; Male; Parenteral Nutrition, Total; Sepsis | 2011 |
Albumin synthesis rates are not responsive to hyperglycemic hyperinsulinemia in postoperative patients.
Topics: Abdomen; Aged; Carbon Isotopes; Case-Control Studies; Glucose; Humans; Hyperglycemia; Hyperinsulinism; Insulin; Leucine; Middle Aged; Postoperative Complications; Serum Albumin | 2011 |
Insulin fails to enhance mTOR phosphorylation, mitochondrial protein synthesis, and ATP production in human skeletal muscle without amino acid replacement.
Topics: Adenosine Triphosphate; Adult; Amino Acids; Carbon Isotopes; Female; Gene Expression Regulation; Humans; Hyperinsulinism; Infusions, Intravenous; Insulin; Insulin, Regular, Human; Leucine; Male; Mitochondria, Muscle; Mitochondrial Proteins; Muscle, Skeletal; Phosphorylation; Protein Processing, Post-Translational; Proto-Oncogene Proteins c-akt; RNA, Messenger; TOR Serine-Threonine Kinases; Young Adult | 2012 |
Enteral delivery of proteins stimulates protein synthesis in human duodenal mucosa in the fed state through a mammalian target of rapamycin-independent pathway.
Topics: Adult; Carbon Isotopes; Deuterium; Dietary Proteins; Duodenum; Enteral Nutrition; Extracellular Signal-Regulated MAP Kinases; Glutamine; Humans; Hyperinsulinism; Intestinal Mucosa; Leucine; Male; Phenylalanine; Phosphatidylinositol 3-Kinase; Phosphorylation; Postprandial Period; Protein Biosynthesis; Protein Processing, Post-Translational; TOR Serine-Threonine Kinases; Up-Regulation; Young Adult | 2013 |
Intravenous insulin decreases protein breakdown in infants on extracorporeal membrane oxygenation.
Topics: Blood Glucose; Cohort Studies; Cross-Over Studies; Extracorporeal Membrane Oxygenation; Female; Glucose; Humans; Hyperinsulinism; Infant; Infant, Newborn; Infant, Newborn, Diseases; Infusions, Intravenous; Insulin; Leucine; Male; Parenteral Nutrition, Total; Pilot Projects; Prospective Studies; Proteins; Treatment Outcome | 2004 |
The influence of sex on the protein anabolic response to insulin.
Topics: Adult; Carbon Isotopes; Dietary Proteins; Energy Metabolism; Female; Glucose; Humans; Hyperinsulinism; Hypoglycemic Agents; Insulin; Leucine; Male; Sex Characteristics; Tritium | 2005 |
Whole-body protein turnover in response to hyperinsulinemia in humans postabsorptively with [15N]glycine as tracer.
Topics: Adult; Ammonia; Blood Glucose; Carbon Isotopes; Cross-Over Studies; Female; Glucose Clamp Technique; Glycine; Humans; Hyperinsulinism; Insulin; Leucine; Male; Nitrogen Isotopes; Nutritional Status; Proteins; Urea | 1995 |
Physiologic hyperinsulinemia stimulates protein synthesis and enhances transport of selected amino acids in human skeletal muscle.
Topics: Adult; Alanine; Amino Acids; Biological Transport; Femoral Vein; Humans; Hyperinsulinism; Insulin; Kinetics; Leucine; Lysine; Male; Mathematics; Models, Biological; Muscle, Skeletal; Phenylalanine; Protein Biosynthesis; Reference Values | 1995 |
Effects of medium- and long-chain fatty acids on whole body leucine and glucose kinetics in man.
Topics: Adult; C-Peptide; Carbon Isotopes; Fatty Acids; Fatty Acids, Nonesterified; Glucagon; Glucose; Glucose Clamp Technique; Humans; Hyperinsulinism; Infusions, Intravenous; Insulin; Keto Acids; Lactic Acid; Leucine; Liver; Male; Oxidation-Reduction; Proteins; Reference Values; Triglycerides | 2002 |
70 other study(ies) available for leucine and Compensatory Hyperinsulinemia
Article | Year |
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Functional analysis of HADH c.99C>G shows that the variant causes the proliferation of pancreatic islets and leu-sensitive hyperinsulinaemia.
