leucine has been researched along with Acetonemia in 12 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 9 (75.00) | 18.7374 |
1990's | 1 (8.33) | 18.2507 |
2000's | 1 (8.33) | 29.6817 |
2010's | 1 (8.33) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
A Gutierrez, M; Hsu, Y; J Lopez, A; K Kennedy, B; M Nguyen, S; Mateen, S; N O'Leary, M; P Mitchell, K; Ramanathan, A; S Sonnet, D; Vockley, J | 1 |
TASHIAN, RE | 1 |
DANCIS, J; HUTZLER, J; LEVITZ, M | 1 |
SILBERMANSCHWARTZMAN, J | 1 |
Bodamer, OA; Hussein, K; Langhans, CD; Leonard, JV; Mayatepek, E; Morris, AA; Rating, D | 1 |
Adibi, SA; Morse, EL; Stanko, RT | 1 |
Porath, U; Schreier, K | 1 |
Grüttner, R; Held, KR; Plettner, C; Singh, S; Sternowsky, HJ | 2 |
Cossarizza, G; Netter, JC; Petrus, M; Rance, F; Sabathie, S | 1 |
Askari, A; Birkhahn, RH; Thomford, NR | 1 |
Chaussain, JL; Georges, P; Job, JC; Olive, G | 1 |
1 review(s) available for leucine and Acetonemia
Article | Year |
---|---|
[Congenital metabolic acidosis in the postnatal period].
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine | 1978 |
11 other study(ies) available for leucine and Acetonemia
Article | Year |
---|---|
Metformin inhibits Branched Chain Amino Acid (BCAA) derived ketoacidosis and promotes metabolic homeostasis in MSUD.
Topics: Amino Acids, Branched-Chain; Animals; Chromatography, Liquid; Disease Models, Animal; Female; Fibroblasts; Homeostasis; Homozygote; Keto Acids; Ketoglutaric Acids; Ketosis; Leucine; Male; Maple Syrup Urine Disease; Mass Spectrometry; Metformin; Mice; Muscle Fibers, Skeletal; Muscle, Skeletal; Mutation | 2016 |
Inhibition of brain glutamic acid decarboxylase by phenylalanine, valine, and leucine derivatives: a suggestion concerning the etiology of the neurological defect in phenylketonuria and branched-chain ketonuria.
Topics: Amino Acids; Brain; Glutamate Decarboxylase; Humans; Intellectual Disability; Ketosis; Leucine; Lyases; Maple Syrup Urine Disease; Metabolic Diseases; Phenylalanine; Phenylketonurias; Valine | 1961 |
THE DIAGNOSIS OF MAPLE SYRUP URINE DISEASE (BRANCHED- CHAIN KETOACIDURIA) BY THE IN VITRO STUDY OF THE PERIPHERAL LEUKOCYTE.
Topics: Chromatography; Humans; In Vitro Techniques; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Maple Syrup Urine Disease; Metabolism; Research; Valine | 1963 |
[CLINICAL, BIOCHEMICAL, AND NEUROPATHOLOGIC ASPECTS OF MAPLE SYRUP URINE DISEASE. A KETOACIDURIA OF THE OPEN CHAIN AMINOACIDS LEUCINE, ISOLEUCINE AND VALINE].
Topics: Amino Acids; Genetics, Medical; Humans; Infant; Isoleucine; Keto Acids; Ketosis; Leucine; Maple Syrup Urine Disease; Nervous System Diseases; Neurosciences; Pathology; Valine | 1963 |
Glucose and leucine kinetics in idiopathic ketotic hypoglycaemia.
Topics: Alanine; Amino Acids, Branched-Chain; Basal Metabolism; Calorimetry, Indirect; Carnitine; Case-Control Studies; Child; Child, Preschool; Fasting; Female; Glucose; Humans; Hypoglycemia; Infant; Insulin; Ketosis; Leucine; Male | 2006 |
Modulation of leucine oxidation and turnover by graded amounts of carbohydrate intake in obese subjects.
Topics: 3-Hydroxybutyric Acid; Adult; Amino Acids; Blood Glucose; Diet, Reducing; Dietary Carbohydrates; Female; Humans; Hydroxybutyrates; Insulin; Ketosis; Leucine; Methylhistidines; Nitrogen; Obesity | 1982 |
[Ketotic hypoglycemia in intermittent branch-chain ketoaciduria. Enzymatic and gas chromatographic studies].
Topics: Child; Chromatography, Gas; Female; Fibroblasts; Humans; Hypoglycemia; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Valine | 1976 |
[Intermittent branched--chain ketoacidurie in ketotic hypoglycemia: investigations to localize the biochemical defect (author's transl)].
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child; Female; Fibroblasts; Humans; Hypoglycemia; Intellectual Disability; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Valine | 1976 |
[Delayed severe decompensation of leucinosis. Significance of emergency blood exchange transfusion. Apropos of 2 cases].
Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Emergencies; Exchange Transfusion, Whole Blood; Family Health; Female; Humans; Ketosis; Leucine; Time Factors | 1990 |
The influence of ketosis on the metabolic response to skeletal trauma.
Topics: Acetoacetates; Acidosis; Animals; Body Weight; Copper; Femoral Fractures; Glucose; Glycerides; Hyperglycemia; Ketone Bodies; Ketosis; Leucine; Male; Nitrogen; Parenteral Nutrition; Rats; Rats, Inbred Strains; Zinc | 1988 |
Glycemic response to 24-hour fast in normal children and children with ketotic hypoglycemia: II. Hormonal and metabolic changes.
Topics: Acidosis; Alanine; Amino Acids; Autoanalysis; Blood Glucose; Child; Child, Preschool; Fasting; Fatty Acids, Nonesterified; Female; Glucagon; Growth Hormone; Hormones; Humans; Hydrocortisone; Hypoglycemia; Insulin; Isoleucine; Ketones; Ketosis; Leucine; Male; Valine | 1974 |