Page last updated: 2024-08-17

histidine and Cerebral Pseudosclerosis

histidine has been researched along with Cerebral Pseudosclerosis in 12 studies

Research

Studies (12)

TimeframeStudies, this research(%)All Research%
pre-19904 (33.33)18.7374
1990's2 (16.67)18.2507
2000's5 (41.67)29.6817
2010's1 (8.33)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Bahde, R; Bhargava, KK; Gupta, S; Kapoor, S; Palestro, CJ; Schilsky, ML1
Efremov, RG; Lutsenko, S; Tsivkovskii, R1
Aoyama, Y; Morifuji, M; Sakakibara, S; Salamatulla, Q; Xu, H1
Abonyi, M; Folhoffer, A; Lakatos, PL1
Cherninkova, S; Jelev, H; Kremensky, I; Mihaylova, V; Raycheva, M; Savov, A; Todorov, T; Tournev, I1
Neumann, PZ; Silverberg, M2
Andrews, NC; Lin, W; Trenor, C1
Czlonkowska, A; Gajda, J; Houwen, RH; Juyn, J; Ploos van Amstel, HK; Rodo, M1
Cauza, E; Ferenci, P; Gangl, A; Polli, C; Ulrich-Pur, H1
Katsuki, Y1
Carson, NA; Martin, VA1

Reviews

1 review(s) available for histidine and Cerebral Pseudosclerosis

ArticleYear
[Wilson disease].
    Orvosi hetilap, 2004, Oct-17, Volume: 145, Issue:42

    Topics: Adenosine Triphosphatases; Cation Transport Proteins; Copper; Copper-Transporting ATPases; Glutamine; Hepatolenticular Degeneration; Histidine; Humans; Mutation

2004

Other Studies

11 other study(ies) available for histidine and Cerebral Pseudosclerosis

ArticleYear
PET with 64Cu-histidine for noninvasive diagnosis of biliary copper excretion in Long-Evans cinnamon rat model of Wilson disease.
    Journal of nuclear medicine : official publication, Society of Nuclear Medicine, 2012, Volume: 53, Issue:6

    Topics: Animals; Bile; Copper; Copper Radioisotopes; Disease Models, Animal; Hepatocytes; Hepatolenticular Degeneration; Histidine; Liver Diseases; Metabolic Clearance Rate; Positron-Emission Tomography; Rats; Rats, Inbred F344; Rats, Inbred LEC

2012
The role of the invariant His-1069 in folding and function of the Wilson's disease protein, the human copper-transporting ATPase ATP7B.
    The Journal of biological chemistry, 2003, Apr-11, Volume: 278, Issue:15

    Topics: Adenosine Triphosphatases; Adenosine Triphosphate; Amino Acid Sequence; Amino Acid Substitution; Base Sequence; Binding Sites; Cation Transport Proteins; Cell Membrane; Copper-Transporting ATPases; DNA Primers; Hepatolenticular Degeneration; Histidine; Humans; Models, Molecular; Molecular Sequence Data; Mutagenesis, Site-Directed; Protein Folding; Protein Structure, Secondary; Recombinant Proteins; Sequence Alignment; Sequence Homology, Amino Acid

2003
Excess dietary histidine decreases the liver copper level and serum alanine aminotransferase activity in Long-Evans Cinnamon rats.
    The British journal of nutrition, 2003, Volume: 90, Issue:3

    Topics: Alanine Transaminase; Animals; Catalase; Copper; Diet; Glutathione Peroxidase; Hepatolenticular Degeneration; Histidine; Lipids; Liver; Male; Organ Size; Rats; Rats, Inbred F344; Rats, Inbred LEC; Species Specificity; Superoxide Dismutase; Weight Gain; Zinc

2003
Wilson's disease in two consecutive generations in a Bulgarian Roma family.
    Journal of neurology, 2007, Volume: 254, Issue:10

    Topics: Adult; Aspartate Aminotransferases; Bulgaria; Child; Family Health; Female; Glutamine; Hepatolenticular Degeneration; Histidine; Humans; Male; Mutation

2007
Metabolic pathways of red blood cell copper in normal humans and in Wilson's disease.
    Nature, 1967, Feb-25, Volume: 213, Issue:5078

    Topics: Amino Acids; Biological Transport; Carbon Isotopes; Cell Membrane Permeability; Child; Copper; Erythrocytes; Hepatolenticular Degeneration; Histidine; Humans; In Vitro Techniques; Kinetics; Male; Models, Theoretical; Radioisotopes

1967
Novel bacterial P-type ATPases with histidine-rich heavy-metal-associated sequences.
    Biochemical and biophysical research communications, 1994, Dec-30, Volume: 205, Issue:3

    Topics: Adenosine Triphosphatases; Amino Acid Sequence; Bacteria; Base Sequence; Cloning, Molecular; DNA Probes; DNA, Complementary; Escherichia coli; Gene Library; Hepatolenticular Degeneration; Histidine; Humans; Menkes Kinky Hair Syndrome; Metals; Molecular Sequence Data; Sequence Homology, Amino Acid; Species Specificity

1994
Very high frequency of the His1069Gln mutation in Polish Wilson disease patients.
    Journal of neurology, 1997, Volume: 244, Issue:9

    Topics: Adolescent; Adult; Amino Acid Substitution; Hepatolenticular Degeneration; Histidine; Humans; Point Mutation; Poland

1997
Distribution of patients with Wilson disease carrying the H1069Q mutation in Austria.
    Wiener klinische Wochenschrift, 2000, Jul-07, Volume: 112, Issue:13

    Topics: Amino Acid Substitution; Austria; Emigration and Immigration; Europe, Eastern; Exons; Female; Hepatolenticular Degeneration; Histidine; Humans; Male; Mutation; Population Surveillance; Prevalence; Surveys and Questionnaires

2000
[Urinary excretion of methylhistidine in children. 2. Methylhistidine metabolism in children].
    Nihon Shonika Gakkai zasshi. Acta paediatrica Japonica, 1969, Oct-01, Volume: 73, Issue:10

    Topics: Child; Child, Preschool; Diet; Dipeptides; Hepatolenticular Degeneration; Histidine; Humans; Infant; Lipidoses; Muscles; Neurofibromatosis 1; Peptides

1969
Inborn metabolic disorders with associated ocular lesions in Northern Ireland.
    Transactions of the ophthalmological societies of the United Kingdom, 1967, Volume: 87

    Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Cataract; Child; Child, Preschool; Cornea; Eye Diseases; Female; Galactosemias; Hepatolenticular Degeneration; Histidine; Homocystinuria; Humans; Infant; Lens, Crystalline; Male; Myopia; Northern Ireland; Pigmentation Disorders; Renal Aminoacidurias

1967
Active copper transport in mammalian tissues--a possible role in Wilson's disease.
    Nature, 1966, Apr-23, Volume: 210, Issue:5034

    Topics: Animals; Asparagine; Carcinoma, Ehrlich Tumor; Copper; Glutamine; Hepatolenticular Degeneration; Histidine; In Vitro Techniques; Kidney; Liver; Radioisotopes; Rats; Threonine

1966