isoleucine has been researched along with Acidosis in 26 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 20 (76.92) | 18.7374 |
| 1990's | 5 (19.23) | 18.2507 |
| 2000's | 1 (3.85) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| CHILDS, B; NYHAN, WL | 1 |
| Astruc, J; Bellet, H; Brunel, D; Froye, E; Luciani, JM; Magnan de Bornier, P | 1 |
| Efron, ML | 1 |
| Edelmann, CM; Finberg, L; Soriano, JR; Taitz, LS | 1 |
| Thompson, JR; Zhou, X | 1 |
| Aoyanagi, N; Fukao, T; Kodama, A; Kondo, N; Kuhara, T; Matsumoto, I; Orii, T; Song, XQ; Tsukino, R; Uemura, S; Watanebe, H | 1 |
| Anderstam, B; Bergström, J; Löfberg, E; Wernerman, J | 1 |
| Bailey, JL; Caban, R; England, BK; Marinovic, AC; Maroni, BJ; Mitch, WE; Price, SR; Reaich, D | 1 |
| Al Amoudi, M; Al Essa, M; Al Jishi, E; Joshi, S; Jumaah, S; Ozand, PT; Rahbeeni, Z; Rashed, MS | 1 |
| Holecek, M; Sprongl, L; Tichý, M; Tilser, I | 1 |
| Balfe, JW; Mamer, OA; Robinson, BH; Sherwood, WG; Taylor, J | 1 |
| Landaas, S | 1 |
| Porath, U; Schreier, K | 1 |
| Bachmann, C; Baumgartner, R; Bremer, HJ; Bruinvis, L; Duran, M; Irle, U; Ketting, D; Przyrembel, H; Wadman, SK | 1 |
| Collombel, C; Cotton, JB; Divry, P; Guibaud, P; Larbre, F; Marcon, G | 1 |
| Grüttner, R; Held, KR; Plettner, C; Singh, S; Sternowsky, HJ | 1 |
| Balgobin, L; Barnes, ND; Gompertz, D; Hull, D | 1 |
| Chaussain, JL; Georges, P; Job, JC; Olive, G | 1 |
| Ando, T; Hull, D; Nyhan, WL; Rasmussen, K | 1 |
| Host, WR; Rush, BF; Serlin, O | 1 |
| Feigin, RD; Hillman, RE; Keating, JP; Tenenbaum, SM | 1 |
| Daum, RS; Delvin, E; Goldman, H; Lamm, P; Mamer, OA; Scriver, CR | 1 |
| Ando, T; Fawcett, N; Julius, RL; Nyhan, WL; Rennert, OM | 1 |
| Hillman, RE; Keating, JP | 1 |
| Isselbacher, KJ; Miller, EM; Tanaka, K | 1 |
| Hsia, YE; Lilljeqvist, AC; Rosenberg, LE | 1 |
1 review(s) available for isoleucine and Acidosis
| Article | Year |
|---|---|
[Congenital metabolic acidosis in the postnatal period].
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine | 1978 |
25 other study(ies) available for isoleucine and Acidosis
| Article | Year |
|---|---|
FURTHER OBSERVATIONS OF A PATIENT WITH HYPERGLYCINEMIA.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Blood; Child; Diet; Diet Therapy; Glycine; Humans; Infections; Isoleucine; Leucine; Leukocyte Count; Methionine; Renal Aminoacidurias; Threonine; Toxicology; Valine | 1964 |
[Neonatal leucinosis with favourable course. Therapeutic problems].
Topics: Acidosis; Child, Preschool; Diagnosis, Differential; Follow-Up Studies; Humans; Infant; Infant, Newborn; Isoleucine; Leucine; Male; Maple Syrup Urine Disease; Neurologic Examination; Peritoneal Dialysis; Seizures; Valine | 1977 |
Isovaleric acidemia.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Chromatography, Gas; Fatty Acids; Female; Humans; Infant; Intellectual Disability; Isoleucine; Leucine; Male; Valine | 1967 |
Hyperglycinemia with ketoacidosis and leukopenia. Metabolic studies on the nature of the defect.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Diet Therapy; Dietary Proteins; Glycine; Humans; Infant; Isoleucine; Leucine; Leukopenia; Lysine; Male; Valine | 1967 |
Regulation of glutamate dehydrogenase by branched-chain amino acids in skeletal muscle from rats and chicks.
