Page last updated: 2024-10-19

inositol and Adult Refsum Disease

inositol has been researched along with Adult Refsum Disease in 10 studies

Inositol: An isomer of glucose that has traditionally been considered to be a B vitamin although it has an uncertain status as a vitamin and a deficiency syndrome has not been identified in man. (From Martindale, The Extra Pharmacopoeia, 30th ed, p1379) Inositol phospholipids are important in signal transduction.
inositol : Any cyclohexane-1,2,3,4,5,6-hexol.
1D-chiro-inositol : Belonging to the inositol family of compounds, D-chiro-inositol (DCI) is an isomer of glucose. It is an important secondary messenger in insulin signal transduction.
muco-inositol : An inositol that is cyclohexane-1,2,3,4,5,6-hexol having a (1R,2R,3r,4R,5S,6r)-configuration.

Research

Studies (10)

TimeframeStudies, this research(%)All Research%
pre-199010 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Dubois-Dalcq, M1
Menu, R1
Buyse, M1
Kayden, HJ1
Reagan, TJ1
Mize, CE1
Herndon, JH1
Steinberg, D2
Kahlke, W2
Wagener, H2
Dieckmann, H1
ThiƩbaut, F1
Kremer, GJ1
Refsum, S1
Blass, JP1
Avign, J1
Wolf, LM1
Laudat, P1
Chaumont, P1
Bonduelle, M1
Thiele, OW1

Other Studies

10 other studies available for inositol and Adult Refsum Disease

ArticleYear
Influence of fatty acids on fine structure of cultured neurons. An experimental approach to Refsum's disease.
    Journal of neuropathology and experimental neurology, 1972, Volume: 31, Issue:4

    Topics: Animals; Culture Techniques; Fatty Acids; Ganglia, Spinal; Inositol; Microscopy, Electron; Nerve Deg

1972
Diffuse cerebral sclerosis erroneously reported as Refsum's syndrome.
    Archives of neurology, 1973, Volume: 28, Issue:5

    Topics: Adult; Brain; Carbon Isotopes; Cerebral Cortex; Demyelinating Diseases; Diagnosis, Differential; Dif

1973
[Studies on the phytol metabolism in lipoidosis heredopathia atactica polyneuritiformis (Refsum's syndrome). The transformation of 3H-phytol into the 3,7,11,15-tetramethylhexadecanoic acid (phytanic acid) of the plasma lipoid fractions].
    Klinische Wochenschrift, 1965, Dec-15, Volume: 43, Issue:24

    Topics: Chromatography, Gas; Fatty Acids; Humans; Inositol; Phospholipids; Refsum Disease; Terpenes; Triglyc

1965
[Discussion apropos of the communication of Messrs. Bonduelle and collaborators, concerning Refsum's syndrome].
    Revue neurologique, 1966, Volume: 115, Issue:5

    Topics: Chromatography; Humans; Inositol; Refsum Disease

1966
Conversion of H3-phytol to phytanic acid and its incorporation into plasma lipid fractions in heredopathia atactica polyneuritiformis.
    Metabolism: clinical and experimental, 1966, Volume: 15, Issue:8

    Topics: Cholesterol; Chromatography, Gas; Fatty Acids; Glycerides; Humans; Inositol; Lipids; Phospholipids;

1966
[Lipid studies in organs of a child with Refsum's syndrome].
    Klinische Wochenschrift, 1966, Sep-15, Volume: 44, Issue:18

    Topics: Blood Chemical Analysis; Child, Preschool; Chromatography, Gas; Fatty Acids; Feces; Freeze Drying; H

1966
[Diagnosis and differential diagnosis of heredopathia atactica polyneuritiformis].
    Deutsche Zeitschrift fur Nervenheilkunde, 1969, Volume: 195, Issue:4

    Topics: Diagnosis, Differential; Humans; Inositol; Polyneuropathies; Refsum Disease

1969
Alpha-hydroxy fatty acids in hereditary ataxic polyneuritis (Refsum's disease).
    Biochimica et biophysica acta, 1969, Jul-29, Volume: 187, Issue:1

    Topics: Animals; Biopsy; Brain; Carbon Isotopes; Diet; Fatty Acids; Female; Humans; Inositol; Male; Myelin S

1969
[Refsum's disease. Clinical and biochemical evolution under a phytol-free diet. Complementary biochemical studies. Supplement of the 1966 report].
    Revue neurologique, 1969, Volume: 120, Issue:2

    Topics: Adult; Biopsy; Child; Demyelinating Diseases; Denervation; Diet; Female; Follow-Up Studies; Humans;

1969
[Refsum's syndrome (Heredopathia atactica polyneuritiformis) and phytic acid].
    Hippokrates, 1970, Volume: 41, Issue:2

    Topics: Animals; Chemical Phenomena; Chemistry; Humans; Inositol; Rats; Refsum Disease

1970