Topics: 3-Hydroxyacyl-CoA Dehydrogenase; Animals; Blood Glucose; Carboxymethylcellulose Sodium; Cell Proliferation; Glucagon; Glucose; Hyperinsulinism; Insulin; Islets of Langerhans; Leucine; Rats; Sodium | 2022 |
The muscle anabolic effect of protein ingestion during a hyperinsulinaemic euglycaemic clamp in middle-aged women is not caused by leucine alone.
Topics: Anabolic Agents; Eating; Female; Glucose; Glucose Clamp Technique; Humans; Hyperinsulinism; Insulin; Leucine; Middle Aged; Muscle Proteins; Signal Transduction; TOR Serine-Threonine Kinases | 2018 |
Effect of 10% dietary protein intake on whole body protein kinetics in type 2 diabetic adults.
Topics: Amino Acids; Blood Glucose; Body Mass Index; Body Weight; Diabetes Mellitus, Type 2; Diet, Protein-Restricted; Dietary Proteins; Energy Intake; Female; Glucose Clamp Technique; Humans; Hyperinsulinism; Insulin; Insulin Resistance; Leucine; Male; Mental Recall; Middle Aged; Obesity; Sex Factors; Waist Circumference | 2015 |
Neurological aspects in hyperinsulinism-hyperammonaemia syndrome.
Topics: Brain Damage, Chronic; Child; Dietary Proteins; Enzyme Activation; Glucose Transporter Type 1; Glutamate Dehydrogenase; Guanosine Triphosphate; Humans; Hyperammonemia; Hyperinsulinism; Hypoglycemia; Leucine; Liver; Mutation, Missense; Neurologic Examination; Pancreas | 2008 |
The Leu262Val polymorphism of presenilin associated rhomboid like protein (PARL) is associated with earlier onset of type 2 diabetes and increased urinary microalbumin creatinine ratio in an Irish case-control population.
Topics: Age of Onset; Albuminuria; Amino Acid Substitution; Animals; Case-Control Studies; Creatinine; Diabetes Mellitus, Type 2; Diabetic Angiopathies; Diabetic Nephropathies; Disease Models, Animal; Genetic Variation; Gerbillinae; Humans; Hyperinsulinism; Ireland; Leucine; Metalloproteases; Mitochondrial Proteins; Polymorphism, Single Nucleotide; Reference Values; Valine | 2009 |
Fibrinogen kinetics and protein turnover in hypertension: Effects of insulin.
Topics: Adult; Biomarkers; Blood Glucose; Case-Control Studies; Deuterium; Fibrinogen; Glucose; Glucose Clamp Technique; Humans; Hyperinsulinism; Hypertension; Indicator Dilution Techniques; Infusions, Intravenous; Insulin; Kinetics; Leucine; Male; Middle Aged; Peptide Hydrolases; Up-Regulation | 2009 |
Substrate metabolism during basal and hyperinsulinemic conditions in adolescents and young-adults with Barth syndrome.
Topics: Adolescent; Adult; Barth Syndrome; Blood Glucose; Body Composition; Echocardiography; Fatty Acids; Glucose; Humans; Hyperinsulinism; Insulin; Leucine; Lipid Metabolism; Lipolysis; Male; Mitochondria; Oxidation-Reduction; Young Adult | 2013 |
Leucine-sensitive hyperinsulinaemic hypoglycaemia in patients with loss of function mutations in 3-Hydroxyacyl-CoA Dehydrogenase.
Topics: 3-Hydroxyacyl CoA Dehydrogenases; Child; Child, Preschool; Female; Glutamate Dehydrogenase; Humans; Hyperinsulinism; Hypoglycemia; Immunoprecipitation; Infant; Insulin; Leucine; Male; Mutation | 2012 |
Insulin resistance and protein metabolism in chronic hemodialysis patients.
