Page last updated: 2024-09-05

isospaglumic acid and Canavan Disease

isospaglumic acid has been researched along with Canavan Disease in 12 studies

Research

Studies (12)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's3 (25.00)18.2507
2000's8 (66.67)29.6817
2010's1 (8.33)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
de Mattos Dutra, A; Dutra-Filho, CS; Henn, NT; Pederzolli, CD; Rockenbach, FJ; Romagna, EC; Sgaravatti, AM; Wajner, M; Wannmacher, CM; Wyse, AT; Zanin, FR1
Baslow, MH; Guilfoyle, DN1
Attwell, D; Hamilton, NB; Káradóttir, R; Kolodziejczyk, K; Wade, A1
Barritault, J; Boespflug-Tanguy, O; Boildieu, N; Eymard-Pierre, E; Mochel, F; Sarret, C; Schiffmann, R; Seguin, F1
Gradowska, W; Krawczyk, H1
Campbell, GA; Ezell, EL; Matalon, R; Michals-Matalon, K; Quast, MJ; Rady, PL; Rassin, DK; Surendran, S; Szucs, S; Tyring, SK; Wei, J1
Moffett, JR; Namboodiri, AM1
Matalon, R; Michals-Matalon, K; Surendran, S; Tyring, SK1
Assadi, M; Bilaniuk, L; Francis, J; Freese, A; Haselgrove, J; Hurh, P; Janson, CG; Leone, P; McPhee, SW; Shera, D; Wang, DJ1
Burlina, AB; Burlina, AP; Corazza, A; Erhard, P; Ferrari, V; Künnecke, B; Seelig, J1
Burlina, AB; Burlina, AP; Ferrari, V; Leon, A; Mazza, MR; Skaper, SD1
Bennett, MJ; Burlina, AB; Burlina, AP; Dionisi-Vici, C; Divry, P; Ferrari, V; Gradowska, W; Jakobs, C; Sewell, AC1

Reviews

2 review(s) available for isospaglumic acid and Canavan Disease

ArticleYear
Preface: a brief review of N-acetylaspartate.
    Advances in experimental medicine and biology, 2006, Volume: 576

    Topics: Animals; Aspartic Acid; Canavan Disease; Dipeptides; Energy Metabolism; Humans; Magnetic Resonance Spectroscopy; Myelin Sheath; Neurons; Osmolar Concentration

2006
Canavan disease: studies on the knockout mouse.
    Advances in experimental medicine and biology, 2006, Volume: 576

    Topics: Amidohydrolases; Animals; Canavan Disease; Dipeptides; gamma-Aminobutyric Acid; Gene Targeting; Genetic Therapy; Glutamic Acid; Humans; Mice; Mice, Knockout; Phenotype; Stem Cell Transplantation

2006

Other Studies

10 other study(ies) available for isospaglumic acid and Canavan Disease

ArticleYear
Intracerebroventricular administration of N-acetylaspartic acid impairs antioxidant defenses and promotes protein oxidation in cerebral cortex of rats.
    Metabolic brain disease, 2009, Volume: 24, Issue:2

    Topics: Animals; Antioxidants; Aspartic Acid; Brain Damage, Chronic; Canavan Disease; Catalase; Cerebral Cortex; Dipeptides; Disease Models, Animal; Glucosephosphate Dehydrogenase; Glutathione Peroxidase; Injections, Intraventricular; Lipid Peroxidation; Male; Neuropeptides; Neurotoxins; Oxidation-Reduction; Oxidative Stress; Rats; Rats, Wistar

2009
Are astrocytes the missing link between lack of brain aspartoacylase activity and the spongiform leukodystrophy in Canavan disease?
    Neurochemical research, 2009, Volume: 34, Issue:9

    Topics: Amidohydrolases; Animals; Aspartic Acid; Astrocytes; Brain; Canavan Disease; Dipeptides; Disease Models, Animal; Extracellular Fluid; Humans; Myelin Sheath

