Page last updated: 2024-10-17

hydrogen sulfide and CBS Deficiency

hydrogen sulfide has been researched along with CBS Deficiency in 5 studies

Hydrogen Sulfide: A flammable, poisonous gas with a characteristic odor of rotten eggs. It is used in the manufacture of chemicals, in metallurgy, and as an analytical reagent. (From Merck Index, 11th ed)
hydrogen sulfide : A sulfur hydride consisting of a single sulfur atom bonded to two hydrogen atoms. A highly poisonous, flammable gas with a characteristic odour of rotten eggs, it is often produced by bacterial decomposition of organic matter in the absence of oxygen.
thiol : An organosulfur compound in which a thiol group, -SH, is attached to a carbon atom of any aliphatic or aromatic moiety.

Research Excerpts

ExcerptRelevanceReference
"Animal models of CBS deficiency have provided invaluable insights into the pathological effects of transsulfuration impairment and of both mild and severe HHcy."2.47Vascular complications of cystathionine β-synthase deficiency: future directions for homocysteine-to-hydrogen sulfide research. ( Beard, RS; Bearden, SE, 2011)

Research

Studies (5)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's3 (60.00)24.3611
2020's2 (40.00)2.80

Authors

AuthorsStudies
Nakladal, D1
Lambooy, SPH1
Mišúth, S1
Čepcová, D1
Joschko, CP1
van Buiten, A1
Goris, M1
Hoogstra-Berends, F1
Kloosterhuis, NJ1
Huijkman, N1
van de Sluis, B1
Diercks, GF1
Buikema, JH1
Henning, RH1
Deelman, LE1
Kožich, V2
Stabler, S1
Krijt, J1
Sokolová, J1
Melenovská, P1
Ješina, P1
Vozdek, R1
Majtán, T1
Kraus, JP1
Kabe, Y1
Yamamoto, T1
Kajimura, M1
Sugiura, Y1
Koike, I1
Ohmura, M1
Nakamura, T1
Tokumoto, Y1
Tsugawa, H1
Handa, H1
Kobayashi, T1
Suematsu, M1
Beard, RS1
Bearden, SE1

Reviews

3 reviews available for hydrogen sulfide and CBS Deficiency

ArticleYear
Lessons Learned from Inherited Metabolic Disorders of Sulfur-Containing Amino Acids Metabolism.
    The Journal of nutrition, 2020, 10-01, Volume: 150, Issue:Suppl 1

    Topics: Amino Acids, Sulfur; Animals; Brain Diseases; Cysteine; Glutathione; Homocysteine; Homocystinuria; H

2020
Cystathionine β-synthase and PGRMC1 as CO sensors.
    Free radical biology & medicine, 2016, Volume: 99

    Topics: Animals; Carbon Monoxide; Cystathionine beta-Synthase; Cytochrome P-450 Enzyme System; ErbB Receptor

2016
Vascular complications of cystathionine β-synthase deficiency: future directions for homocysteine-to-hydrogen sulfide research.
    American journal of physiology. Heart and circulatory physiology, 2011, Volume: 300, Issue:1

    Topics: Animals; Disease Models, Animal; Homocysteine; Homocystinuria; Humans; Hydrogen Sulfide; Mice; Vascu

2011

Other Studies

2 other studies available for hydrogen sulfide and CBS Deficiency

ArticleYear
Homozygous whole body Cbs knockout in adult mice features minimal pathology during ageing despite severe homocysteinemia.
    FASEB journal : official publication of the Federation of American Societies for Experimental Biology, 2022, Volume: 36, Issue:4

    Topics: Aging; Alopecia; Animals; Cystathionine beta-Synthase; Disease Models, Animal; Female; Homocystinuri

2022
Thioethers as markers of hydrogen sulfide production in homocystinurias.
    Biochimie, 2016, Volume: 126

    Topics: Alanine; Cells, Cultured; Cystathionine; Cystathionine beta-Synthase; Female; Fibroblasts; Homocysti

2016