leucine and Acidosis

leucine has been researched along with Acidosis in 64 studies

Research

Studies (64)

Timeframe	Studies, this research(%)	All Research%
pre-1990	41 (64.06)	18.7374
1990's	11 (17.19)	18.2507
2000's	8 (12.50)	29.6817
2010's	4 (6.25)	24.3611
2020's	0 (0.00)	2.80

Authors

Authors	Studies
Cowan, TM; Cusmano-Ozog, K; Enns, GM; Scott, AI	1
Chen, Y; McIntire, K; Rabkin, R; Sood, S	1
Coker, M; Duran, M; Habif, S; Kalkan Ucar, S; Karapinar, B; Kitis, O; Saz, EU; Ucar, H	1
Appell, M; Bross, R; Kopple, JD; Mehrotra, R; Tso, L; Wang, H	1
Garibotto, G; Millioni, R; Puricelli, L; Saffioti, S; Sofia, A; Tessari, P; Verzola, D; Vettore, M	1
Burke, LM; Coffey, VG; Garnham, AP; Hawley, JA; Moore, DR; Phillips, SM; Ross, ML; Slater, GR; Stellingwerff, T; Tipton, KD	1
CHILDS, B; NYHAN, WL	1
BUSE, J; BUSE, MG; KRECH, LH; MCMASTER, J	1
Chládek, J; Holecek, M; Kadlcíková, J; Kukan, M; Mislanová, C; Safránek, R; Sprongl, L	1
Holecek, M; Kadlcíková, J; Rysavá, R; Safránek, R; Sprongl, L	1
Deferrari, G; Garibotto, G; Procopio, V; Robaudo, C; Russo, R; Saffioti, S; Sala, MR; Sofia, A; Tessari, P; Verzola, D; Vettore, M	1
Astruc, J; Bellet, H; Brunel, D; Froye, E; Luciani, JM; Magnan de Bornier, P	1
Efron, ML	1
Edelmann, CM; Finberg, L; Soriano, JR; Taitz, LS	1
Isselbacher, KJ; Tanaka, K	1
French, NP; Grauaug, A; Wysocki, SJ	1
Bartlett, K; Clayton, B; Hyde, J; Leonard, JV; Seakins, JW; Wilson, J	1
Channon, SM; Goodship, TH; Graham, KA; Hetherington, C; Reaich, D; Scrimgeour, CM; Wilkinson, R	1
Channon, SM; Downie, S; Gilmour, E; Goodship, TH; Graham, KA; Passlick-Deetjen, J; Reaich, D	1
Thompson, JR; Zhou, X	1
Milley, JR	1
Anderstam, B; Bergström, J; Löfberg, E; Wernerman, J	1
Ballmer, PE	1
Flanigan, MJ; Lim, VS; Yarasheski, KE	1
Channon, SM; Downie, S; Goodship, TH; Graham, KA; Reaich, D	1
Boirie, Y; Bresson, JL; Broyer, M; Gagnadoux, MF; Niaudet, P	1
Holecek, M; Sprongl, L; Tichý, M; Tilser, I	1
Bevington, A; Brown, J; Walls, J	1
Landaas, S	1
Ballard, FJ; Hanson, RW; Iynedjian, PB	1
Porath, U; Schreier, K	1
Genel, M; Mantagos, S; Tanaka, K	1
Cohn, RM; Puschak, R; Rothman, R; Segal, S; Yudkoff, M	1
Hähnel, R; Panegyres, PK; Wilkinson, SP; Wong, CY; Wysocki, SJ	1
Collombel, C; Cotton, JB; Divry, P; Guibaud, P; Larbre, F; Marcon, G	1
Grüttner, R; Held, KR; Plettner, C; Singh, S; Sternowsky, HJ	1
Channon, SM; Goodship, TH; Reaich, D; Scrimgeour, CM	1
Bailey, J; England, BK; Logue, B; Masud, T; May, RC	1
Arnaud, MJ; Bloesch, D; Keller, U; Küry, D; Stauffacher, W; Straumann, E; Thélin, A	1
Buchanan, D; Dasouki, M; Gibson, KM; Mercer, N; Thoene, J	1
Haymond, MW; Miles, JM; Rodriguez, NR; Schwenk, WF	1
Hähnel, R; Wysocki, SJ	1
Askari, A; Birkhahn, RH; Thomford, NR	1
Hara, Y; Kelly, RA; May, RC; Mitch, WE	1
Kelly, RA; May, RC; Mitch, WE	1
Draffan, GH; Gompertz, D; Hull, D; Watts, JL	1
Callaghan, P; Newman, CG; Wilson, BD; Young, L	1
Blum, KU	1
Grumbach, MM; Kaplan, SL; Schotland, MG	1
Ito, T; Kikuchi, T; Kumagaya, M; Matsuo, N; Tsuchiya, H	1
Baird, GD; Heitzman, RJ; Hibbitt, KG	1
Budd, MA; Crawford, JD; Efron, ML; Holmes, LB; Isselbacher, KJ; Tanaka, K	1
Chaussain, JL; Georges, P; Job, JC; Olive, G	1
Host, WR; Rush, BF; Serlin, O	1
Mandell, R; Shih, VE; Tanaka, K	1
Thorell, JI; Victorin, LH	1
Chang, AY; Schneider, DI	1
Erickson, AM; Levy, HL; Lott, IT	1
Budd, MA; Efron, ML; Isselbacher, KJ; Tanaka, K	1
Isselbacher, KJ; Miller, EM; Tanaka, K	1
Collombel, C; Guerrier, G; Guibaud, P; Hartemann, E; Larbre, F	1
Hsia, YE; Lilljeqvist, AC; Rosenberg, LE	1
Pitts, RF	1
Bignall, MC; Elebute, O; Lotspeich, WD	1

