i(3)so3-galactosylceramide and Niemann-Pick-Diseases

i(3)so3-galactosylceramide has been researched along with Niemann-Pick-Diseases* in 11 studies

Reviews

3 review(s) available for i(3)so3-galactosylceramide and Niemann-Pick-Diseases

ArticleYear
Disorders of lipid metabolism.
    Biochemical Society symposium, 1972, Issue:35

    Topics: Adult; Animals; Bone Marrow; Cell Line; Ceramides; Child; Fabry Disease; Fucose; Galactose; Gangliosides; Gaucher Disease; Genetic Variation; Glycolipids; Glycoside Hydrolases; Humans; Leukemia, Myeloid; Leukodystrophy, Globoid Cell; Leukodystrophy, Metachromatic; Lipid Metabolism, Inborn Errors; Lipidoses; Mice; Niemann-Pick Diseases; Sulfoglycosphingolipids

1972
[Biochemical aspects of sphingolipidosis].
    Annales de biologie clinique, 1972, Volume: 30, Issue:6

    Topics: Ceramides; Diffuse Cerebral Sclerosis of Schilder; Female; Galactosidases; Gangliosides; Gaucher Disease; Glucosidases; Glycolipids; Humans; Lipid Metabolism, Inborn Errors; Lipidoses; Male; Niemann-Pick Diseases; Pregnancy; Pregnancy Complications; Sphingolipids; Sphingomyelins; Sphingosine; Sulfoglycosphingolipids

1972
Sphingolipid metabolism in neural tissues.
    Neurosciences research, 1969, Volume: 2, Issue:0

    Topics: Animals; Brain; Carbon Radioisotopes; Cerebrosides; Gangliosides; Humans; Leukodystrophy, Globoid Cell; Leukodystrophy, Metachromatic; Lipidoses; Nervous System; Niemann-Pick Diseases; Rabbits; Sphingolipids; Sphingomyelins; Sphingosine; Sulfoglycosphingolipids

1969

Other Studies

8 other study(ies) available for i(3)so3-galactosylceramide and Niemann-Pick-Diseases

ArticleYear
[Clinical-, histoenzymological-, ultrastructural-, biochemical study of one case of Niemann-Pick disease (B form) (author's transl)].
    Acta histochemica, 1977, Volume: 59, Issue:1

    Topics: Adult; Fatty Acids; Female; Follow-Up Studies; Gangliosides; Glycosaminoglycans; Humans; Hydrolases; Infant; Lipid Metabolism; Liver; Macrophages; Niemann-Pick Diseases; Phospholipids; Sulfoglycosphingolipids

1977
Unusual glycolipids in brain cortex of a visceral lipidosis (Niemann-Pick disease?).
    Hoppe-Seyler's Zeitschrift fur physiologische Chemie, 1974, Volume: 355, Issue:5

    Topics: Brain Chemistry; Ceramides; Cerebral Cortex; Cerebrosides; Child; Cholesterol; Chromatography; Chromatography, Gas; Chromatography, Thin Layer; Fatty Acids; Female; Gangliosides; Glycolipids; Hexoses; Humans; Lipidoses; Lipids; Male; Niemann-Pick Diseases; Sulfoglycosphingolipids

1974
Inborn errors of lipid metabolism.
    Advances in enzymology and related areas of molecular biology, 1973, Volume: 38

    Topics: Ceramides; Cerebrosides; Fabry Disease; Fucose; Galactosidases; Gaucher Disease; Glycolipids; Glycoside Hydrolases; Hexosaminidases; Humans; Leukodystrophy, Globoid Cell; Leukodystrophy, Metachromatic; Lipid Metabolism, Inborn Errors; Lipidoses; Neuraminic Acids; Niemann-Pick Diseases; Organ Specificity; Sphingomyelins; Sulfoglycosphingolipids

1973
The adnormal biochemistry of inherited disorders of lipid metabolism.
    Federation proceedings, 1973, Volume: 32, Issue:6

    Topics: Brain; Ceramides; Cerebrosides; Diffuse Cerebral Sclerosis of Schilder; Female; Fibroblasts; Galactose; Galactosidases; Gaucher Disease; Glucose; Glycolipids; Glycoside Hydrolases; Hexosaminidases; Humans; Intestines; Kidney; Leukocytes; Lipid Metabolism, Inborn Errors; Lipidoses; Liver; Male; Muscles; Niemann-Pick Diseases; Phosphoric Diester Hydrolases; Sphingomyelins; Spleen; Sulfoglycosphingolipids; Syndrome

1973
Brain lipids of a case of juvenile Niemann-Pick disease.
    Journal of neurochemistry, 1973, Volume: 21, Issue:6

    Topics: Aldehydes; Brain Chemistry; Ceramides; Cerebral Cortex; Cerebrosides; Child; Chromatography, Gas; Chromatography, Thin Layer; Dialysis; Fatty Acids; Female; Humans; Lipids; Male; Niemann-Pick Diseases; Phospholipids; Plasmalogens; Sphingomyelins; Sulfoglycosphingolipids

1973
[The cherry-red spot of the macula as the manifestation of a storage disease].
    Klinische Monatsblatter fur Augenheilkunde, 1972, Volume: 161, Issue:2

    Topics: Child; Diffuse Cerebral Sclerosis of Schilder; Eye Manifestations; Gangliosides; Humans; Infant, Newborn; Intellectual Disability; Lipid Metabolism, Inborn Errors; Lipidoses; Lipopolysaccharides; Macula Lutea; Male; Niemann-Pick Diseases; Pigmentation Disorders; Respiratory Distress Syndrome, Newborn; Sphingolipids; Sphingomyelins; Sulfoglycosphingolipids; Syndrome

1972
[Enzyme defects of fat metabolism].
    Wiener klinische Wochenschrift, 1971, Sep-03, Volume: 83, Issue:35

    Topics: Diffuse Cerebral Sclerosis of Schilder; Galactosidases; Gaucher Disease; Glycolipids; Humans; Lipid Metabolism, Inborn Errors; Lipidoses; Lipoprotein Lipase; Niemann-Pick Diseases; Refsum Disease; Sulfoglycosphingolipids; Triglycerides

1971
An autopsy case of metachromatic leucodystrophy.
    Acta pathologica japonica, 1971, Volume: 21, Issue:3

    Topics: Adrenal Medulla; Autopsy; Brain Chemistry; Cholesterol; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Gallbladder; Gaucher Disease; Histocytochemistry; Humans; Kidney; Lipidoses; Lipids; Liver; Microscopy, Electron; Mucopolysaccharidoses; Niemann-Pick Diseases; Pancreas; Phospholipids; Sulfoglycosphingolipids

1971