Topics: Adult; Aged; Amino Acids; Black or African American; Blood Glucose; Body Composition; Chromatography, High Pressure Liquid; Cross-Sectional Studies; Dose-Response Relationship, Drug; Female; Glucose Clamp Technique; Humans; Hyperinsulinism; Insulin; Insulin Resistance; Leucine; Male; Middle Aged; Proteins; Renal Dialysis; Sarcopenia; Sensitivity and Specificity | 2013 |
Amino acid and alpha-keto acid-induced hyperinsulinism in the leucine-sensitive type of infantile and childhood hypoglycemia.
Topics: Amino Acids; Child; Humans; Hyperinsulinism; Hypoglycemia; Infant; Keto Acids; Leucine; Seizures | 1960 |
Hyperinsulinemia in 1-leucine-sensitive hypoglycemia in an adult.
Topics: Adenoma, Islet Cell; Adult; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Medical Records; Pancreatic Neoplasms | 1961 |
[HYPOGLYCEMIC REACTION TO LEUCINE, VALINE AND PHENYLALANINE IN A CASE OF DIFFUSE HYPERPLASIA OF THE BETA CELLS].
Topics: Glucose Tolerance Test; Humans; Hyperinsulinism; Hyperplasia; Hypoglycemia; Hypoglycemic Agents; Insulin-Secreting Cells; Islands; Islets of Langerhans; Leucine; Pathology; Pharmacology; Phenylalanine; Tolbutamide; Valine | 1963 |
FUNCTIONING ISLET CELL ADENOMA.
Topics: Adenoma, Islet Cell; Cerebrovascular Disorders; Diagnosis, Differential; Geriatrics; Humans; Hyperinsulinism; Leucine; Pancreatic Neoplasms; Tolbutamide | 1964 |
L-LEUCINE SENSITIVITY AND GLUCOSE TOLERANCE IN NORMAL SUBJECTS.
Topics: Blood Glucose; Carbohydrate Metabolism; Diabetes Mellitus; Diagnosis; Glucose Tolerance Test; Humans; Hyperinsulinism; Leucine | 1964 |
PLASMA INSULIN IN ORGANIC HYPERINSULINISM: COMPARATIVE EFFECTS OF TOLBUTAMIDE, LEUCINE AND GLUCOSE.
Topics: Adenoma, Islet Cell; Blood; Blood Chemical Analysis; Blood Glucose; Glucagon; Glucose; Humans; Hyperglycemia; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Pancreatic Neoplasms; Pharmacology; Surgical Procedures, Operative; Tolbutamide | 1964 |
A case of hyperinsulinism/hyperammonaemia syndrome: usefulness of the oral protein tolerance for the evaluation of treatment.
Topics: Child; Exons; Female; Glutamate Dehydrogenase; Humans; Hyperammonemia; Hyperinsulinism; Hypoglycemia; Leucine; Mutation; Syndrome | 2005 |
Maternal hyperinsulinemia predisposes rat fetuses for hyperinsulinemia, and adult-onset obesity and maternal mild food restriction reverses this phenotype.
Topics: Animals; Animals, Newborn; Arginine; Basic Helix-Loop-Helix Transcription Factors; Blood Glucose; Body Weight; Diet; Dietary Carbohydrates; Female; Fetus; Gene Expression; Glucose; Hepatocyte Nuclear Factor 3-beta; Homeodomain Proteins; Hyperinsulinism; Insulin; Islets of Langerhans; Leucine; Lipids; Male; Obesity; Pregnancy; Prenatal Exposure Delayed Effects; Proinsulin; Protein Precursors; Rats; Rats, Sprague-Dawley; RNA, Messenger; Trans-Activators | 2006 |
Clinical features and insulin regulation in infants with a syndrome of prolonged neonatal hyperinsulinism.
Topics: Antihypertensive Agents; Calcium; Case-Control Studies; Diazoxide; Enteral Nutrition; Fasting; Female; Glucose; Humans; Hyperinsulinism; Hypoglycemia; Hypoglycemic Agents; Infant; Infant, Newborn; Infusions, Intravenous; Insulin; Insulin Secretion; Leucine; Male; Prospective Studies; Risk Factors; Sweetening Agents; Tolbutamide | 2006 |
Effects of a GTP-insensitive mutation of glutamate dehydrogenase on insulin secretion in transgenic mice.