Reviews

1 review(s) available for leucine and Acidosis

Article	Year
[Congenital metabolic acidosis in the postnatal period]. Deutsche medizinische Wochenschrift (1946), 1978, Jun-02, Volume: 103, Issue:22 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine	1978

Article

Year

[Congenital metabolic acidosis in the postnatal period].

Deutsche medizinische Wochenschrift (1946), 1978, Jun-02, Volume: 103, Issue:22

Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine

1978

Trials

2 trial(s) available for leucine and Acidosis

Article	Year
Effect of high-normal compared with low-normal arterial pH on protein balances in automated peritoneal dialysis patients. The American journal of clinical nutrition, 2009, Volume: 90, Issue:6 Topics: Acidosis; Adult; Aged; Arteries; Cross-Over Studies; Female; Humans; Hydrogen-Ion Concentration; Kidney Failure, Chronic; Leucine; Male; Middle Aged; Muscle, Skeletal; Nitrogen; Peritoneal Dialysis; Proteins	2009
Preexercise aminoacidemia and muscle protein synthesis after resistance exercise. Medicine and science in sports and exercise, 2012, Volume: 44, Issue:10 Topics: Acidosis; Adult; Amino Acids; Humans; Leg; Leucine; Male; Milk Proteins; Muscle Proteins; Muscle, Skeletal; Phosphorylation; Resistance Training; Ribosomal Protein S6 Kinases, 70-kDa; Serine; Sweetening Agents; Threonine; Whey Proteins	2012

Article

Year

Effect of high-normal compared with low-normal arterial pH on protein balances in automated peritoneal dialysis patients.

The American journal of clinical nutrition, 2009, Volume: 90, Issue:6

Topics: Acidosis; Adult; Aged; Arteries; Cross-Over Studies; Female; Humans; Hydrogen-Ion Concentration; Kidney Failure, Chronic; Leucine; Male; Middle Aged; Muscle, Skeletal; Nitrogen; Peritoneal Dialysis; Proteins

2009

Preexercise aminoacidemia and muscle protein synthesis after resistance exercise.

Medicine and science in sports and exercise, 2012, Volume: 44, Issue:10

Topics: Acidosis; Adult; Amino Acids; Humans; Leg; Leucine; Male; Milk Proteins; Muscle Proteins; Muscle, Skeletal; Phosphorylation; Resistance Training; Ribosomal Protein S6 Kinases, 70-kDa; Serine; Sweetening Agents; Threonine; Whey Proteins

