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hexacosanoic acid and Alpers Diffuse Degeneration of Cerebral Gray Matter with Hepatic Cirrhosis

hexacosanoic acid has been researched along with Alpers Diffuse Degeneration of Cerebral Gray Matter with Hepatic Cirrhosis in 18 studies

Research

Studies (18)

TimeframeStudies, this research(%)All Research%
pre-199017 (94.44)18.7374
1990's1 (5.56)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Brown, FR; Liu, A; Moser, AE; Moser, HW; Sacktor, N; Van Duyn, MA1
Op't Hof, J; Pretorius, PJ; Reinecke, CJ1
Kawamura, N; Kishimoto, Y; Moser, AB; Moser, HW; Murphy, J; Schaumburg, H; Suzuki, K1
Sadeghi-Nejad, A; Senior, B1
Borel, J; Cornblath, D; Moser, AB; Moser, HW; Naidu, S; Odone, A; Sanders, DB1
Schutgens, RB; Tager, JM; van den Bosch, H; van Roermund, CW; Wanders, RJ1
Avigan, J; Dammann, AL; Jennings, SS; Leshner, RT; Phillips, MW; Proud, VK; Rizzo, WB1
Moser, HW; Naidu, S; Watkins, PA1
Handa, S; Kushi, Y; Sano, M; Tsukagoshi, H; Yokota, T1
Antoku, Y; Gotoh, I; Imanishi, K; Iwashita, H; Sakai, T; Tsukamoto, K1
Schram, AW; Schutgens, RB; Tager, JM; van den Bosch, H; van Roermund, CW; van Wijland, MJ; Wanders, RJ1
Monma, N; Saiki, K; Satodate, R; Satoh, S; Satoh, T1
Kodama, S; Nishio, H; Ohno, M; Onaga, A; Saeki, Y; Shimada, M; Tanaka, K; Yamano, T1
Boué, A; Boué, J; Dumez, Y; Heilig, R; Larsen, JW; Mandel, JL; Moser, A; Moser, H; Oberle, I1
Avigan, J; Campbell, B; Cranin, D; Phillips, MW; Rizzo, WB; Watkins, PA1
Kodama, S; Matsuo, T; Nishio, H; Takahashi, T; Takumi, T; Tsubota, T; Yokoyama, S1
Antoku, Y; Goto, I; Iwashita, H; Katafuchi, Y; Kuroiwa, Y; Ochiai, J; Sakai, T1
Ariga, T; Miyatake, T; Sano-Kawamura, T; Tsuji, S1

Reviews

1 review(s) available for hexacosanoic acid and Alpers Diffuse Degeneration of Cerebral Gray Matter with Hepatic Cirrhosis

ArticleYear
Adrenoleukodystrophy: biochemical procedures in diagnosis, prevention and treatment.
    Journal of inherited metabolic disease, 1987, Volume: 10 Suppl 1

    Topics: Adrenoleukodystrophy; Bone Marrow Transplantation; Child; Chromosome Mapping; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Genetic Carrier Screening; Humans; Phenotype; Pregnancy; Prenatal Diagnosis; X Chromosome

1987

Other Studies

17 other study(ies) available for hexacosanoic acid and Alpers Diffuse Degeneration of Cerebral Gray Matter with Hepatic Cirrhosis

ArticleYear
The design of a diet restricted in saturated very long-chain fatty acids: therapeutic application in adrenoleukodystrophy.
    The American journal of clinical nutrition, 1984, Volume: 40, Issue:2

    Topics: Adrenoleukodystrophy; Adult; Dietary Fats; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Food Analysis; Fruit; Humans; Male; Vegetables

1984
Biochemical evidence for clinically diagnosed adrenoleucodystrophy in two brothers.
    South African medical journal = Suid-Afrikaanse tydskrif vir geneeskunde, 1984, May-26, Volume: 65, Issue:21

    Topics: Adrenoleukodystrophy; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Erythrocytes; Fatty Acids; Fibroblasts; Humans; Male; Occipital Lobe; Skin

1984
Adrenoleukodystrophy: elevated C26 fatty acid in cultured skin fibroblasts.
    Annals of neurology, 1980, Volume: 7, Issue:6

    Topics: Adolescent; Adrenal Insufficiency; Adult; Cells, Cultured; Child; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Fibroblasts; Genetic Carrier Screening; Humans; Male; Middle Aged; Skin; Syndrome

1980
Adrenomyeloneuropathy presenting as Addison's disease in childhood.
    The New England journal of medicine, 1990, Jan-04, Volume: 322, Issue:1

    Topics: Addison Disease; Adolescent; Adrenoleukodystrophy; Adult; Brain; Child; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Genetic Linkage; Humans; Infant; Magnetic Resonance Imaging; Male; Sex Factors

1990
A new dietary therapy for adrenoleukodystrophy: biochemical and preliminary clinical results in 36 patients.
    Annals of neurology, 1987, Volume: 21, Issue:3

    Topics: Adrenoleukodystrophy; Dietary Fats; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Heterozygote; Humans; Infant, Newborn; Male; Neural Conduction; Oleic Acid; Oleic Acids; Refsum Disease