Topics: Adenosine Diphosphate; Adenosine Triphosphate; Animals; Calcium Signaling; Glucose; Glutamate Dehydrogenase; Glutamine; Guanosine Triphosphate; Humans; Hyperinsulinism; In Vitro Techniques; Insulin; Insulin Secretion; Islets of Langerhans; Kinetics; Leucine; Mice; Mice, Inbred C57BL; Mice, Transgenic; Models, Biological; Mutation; Recombinant Proteins | 2006 |
Effect of hyperinsulinemia on amino acid utilization and oxidation independent of glucose metabolism in the ovine fetus.
Topics: Algorithms; Amino Acids; Amino Acids, Branched-Chain; Animals; Blood Gas Analysis; Blood Glucose; Female; Fetus; Glucose; Hyperinsulinism; Insulin; Kinetics; Lactic Acid; Leucine; Oxidation-Reduction; Pregnancy; Sheep | 2006 |
Insulin resistance of protein metabolism in type 2 diabetes.
Topics: Adult; Amino Acids; Blood Chemical Analysis; Body Mass Index; Diabetes Mellitus, Type 2; Female; Follicular Phase; Glucose Clamp Technique; Humans; Hyperinsulinism; Insulin; Insulin Resistance; Leucine; Male; Middle Aged; Proteins; Reference Values | 2008 |
Hypoglycemia in maple syrup urine disease.
Topics: Animals; Caseins; Female; Gluconeogenesis; Glucose; Glucose Tolerance Test; Glycogen; Humans; Hyperinsulinism; Hypoglycemia; In Vitro Techniques; Infant; Leucine; Male; Maple Syrup Urine Disease; Rats | 1967 |
Characterization of beta-cell specific function of isolated pancreatic islets from hyperglycemic C57BL/KsJ-db/db mice.
Topics: Animals; Blood Glucose; Cells, Cultured; Hyperglycemia; Hyperinsulinism; Insulin; Islets of Langerhans; Leucine; Male; Mice; Mice, Inbred C57BL; Mice, Inbred Strains; Proinsulin; Protein Precursors | 1982 |
Persistent leucine sensitivity following partial pancreatectomy and diazoxide treatment. Therapeutic response.
Topics: Child, Preschool; Diazoxide; Female; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Pancreatectomy; Pancreatic Diseases; Seizures | 1983 |
[Long-term diazoxide therapy in recurrent leucine-sensitive hypoglycemia (author's transl)].
Topics: Child, Preschool; Diazoxide; Female; Growth; Humans; Hyperinsulinism; Hypoglycemia; Infant; Infant, Newborn; Leucine | 1980 |
Response of leucine metabolism to hyperinsulinemia under amino acid replacement in experimental hyperthyroidism.
Topics: Adult; Amino Acids; Blood Glucose; Carbon Dioxide; Humans; Hyperinsulinism; Hyperthyroidism; Insulin; Keto Acids; Kinetics; Leucine; Male; Reference Values; Respiration | 1995 |
Defective insulin action on protein and glucose metabolism during chronic hyperinsulinemia in subjects with benign insulinoma.
Topics: Adult; Blood Glucose; Carbon Radioisotopes; Chronic Disease; Glucose; Glucose Clamp Technique; Humans; Hyperinsulinism; Insulin; Insulinoma; Keto Acids; Leucine; Liver; Middle Aged; Pancreatic Neoplasms; Proteins; Radioisotope Dilution Technique; Reference Values; Tritium | 1995 |
Time-dependent regulation by insulin of leucine metabolism in young healthy adults.
Topics: Adolescent; Adult; Amino Acids; Blood Glucose; Calorimetry, Indirect; Female; Glucagon; Humans; Hyperinsulinism; Insulin; Keto Acids; Leucine; Male; Osmolar Concentration; Oxidation-Reduction; Reference Values; Time Factors | 1994 |
Differential effects of hyperglycemia and hyperinsulinemia on leucine rate of appearance in normal humans.
