leucine and 3-Methylglutaconic Aciduria, Type II

leucine has been researched along with 3-Methylglutaconic Aciduria, Type II in 2 studies

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's1 (50.00)24.3611
2020's1 (50.00)2.80

Authors

AuthorsStudies
Bashir, A; Bittel, AJ; Bohnert, KL; Byrne, BJ; Cade, WT; de Las Fuentes, L; Gropler, RJ; Laforest, R; Pacak, CA; Peterson, LR; Reeds, DN; Woodard, PK1
Byrne, BJ; Cade, WT; Crowley, JR; Maisenbacher, M; O'Connor, R; Peterson, LR; Reeds, DN; Spencer, CT; Waggoner, AD1

Other Studies

2 other study(ies) available for leucine and 3-Methylglutaconic Aciduria, Type II

ArticleYear
Myocardial glucose and fatty acid metabolism is altered and associated with lower cardiac function in young adults with Barth syndrome.
    Journal of nuclear cardiology : official publication of the American Society of Nuclear Cardiology, 2021, Volume: 28, Issue:4

    Topics: Adult; Barth Syndrome; Case-Control Studies; Echocardiography; Fatty Acids; Glucose; Humans; Leucine; Magnetic Resonance Spectroscopy; Male; Myocardium; Positron-Emission Tomography; Ventricular Function, Left; Young Adult

2021
Substrate metabolism during basal and hyperinsulinemic conditions in adolescents and young-adults with Barth syndrome.
    Journal of inherited metabolic disease, 2013, Volume: 36, Issue:1

    Topics: Adolescent; Adult; Barth Syndrome; Blood Glucose; Body Composition; Echocardiography; Fatty Acids; Glucose; Humans; Hyperinsulinism; Insulin; Leucine; Lipid Metabolism; Lipolysis; Male; Mitochondria; Oxidation-Reduction; Young Adult

2013