2012

Other Studies

61 other study(ies) available for leucine and Acidosis

Article	Year
Correction of hyperleucinemia in MSUD patients on leucine-free dietary therapy. Molecular genetics and metabolism, 2017, Volume: 122, Issue:4 Topics: Acidosis; Adolescent; Child; Child, Preschool; Diet; Female; Humans; Infant; Infant, Newborn; Leucine; Male; Maple Syrup Urine Disease; Retrospective Studies; Treatment Outcome	2017
Acute acidosis attenuates leucine stimulated signal transduction and protein synthesis in rat skeletal muscle. American journal of nephrology, 2014, Volume: 40, Issue:4 Topics: Acidosis; Animals; Body Weight; Insulin; Leucine; Male; Muscle, Skeletal; Protein Biosynthesis; Rats, Sprague-Dawley; Ribosomal Protein S6 Kinases; Signal Transduction; TOR Serine-Threonine Kinases	2014
The first use of N-carbamylglutamate in a patient with decompensated maple syrup urine disease. Metabolic brain disease, 2009, Volume: 24, Issue:3 Topics: Acidosis; Ammonia; Brain; Child, Preschool; Consanguinity; Female; Glutamates; Humans; Infant, Newborn; Leucine; Magnetic Resonance Imaging; Maple Syrup Urine Disease	2009
Effects of chronic metabolic acidosis on splanchnic protein turnover and oxygen consumption in human beings. Gastroenterology, 2010, Volume: 138, Issue:4 Topics: Acidosis; Adult; Ammonia; Chronic Disease; Female; Humans; Leucine; Male; Mesentery; Middle Aged; Oxygen Consumption; Proteins	2010
FURTHER OBSERVATIONS OF A PATIENT WITH HYPERGLYCINEMIA. Pediatrics, 1964, Volume: 33 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Blood; Child; Diet; Diet Therapy; Glycine; Humans; Infections; Isoleucine; Leucine; Leukocyte Count; Methionine; Renal Aminoacidurias; Threonine; Toxicology; Valine	1964
THE EFFECT OF TRIS (HYDROXYMETHYL) AMINOMETHANE ON GLUCOSE UTILIZATION OF SKELETAL MUSCLE. Metabolism: clinical and experimental, 1964, Volume: 13 Topics: Acidosis; Animals; Carbohydrate Metabolism; Carbon Isotopes; Dogs; Glucose; Hypoglycemia; Insulin; Lactates; Leucine; Metabolism; Methylamines; Muscle, Skeletal; Muscles; Propylene Glycols; Proteins; Rabbits; Rats; Research; Tromethamine	1964
Effect of acute acidosis on protein and amino acid metabolism in rats. Clinical nutrition (Edinburgh, Scotland), 2003, Volume: 22, Issue:5 Topics: Acidosis; Acute Disease; Amino Acids; Animals; Carbon Radioisotopes; Female; Leucine; Male; Muscle, Skeletal; Oxidation-Reduction; Proteins; Rats; Rats, Wistar	2003
Acute effects of acidosis on protein and amino acid metabolism in perfused rat liver. International journal of experimental pathology, 2003, Volume: 84, Issue:4 Topics: Acidosis; Amino Acids; Animals; Hydrogen-Ion Concentration; Leucine; Liver; Male; Organ Culture Techniques; Proteins; Rats; Rats, Wistar	2003
Kidney protein dynamics and ammoniagenesis in humans with chronic metabolic acidosis. Journal of the American Society of Nephrology : JASN, 2004, Volume: 15, Issue:6 Topics: Acidosis; Adult; Amino Acids; Ammonia; Catheterization; Chronic Disease; Female; Glomerular Filtration Rate; Glucose; Humans; Hydrogen-Ion Concentration; Keto Acids; Kidney; Kinetics; Lactates; Leucine; Male; Oxygen; Regression Analysis	2004
[Neonatal leucinosis with favourable course. Therapeutic problems]. Annales de pediatrie, 1977, Volume: 24, Issue:8-9 Topics: Acidosis; Child, Preschool; Diagnosis, Differential; Follow-Up Studies; Humans; Infant; Infant, Newborn; Isoleucine; Leucine; Male; Maple Syrup Urine Disease; Neurologic Examination; Peritoneal Dialysis; Seizures; Valine	1977
Isovaleric acidemia. American journal of diseases of children (1960), 1967, Volume: 113, Issue:1 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Chromatography, Gas; Fatty Acids; Female; Humans; Infant; Intellectual Disability; Isoleucine; Leucine; Male; Valine	1967
