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hydrogen carbonate and Adult Fanconi Syndrome

hydrogen carbonate has been researched along with Adult Fanconi Syndrome in 39 studies

Bicarbonates: Inorganic salts that contain the -HCO3 radical. They are an important factor in determining the pH of the blood and the concentration of bicarbonate ions is regulated by the kidney. Levels in the blood are an index of the alkali reserve or buffering capacity.
hydrogencarbonate : The carbon oxoanion resulting from the removal of a proton from carbonic acid.

Research Excerpts

ExcerptRelevanceReference
"The development of renal tubular acidosis in this condition further impairs renal function and we suggest that correction of systemic acidosis might improve renal function and prevent further decline in these patients."2.38Renal failure in adult onset hypophosphatemic osteomalacia with Fanconi syndrome: a family study and review of the literature. ( Bateman, JM; Harrison, NA; Ledingham, JG; Smith, R, 1991)
"Proximal renal tubular acidosis (pRTA) is characterized by a defect in the ability of the proximal convoluted tubule to reabsorb bicarbonate."1.91Rickets in proximal renal tubular acidosis: a case series of six distinct etiologies. ( Agrawal, N; Bhattacharjee, R; Chakraborty, PP; Das, D; Deshpande, A; Dhar, A; Roy, A; Singhania, P, 2023)
"Zoledronic acid (ZA) is an antiresorptive agent typically used for fracture prevention in postmenopausal osteoporosis, malignancy-associated metastatic bone lesions, and as a treatment for hypercalcemia."1.72Zoledronic Acid-Associated Fanconi Syndrome in Patients With Cancer. ( Gupta, S; Mount, DB; Nigwekar, SU; Portales-Castillo, I; Rennke, HG; Yu, EW, 2022)
"A boy with Lowe syndrome who manifested renal Fanconi syndrome by severe hypophosphatemic rickets, failure to thrive, and metabolic acidosis failed to improve with conventional bolus therapy of phosphate and bicarbonate."1.28Severe rickets in Lowe syndrome: treatment with continuous nasogastric infusion. ( Mimouni, F; Redfield, VA; Strife, FC; Tsang, RC, 1991)
"Osteomalacia was shown by a radiological bone survey."1.25Fanconi's syndrome in an adult. A case history. ( Naidoo, PM, 1975)
"Renal tubular acidosis has persisted in all four patients for at least 3 yr, and in three for 4 years."1.25Renal tubular acidosis in infants: the several kinds, including bicarbonate-wasting, classic renal tubular acidosis. ( McSherry, E; Morris, RC; Sebastian, A, 1972)

Research

Studies (39)

TimeframeStudies, this research(%)All Research%
pre-199029 (74.36)18.7374
1990's6 (15.38)18.2507
2000's1 (2.56)29.6817
2010's1 (2.56)24.3611
2020's2 (5.13)2.80

Authors

AuthorsStudies
Portales-Castillo, I1
Mount, DB1
Nigwekar, SU1
Yu, EW1
Rennke, HG1
Gupta, S1
Singhania, P1
Dhar, A1
Deshpande, A1
Das, D1
Agrawal, N1
Chakraborty, PP1
Bhattacharjee, R1
Roy, A1
Lee, JJ1
Tripi, LM1
Erbe, RW1
Garimella-Krovi, S1
Springate, JE1
Sanaka, T1
Justado Ruiz-Capillas, JJ1
García Puig, J1
Molina, F1
García Delgado, E1
Arnalich, F1
Mateos Antón, F1
Vázquez, JJ1
McSherry, E4
Szczepańska, M1
Angielski, S2
Segal, LS1
Palumbo, RC1
Robertson, WW1
Nissim, I1
Weinberg, JM1
Haffner, D1
Weinfurth, A1
Seidel, C1
Manz, F1
Schmidt, H1
Waldherr, R1
Bremer, HJ1
Mehls, O1
Schärer, K1
Rogulski, J1
Lameire, N1
Mussche, M1
Baele, G1
Kint, J1
Ringoir, S1
Naidoo, PM1
Arant, BS1
Greifer, I1
Edelmann, CM2
Spitzer, A1
Harrison, NA1
Bateman, JM1
Ledingham, JG1
Smith, R1
Redfield, VA1
Mimouni, F1
Strife, FC1
Tsang, RC1
Nishinakamura, R1
Kurokawa, K1
Gougoux, A1
Zan, N1
Dansereau, D1
Vinay, P1
Itoh, K1
Komatsu, Y1
Wen, SF1
Friedman, AL1
Oberley, TD1
Kitagawa, T1
Oowada, M1
Santos-Atherton, D1
Frenk, S1
Pronicka, E1
Rowińska, E1
Miłoszewska, E1
Shvil, Y1
Wald, H1
Popovtzer, MM1
Al-Bander, H1
Etheredge, SB1
Paukert, T1
Humphreys, MH1
Morris, RC6
Bennett, WM1
Hempel, KH1
Berland, JE1
Porter, GA1
Kokot, F1
Kalus-Witkowicz, H1
Shioji, R1
Sasaki, Y1
Hurukawa, Y1
Saito, H1
Michimata, Y1
Kamm, DE1
Fischer, MS1
Palma-Carlos, AG1
Martins Prata, M1
Gomes d'Oliveira, JJ1
Migueis-Clode, MH1
Rodriguez-Soriano, J1
Sebastian, A3
Lee, DB1
Drinkard, JP1
Rosen, VJ1
Gonick, HC1
Kranhold, JF1
Ueki, I1
Rampini, S1
Fanconi, A1
Illig, R1
Prader, A1
Houston, IB1

