Page last updated: 2024-08-21

isovaleric acid and Acidosis

isovaleric acid has been researched along with Acidosis in 11 studies

Research

Studies (11)

TimeframeStudies, this research(%)All Research%
pre-19904 (36.36)18.7374
1990's5 (45.45)18.2507
2000's1 (9.09)29.6817
2010's1 (9.09)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Abboud, G; Feillet, F; Guéant, JL; Kimmoun, A; Merten, M; Strazeck, J1
Cayonu, N; Erdem, E; Uysalol, E; Yildirmak, ZY1
Kikawa, Y; Kikuchi, K; Ohta, S; Okamoto, M; Shigematsu, Y; Sudo, M1
French, NP; Grauaug, A; Wysocki, SJ1
Burton, BK; Challa, VR; Fischer, AQ; McLean, WT1
Chiba, T; Ito, T; Kajita, M; Kidouchi, K; Niwa, T; Sugiyama, N; Wada, Y1
Henretig, FM; Kaplan, P; Krantz, I; Mehta, KC; Osterhoudt, KC; Zsolway, K1
Burton, BK; Geldner, P; Laurito, CE; Pygon, BH; Weinberg, GL1
Corbella, L; Depetris de Boldini, C; Dodelson de Kremer, R; Hliba, E; Paschini de Capra, A1
Caruso, U; Cerone, R; Pesce, F; Romano, C1
Josephson, MW; Oliphant, C; Tsai, MY1

Other Studies

11 other study(ies) available for isovaleric acid and Acidosis

ArticleYear
Acute decompensation of isovaleric acidemia induced by Graves' disease.
    Intensive care medicine, 2008, Volume: 34, Issue:12

    Topics: Acidosis; Carnitine; Diet, Protein-Restricted; Female; Graves Disease; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Pentanoic Acids; Vitamin B Complex; Young Adult

2008
Chronic intermittent form of isovaleric acidemia mimicking diabetic ketoacidosis.
    Journal of pediatric endocrinology & metabolism : JPEM, 2010, Volume: 23, Issue:5

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child; Chronic Disease; Diabetic Ketoacidosis; Diagnosis, Differential; Female; Hemiterpenes; Humans; Hyperglycemia; Pentanoic Acids; Treatment Outcome

2010
A simple method of determining 4-hydroxyisovaleric acid and its level in a patient with isovaleric acidemia.
    Clinica chimica acta; international journal of clinical chemistry, 1984, Apr-27, Volume: 138, Issue:3

    Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Ketosis; Pentanoic Acids; Valerates

1984
Organic aciduria associated with isovaleric acidemia.
    Clinical chemistry, 1983, Volume: 29, Issue:5

    Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Infant; Leucine; Pentanoic Acids; Valerates

1983
Cerebellar hemorrhage complicating isovaleric acidemia: a case report.
    Neurology, 1981, Volume: 31, Issue:6

    Topics: Acidosis; Cerebellar Diseases; Cerebral Hemorrhage; Female; Hemiterpenes; Humans; Infant, Newborn; Pentanoic Acids; Valerates

1981
Liquid chromatographic-atmospheric pressure chemical ionization mass spectrometric analysis of glycine conjugates and urinary isovalerylglycine in isovaleric acidemia.
    Journal of chromatography. B, Biomedical applications, 1995, Aug-18, Volume: 670, Issue:2

    Topics: Acidosis; Administration, Oral; Carnitine; Child, Preschool; Chromatography, Liquid; Female; Glucuronates; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Male; Mass Spectrometry; Pentanoic Acids

1995
Lessons from the late diagnosis of isovaleric acidemia in a five-year-old boy.
    The Journal of pediatrics, 1996, Volume: 129, Issue:2

    Topics: Acid-Base Equilibrium; Acidosis; Child, Preschool; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Male; Metabolism, Inborn Errors; Pentanoic Acids; Sodium Bicarbonate

1996
Malignant ventricular dysrhythmias in a patient with isovaleric acidemia receiving general and local anesthesia for suction lipectomy.
    Journal of clinical anesthesia, 1997, Volume: 9, Issue:8

    Topics: Acidosis; Adolescent; Anesthesia, General; Anesthesia, Local; Anesthetics, Local; Bupivacaine; Carnitine; Electrocardiography; Female; Hemiterpenes; Humans; Intraoperative Complications; Lipectomy; Pentanoic Acids; Ventricular Dysfunction

1997
[Phenotypic expression variation of isovaleric acidemia in Argentinian patients. A long term follow-up].
    Medicina, 1992, Volume: 52, Issue:2

    Topics: Acidosis; Brain; Child, Preschool; Chromatography, Thin Layer; Family; Female; Follow-Up Studies; Glycine; Hemiterpenes; Humans; Infant; Isovaleryl-CoA Dehydrogenase; Liver; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Phenotype

1992
Acute neonatal isovaleric acidaemia presented without acidosis or ketonuria.
    Journal of inherited metabolic disease, 1991, Volume: 14, Issue:1

    Topics: Acidosis; Dietary Proteins; Female; Glycine; Hemiterpenes; Humans; Infant; Ketones; Male; Metabolism, Inborn Errors; Pentanoic Acids

1991
Identification of metabolites diagnostic for organic acidurias by simultaneous dual-column capillary gas chromatography.
    Journal of chromatography, 1985, May-31, Volume: 341, Issue:1

    Topics: Acidosis; Chromatography, Gas; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Indicators and Reagents; Maple Syrup Urine Disease; Pentanoic Acids; Propionates

1985