Hyperglycinemia with ketoacidosis and leukopenia. Metabolic studies on the nature of the defect. Pediatrics, 1967, Volume: 39, Issue:6 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Diet Therapy; Dietary Proteins; Glycine; Humans; Infant; Isoleucine; Leucine; Leukopenia; Lysine; Male; Valine	1967
The isolation and identification of N-isovalerylglycine from urine of patients with isovaleric acidemia. The Journal of biological chemistry, 1967, Jun-25, Volume: 242, Issue:12 Topics: Acidosis; Amino Acids; Chemistry, Clinical; Child; Child, Preschool; Chromatography, Gas; Coenzyme A; Female; Humans; In Vitro Techniques; Leucine; Magnetic Resonance Spectroscopy; Male; Spectrum Analysis; Valerates	1967
Organic aciduria associated with isovaleric acidemia. Clinical chemistry, 1983, Volume: 29, Issue:5 Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Infant; Leucine; Pentanoic Acids; Valerates	1983
Inherited disorders of 3-methylcrotonyl CoA carboxylation. Archives of disease in childhood, 1981, Volume: 56, Issue:1 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Biotin; Carbon-Carbon Ligases; Central Nervous System Diseases; Female; Humans; Infant; Infant, Newborn; Leucine; Ligases	1981
Insulin-mediated changes in PD and glucose uptake after correction of acidosis in humans with CRF. The American journal of physiology, 1995, Volume: 268, Issue:1 Pt 1 Topics: Acidosis; Adult; Aged; Amino Acids; Bicarbonates; Blood Pressure; Body Weight; Female; Glucose; Glucose Clamp Technique; Humans; Hydrogen-Ion Concentration; Kidney Failure, Chronic; Leucine; Male; Middle Aged; Sodium Bicarbonate	1995
Correction of acidosis in CAPD decreases whole body protein degradation. Kidney international, 1996, Volume: 49, Issue:5 Topics: Acidosis; Adult; Amino Acids; Blood Pressure; Body Weight; Female; Humans; Hydrogen-Ion Concentration; Kidney Failure, Chronic; Kinetics; Leucine; Male; Middle Aged; Peritoneal Dialysis, Continuous Ambulatory; Proteins; Urea	1996
Regulation of glutamate dehydrogenase by branched-chain amino acids in skeletal muscle from rats and chicks. The international journal of biochemistry & cell biology, 1996, Volume: 28, Issue:7 Topics: Acidosis; Amino Acids, Branched-Chain; Ammonium Chloride; Animals; Chickens; Glutamate Dehydrogenase; Glutamine; Isoleucine; Keto Acids; Kinetics; Leucine; Male; Mitochondria, Muscle; Muscle, Skeletal; Rats; Rats, Sprague-Dawley; Valine	1996
Ovine fetal leucine kinetics and protein metabolism during acute metabolic acidosis. The American journal of physiology, 1997, Volume: 272, Issue:2 Pt 1 Topics: Acidosis; Acute Disease; Animals; Carbohydrate Metabolism; Fetal Blood; Fetus; Hormones; Kinetics; Leucine; Oxygen Consumption; Proteins; Sheep	1997
Correction of acidosis in dialysis patients increases branched-chain and total essential amino acid levels in muscle. Clinical nephrology, 1997, Volume: 48, Issue:4 Topics: Acidosis; Adult; Aged; Aged, 80 and over; Amino Acids, Branched-Chain; Amino Acids, Essential; Bicarbonates; Dialysis; Female; Humans; Isoleucine; Leucine; Male; Middle Aged; Muscle, Skeletal; Valine	1997
Measurement of albumin synthesis in humans using stable isotopes. Zeitschrift fur Ernahrungswissenschaft, 1997, Volume: 36, Issue:4 Topics: Acidosis; Carbon Isotopes; Deuterium; Humans; Injections, Intravenous; Insulin-Like Growth Factor I; Isotope Labeling; Leucine; Phenylalanine; Reference Values; Serum Albumin	1997
The effect of uraemia, acidosis, and dialysis treatment on protein metabolism: a longitudinal leucine kinetic study. Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association, 1998, Volume: 13, Issue:7 Topics: Acidosis; Case-Control Studies; Female; Humans; Kidney Failure, Chronic; Leucine; Longitudinal Studies; Male; Middle Aged; Nutrition Disorders; Nutritional Status; Peritoneal Dialysis, Continuous Ambulatory; Proteins; Renal Dialysis; Sodium Bicarbonate; Uremia	1998