Reviews

7 reviews available for hydrogen carbonate and Adult Fanconi Syndrome

ArticleYear
[Carbonic anhydrase II deficiency and Fanconi syndrome: Pathogenesis, pathophysiology, and therapy].
    Nihon rinsho. Japanese journal of clinical medicine, 2006, Volume: 64 Suppl 2

    Topics: Acidosis, Renal Tubular; Alkalies; Bicarbonates; Bone Marrow Transplantation; Carbonic Anhydrase II;

2006
Renal tubular acidosis in childhood.
    Kidney international, 1981, Volume: 20, Issue:6

    Topics: Acidosis, Renal Tubular; Bicarbonates; Child; Child, Preschool; Collagen; Diet, Sodium-Restricted; E

1981
Renal failure in adult onset hypophosphatemic osteomalacia with Fanconi syndrome: a family study and review of the literature.
    Clinical nephrology, 1991, Volume: 35, Issue:4

    Topics: Acidosis, Renal Tubular; Adolescent; Adult; Bicarbonates; Child; Child, Preschool; Diabetes Complica

1991
[Inborn errors of metabolism and renal tubular acidosis].
    Nihon rinsho. Japanese journal of clinical medicine, 1985, Volume: 43, Issue:9

    Topics: Acidosis, Renal Tubular; Adenosine Triphosphate; Age Factors; Animals; Bicarbonates; Fanconi Syndrom

1985
[Hydrogen ion excretion by the kidneys--physiological and clinical aspects (author's transl)].
    Przeglad lekarski, 1974, Volume: 31, Issue:3

    Topics: Acid-Base Equilibrium; Acidosis, Renal Tubular; Ammonia; Bicarbonates; Body Fluids; Buffers; Carboni

1974
Renal tubular acidosis.
    Annual review of medicine, 1969, Volume: 20

    Topics: Acid-Base Equilibrium; Acidosis, Renal Tubular; Adult; Animals; Bicarbonates; Cataract; Child; Dogs;

1969
Renal tubular acidosis. Mechanisms, classification and implications.
    The New England journal of medicine, 1969, Dec-18, Volume: 281, Issue:25

    Topics: Acidosis, Renal Tubular; Adult; Bicarbonates; Carbohydrate Metabolism, Inborn Errors; Fanconi Syndro

1969

Trials

1 trial available for hydrogen carbonate and Adult Fanconi Syndrome

ArticleYear
Body growth in primary de Toni-Debré-Fanconi syndrome.
    Pediatric nephrology (Berlin, Germany), 1997, Volume: 11, Issue:1

    Topics: Adolescent; Bicarbonates; Body Height; Calcium; Child; Child, Preschool; Fanconi Syndrome; Female; G

1997

Other Studies

31 other studies available for hydrogen carbonate and Adult Fanconi Syndrome

ArticleYear
Zoledronic Acid-Associated Fanconi Syndrome in Patients With Cancer.
    American journal of kidney diseases : the official journal of the National Kidney Foundation, 2022, Volume: 80, Issue:4

    Topics: Acute Kidney Injury; Amino Acids; Bicarbonates; Bone Density Conservation Agents; Fanconi Syndrome;

2022
Rickets in proximal renal tubular acidosis: a case series of six distinct etiologies.
    Journal of pediatric endocrinology & metabolism : JPEM, 2023, Sep-26, Volume: 36, Issue:9

    Topics: Acid-Base Equilibrium; Acidosis; Acidosis, Renal Tubular; Bicarbonates; Child; Fanconi Syndrome; Hum

2023
A mitochondrial DNA deletion presenting with corneal clouding and severe Fanconi syndrome.
    Pediatric nephrology (Berlin, Germany), 2012, Volume: 27, Issue:5