2009
The effect of N-acetyl-aspartyl-glutamate and N-acetyl-aspartate on white matter oligodendrocytes.
    Brain : a journal of neurology, 2009, Volume: 132, Issue:Pt 6

    Topics: Action Potentials; Animals; Aspartic Acid; Calcium; Canavan Disease; Cerebellum; Dipeptides; Evoked Potentials; Glutamic Acid; Hydrolysis; Oligodendroglia; Patch-Clamp Techniques; Pelizaeus-Merzbacher Disease; Rats; Receptors, N-Methyl-D-Aspartate; Tissue Culture Techniques

2009
Elevated CSF N-acetylaspartylglutamate suggests specific molecular diagnostic abnormalities in patients with white matter diseases.
    Biochimica et biophysica acta, 2010, Volume: 1802, Issue:11

    Topics: Adolescent; Adult; Biomarkers; Canavan Disease; Child; Child, Preschool; Dipeptides; Female; Gene Duplication; Humans; Magnetic Resonance Spectroscopy; Male; Molecular Structure; Myelin Proteolipid Protein; Organic Anion Transporters; Pelizaeus-Merzbacher Disease; Point Mutation; Sensitivity and Specificity; Symporters

2010
Characterisation of the 1H and 13C NMR spectra of N-acetylaspartylglutamate and its detection in urine from patients with Canavan disease.
    Journal of pharmaceutical and biomedical analysis, 2003, Mar-10, Volume: 31, Issue:3

    Topics: Canavan Disease; Child; Dipeptides; Humans; Hydrogen-Ion Concentration; Indicators and Reagents; Magnetic Resonance Spectroscopy; Protons

2003
Expression of glutamate transporter, GABRA6, serine proteinase inhibitor 2 and low levels of glutamate and GABA in the brain of knock-out mouse for Canavan disease.
    Brain research bulletin, 2003, Aug-30, Volume: 61, Issue:4

    Topics: Amino Acid Transport System X-AG; Analysis of Variance; Animals; Azo Compounds; Brain Chemistry; Canavan Disease; Creatine; Dipeptides; Disease Models, Animal; gamma-Aminobutyric Acid; Glutamic Acid; In Vitro Techniques; Insect Proteins; Magnetic Resonance Spectroscopy; Mice; Mice, Knockout; Oligonucleotide Array Sequence Analysis; Receptors, GABA-A; Reverse Transcriptase Polymerase Chain Reaction; RNA, Messenger; Sequence Analysis, Protein

2003
Natural history of Canavan disease revealed by proton magnetic resonance spectroscopy (1H-MRS) and diffusion-weighted MRI.
    Neuropediatrics, 2006, Volume: 37, Issue:4

    Topics: Age Factors; Aspartic Acid; Atrophy; Brain; Canavan Disease; Case-Control Studies; Child, Preschool; Confidence Intervals; Diffusion Magnetic Resonance Imaging; Dipeptides; Female; Humans; Infant; Magnetic Resonance Spectroscopy; Male; Protons; Reference Values

2006
Detection of increased urinary N-acetylaspartylglutamate in Canavan disease.
    European journal of pediatrics, 1994, Volume: 153, Issue:7

    Topics: Canavan Disease; Child; Child, Preschool; Dipeptides; Female; Humans; Male

1994
N-acetylaspartylglutamate selectively inhibits neuronal responses to N-methyl-D-aspartic acid in vitro.
    Journal of neurochemistry, 1994, Volume: 63, Issue:3

    Topics: Animals; Aspartic Acid; Canavan Disease; Cell Survival; Cells, Cultured; Cerebellum; Culture Media; Dipeptides; Kainic Acid; Mice; Mice, Inbred BALB C; N-Methylaspartate; Neurons

1994
N-acetylaspartylglutamate in Canavan disease: an adverse effector?
    European journal of pediatrics, 1999, Volume: 158, Issue:5

    Topics: Adolescent; Canavan Disease; Child; Child, Preschool; Dipeptides; Electrophoresis, Capillary; Humans; Infant; Infant, Newborn; Neuropeptides

1999