Correction of acidosis in hemodialysis decreases whole-body protein degradation. Journal of the American Society of Nephrology : JASN, 1997, Volume: 8, Issue:4 Topics: Acidosis; Adult; Aged; Amino Acids; Bicarbonates; Blood Proteins; Body Composition; Body Mass Index; Dietary Carbohydrates; Dietary Proteins; Female; Humans; Infusions, Intravenous; Kidney Failure, Chronic; Leucine; Male; Renal Dialysis; Urea	1997
Alterations of protein metabolism by metabolic acidosis in children with chronic renal failure. Kidney international, 2000, Volume: 58, Issue:1 Topics: Acidosis; Bicarbonates; Carbon Isotopes; Child, Preschool; Dietary Proteins; Energy Metabolism; Fasting; Female; Humans; Infant; Kidney Failure, Chronic; Leucine; Male; Nutrition Disorders; Protein-Energy Malnutrition	2000
Leucine and protein metabolism in rats with chronic renal insufficiency. Experimental and toxicologic pathology : official journal of the Gesellschaft fur Toxikologische Pathologie, 2001, Volume: 53, Issue:1 Topics: Acidosis; Animals; Body Weight; Cholesterol; Creatinine; Disease Models, Animal; Eating; Isoleucine; Kidney Failure, Chronic; Leucine; Male; Muscle, Skeletal; Nephrectomy; Proteins; Rats; Rats, Wistar; Urea; Uremia; Valine	2001
Leucine suppresses acid-induced protein wasting in L6 rat muscle cells. European journal of clinical investigation, 2001, Volume: 31, Issue:6 Topics: Acidosis; Animals; Caprylates; Cell Line; Fatty Acids, Nonesterified; Glycolysis; Hydrogen-Ion Concentration; Leucine; Muscle Proteins; Muscle, Skeletal; Rats; Wasting Syndrome	2001
Accumulation of 3-hydroxyisobutyric acid, 2-methyl-3-hydroxybutyric acid and 3-hydroxyisovaleric acid in ketoacidosis. Clinica chimica acta; international journal of clinical chemistry, 1975, Oct-15, Volume: 64, Issue:2 Topics: Acetates; Acidosis; Animals; Child; Child, Preschool; Chromatography, Gas; Diabetes Mellitus; Diabetic Ketoacidosis; Glutarates; Humans; Hydroxy Acids; Hydroxybutyrates; Infant; Isoleucine; Leucine; Male; Mass Spectrometry; Rats; Streptozocin; Valerates; Valine	1975
The regulation of phosphoenolpyruvate carboxykinase (GTP) synthesis in rat kidney cortex. The role of acid-base balance and glucocorticoids. The Journal of biological chemistry, 1975, Jul-25, Volume: 250, Issue:14 Topics: Acidosis; Adrenalectomy; Ammonium Chloride; Animals; Bicarbonates; Cyclic AMP; Cycloheximide; Cytosol; Dactinomycin; Deoxyadenosines; Diabetes Mellitus, Experimental; Electrophoresis, Polyacrylamide Gel; Enzyme Induction; Goats; Guanosine Triphosphate; Insulin; Kidney Cortex; Leucine; Liver; Male; Phosphoenolpyruvate Carboxykinase (GTP); Rats; Triamcinolone	1975
Ethylmalonic-adipic aciduria. In vivo and in vitro studies indicating deficiency of activities of multiple acyl-CoA dehydrogenases. The Journal of clinical investigation, 1979, Volume: 64, Issue:6 Topics: Acidosis; Adipates; Cells, Cultured; Child, Preschool; Dietary Fats; Fatty Acid Desaturases; Fatty Acids; Female; Humans; Leucine; Lysine; Malonates; Triglycerides	1979
Glycine therapy in isovaleric acidemia. The Journal of pediatrics, 1978, Volume: 92, Issue:5 Topics: Acidosis; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Drug Administration Schedule; Female; Glycine; Humans; Keto Acids; Ketone Bodies; Lactates; Leucine; Pyruvates; Valerates	1978
3-Hydroxy-3-methylglutaric aciduria, combined with 3-methylglutaconic aciduria. Clinica chimica acta; international journal of clinical chemistry, 1976, Aug-02, Volume: 70, Issue:3 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Chromatography, Gas; Glutarates; Humans; Hydroxybutyrates; Infant; Leucine; Mass Spectrometry	1976