1987
Impaired ability of peroxisomes to activate very-long-chain fatty acids in X-linked adrenoleukodystrophy.
    Lancet (London, England), 1988, Jul-16, Volume: 2, Issue:8603

    Topics: Adrenoleukodystrophy; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Humans; Male; Microbodies

1988
Adrenoleukodystrophy: dietary oleic acid lowers hexacosanoate levels.
    Annals of neurology, 1987, Volume: 21, Issue:3

    Topics: Adrenoleukodystrophy; Dietary Fats; Diffuse Cerebral Sclerosis of Schilder; Erythrocytes; Fatty Acids; Female; Heterozygote; Humans; Male; Oleic Acid; Oleic Acids; Peripheral Nervous System Diseases

1987
[Two adult cases of adrenoleukodystrophy with clinical features of striatonigral degeneration--a probable variant of adrenoleukodystrophy].
    Rinsho shinkeigaku = Clinical neurology, 1988, Volume: 28, Issue:9

    Topics: Adrenoleukodystrophy; Aged; Corpus Striatum; Diagnosis, Differential; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Humans; Magnetic Resonance Imaging; Male; Middle Aged; Sphingomyelins; Substantia Nigra

1988
Carrier detection for adrenoleukodystrophy by high-performance liquid chromatography.
    Experimental neurology, 1988, Volume: 100, Issue:3

    Topics: Adrenoleukodystrophy; Chromatography, High Pressure Liquid; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Genetic Carrier Screening; Humans; Lipids; Skin

1988
Direct demonstration that the deficient oxidation of very long chain fatty acids in X-linked adrenoleukodystrophy is due to an impaired ability of peroxisomes to activate very long chain fatty acids.
    Biochemical and biophysical research communications, 1988, Jun-16, Volume: 153, Issue:2

    Topics: Adrenoleukodystrophy; Catalase; Cell Fractionation; Cells, Cultured; Centrifugation, Density Gradient; Diffuse Cerebral Sclerosis of Schilder; Fatty Acid Synthases; Fatty Acids; Humans; Microbodies; Microsomes; Mitochondria; Skin

1988
Adrenoleukodystrophy. Report of an autopsy case with adrenoleukomyeloneuropathy.
    Acta pathologica japonica, 1986, Volume: 36, Issue:7

    Topics: Adrenoleukodystrophy; Adult; Autopsy; Cerebrosides; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Histocytochemistry; Humans; Immunoenzyme Techniques; Male; Microscopy, Electron; Spinal Cord; Sulfoglycosphingolipids

1986
Electronmicroscopic study on biopsied rectal mucosa in adrenoleukodystrophy.
    Neurology, 1987, Volume: 37, Issue:6

    Topics: Adrenoleukodystrophy; Child; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Humans; Male; Microscopy, Electron; Mucous Membrane; Rectum

1987
First trimester prenatal diagnosis of adrenoleukodystrophy by determination of very long chain fatty acid levels and by linkage analysis to a DNA probe.
    Human genetics, 1985, Volume: 69, Issue:3

    Topics: Adrenoleukodystrophy; Cells, Cultured; Chorionic Villi; Chromosome Mapping; Diffuse Cerebral Sclerosis of Schilder; DNA; Fatty Acids; Female; Genetic Linkage; Genetic Markers; Humans; Male; Pedigree; Pregnancy; Pregnancy Trimester, First; Prenatal Diagnosis; X Chromosome

1985
Adrenoleukodystrophy: oleic acid lowers fibroblast saturated C22-26 fatty acids.
    Neurology, 1986, Volume: 36, Issue:3

    Topics: Adrenoleukodystrophy; Animals; Cattle; Cell Line; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Fibroblasts; Humans; In Vitro Techniques; Male; Oleic Acid; Oleic Acids; Skin

1986
Adrenoleukodystrophy without adrenal insufficiency and its magnetic resonance imaging.
    Journal of neurology, 1985, Volume: 232, Issue:5

    Topics: Adolescent; Adrenoleukodystrophy; Brain; Chemical Phenomena; Chemistry; Child; Diffuse Cerebral Sclerosis of Schilder; Erythrocyte Membrane; Fatty Acids; Humans; Magnetic Resonance Spectroscopy; Male; Membrane Proteins; Sphingomyelins

1985
Very long-chain fatty acids in neutral lipids and glycerophospholipids of adrenoleukodystrophy-cultured skin fibroblasts.
    Journal of the neurological sciences, 1985, Volume: 71, Issue:2-3

    Topics: Adrenoleukodystrophy; Carrier State; Cells, Cultured; Cholesterol Esters; Chromatography, High Pressure Liquid; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Humans; Phospholipids; Skin; Triglycerides

1985
Metabolism of [17,18-3H2]hexacosanoic acid and [15,16-3H2]lignoceric acid in cultured skin fibroblasts from patients with adrenoleukodystrophy (ALD) and adrenomyeloneuropathy (AMN).
    Journal of the neurological sciences, 1985, Volume: 71, Issue:2-3

    Topics: Adrenoleukodystrophy; Cells, Cultured; Centrifugation, Density Gradient; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Humans; Skin; Solubility

1985