i(3)so3-galactosylceramide has been researched along with Adrenal-Insufficiency* in 2 studies
2 other study(ies) available for i(3)so3-galactosylceramide and Adrenal-Insufficiency
| Article | Year |
|---|---|
Reverse phase high-performance liquid chromatography of cerebrosides,sulfatides, and ceramides: microanalysis of homolog composition without hydrolysis and application to cerebroside analysis in peripheral nerves of adrenoleukodystrophy pateints.
Topics: Adrenal Insufficiency; Ceramides; Cerebrosides; Chromatography, Gas; Chromatography, High Pressure Liquid; Fatty Acids; Humans; Microchemistry; Peripheral Nerves; Structure-Activity Relationship; Sulfoglycosphingolipids | 1980 |
Galactolipid fatty acid composition in adrenoleukodystrophy.
The non-hydroxy and hydroxy fatty acids of the major brain galactosphingolipids, cerebroside and sulphatide, have been isolated from white matter, gray matter and myelin of 2 children with adrenoleukodystrophy and from a corresponding control. In addition, cerebroside fatty acids were recovered from a myelin-related fraction on 1 patient. In comparison to control observations, myelin and the myelin-related fraction cerebroside demonstrate a loss of C24:1 and C24h:o fatty acids from normal and hydroxy fatty acid fractions, respectively. White and gray matter galactolipids isolated from 1 patient indicated a signficant increase in short chain (C16, C18 and C18:1) non-hydroxy fatty acids. In the isolated diseased myelin, the ratio of cerebroside hydroxy to non-hydroxy fatty acids was elevated about 1.5 times above the value for normal myelin, whereas the ratio derived for the myelin-related fraction was about two-thirds the values for the control myelin cerebroside. Topics: Adrenal Insufficiency; Brain Chemistry; Brain Diseases; Cerebrosides; Child; Fatty Acids; Humans; Myelin Sheath; Sulfoglycosphingolipids | 1977 |