hexacosanoic acid has been researched along with Addison Disease and Cerebral Sclerosis in 39 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 20 (51.28) | 18.7374 |
| 1990's | 3 (7.69) | 18.2507 |
| 2000's | 11 (28.21) | 29.6817 |
| 2010's | 5 (12.82) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Ben Youssef, IT; Feki, M; Kaabachi, N; Kraoua, I; Nasrallah, F; Omar, S; Sanhaji, H; Zidi, W | 1 |
| Brites, P; El Mrabet, L; Mooyer, PA; Wanders, RJ; Waterham, HR | 1 |
| Blank, D; Bonfim, C; Coelho, Dl; Costa, ML; da Silva, AC; de Castro, CG; Deon, M; Giugliani, R; Gregianin, L; Jardim, LB; Renck, L; Vargas, CR; Vedolin, L; Villanueva, MM | 1 |
| Hamilton, JA; Jasuja, R; Pillai, BK; Simard, JR | 1 |
| Brown, A; Ingram, G; Jardine, P; Robertson, NP; Scolding, NJ; Steward, CG; Wilkins, A | 1 |
| de Visser, M; Dijkgraaf, MG; Engelen, M; Hijzen, M; Kemp, S; Ofman, R; Poll-The, BT; van der Wardt, LA; van Geel, BM; Wanders, RJ | 1 |
| Aiello, C; Bizzarri, C; Cappa, M; Di Biase, A; Giannone, G | 1 |
| Dijkstra, IM; Engelen, M; Fourcade, S; Houten, SM; Kemp, S; Ofman, R; Poll-The, BT; Pujol, A; Sanders, RJ; Schackmann, MJ; Wanders, RJ | 1 |
| Dadali, EL; Goncharov, VM; Karmanov, ME; Lomonosova, EZ; Rudenskaia, GE; Shekhter, OV; Solokha, OA; Zakharova, EIu | 1 |
| Attorri, L; Di Benedetto, R; Di Biase, A; Fiorentini, C; Pietraforte, D; Salvati, S; Travaglione, S | 1 |
| Bezman, L; Brereton, NH; Dubey, P; Jones, RO; Loes, DJ; Lu, SE; Melhem, ER; Moser, AB; Moser, HW; Muenz, LR; Odone, A; Raymond, GV; Xu, J | 1 |
| Barschak, AG; Coelho, DM; Deon, M; Garcia, MP; Giugliani, R; Jardim, LB; Pigatto, M; Schimit, GO; Sitta, A; Vargas, CR; Wajner, M | 1 |
| Attorri, L; David, G; Denti, MA; Di Benedetto, R; Di Biase, A; Salvati, S; Sanchez, M | 1 |
| Duval, C; Ferrer, I; Fourcade, S; Galino, J; Jove, M; Kemp, S; López-Erauskin, J; Naudi, A; Pamplona, R; Portero-Otin, M; Pujol, A; Villarroya, F | 1 |
| Poulos, A; Sharp, P | 1 |
| Brown, FR; Liu, A; Moser, AE; Moser, HW; Sacktor, N; Van Duyn, MA | 1 |
| Benke, PJ; Brown, FR; Kelley, RI; Moser, AE; Moser, HW; Singh, I; Solish, GI | 1 |
| Op't Hof, J; Pretorius, PJ; Reinecke, CJ | 1 |
| Aveldaño, MI; Donnari, D | 1 |
| Barbosa, E; Betros, R; Craver, JR; Curé, JK; Key, LL; Khan, M; Pai, GS; Singh, I | 1 |
| Blasevich, M; Cavarretta, I; Galli, C; Magnaghi, V; Melcangi, RC; Papini, N; Petroni, A | 1 |
| Blomstrand, S; Conradi, NG; Hindmarsh, T; Kyllerman, M; Månsson, JE | 1 |
| Sadeghi-Nejad, A; Senior, B | 1 |
| Derwas, N; Poulos, A; Singh, H | 1 |
| Borel, J; Cornblath, D; Moser, AB; Moser, HW; Naidu, S; Odone, A; Sanders, DB | 1 |
| Schutgens, RB; Tager, JM; van den Bosch, H; van Roermund, CW; Wanders, RJ | 1 |
| Avigan, J; Dammann, AL; Jennings, SS; Leshner, RT; Phillips, MW; Proud, VK; Rizzo, WB | 1 |
| Moser, HW; Naidu, S; Watkins, PA | 1 |
| Harada, Y; Iwasaki, Y; Kanja, K; Kawahara, K; Kusaka, T; Maruyama, Y; Nakano, H; Nanba, S; Ono, S; Sasai, H | 1 |
| Handa, S; Kushi, Y; Sano, M; Tsukagoshi, H; Yokota, T | 1 |
| Antoku, Y; Gotoh, I; Imanishi, K; Iwashita, H; Sakai, T; Tsukamoto, K | 1 |
| Schram, AW; Schutgens, RB; Tager, JM; van den Bosch, H; van Roermund, CW; van Wijland, MJ; Wanders, RJ | 1 |
| Monma, N; Saiki, K; Satodate, R; Satoh, S; Satoh, T | 1 |
| Kodama, S; Nishio, H; Ohno, M; Onaga, A; Saeki, Y; Shimada, M; Tanaka, K; Yamano, T | 1 |
| Boué, A; Boué, J; Dumez, Y; Heilig, R; Larsen, JW; Mandel, JL; Moser, A; Moser, H; Oberle, I | 1 |
| Avigan, J; Campbell, B; Cranin, D; Phillips, MW; Rizzo, WB; Watkins, PA | 1 |
| Kodama, S; Matsuo, T; Nishio, H; Takahashi, T; Takumi, T; Tsubota, T; Yokoyama, S | 1 |
| Antoku, Y; Goto, I; Iwashita, H; Katafuchi, Y; Kuroiwa, Y; Ochiai, J; Sakai, T | 1 |
| Ariga, T; Miyatake, T; Sano-Kawamura, T; Tsuji, S | 1 |
2 review(s) available for hexacosanoic acid and Addison Disease and Cerebral Sclerosis
| Article | Year |
|---|---|
[Clinical heterogeneity of X-linked adrenoleukodystrophy ].