Topics: Adult; Blood Glucose; Female; Glucagon; Glucose Clamp Technique; Humans; Hyperglycemia; Hyperinsulinism; Insulin; Insulin Infusion Systems; Leucine; Male; Middle Aged; Reference Values; Somatostatin | 1993 |
Combined pancreas and kidney transplantation normalizes protein metabolism in insulin-dependent diabetic-uremic patients.
Topics: Adult; Blood Glucose; Diabetes Mellitus, Type 1; Female; Hemoglobins; Hormones; Humans; Hyperinsulinism; Immunosuppression Therapy; Keto Acids; Kidney Failure, Chronic; Kidney Transplantation; Leucine; Male; Nitrogen; Oxidation-Reduction; Pancreas Transplantation; Proteins; Uremia; Uveitis, Posterior | 1994 |
The effect of systemic hyperinsulinemia with concomitant amino acid infusion on skeletal muscle protein turnover in the human forearm.
Topics: Adult; Aged; Amino Acids; Amino Acids, Branched-Chain; Blood Glucose; Carbon Radioisotopes; Chromatography, High Pressure Liquid; Female; Forearm; Glucagon; Humans; Hyperinsulinism; Insulin; Leucine; Male; Middle Aged; Muscle Proteins; Muscles; Phenylalanine; Time Factors; Tritium | 1994 |
Biochemical evaluation of a patient with a familial form of leucine-sensitive hypoglycemia and concomitant hyperammonemia.
Topics: Adult; Ammonia; Drug Resistance; Female; Glutamates; Humans; Hyperinsulinism; Hypoglycemia; Infant; Leucine; Male | 1996 |
Contribution of amino acids and insulin to protein anabolism during meal absorption.
Topics: Administration, Oral; Adult; Amino Acids; Antithrombin III; Blood Glucose; C-Peptide; Carbon Radioisotopes; Eating; Fatty Acids, Nonesterified; Female; Fibrinogen; Glucagon; Glucose; Humans; Hyperinsulinism; Immunoglobulin G; Insulin; Intestinal Absorption; Keto Acids; Kinetics; Leucine; Lipid Metabolism; Lipids; Male; Protein Biosynthesis; Proteins; Radioisotope Dilution Technique; Serum Albumin | 1996 |
Spectrophometric assay for measuring branched-chain amino acid concentrations: application for measuring the sensitivity of protein metabolism to insulin.
Topics: Amino Acid Oxidoreductases; Amino Acids, Branched-Chain; Blood Proteins; Chromatography, High Pressure Liquid; Enzyme Stability; Humans; Hyperinsulinism; Insulin; Isoleucine; Kinetics; Leucine; Leucine Dehydrogenase; NAD; Spectrophotometry; Valine | 1996 |
Defective regulation of triglyceride metabolism by insulin in the liver in NIDDM.
Topics: Apolipoproteins B; Cholesterol; Cholesterol, HDL; Deuterium; Diabetes Mellitus, Type 2; Fatty Acids, Nonesterified; Glucose Clamp Technique; Humans; Hyperglycemia; Hyperinsulinism; Infusions, Intravenous; Insulin; Leucine; Lipoproteins, VLDL; Liver; Male; Middle Aged; Models, Biological; Radioisotope Dilution Technique; Reference Values; Triglycerides | 1997 |
Pancreatic beta-cell regeneration after 48-h glucose infusion in mildly diabetic rats is not correlated with functional improvement.
Topics: Animals; Arginine; Blood Glucose; Diabetes Mellitus, Experimental; Glucose; Hyperglycemia; Hyperinsulinism; Immunoenzyme Techniques; In Vitro Techniques; Insulin; Insulin Secretion; Islets of Langerhans; Leucine; Male; Rats; Rats, Wistar; Regeneration | 1998 |
Response of leucine metabolism to hyperinsulinemia in hypothyroid patients before and after thyroxine replacement.
Topics: Adult; Amino Acids; Blood Glucose; Carbon Dioxide; Humans; Hyperinsulinism; Hypothyroidism; Insulin; Keto Acids; Leucine; Middle Aged; Respiration | 2000 |
Acute insulin responses to leucine in children with the hyperinsulinism/hyperammonemia syndrome.
