hydracrylic acid has been researched along with Propionic Acidemia in 6 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 6 (100.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Brunengraber, H; Chapman, KA; Cline, GW; Han, Y; Hess, JP; Tochtrop, GP; Wilson, KA; Zhang, GF; Zhang, M | 1 |
Bailey, C; Cantor, NL; Ernst, SL; Gappmaier, E; Longo, N; Pasquali, M; Price, LB | 1 |
Arnoux, JB; Barbier, V; Bonnefont, JP; Brassier, A; Canouï, P; de la Bâtie, CD; De Lonlay, P; Gobin, S; Guemann, AS; Habarou, F; Lacaille, F; Ottolenghi, C; Ouss, L; Pontoizeau, C; Roda, C; Valayannopoulos, V | 1 |
Baráth, Á; Baumgartner, MR; Fingerhut, R; Gramer, G; Hoffmann, GF; Klinke, G; Kölker, S; Monostori, P; Okun, JG; Richter, S | 1 |
Ah Mew, N; Chapman, KA; Wongkittichote, P | 1 |
Acquaviva, C; Arnoux, JB; Barbier, V; Benoist, JF; Boddaert, N; Bonnefont, JP; de Lonlay, P; Desguerre, I; Habarou, F; Nizon, M; Ottolenghi, C; Rabier, D; Touati, G; Valayannopoulos, V | 1 |
1 review(s) available for hydracrylic acid and Propionic Acidemia
Article | Year |
---|---|
Propionyl-CoA carboxylase - A review.
Topics: Carbon-Carbon Ligases; Humans; Hyperammonemia; Lactic Acid; Methylmalonyl-CoA Decarboxylase; Mutation; Propionic Acidemia; Structure-Activity Relationship | 2017 |
1 trial(s) available for hydracrylic acid and Propionic Acidemia
Article | Year |
---|---|
Anaplerotic therapy in propionic acidemia.
Topics: Amino Acids; Ammonia; Carbon-Carbon Ligases; Child; Child, Preschool; Citrates; Citric Acid; Citric Acid Cycle; Dietary Supplements; Female; Glutamine; Humans; Lactic Acid; Male; Ornithine; Propionic Acidemia; Treatment Outcome | 2017 |
4 other study(ies) available for hydracrylic acid and Propionic Acidemia
Article | Year |
---|---|
Inter-relations between 3-hydroxypropionate and propionate metabolism in rat liver: relevance to disorders of propionyl-CoA metabolism.
Topics: Acyl Coenzyme A; Ammonium Compounds; Animals; Carbon Isotopes; Citrates; Citric Acid Cycle; Lactic Acid; Liver; Liver Transplantation; Male; Oxidation-Reduction; Propionates; Propionic Acidemia; Proteolysis; Rats; Rats, Sprague-Dawley | 2017 |
Autism spectrum disorders in propionic acidemia patients.
Topics: Adolescent; Adult; Autism Spectrum Disorder; Child; Child, Preschool; Female; Humans; Intellectual Disability; Lactic Acid; Male; Methylmalonyl-CoA Decarboxylase; Propionic Acidemia; Young Adult | 2018 |
Simultaneous determination of 3-hydroxypropionic acid, methylmalonic acid and methylcitric acid in dried blood spots: Second-tier LC-MS/MS assay for newborn screening of propionic acidemia, methylmalonic acidemias and combined remethylation disorders.
Topics: Amino Acid Metabolism, Inborn Errors; Chromatography, Liquid; Citrates; Dried Blood Spot Testing; Female; Humans; Infant, Newborn; Lactic Acid; Male; Mass Screening; Mass Spectrometry; Methylmalonic Acid; Propionic Acidemia | 2017 |
Long-term neurological outcome of a cohort of 80 patients with classical organic acidurias.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Female; Humans; Lactic Acid; Male; Methylmalonic Acid; Propionic Acidemia; Radiography; Young Adult | 2013 |