    Topics: Acid-Base Imbalance; Acidosis; Bicarbonates; Child, Preschool; Corneal Opacity; DNA, Mitochondrial;

2012
[Monoclonal IgG lambda paraprotein, Fanconi's syndrome of the adult, and osteomalacia (author's transl)].
    Medicina clinica, 1981, May-10, Volume: 76, Issue:10

    Topics: Aged; Bicarbonates; Fanconi Syndrome; Female; Humans; Immunoglobulin G; Immunoglobulin lambda-Chains

1981
Prevention of maleate-induced tubular dysfunction by acetoacetate.
    The American journal of physiology, 1980, Volume: 239, Issue:1

    Topics: Acetoacetates; Animals; Bicarbonates; Calcium; Dose-Response Relationship, Drug; Fanconi Syndrome; G

1980
The development of rickets as a complication of chemotherapy for the treatment of Wilms' tumor.
    Orthopedics, 1995, Volume: 18, Issue:3

    Topics: Antineoplastic Combined Chemotherapy Protocols; Bicarbonates; Calcitriol; Child; Child, Preschool; F

1995
Glycine attenuates Fanconi syndrome induced by maleate or ifosfamide in rats.
    Kidney international, 1996, Volume: 49, Issue:3

    Topics: Administration, Oral; Animals; Bicarbonates; Blood Urea Nitrogen; Creatinine; Fanconi Syndrome; Glyc

1996
Metabolic studies in experimental renal dysfunction resulting from maleate administration.
    Current problems in clinical biochemistry, 1975, Volume: 4

    Topics: Acetoacetates; Animals; Bicarbonates; Calcium; Coenzyme A; Disease Models, Animal; Fanconi Syndrome;

1975
Hereditary fructose intolerance: a difficult diagnosis in the adult.
    The American journal of medicine, 1978, Volume: 65, Issue:3

    Topics: Acidosis, Renal Tubular; Adult; Age Factors; Bicarbonates; Carbohydrate Metabolism, Inborn Errors; C

1978
Fanconi's syndrome in an adult. A case history.
    South African medical journal = Suid-Afrikaanse tydskrif vir geneeskunde, 1975, Jul-19, Volume: 49, Issue:31

    Topics: Adult; Bicarbonates; Fanconi Syndrome; Female; Glycosuria; Humans; Hydrogen-Ion Concentration; Hypok

1975
Effect of chronic salt and water loading on the tubular defects of a child with Fanconi syndrome (cystinosis).
    Pediatrics, 1976, Volume: 58, Issue:3

    Topics: Absorption; Bicarbonates; Child, Preschool; Fanconi Syndrome; Humans; Kidney Tubules; Kidney Tubules

1976
Severe rickets in Lowe syndrome: treatment with continuous nasogastric infusion.
    Pediatric nephrology (Berlin, Germany), 1991, Volume: 5, Issue:6

    Topics: Acidosis; Bicarbonates; Child, Preschool; Fanconi Syndrome; Humans; Infusions, Parenteral; Intubatio

1991
[Physiopathology and treatment of kidney tubule disorders].
    Nihon Naika Gakkai zasshi. The Journal of the Japanese Society of Internal Medicine, 1990, Feb-10, Volume: 79, Issue:2

    Topics: Acidosis, Renal Tubular; Bartter Syndrome; Bicarbonates; Fanconi Syndrome; Humans; Hypophosphatemia,

1990
Experimental Fanconi's syndrome resulting from 4-pentenoate infusion in the dog.
    The American journal of physiology, 1989, Volume: 257, Issue:6 Pt 2

    Topics: Amino Acids; Animals; Bicarbonates; Blood Glucose; Dogs; Fanconi Syndrome; Fatty Acids, Monounsatura

1989
[Kidney tubular transport disorders. Fanconi syndrome].
    Nihon rinsho. Japanese journal of clinical medicine, 1989, Volume: 47, Issue:7

    Topics: Amino Acids; Bicarbonates; Fanconi Syndrome; Glucose; Humans; Kidney Tubules, Proximal; Phosphates

1989
Two case studies from a family with primary Fanconi syndrome.
    American journal of kidney diseases : the official journal of the National Kidney Foundation, 1989, Volume: 13, Issue:3

    Topics: Adolescent; Adult; Bicarbonates; Fanconi Syndrome; Female; Glomerular Filtration Rate; Humans; Hydro

1989
The functional response to furosemide in a case of de Toni-Debre-Fanconi disease.
    Acta endocrinologica. Supplementum, 1986, Volume: 279

    Topics: Adolescent; Amino Acids; Bicarbonates; Fanconi Syndrome; Furosemide; Glycosuria; Humans; Kidney Tubu