Topics: Adolescent; Adult; Amino Acid Substitution; Ammonia; Blood Glucose; Child; Child, Preschool; Diazoxide; Female; Glutamate Dehydrogenase; Humans; Hyperammonemia; Hyperinsulinism; Infant; Insulin; Insulin Secretion; Leucine; Male; Point Mutation; Syndrome | 2001 |
Hyperinsulinism and hyperammonemia syndrome: report of twelve unrelated patients.
Topics: Adolescent; Blood Glucose; Child; Child, Preschool; Diet; Female; Glutamate Dehydrogenase; Guanosine Triphosphate; Humans; Hyperammonemia; Hyperinsulinism; Infant; Infant, Newborn; Leucine; Lymphocytes; Male; Syndrome | 2001 |
Hypoglycemia: a perspective.
Topics: Adenoma, Islet Cell; Citric Acid Cycle; Diabetes Complications; Diazoxide; Female; Glucose; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Liver; Liver Diseases; Middle Aged; Muscles; Pancreatic Neoplasms; Streptozocin; Tolbutamide | 1975 |
[Hypoglycemia. 3. Hypoglycemias caused by defined metabolic defects; hormonal regulation of blood glucose concentration and its disorders].
Topics: Fructose-1,6-Diphosphatase Deficiency; Galactose; Gluconeogenesis; Glucosephosphate Dehydrogenase Deficiency; Glycogen; Glycogen Storage Disease; Glycoside Hydrolases; Humans; Hyperinsulinism; Hypoglycemia; Hypothyroidism; Insulin; Lactates; Leucine; Parathyroid Hormone; Phosphorylases; Pyruvate Carboxylase Deficiency Disease | 1976 |
Carbohydrate metabolism and insulin resistance in myotonia dystrophica.
Topics: Adult; Aged; Arginine; Blood Glucose; Carbohydrate Metabolism; Diabetes Mellitus; Female; Fructose; Galactose; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Insulin; Insulin Resistance; Insulin Secretion; Islets of Langerhans; Leucine; Male; Middle Aged; Myotonic Dystrophy; Sorbitol; Tolbutamide; Xylose | 1977 |
[Leucine-sensitive hypoglycaemia and its treatment with diazoxide (author's transl)].
Topics: Amino Acid Metabolism, Inborn Errors; Blood Glucose; Diazoxide; Dietary Proteins; Female; Humans; Hyperinsulinism; Hypoglycemia; Infant; Insulin; Leucine; Prognosis; Seizures | 1976 |
Insulin secretion by perfused islets from the obese Zucker rat.
Topics: Animals; Glucose; Hyperinsulinism; In Vitro Techniques; Insulin; Insulin Secretion; Islets of Langerhans; Leucine; Male; Obesity; Perfusion; Rats; Stimulation, Chemical | 1975 |
Plasma C-peptide and diagnosis of factitious hyperinsulinism. Study of an insulin-dependent diabetic patient with "spontaneous" hypoglycemia.
Topics: Diabetes Mellitus; Diagnosis, Differential; Glucagon; Glucose; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Iodine Radioisotopes; Leucine; Male; Middle Aged; Peptides; Radioimmunoassay; Substance-Related Disorders; Tolbutamide | 1975 |
[Diagnosis of organic hyperinsulinism].
Topics: Diagnosis, Differential; Diazoxide; Fasting; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Radiography; Radionuclide Imaging; Tolbutamide | 1975 |
Hypoglycemia and endogenous hyperinsulinism complicating diabetes mellitus. Application of the C-peptide assay to diagnosis and therapy.
Topics: Blood Glucose; Diabetes Complications; Diabetes Mellitus; Growth Hormone; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Male; Middle Aged; Pancreatectomy; Peptides; Tolbutamide | 1975 |
Effect of hyperinsulinemia on whole body and skeletal muscle leucine carbon kinetics in humans.