[A form of late propionic acidemia]. Archives francaises de pediatrie, 1975, Volume: 32, Issue:3 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Blood Glucose; Child, Preschool; Coma; Dietary Proteins; Female; Humans; Isoleucine; Leucine; Male; Neurologic Manifestations; Propionates	1975
[Intermittent branched--chain ketoacidurie in ketotic hypoglycemia: investigations to localize the biochemical defect (author's transl)]. Monatsschrift fur Kinderheilkunde, 1976, Volume: 124, Issue:2 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child; Female; Fibroblasts; Humans; Hypoglycemia; Intellectual Disability; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Valine	1976
Ammonium chloride-induced acidosis increases protein breakdown and amino acid oxidation in humans. The American journal of physiology, 1992, Volume: 263, Issue:4 Pt 1 Topics: Acidosis; Adult; Amino Acids; Ammonium Chloride; Bicarbonates; Carbon Dioxide; Female; Humans; Hydrogen-Ion Concentration; Leucine; Male; Oxidation-Reduction; Proteins	1992
Metabolic acidosis accelerates whole body protein degradation and leucine oxidation by a glucocorticoid-dependent mechanism. Mineral and electrolyte metabolism, 1992, Volume: 18, Issue:2-5 Topics: Acidosis; Amino Acids; Animals; Glucocorticoids; Kidney Failure, Chronic; Leucine; Male; Muscles; Oxidation-Reduction; Proteins; Rats; Rats, Sprague-Dawley	1992
Effect of acute acidosis and alkalosis on leucine kinetics in man. Clinical physiology (Oxford, England), 1992, Volume: 12, Issue:1 Topics: Acidosis; Adult; Alkalosis; Bicarbonates; Blood Glucose; Fatty Acids, Nonesterified; Humans; Hydrogen-Ion Concentration; Keto Acids; Kinetics; Leucine; Lipolysis; Male; Proteins	1992
3-Hydroxy-3-methylglutaric aciduria: response to carnitine therapy and fat and leucine restriction. Journal of inherited metabolic disease, 1987, Volume: 10, Issue:2 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Carnitine; Dietary Fats; Dietary Proteins; Female; Glutarates; Humans; Infant, Newborn; Leucine; Meglutol; Oxo-Acid-Lyases	1987
Effects of acute metabolic acidosis and alkalosis on leucine metabolism in conscious dogs. Diabetes, 1989, Volume: 38, Issue:7 Topics: 3-Hydroxybutyric Acid; Acetoacetates; Acidosis; Alkalosis; Amino Acids; Animals; Bicarbonates; Blood Gas Analysis; Blood Glucose; Consciousness; Dogs; Fatty Acids, Nonesterified; Glucagon; Hydrochloric Acid; Hydrogen-Ion Concentration; Hydroxybutyrates; Infusions, Intra-Arterial; Insulin; Keto Acids; Leucine; Oxidation-Reduction; Pyruvates; Sodium; Sodium Bicarbonate; Sodium Chloride	1989
3-Hydroxy-3-methylglutaryl-coenzyme a lyase deficiency: a review. Journal of inherited metabolic disease, 1986, Volume: 9, Issue:3 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child; Dietary Carbohydrates; Dietary Proteins; Female; Genes, Recessive; Humans; Hypoglycemia; Leucine; Male; Oxo-Acid-Lyases	1986
The influence of ketosis on the metabolic response to skeletal trauma. The Journal of surgical research, 1988, Volume: 44, Issue:2 Topics: Acetoacetates; Acidosis; Animals; Body Weight; Copper; Femoral Fractures; Glucose; Glycerides; Hyperglycemia; Ketone Bodies; Ketosis; Leucine; Male; Nitrogen; Parenteral Nutrition; Rats; Rats, Inbred Strains; Zinc	1988
Acidosis, not azotemia, stimulates branched-chain, amino acid catabolism in uremic rats. Kidney international, 1987, Volume: 32, Issue:6 Topics: Acidosis; Amino Acids, Branched-Chain; Animals; Dietary Proteins; Kidney Failure, Chronic; Leucine; Male; Muscles; Nephrectomy; Rats; Rats, Inbred Strains; Uremia; Valine	1987
