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isovaleric acid and Lipid Metabolism, Inborn Error

isovaleric acid has been researched along with Lipid Metabolism, Inborn Error in 2 studies

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19901 (50.00)18.7374
1990's1 (50.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Chace, DH; Heales, SJ; Kahler, SG; Millington, DS; Roe, CR; Roe, DS; Van Hove, JL1
Amendt, BA; Rhead, WJ1

Other Studies

2 other study(ies) available for isovaleric acid and Lipid Metabolism, Inborn Error

ArticleYear
Intravenous L-carnitine and acetyl-L-carnitine in medium-chain acyl-coenzyme A dehydrogenase deficiency and isovaleric acidemia.
    Pediatric research, 1994, Volume: 35, Issue:1

    Topics: Acetylcarnitine; Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Female; Hemiterpenes; Humans; Injections, Intravenous; Lipid Metabolism, Inborn Errors; Pentanoic Acids; Safety

1994
Catalytic defect of medium-chain acyl-coenzyme A dehydrogenase deficiency. Lack of both cofactor responsiveness and biochemical heterogeneity in eight patients.
    The Journal of clinical investigation, 1985, Volume: 76, Issue:3

    Topics: Acyl Coenzyme A; Acyl-CoA Dehydrogenases; Adult; Fibroblasts; Flavin-Adenine Dinucleotide; Hemiterpenes; Humans; Infant; Isovaleryl-CoA Dehydrogenase; Lipid Metabolism, Inborn Errors; Male; Methylphenazonium Methosulfate; Mitochondria, Liver; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Subcellular Fractions

1985