Page last updated: 2024-08-17

histidine and Canavan Disease

histidine has been researched along with Canavan Disease in 3 studies

Research

Studies (3)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's2 (66.67)18.2507
2000's1 (33.33)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Berrin, JG; Giardina, T; Herga, S; Perrier, J; Puigserver, A1
de Jong, JG; Engelke, U; Gabreƫls, FJ; Heerschap, A; Wendel, U; Wevers, RA1
Baslow, MH; Resnik, TR1

Reviews

1 review(s) available for histidine and Canavan Disease

ArticleYear
Canavan disease. Analysis of the nature of the metabolic lesions responsible for development of the observed clinical symptoms.
    Journal of molecular neuroscience : MN, 1997, Volume: 9, Issue:2

    Topics: Amidohydrolases; Animals; Aspartic Acid; Canavan Disease; Central Nervous System; Female; Fetal Diseases; Histidine; Humans; Pregnancy

1997

Other Studies

2 other study(ies) available for histidine and Canavan Disease

ArticleYear
Identification of the zinc binding ligands and the catalytic residue in human aspartoacylase, an enzyme involved in Canavan disease.
    FEBS letters, 2006, Oct-30, Volume: 580, Issue:25

    Topics: Amidohydrolases; Amino Acid Sequence; Amino Acid Substitution; Base Sequence; Canavan Disease; Catalytic Domain; DNA, Complementary; Escherichia coli; Glutamic Acid; Histidine; Humans; In Vitro Techniques; Kinetics; Ligands; Models, Molecular; Molecular Sequence Data; Molecular Weight; Mutagenesis, Site-Directed; Recombinant Proteins; Sequence Homology, Amino Acid; Zinc

2006
Standardized method for high-resolution 1H-NMR of cerebrospinal fluid.
    Clinical chemistry, 1995, Volume: 41, Issue:5

    Topics: Adult; Amino Acids; Canavan Disease; Carbon-Carbon Ligases; Cerebrospinal Fluid; Child; Female; Gas Chromatography-Mass Spectrometry; Histidine; Humans; Hydrogen-Ion Concentration; Lactates; Lactic Acid; Ligases; Magnetic Resonance Spectroscopy; Male; Metabolism, Inborn Errors; Sensitivity and Specificity; Valerates; Volatilization

1995