Topics: Acidosis; Amino Acids, Branched-Chain; Ammonium Chloride; Animals; Chickens; Glutamate Dehydrogenase; Glutamine; Isoleucine; Keto Acids; Kinetics; Leucine; Male; Mitochondria, Muscle; Muscle, Skeletal; Rats; Rats, Sprague-Dawley; Valine | 1996 |
Mild form of beta-ketothiolase deficiency (mitochondrial acetoacetyl-CoA thiolase deficiency) in two Japanese siblings: identification of detectable residual activity and cross-reactive material in EB-transformed lymphocytes.
Topics: Acetyl-CoA C-Acyltransferase; Acidosis; Amino Acid Metabolism, Inborn Errors; Cell Line, Transformed; Child; Coenzyme A-Transferases; Consanguinity; Glycine; Humans; Infant, Newborn; Isoleucine; Japan; Ketone Bodies; Lymphocytes; Male; Nuclear Family | 1996 |
Correction of acidosis in dialysis patients increases branched-chain and total essential amino acid levels in muscle.
Topics: Acidosis; Adult; Aged; Aged, 80 and over; Amino Acids, Branched-Chain; Amino Acids, Essential; Bicarbonates; Dialysis; Female; Humans; Isoleucine; Leucine; Male; Middle Aged; Muscle, Skeletal; Valine | 1997 |
Mechanisms contributing to muscle-wasting in acute uremia: activation of amino acid catabolism.
Topics: 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide); Acidosis; Acute Disease; Administration, Oral; Amino Acids; Animals; Carbonates; Enzyme Activation; Isoenzymes; Isoleucine; Ketone Oxidoreductases; Male; Mitochondria; Multienzyme Complexes; Muscle, Skeletal; Rats; Rats, Sprague-Dawley; RNA, Messenger; Transfer RNA Aminoacylation; Uremia; Valine; Wasting Syndrome | 1998 |
Infectious complications of propionic acidemia in Saudia Arabia.
Topics: Acidosis; Humans; Infant; Infections; Isoleucine; Metabolism, Inborn Errors; Retrospective Studies; Saudi Arabia | 1998 |
Leucine and protein metabolism in rats with chronic renal insufficiency.
Topics: Acidosis; Animals; Body Weight; Cholesterol; Creatinine; Disease Models, Animal; Eating; Isoleucine; Kidney Failure, Chronic; Leucine; Male; Muscle, Skeletal; Nephrectomy; Proteins; Rats; Rats, Wistar; Urea; Uremia; Valine | 2001 |
Acetoacetyl CoA thiolase deficiency: a cause of severe ketoacidosis in infancy simulating salicylism.
Topics: Acetoacetates; Acetyl-CoA C-Acetyltransferase; Acetyltransferases; Acidosis; Adolescent; Carbon Dioxide; Child, Preschool; Chromatography, Gas; Deficiency Diseases; Diagnosis, Differential; Fatty Acids; Female; Humans; Isoleucine; Ketone Bodies; Ketosis; Mass Spectrometry; Oxidation-Reduction; Salicylates | 1979 |
Accumulation of 3-hydroxyisobutyric acid, 2-methyl-3-hydroxybutyric acid and 3-hydroxyisovaleric acid in ketoacidosis.
Topics: Acetates; Acidosis; Animals; Child; Child, Preschool; Chromatography, Gas; Diabetes Mellitus; Diabetic Ketoacidosis; Glutarates; Humans; Hydroxy Acids; Hydroxybutyrates; Infant; Isoleucine; Leucine; Male; Mass Spectrometry; Rats; Streptozocin; Valerates; Valine | 1975 |
Propionyl-CoA carboxylase deficiency with overflow of metabolites of isoleucine catabolism at all levels.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Carboxy-Lyases; Child; Female; Fibroblasts; Humans; Intellectual Disability; Isoleucine; Muscle Spasticity; Paraplegia | 1979 |
[A form of late propionic acidemia].
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Blood Glucose; Child, Preschool; Coma; Dietary Proteins; Female; Humans; Isoleucine; Leucine; Male; Neurologic Manifestations; Propionates | 1975 |
[Intermittent branched--chain ketoacidurie in ketotic hypoglycemia: investigations to localize the biochemical defect (author's transl)].
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child; Female; Fibroblasts; Humans; Hypoglycemia; Intellectual Disability; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Valine | 1976 |
Biotin-responsive propionicacidaemia.