Metabolic acidosis stimulates protein degradation in rat muscle by a glucocorticoid-dependent mechanism. The Journal of clinical investigation, 1986, Volume: 77, Issue:2 Topics: Acidosis; Adrenalectomy; Ammonium Chloride; Animals; Body Weight; Dexamethasone; Hydrogen-Ion Concentration; In Vitro Techniques; Indomethacin; Insulin; Leucine; Male; Muscle Proteins; Muscles; Nitrogen; Protease Inhibitors; Rats; Rats, Inbred Strains	1986
Biotin-responsive beta-methylcrotonylglycinuria. Lancet (London, England), 1971, Jul-03, Volume: 2, Issue:7714 Topics: Acidosis; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Carbon Dioxide; Carboxy-Lyases; Chromatography, Gas; Fatty Acids; Glycine; Humans; Infant; Leucine; Male; Partial Pressure; Valerates; Valine; Vomiting	1971
Neonatal death associated with isovalericacidaemia. Lancet (London, England), 1967, Aug-26, Volume: 2, Issue:7513 Topics: Acidosis; Bicarbonates; Chromatography; Chromatography, Gas; Coenzyme A; Electrolytes; Fatty Acids; Fatty Acids, Nonesterified; Glucose; Hemorrhage; Humans; Hypocalcemia; Infant Mortality; Infant, Newborn; Leucine; Male; Metabolism, Inborn Errors; Valerates	1967
[Blood cells as indicators of metabolic disorders]. Zeitschrift fur klinische Chemie und klinische Biochemie, 1967, Volume: 5, Issue:5 Topics: Acidosis; Adrenal Insufficiency; Alcoholism; Alkalosis; Diabetes Mellitus; Down Syndrome; Electrolytes; Erythrocytes; Galactosemias; Glucosephosphate Dehydrogenase; Glycogen Storage Disease; Humans; Hyperaldosteronism; Hypertension; Hyperthyroidism; Kidney Failure, Chronic; Leucine; Leukocytes; Maple Syrup Urine Disease; Metabolic Diseases; Muscular Dystrophies; Paralyses, Familial Periodic; Potassium; Sodium; Vitamin B Deficiency	1967
The tolbutamide tolerance texxt in the evaluation of childhood hypoglycemia. Pediatrics, 1967, Volume: 39, Issue:6 Topics: Acidosis; Adenoma, Islet Cell; Child; Child, Preschool; Diagnosis, Differential; Humans; Hypoglycemia; Infant; Leucine; Tolbutamide	1967
[Case of ketotic hypoglycemia]. Nihon Shonika Gakkai zasshi. Acta paediatrica Japonica, 1969, Mar-01, Volume: 73, Issue:3 Topics: Acidosis; Adrenocorticotropic Hormone; Blood Glucose; Child, Preschool; Female; Glucagon; Glucose Tolerance Test; Humans; Hypoglycemia; Insulin; Leucine	1969
Effects of starvation on intermediary metabolism in the lactating cow. A comparison with metabolic changes occurring during bovine ketosis. The Biochemical journal, 1972, Volume: 128, Issue:5 Topics: Acidosis; Adenosine Triphosphate; Animals; Blood Glucose; Cattle; Cattle Diseases; Citrates; Fatty Acids, Nonesterified; Female; Glucose; Glycogen; Ketone Bodies; Lactation; Leucine; Liver; NAD; Oxaloacetates; Phosphoenolpyruvate; Pregnancy; Serine; Starvation	1972
Isovaleric acidemia. Clinical features of a new genetic defect of leucine metabolism. The New England journal of medicine, 1967, Aug-17, Volume: 277, Issue:7 Topics: Acidosis; Adult; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Coma; Female; Humans; Intellectual Disability; Leucine; Male; Oxidoreductases; Pentanoic Acids	1967
Glycemic response to 24-hour fast in normal children and children with ketotic hypoglycemia: II. Hormonal and metabolic changes. The Journal of pediatrics, 1974, Volume: 85, Issue:6 Topics: Acidosis; Alanine; Amino Acids; Autoanalysis; Blood Glucose; Child; Child, Preschool; Fasting; Fatty Acids, Nonesterified; Female; Glucagon; Growth Hormone; Hormones; Humans; Hydrocortisone; Hypoglycemia; Insulin; Isoleucine; Ketones; Ketosis; Leucine; Male; Valine	1974
Hyperalimentation in cirrhotic patients. American journal of surgery, 1972, Volume: 123, Issue:1 Topics: Acid-Base Equilibrium; Acidosis; Alanine Transaminase; Alkaline Phosphatase; Amino Acids; Ammonia; Arginine; Carbon Dioxide; Caseins; Catheterization; Cysteine; Diet Therapy; Fibrin; Glutamine; Glycine; Histidine; Humans; Isoleucine; Leucine; Liver; Liver Cirrhosis; Lysine; Methionine; Parenteral Nutrition; Phenylalanine; Potassium; Sodium; Threonine; Tryptophan	1972
