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hydroxyproline and Pseudoxanthoma Elasticum

hydroxyproline has been researched along with Pseudoxanthoma Elasticum in 12 studies

Hydroxyproline: A hydroxylated form of the imino acid proline. A deficiency in ASCORBIC ACID can result in impaired hydroxyproline formation.
hydroxyproline : A proline derivative that is proline substituted by at least one hydroxy group.

Pseudoxanthoma Elasticum: An inherited disorder of connective tissue with extensive degeneration and calcification of ELASTIC TISSUE primarily in the skin, eye, and vasculature. At least two forms exist, autosomal recessive and autosomal dominant. This disorder is caused by mutations of one of the ATP-BINDING CASSETTE TRANSPORTERS. Patients are predisposed to MYOCARDIAL INFARCTION and GASTROINTESTINAL HEMORRHAGE.

Research Excerpts

ExcerptRelevanceReference
"Hydroxyproline content was reduced approximately 46% and 24% in cases 1 and 2, respectively."1.29Biochemical analyses of macromolecular matrix components in patients with pseudoxanthoma elasticum. ( Nishikawa, T; Sakuraoka, K; Seyama, Y; Tajima, S, 1994)

Research

Studies (12)

TimeframeStudies, this research(%)All Research%
pre-199011 (91.67)18.7374
1990's1 (8.33)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Sakuraoka, K1
Tajima, S1
Nishikawa, T1
Seyama, Y1
Uitto, J2
Lambert, D1
Dubost, M1
Mugneret, F1
Justrabo, E1
Putelat, R1
Chapuis, JL1
Blumenkrantz, N2
Danielsen, L3
Asboe-Hansen, G2
Alinder, I1
Boström, H1
Langness, U1
Kreysel, HW3
Thiel, HJ1
Paetzold, OH1
Gnoyke, U1
Köhler, N1
Mikol, F1
Mikol, J1
Leclere, J1
Lindy, S1
Turto, H1
Korting, GW1
Holzmann, H1

Reviews

1 review available for hydroxyproline and Pseudoxanthoma Elasticum

ArticleYear
Biochemistry of the elastic fibers in normal connective tissues and its alterations in diseases.
    The Journal of investigative dermatology, 1979, Volume: 72, Issue:1

    Topics: Amino Acids; Arteriosclerosis; Chemical Phenomena; Chemistry; Collagen Diseases; Connective Tissue;

1979

Other Studies

11 other studies available for hydroxyproline and Pseudoxanthoma Elasticum

ArticleYear
Biochemical analyses of macromolecular matrix components in patients with pseudoxanthoma elasticum.
    The Journal of dermatology, 1994, Volume: 21, Issue:2

    Topics: Adult; Collagen; Elastin; Extracellular Matrix; Female; Glycosaminoglycans; Humans; Hydroxyproline;

1994
[Elastic pseudoxanthoma associated with lipid metabolism disorders].
    La Nouvelle presse medicale, 1975, Apr-12, Volume: 4, Issue:15

    Topics: Alkaline Phosphatase; Child; Cholesterol; Diabetes Complications; Diabetes Mellitus; Glucose Toleran

1975
Biosynthesis of collagen in pseudoxanthoma elasticum.
    Acta dermato-venereologica, 1973, Volume: 53, Issue:6

    Topics: Adult; Biopsy; Carbon Radioisotopes; Collagen; Connective Tissue; Glutamine; Humans; Hydroxylysine;

1973
Biosynthesis of elastin pseudoxanthoma elasticum.
    Acta dermato-venereologica, 1973, Volume: 53, Issue:6

    Topics: Biopsy; Carbon Radioisotopes; Elastin; Glutamine; Humans; Hydroxyproline; Microbial Collagenase; Pro

1973
Clinical studies on a Swedish material of pseudoxanthoma elasticum.
    Acta medica Scandinavica, 1972, Volume: 191, Issue:4

    Topics: Adolescent; Adult; Aged; Angina Pectoris; Angioid Streaks; Cardiomegaly; Child; Child, Preschool; El

1972
[The pathogenesis of Darier-Grönblad-Strandberg syndrome (author's transl)].
    Klinische Wochenschrift, 1974, Feb-15, Volume: 52, Issue:4

    Topics: Adolescent; Adult; Age Factors; Angioid Streaks; Child; Collagen; Creatinine; Glycosaminoglycans; Hu

1974
[Clinical significance of urinary hydroxyproline excretion].
    Die Medizinische Welt, 1973, Oct-26, Volume: 24, Issue:43

    Topics: Dermatomyositis; Humans; Hydroxyproline; Lupus Erythematosus, Systemic; Middle Aged; Pseudoxanthoma

1973
[Clinical aspects of collagen like protein in sera (author's transl)].
    Archiv fur dermatologische Forschung, 1974, Volume: 249, Issue:1

    Topics: Blood Proteins; Collagen; Collagen Diseases; Dermatomyositis; Humans; Hydroxyproline; Pseudoxanthoma

1974
[Aneurysmal dilatations of the internal carotid arteries and cutaneous calcinosis during systemic elastorrhexis. Trial treatment with calcitonin].
    Annales de medecine interne, 1974, Volume: 125, Issue:3

    Topics: Adult; Alkaline Phosphatase; Aneurysm; Angioid Streaks; Bone and Bones; Calcinosis; Calcitonin; Calc

1974
Biochemical characterization of pseudoxanthoma elasticum: collagen biosynthesis in the skin.
    The Journal of investigative dermatology, 1971, Volume: 57, Issue:1

    Topics: Adult; Biopsy; Carbon Isotopes; Collagen; Culture Techniques; DNA; Female; Humans; Hydroxyproline; M

1971
[On humoral collagen-hints in pseudoxanthoma elasticum].
    Archiv fur klinische und experimentelle Dermatologie, 1968, May-09, Volume: 231, Issue:4

    Topics: Adult; Collagen Diseases; Hexosamines; Humans; Hydroxyproline; Male; Pseudoxanthoma Elasticum

1968