Topics: Amino Acids; Bicarbonates; Carbon Radioisotopes; Female; Humans; Hyperinsulinism; Insulin; Kinetics; Leucine; Male; Middle Aged; Models, Biological; Muscles; Radioisotope Dilution Technique; Sodium; Sodium Bicarbonate | 1992 |
Effect of hyperinsulinemia on ovine fetal leucine kinetics during prolonged maternal fasting.
Topics: Animals; Carbon; Fasting; Female; Fetus; Hyperinsulinism; Kinetics; Leucine; Maternal-Fetal Exchange; Nitrogen; Pregnancy; Pregnancy, Animal; Sheep; Time Factors | 1992 |
Increased protein turnover in obese women.
Topics: Abdomen; Adult; Body Mass Index; Body Weight; Female; Glucose Tolerance Test; Hip; Humans; Hyperglycemia; Hyperinsulinism; Insulin; Insulin Resistance; Leucine; Magnetic Resonance Imaging; Middle Aged; Obesity; Proteins | 1992 |
Effect of systemic hyperinsulinemia in cancer patients.
Topics: Body Weight; Female; Gastrointestinal Neoplasms; Glucose; Humans; Hyperinsulinism; Leucine; Lung Neoplasms; Male; Middle Aged; Proteins | 1992 |
Differential effects of insulin resistance on leucine and glucose kinetics in obesity.
Topics: Adult; Amino Acids, Branched-Chain; Blood Glucose; Carbon Isotopes; Female; Glucose; Humans; Hyperinsulinism; Insulin Resistance; Kinetics; Leucine; Obesity | 1991 |
Euglycemic hyperinsulinemia augments amino acid uptake by human leg tissues during hyperaminoacidemia.
Topics: Adult; Amino Acids; Bicarbonates; Carbon Isotopes; Female; Glucose; Glucose Clamp Technique; Humans; Hyperinsulinism; Insulin; Kinetics; Leucine; Male; Muscles; Nitrogen Isotopes; Phenylalanine; Sodium; Sodium Bicarbonate | 1990 |
Differential effects of hyperinsulinemia and hyperaminoacidemia on leucine-carbon metabolism in vivo. Evidence for distinct mechanisms in regulation of net amino acid deposition.
Topics: Amino Acids; Blood Glucose; Carbon; Female; Glucagon; Humans; Hyperinsulinism; Insulin; Keto Acids; Kinetics; Leucine; Male | 1987 |
Further studies on the amelioration of the characteristics of New Zealand Obese (NZO) mice following implantation of islets of Langerhans.
Topics: Animals; Blood Glucose; Body Weight; Cytological Techniques; Diffusion; Hyperglycemia; Hyperinsulinism; Insulin; Islets of Langerhans; Islets of Langerhans Transplantation; Leucine; Male; Mice; Mice, Inbred Strains; Micropore Filters; Obesity; Peritoneal Cavity; Proinsulin; Streptozocin; Time Factors; Transplantation, Homologous; Tritium | 1974 |
Biochemical studies in a patient with hyperinsulinism.
Topics: Adenoma, Islet Cell; Adult; Female; Glucagon; Glucose Tolerance Test; Humans; Hydrocortisone; Hyperinsulinism; Hypoglycemia; Leucine; Pancreatic Neoplasms; Tolbutamide | 1966 |
The diagnosis of insuloma.
Topics: Adenoma, Islet Cell; Adult; Aged; Diagnosis, Differential; Fasting; Female; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Male; Middle Aged; Radiography; Tolbutamide | 1967 |
[Current methods of study and morphologic findings in B-cell adenoma of the pancreas].
Topics: Adenoma, Islet Cell; Adolescent; Blood Glucose; Diagnosis, Differential; Female; Glucose Tolerance Test; Humans; Hyperinsulinism; Leucine; Microscopy, Electron; Pancreas; Pancreatic Neoplasms; Tolbutamide | 1967 |
Further studies on diazoxide suppression of insulin release from abnormal and normal islet tissue in man.
Topics: Adenoma, Islet Cell; Arginine; Blood Glucose; Catecholamines; Depression, Chemical; Diazoxide; Female; Glucagon; Glucose; Humans; Hyperglycemia; Hyperinsulinism; Hypoglycemia; Insulin; Insulin Secretion; Islets of Langerhans; Leucine; Male; Tolbutamide; Trichlormethiazide | 1968 |
Glucagon test for insulinoma: a chemical study in 25 cases.