Diagnosis of isovaleric acidemia in cultured fibroblasts. Clinica chimica acta; international journal of clinical chemistry, 1973, Nov-15, Volume: 48, Issue:4 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Carbon Radioisotopes; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Heterozygote; Humans; Infant, Newborn; Leucine; Pregnancy; Prenatal Diagnosis; Skin; Valerates	1973
Plasma insulin and blood glucose during long-term treatment with diazoxide for infant hypoglycemia. Acta paediatrica Scandinavica, 1974, Volume: 63, Issue:2 Topics: Acidosis; Blood Glucose; Child, Preschool; Diazoxide; Follow-Up Studies; Glucose; Glucose Tolerance Test; Humans; Hypertrichosis; Hypoglycemia; Infant; Infant, Newborn; Insulin; Intellectual Disability; Leucine; Stimulation, Chemical; Time Factors	1974
Metabolic abnormalities in the pancreatic islets and livers of the diabetic Chinese hamster. Diabetologia, 1970, Volume: 6, Issue:3 Topics: Acidosis; Animals; Blood Glucose; Carbon Isotopes; Cricetinae; Diabetes Mellitus; Disease Models, Animal; Glucokinase; Gluconeogenesis; Hexokinase; Insulin; Insulin Secretion; Islets of Langerhans; L-Lactate Dehydrogenase; Leucine; Liver; Liver Glycogen; Organ Size; Phosphogluconate Dehydrogenase; Pyruvate Kinase; Pyruvates	1970
Dietary treatment of an infant with isovaleric acidemia. Pediatrics, 1972, Volume: 49, Issue:4 Topics: Acidosis; Diet Therapy; Fatty Acids; Humans; Infant; Leucine; Male; Valerates	1972
Isovaleric acidemia: a new genetic defect of leucine metabolism. Proceedings of the National Academy of Sciences of the United States of America, 1966, Volume: 56, Issue:1 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Butyrates; Caproates; Child, Preschool; Chromatography, Gas; Coenzyme A; Fatty Acids; Female; Humans; Leucine; Male; Propionates; Valerates	1966
Hypoglycin A: a specific inhibitor of isovaleryl CoA dehydrogenase. Proceedings of the National Academy of Sciences of the United States of America, 1971, Volume: 68, Issue:1 Topics: Acidosis; Alanine; Amino Acid Metabolism, Inborn Errors; Animals; Butyrates; Caproates; Carbon Dioxide; Carbon Isotopes; Carnitine; Chromatography, Gas; Coenzyme A; Cyclopropanes; In Vitro Techniques; Isoleucine; Leucine; Male; Oxidoreductases; Plant Poisoning; Rats; Valerates; Vomiting	1971
[Glycinosis with acidocetosis of late revelation and favorable evolution]. Archives francaises de pediatrie, 1970, Volume: 27, Issue:5 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Amino Acids; Child; Child, Preschool; Glutamates; Glycine; Glyoxylates; Humans; Infant; Intelligence; Leucine; Male; Osteoporosis; Oxalates; Psychomotor Disorders; Serine	1970
Vitamin B12-dependent methylmalonicaciduria: amino acid toxicity, long chain ketonuria, and protective effect of vitamin B12. Pediatrics, 1970, Volume: 46, Issue:4 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Coenzyme A; Diet Therapy; Dietary Proteins; Humans; Isoleucine; Ketones; Leucine; Leukocytes; Male; Malonates; Methionine; Nutritional Requirements; Propionates; Threonine; Valine; Vitamin B 12	1970
Metabolism of amino acids by the perfused rat kidney. The American journal of physiology, 1971, Volume: 220, Issue:4 Topics: Acidosis; Alanine; Amino Acids; Ammonia; Animals; Aspartic Acid; Glucose; Glutamates; Glutamine; Glycine; Ketoglutaric Acids; Kidney; Leucine; Perfusion; Rats	1971
Renal protein and ammonia biochemistry in NH4Cl acidosis and after uninephrectomy. The American journal of physiology, 1968, Volume: 215, Issue:2 Topics: Acidosis; Ammonia; Ammonium Chloride; Animals; Carbon Isotopes; Dactinomycin; Female; Glutaminase; Glutamine; Hyperplasia; Kidney; Leucine; Methods; Nephrectomy; Protein Biosynthesis; Proteins; Rats; Regional Blood Flow; RNA	1968