Topics: Acidosis; Biotin; Carboxy-Lyases; Child, Preschool; Chromatography, Gas; Diet Therapy; Glycine; Humans; Isoleucine; Ketones; Ligases; Male; Metabolism, Inborn Errors; Phosphotransferases; Propionates | 1970 |
Glycemic response to 24-hour fast in normal children and children with ketotic hypoglycemia: II. Hormonal and metabolic changes.
Topics: Acidosis; Alanine; Amino Acids; Autoanalysis; Blood Glucose; Child; Child, Preschool; Fasting; Fatty Acids, Nonesterified; Female; Glucagon; Growth Hormone; Hormones; Humans; Hydrocortisone; Hypoglycemia; Insulin; Isoleucine; Ketones; Ketosis; Leucine; Male; Valine | 1974 |
3-hydroxypropionate: significance of -oxidation of propionate in patients with propionic acidemia and methylmalonic acidemia.
Topics: Acidosis; Carbon Isotopes; Chromatography; Chromatography, Paper; Citrates; Humans; Hydroxylation; Injections, Intravenous; Isoleucine; Malonates; Mass Spectrometry; Metabolism, Inborn Errors; Oxidation-Reduction; Propionates; Valine | 1972 |
Hyperalimentation in cirrhotic patients.
Topics: Acid-Base Equilibrium; Acidosis; Alanine Transaminase; Alkaline Phosphatase; Amino Acids; Ammonia; Arginine; Carbon Dioxide; Caseins; Catheterization; Cysteine; Diet Therapy; Fibrin; Glutamine; Glycine; Histidine; Humans; Isoleucine; Leucine; Liver; Liver Cirrhosis; Lysine; Methionine; Parenteral Nutrition; Phenylalanine; Potassium; Sodium; Threonine; Tryptophan | 1972 |
Hyperglycinemia with ketosis due to a defect in isoleucine metabolism: a preliminary report.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Diet Therapy; Dietary Proteins; Female; Fibroblasts; Glycine; Humans; Infant; Isoleucine; Syndrome | 1972 |
An inherited disorder of isoleucine catabolism causing accumulation of alpha-methylacetoacetate and alpha-methyl-beta -hydroxybutyrate, and intermittent metabolic acidosis.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Butyrates; Cells, Cultured; Child; Child, Preschool; Chromatography, Gas; Chromatography, Paper; Chromatography, Thin Layer; Female; Fibroblasts; Glycine; Humans; Hydroxybutyrates; Infant; Isoleucine; Keto Acids; Ketones; Male; Mass Spectrometry; Mutation; Pedigree; Phenotype; Skin; Valerates | 1973 |
Response to dietary therapy in B 12 unresponsive methylmalonic acidemia.
Topics: Acidosis; Agranulocytosis; Blood Glucose; Cephalometry; Child Development; Diet Therapy; Electroencephalography; Female; Growth Disorders; Humans; Infant; Intelligence; Isoleucine; Lymphocytosis; Malonates; Metabolism, Inborn Errors; Methionine; Otitis Media; Threonine; Valine; Vitamin B 12 | 1973 |
Beta-ketothiolase deficiency as a cause of the "ketotic hyperglycinemia syndrome".
Topics: Acetoacetates; Acidosis; Acyltransferases; Amino Acid Metabolism, Inborn Errors; Butanones; Carbon Radioisotopes; Child; Chromatography, Thin Layer; Coenzyme A; Dinitrophenols; Fibroblasts; Glycine; Humans; Hydrazones; Hydroxybutyrates; Isoleucine; Malonates; Propionates | 1974 |
Hypoglycin A: a specific inhibitor of isovaleryl CoA dehydrogenase.
Topics: Acidosis; Alanine; Amino Acid Metabolism, Inborn Errors; Animals; Butyrates; Caproates; Carbon Dioxide; Carbon Isotopes; Carnitine; Chromatography, Gas; Coenzyme A; Cyclopropanes; In Vitro Techniques; Isoleucine; Leucine; Male; Oxidoreductases; Plant Poisoning; Rats; Valerates; Vomiting | 1971 |
Vitamin B12-dependent methylmalonicaciduria: amino acid toxicity, long chain ketonuria, and protective effect of vitamin B12.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Coenzyme A; Diet Therapy; Dietary Proteins; Humans; Isoleucine; Ketones; Leucine; Leukocytes; Male; Malonates; Methionine; Nutritional Requirements; Propionates; Threonine; Valine; Vitamin B 12 | 1970 |