isovaleric acid has been researched along with Acidosis in 11 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 4 (36.36) | 18.7374 |
1990's | 5 (45.45) | 18.2507 |
2000's | 1 (9.09) | 29.6817 |
2010's | 1 (9.09) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Abboud, G; Feillet, F; Guéant, JL; Kimmoun, A; Merten, M; Strazeck, J | 1 |
Cayonu, N; Erdem, E; Uysalol, E; Yildirmak, ZY | 1 |
Kikawa, Y; Kikuchi, K; Ohta, S; Okamoto, M; Shigematsu, Y; Sudo, M | 1 |
French, NP; Grauaug, A; Wysocki, SJ | 1 |
Burton, BK; Challa, VR; Fischer, AQ; McLean, WT | 1 |
Chiba, T; Ito, T; Kajita, M; Kidouchi, K; Niwa, T; Sugiyama, N; Wada, Y | 1 |
Henretig, FM; Kaplan, P; Krantz, I; Mehta, KC; Osterhoudt, KC; Zsolway, K | 1 |
Burton, BK; Geldner, P; Laurito, CE; Pygon, BH; Weinberg, GL | 1 |
Corbella, L; Depetris de Boldini, C; Dodelson de Kremer, R; Hliba, E; Paschini de Capra, A | 1 |
Caruso, U; Cerone, R; Pesce, F; Romano, C | 1 |
Josephson, MW; Oliphant, C; Tsai, MY | 1 |
11 other study(ies) available for isovaleric acid and Acidosis
Article | Year |
---|---|
Acute decompensation of isovaleric acidemia induced by Graves' disease.
Topics: Acidosis; Carnitine; Diet, Protein-Restricted; Female; Graves Disease; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Pentanoic Acids; Vitamin B Complex; Young Adult | 2008 |
Chronic intermittent form of isovaleric acidemia mimicking diabetic ketoacidosis.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child; Chronic Disease; Diabetic Ketoacidosis; Diagnosis, Differential; Female; Hemiterpenes; Humans; Hyperglycemia; Pentanoic Acids; Treatment Outcome | 2010 |
A simple method of determining 4-hydroxyisovaleric acid and its level in a patient with isovaleric acidemia.
Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Ketosis; Pentanoic Acids; Valerates | 1984 |
Organic aciduria associated with isovaleric acidemia.
Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Infant; Leucine; Pentanoic Acids; Valerates | 1983 |
Cerebellar hemorrhage complicating isovaleric acidemia: a case report.
Topics: Acidosis; Cerebellar Diseases; Cerebral Hemorrhage; Female; Hemiterpenes; Humans; Infant, Newborn; Pentanoic Acids; Valerates | 1981 |
Liquid chromatographic-atmospheric pressure chemical ionization mass spectrometric analysis of glycine conjugates and urinary isovalerylglycine in isovaleric acidemia.
Topics: Acidosis; Administration, Oral; Carnitine; Child, Preschool; Chromatography, Liquid; Female; Glucuronates; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Male; Mass Spectrometry; Pentanoic Acids | 1995 |
Lessons from the late diagnosis of isovaleric acidemia in a five-year-old boy.
Topics: Acid-Base Equilibrium; Acidosis; Child, Preschool; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Male; Metabolism, Inborn Errors; Pentanoic Acids; Sodium Bicarbonate | 1996 |
Malignant ventricular dysrhythmias in a patient with isovaleric acidemia receiving general and local anesthesia for suction lipectomy.
Topics: Acidosis; Adolescent; Anesthesia, General; Anesthesia, Local; Anesthetics, Local; Bupivacaine; Carnitine; Electrocardiography; Female; Hemiterpenes; Humans; Intraoperative Complications; Lipectomy; Pentanoic Acids; Ventricular Dysfunction | 1997 |
[Phenotypic expression variation of isovaleric acidemia in Argentinian patients. A long term follow-up].
Topics: Acidosis; Brain; Child, Preschool; Chromatography, Thin Layer; Family; Female; Follow-Up Studies; Glycine; Hemiterpenes; Humans; Infant; Isovaleryl-CoA Dehydrogenase; Liver; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Phenotype | 1992 |
Acute neonatal isovaleric acidaemia presented without acidosis or ketonuria.
Topics: Acidosis; Dietary Proteins; Female; Glycine; Hemiterpenes; Humans; Infant; Ketones; Male; Metabolism, Inborn Errors; Pentanoic Acids | 1991 |
Identification of metabolites diagnostic for organic acidurias by simultaneous dual-column capillary gas chromatography.
Topics: Acidosis; Chromatography, Gas; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Indicators and Reagents; Maple Syrup Urine Disease; Pentanoic Acids; Propionates | 1985 |