leucine and Acetonemia

leucine has been researched along with Acetonemia in 12 studies

Research

Studies (12)

TimeframeStudies, this research(%)All Research%
pre-19909 (75.00)18.7374
1990's1 (8.33)18.2507
2000's1 (8.33)29.6817
2010's1 (8.33)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
A Gutierrez, M; Hsu, Y; J Lopez, A; K Kennedy, B; M Nguyen, S; Mateen, S; N O'Leary, M; P Mitchell, K; Ramanathan, A; S Sonnet, D; Vockley, J1
TASHIAN, RE1
DANCIS, J; HUTZLER, J; LEVITZ, M1
SILBERMANSCHWARTZMAN, J1
Bodamer, OA; Hussein, K; Langhans, CD; Leonard, JV; Mayatepek, E; Morris, AA; Rating, D1
Adibi, SA; Morse, EL; Stanko, RT1
Porath, U; Schreier, K1
Grüttner, R; Held, KR; Plettner, C; Singh, S; Sternowsky, HJ2
Cossarizza, G; Netter, JC; Petrus, M; Rance, F; Sabathie, S1
Askari, A; Birkhahn, RH; Thomford, NR1
Chaussain, JL; Georges, P; Job, JC; Olive, G1

Reviews

1 review(s) available for leucine and Acetonemia

ArticleYear
[Congenital metabolic acidosis in the postnatal period].
    Deutsche medizinische Wochenschrift (1946), 1978, Jun-02, Volume: 103, Issue:22

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine

1978

Other Studies

11 other study(ies) available for leucine and Acetonemia

ArticleYear
Metformin inhibits Branched Chain Amino Acid (BCAA) derived ketoacidosis and promotes metabolic homeostasis in MSUD.
    Scientific reports, 2016, 07-04, Volume: 6

    Topics: Amino Acids, Branched-Chain; Animals; Chromatography, Liquid; Disease Models, Animal; Female; Fibroblasts; Homeostasis; Homozygote; Keto Acids; Ketoglutaric Acids; Ketosis; Leucine; Male; Maple Syrup Urine Disease; Mass Spectrometry; Metformin; Mice; Muscle Fibers, Skeletal; Muscle, Skeletal; Mutation

2016
Inhibition of brain glutamic acid decarboxylase by phenylalanine, valine, and leucine derivatives: a suggestion concerning the etiology of the neurological defect in phenylketonuria and branched-chain ketonuria.
    Metabolism: clinical and experimental, 1961, Volume: 10

    Topics: Amino Acids; Brain; Glutamate Decarboxylase; Humans; Intellectual Disability; Ketosis; Leucine; Lyases; Maple Syrup Urine Disease; Metabolic Diseases; Phenylalanine; Phenylketonurias; Valine

1961
THE DIAGNOSIS OF MAPLE SYRUP URINE DISEASE (BRANCHED- CHAIN KETOACIDURIA) BY THE IN VITRO STUDY OF THE PERIPHERAL LEUKOCYTE.
    Pediatrics, 1963, Volume: 32

    Topics: Chromatography; Humans; In Vitro Techniques; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Maple Syrup Urine Disease; Metabolism; Research; Valine

1963
[CLINICAL, BIOCHEMICAL, AND NEUROPATHOLOGIC ASPECTS OF MAPLE SYRUP URINE DISEASE. A KETOACIDURIA OF THE OPEN CHAIN AMINOACIDS LEUCINE, ISOLEUCINE AND VALINE].
    Anales. Universidad Nacional Mayor de San Marcos. Facultad de Medicina, 1963, Volume: 46

    Topics: Amino Acids; Genetics, Medical; Humans; Infant; Isoleucine; Keto Acids; Ketosis; Leucine; Maple Syrup Urine Disease; Nervous System Diseases; Neurosciences; Pathology; Valine

1963
Glucose and leucine kinetics in idiopathic ketotic hypoglycaemia.
    Archives of disease in childhood, 2006, Volume: 91, Issue:6

    Topics: Alanine; Amino Acids, Branched-Chain; Basal Metabolism; Calorimetry, Indirect; Carnitine; Case-Control Studies; Child; Child, Preschool; Fasting; Female; Glucose; Humans; Hypoglycemia; Infant; Insulin; Ketosis; Leucine; Male

2006
Modulation of leucine oxidation and turnover by graded amounts of carbohydrate intake in obese subjects.
    Metabolism: clinical and experimental, 1982, Volume: 31, Issue:6

    Topics: 3-Hydroxybutyric Acid; Adult; Amino Acids; Blood Glucose; Diet, Reducing; Dietary Carbohydrates; Female; Humans; Hydroxybutyrates; Insulin; Ketosis; Leucine; Methylhistidines; Nitrogen; Obesity

1982
[Ketotic hypoglycemia in intermittent branch-chain ketoaciduria. Enzymatic and gas chromatographic studies].
    Monatsschrift fur Kinderheilkunde, 1976, Volume: 124, Issue:5

    Topics: Child; Chromatography, Gas; Female; Fibroblasts; Humans; Hypoglycemia; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Valine

1976
[Intermittent branched--chain ketoacidurie in ketotic hypoglycemia: investigations to localize the biochemical defect (author's transl)].
    Monatsschrift fur Kinderheilkunde, 1976, Volume: 124, Issue:2

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child; Female; Fibroblasts; Humans; Hypoglycemia; Intellectual Disability; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Valine

1976
[Delayed severe decompensation of leucinosis. Significance of emergency blood exchange transfusion. Apropos of 2 cases].
    Annales de pediatrie, 1990, Volume: 37, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Emergencies; Exchange Transfusion, Whole Blood; Family Health; Female; Humans; Ketosis; Leucine; Time Factors

1990
The influence of ketosis on the metabolic response to skeletal trauma.
    The Journal of surgical research, 1988, Volume: 44, Issue:2

    Topics: Acetoacetates; Acidosis; Animals; Body Weight; Copper; Femoral Fractures; Glucose; Glycerides; Hyperglycemia; Ketone Bodies; Ketosis; Leucine; Male; Nitrogen; Parenteral Nutrition; Rats; Rats, Inbred Strains; Zinc

1988
Glycemic response to 24-hour fast in normal children and children with ketotic hypoglycemia: II. Hormonal and metabolic changes.
    The Journal of pediatrics, 1974, Volume: 85, Issue:6

    Topics: Acidosis; Alanine; Amino Acids; Autoanalysis; Blood Glucose; Child; Child, Preschool; Fasting; Fatty Acids, Nonesterified; Female; Glucagon; Growth Hormone; Hormones; Humans; Hydrocortisone; Hypoglycemia; Insulin; Isoleucine; Ketones; Ketosis; Leucine; Male; Valine

1974