leucine and Acid Alpha-Glucosidase Deficiency
leucine has been researched along with Acid Alpha-Glucosidase Deficiency in 6 studies
Research
Studies (6)
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 4 (66.67) | 18.7374 |
1990's | 1 (16.67) | 18.2507 |
2000's | 1 (16.67) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors
Authors | Studies |
---|---|
Gieselmann, V; Hasilik, A; Kalsbeek, R; Oude Elferink, R; Steckel, F; Tager, JM; von Figura, K; Waheed, A | 1 |
Bodamer, OA; Halliday, D; Leonard, JV | 2 |
Chubb, D; Conaglen, JV; Hesp, R; Scobie, IN; Sönksen, PH; Spencer, G; Trend, PS; Umpleby, AM; Wiles, CM; Williams, CD | 1 |
Macleod, AF; Scobie, IN; Sonksen, PH; Spencer, GT; Trend, PS; Umpleby, AM; Wiles, CM | 1 |
Kroos, M; Oude Elferink, RP; Reuser, AJ; Tager, JM | 1 |
Reviews
1 review(s) available for leucine and Acid Alpha-Glucosidase Deficiency
Article | Year |
---|---|
Dietary treatment in late-onset acid maltase deficiency.
Topics: Adolescent; Adult; Age of Onset; Alanine; Energy Metabolism; Glucose; Glycogen Storage Disease Type II; Humans; Leucine; Middle Aged | 1997 |
Trials
1 trial(s) available for leucine and Acid Alpha-Glucosidase Deficiency
Article | Year |
---|---|
The effect of a high protein diet on leucine and alanine turnover in acid maltase deficiency.
Topics: Adult; Alanine; alpha-Glucosidases; Clinical Trials as Topic; Dietary Proteins; Female; Follow-Up Studies; Glucan 1,4-alpha-Glucosidase; Glucose Tolerance Test; Glycogen Storage Disease Type II; Humans; Lactates; Lactic Acid; Leucine; Male; Middle Aged; Random Allocation | 1989 |
Other Studies
4 other study(ies) available for leucine and Acid Alpha-Glucosidase Deficiency
Article | Year |
---|---|
Biosynthesis of acid alpha-glucosidase in late-onset forms of glycogenosis type II (Pompe's disease).
Topics: alpha-Glucosidases; Cathepsin D; Cathepsins; Cell Line; Fibroblasts; Glucosidases; Glycogen Storage Disease; Glycogen Storage Disease Type II; Humans; Leucine; Methionine; Time Factors | 1982 |
The effects of l-alanine supplementation in late-onset glycogen storage disease type II.
Topics: Adolescent; Adult; Alanine; Energy Metabolism; Female; Glucose; Glycogen Storage Disease Type II; Humans; Kinetics; Leucine; Male; Middle Aged | 2000 |
Protein turnover in acid maltase deficiency before and after treatment with a high protein diet.
Topics: Adult; alpha-Glucosidases; Dietary Proteins; Glucan 1,4-alpha-Glucosidase; Glucose Tolerance Test; Glucosidases; Glycogen Storage Disease; Glycogen Storage Disease Type II; Humans; Leucine; Male; Muscle Proteins | 1987 |
Defects in synthesis, phosphorylation, and maturation of acid alpha-glucosidase in glycogenosis type II.
Topics: Adolescent; Adult; alpha-Glucosidases; beta-N-Acetylhexosaminidases; Electrophoresis, Polyacrylamide Gel; Fibroblasts; Glucan 1,4-alpha-Glucosidase; Glucosidases; Glycogen Storage Disease; Glycogen Storage Disease Type II; Hexosaminidases; Humans; Infant; Leucine; Male; Mannose; Phosphates; Phosphorylation | 1985 |