Topics: Adenoma, Islet Cell; Adult; Blood Glucose; Diagnosis, Differential; Female; Glucagon; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Male; Middle Aged; Tolbutamide | 1968 |
Islet cell tumor with hypoglycemia.
Topics: Adenoma, Islet Cell; Adolescent; Adult; Female; Glucagon; Glucose Tolerance Test; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Leucine; Middle Aged; Pancreatectomy; Pancreatic Neoplasms; Radioimmunoassay; Tolbutamide | 1971 |
Morphometric and ultrastructural studies in an infant with leucine-sensitive hypoglycemia, hyperinsulinism and islet hyperplasia.
Topics: Biopsy; Blood Glucose; Female; Histocytochemistry; Humans; Hyperinsulinism; Hypertrophy; Hypoglycemia; Infant, Newborn; Infant, Newborn, Diseases; Insulin; Islets of Langerhans; Leucine; Microscopy, Electron; Pancreas | 1974 |
Metabolic aspects of the Beckwith-Wiedemann syndrome.
Topics: Abnormalities, Multiple; Adrenal Gland Diseases; Blood Glucose; Child, Preschool; Diazoxide; Epinephrine; Glucagon; Glucose; Glucose Tolerance Test; Growth Hormone; Hernia, Umbilical; Humans; Hydrocortisone; Hyperinsulinism; Hypoglycemia; Infant, Newborn; Infant, Newborn, Diseases; Insulin; Kidney Diseases; Leucine; Male; Tolbutamide; Tongue; Umbilicus | 1973 |
Hyperinsulin response to oral leucine in obesity and acromegaly.
Topics: Acromegaly; Blood Glucose; Fatty Acids, Nonesterified; Glucose Tolerance Test; Growth Hormone; Humans; Hyperinsulinism; Insulin; Leucine; Male; Obesity | 1973 |
[Hypoglycemia].
Topics: Child; Dietary Carbohydrates; Epinephrine; Gastrointestinal Hormones; Glucagon; Gluconeogenesis; Glucose; Humans; Hyperglycemia; Hyperinsulinism; Hypoglycemia; Hypoglycemic Agents; Insulin; Intestinal Absorption; Leucine; Liver Glycogen; Pancreatic Neoplasms; Thyroid Hormones; Tolbutamide | 1973 |
Plasma insulin in patients with myotonic dystrophy and their relatives.
Topics: Adolescent; Adult; Aged; Amino Acids; Antigens; Arginine; Child; Child, Preschool; Electromyography; Female; Glucagon; Glucose Tolerance Test; Heterozygote; Humans; Hyperinsulinism; Insulin; Leucine; Male; Middle Aged; Muscles; Myotonic Dystrophy; Tolbutamide | 1974 |
[Childhood hypoglycemia with convulsions].
Topics: Blood Glucose; Child, Preschool; Electroencephalography; Epinephrine; Fasting; Female; Glucagon; Humans; Hyperinsulinism; Hypoglycemia; Infant; Insulin; Leucine; Male; Prednisone; Seizures; Spasms, Infantile; Time Factors | 1974 |
[Hypoglycemia induced by leucine. Study of a case].
Topics: Child, Preschool; Humans; Hyperinsulinism; Hypoglycemia; Leucine; Male | 1971 |
[Functional exploration of insulin secretion in sponteaneous hypoglycemia].
Topics: Adenoma; Arginine; Glucagon; Glucose; Humans; Hyperinsulinism; Hypoglycemia; Insulin; Insulin Secretion; Leucine; Pancreas; Pancreatic Neoplasms; Tolbutamide | 1967 |
Stimulation of insulin secretion by amino acids.
Topics: Adult; Amino Acids; Arginine; Blood Glucose; Fatty Acids; Female; Histidine; Humans; Hyperinsulinism; Insulin; Isoleucine; Leucine; Lysine; Male; Methionine; Phenylalanine; Threonine; Tryptophan; Valine | 1966 |