1986
Tubular function of kidney after galactose loading in two patients with glycogen storage disease type XL.
    Journal of inherited metabolic disease, 1987, Volume: 10, Issue:3

    Topics: Adolescent; Adult; Bicarbonates; Fanconi Syndrome; Galactose; Galactosemias; Glycogen Storage Diseas

1987
Effect of bicarbonate and phosphate on renal phosphate leak in experimental Fanconi syndrome.
    The American journal of physiology, 1987, Volume: 252, Issue:2 Pt 2

    Topics: Animals; Bicarbonates; Fanconi Syndrome; Injections, Intravenous; Kidney; Male; Natriuresis; Phospha

1987
Phosphate loading attenuates renal tubular dysfunction induced by maleic acid in the dog.
    The American journal of physiology, 1985, Volume: 248, Issue:4 Pt 2

    Topics: Acidosis, Renal Tubular; Amino Acids; Animals; Bicarbonates; Chlorides; Dogs; Fanconi Syndrome; Fema

1985
Renal tubular acidosis.
    Archives of internal medicine, 1968, Volume: 121, Issue:1

    Topics: Acidosis, Renal Tubular; Bicarbonates; Blood Urea Nitrogen; Chronic Disease; Electrolytes; Fanconi S

1968
Oral administration of sodium bicarbonate to patients with renal tubular acidosis.
    The Tohoku journal of experimental medicine, 1974, Volume: 114, Issue:1

    Topics: Acidosis, Renal Tubular; Administration, Oral; Adolescent; Adult; Aged; Bicarbonates; Fanconi Syndro

1974
Proximal renal tubular acidosis and the Fanconi syndrome in a patient with hypergammaglobulinemia.
    Nephron, 1972, Volume: 9, Issue:4

    Topics: Acidosis, Renal Tubular; Ammonium Chloride; Bicarbonates; Fanconi Syndrome; Female; Follow-Up Studie

1972
[Tubulopathies and amyloid disease: 2 cases of De Toni-Debré-Fanconi syndrome].
    La Nouvelle presse medicale, 1973, Feb-24, Volume: 2, Issue:8

    Topics: Acidosis, Renal Tubular; Amyloidosis; Bicarbonates; Calcium; Fanconi Syndrome; Glycosuria, Renal; Hu

1973
Renal tubular acidosis in infants: the several kinds, including bicarbonate-wasting, classic renal tubular acidosis.
    The Journal of clinical investigation, 1972, Volume: 51, Issue:3

    Topics: Acidosis, Renal Tubular; Bicarbonates; Carbon Dioxide; Child, Preschool; Fanconi Syndrome; Female; G

1972
The adult Fanconi syndrome: observations on etiology, morphology, renal function and mineral metabolism in three patients.
    Medicine, 1972, Volume: 51, Issue:2

    Topics: Adult; Bicarbonates; Biological Transport; Calcium; Fanconi Syndrome; Glycosuria; Humans; Ilium; Kid

1972
Modulation of proximal and distal tubule function in the Fanconi syndrome.
    Birth defects original article series, 1970, Volume: 6, Issue:3

    Topics: Acidosis, Renal Tubular; Adult; Bicarbonates; Child; Fanconi Syndrome; Glomerular Filtration Rate; H

1970
An experimental renal acidification defect in patients with hereditary fructose intolerance. II. Its distinction from classic renal tubular acidosis; its resemblance to the renal acidification defect associated with the Fanconi syndrome of children with c
    The Journal of clinical investigation, 1968, Volume: 47, Issue:7

    Topics: Acid-Base Equilibrium; Acidosis; Acidosis, Renal Tubular; Adolescent; Adult; Bicarbonates; Carbohydr

1968
Renal amyloidosis, nephrotic syndrome, and impaired renal tubular reabsorption of bicarbonate.
    Annals of internal medicine, 1968, Volume: 69, Issue:3

    Topics: Absorption; Acidosis, Renal Tubular; Adult; Amyloidosis; Bicarbonates; Fanconi Syndrome; Glycosuria;

1968
Effect of hydrochlorothiazide on proximal renal tubular acidosis in a patient with idiopathic "de toni-debré-fanconi syndrome".
    Helvetica paediatrica acta, 1968, Volume: 23, Issue:1

    Topics: Acidosis; Adolescent; Bicarbonates; Calcium; Fanconi Syndrome; Female; Humans; Hydrochlorothiazide;

1968
Fanconi's syndrome with renal salt wasting and alkalosis.
    Archives of disease in childhood, 1969, Volume: 44, Issue:233

    Topics: Alkalosis; Bicarbonates; Child, Preschool; Fanconi Syndrome; Humans; Kidney Tubules; Male; Sodium; S

1969