Topics: Adrenocortical Hyperfunction; Adrenoleukodystrophy; Age Factors; ATP Binding Cassette Transporter, Subfamily D, Member 1; ATP-Binding Cassette Transporters; Chromosomes, Human, X; Fatty Acids; Female; Genetic Linkage; Genetic Testing; Humans; Male; Tics | 2002 |
Adrenoleukodystrophy: biochemical procedures in diagnosis, prevention and treatment.
Topics: Adrenoleukodystrophy; Bone Marrow Transplantation; Child; Chromosome Mapping; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Genetic Carrier Screening; Humans; Phenotype; Pregnancy; Prenatal Diagnosis; X Chromosome | 1987 |
2 trial(s) available for hexacosanoic acid and Addison Disease and Cerebral Sclerosis
| Article | Year |
|---|---|
Lovastatin in X-linked adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Cholesterol, LDL; Cross-Over Studies; Double-Blind Method; Fatty Acids; Humans; Hydroxymethylglutaryl-CoA Reductase Inhibitors; Lovastatin; Pilot Projects | 2010 |
Lovastatin therapy for X-linked adrenoleukodystrophy: clinical and biochemical observations on 12 patients.
Topics: Adrenoleukodystrophy; Adult; Aged; Aspartate Aminotransferases; Child; Creatine Kinase; Fatty Acids; Female; Follow-Up Studies; Humans; Hydroxymethylglutaryl-CoA Reductase Inhibitors; Lovastatin; Male; Middle Aged; Platelet Count; Treatment Outcome | 2000 |
35 other study(ies) available for hexacosanoic acid and Addison Disease and Cerebral Sclerosis
| Article | Year |
|---|---|
X-linked Adrenoleukodystrophy, The Tunisian Experience.
Topics: Adolescent; Adrenoleukodystrophy; Adult; Child; Child, Preschool; Chromatography, Gas; Family Health; Fatty Acids; Female; Humans; Male; Middle Aged; Pattern Recognition, Automated; Phenotype; Reproducibility of Results; Retrospective Studies; Tunisia | 2015 |
Plasmalogens participate in very-long-chain fatty acid-induced pathology.
Topics: Adrenoleukodystrophy; Animals; Astrocytes; Axons; Blotting, Western; Brain; Chemokine CCL22; Demyelinating Diseases; Fatty Acids; Male; Mice; Mice, Inbred C57BL; Mice, Knockout; Microglia; Peroxisomal Targeting Signal 2 Receptor; Peroxisomes; Plasmalogens; Receptors, Cytoplasmic and Nuclear | 2009 |
X-linked adrenoleukodystrophy: clinical course and minimal incidence in South Brazil.
Topics: Adrenoleukodystrophy; Brazil; Chromatography, Gas; Chromosomes, Human, X; Coenzyme A Ligases; Disease Progression; Family Health; Fatty Acids; Hematopoietic Stem Cell Transplantation; Humans; Longitudinal Studies; Male; Retrospective Studies; Severity of Illness Index; Statistics, Nonparametric | 2010 |
Fast diffusion of very long chain saturated fatty acids across a bilayer membrane and their rapid extraction by cyclodextrins: implications for adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; beta-Cyclodextrins; Biological Transport; Cell Line; Cell Membrane; Diffusion; Eicosanoic Acids; Fatty Acids; Fluorescent Dyes; Humans; Lipid Bilayers; Phosphatidylcholines; Spectrometry, Fluorescence | 2009 |
Very long chain fatty acid levels in patients diagnosed with multiple sclerosis.
Topics: Adrenoleukodystrophy; Adult; Biomarkers; Fatty Acids; Female; Genotype; Humans; Male; Middle Aged; Multiple Sclerosis; Multiple Sclerosis, Chronic Progressive; Pedigree; Phenotype | 2009 |
Is subclinical adrenal failure in adrenoleukodystrophy/adrenomyeloneuropathy reversible?
Topics: Adrenal Glands; Adrenal Insufficiency; Adrenocorticotropic Hormone; Adrenoleukodystrophy; Adult; Dietary Fats; Drug Combinations; Erucic Acids; Fatty Acids; Humans; Hydrocortisone; Triolein | 2011 |
Bezafibrate lowers very long-chain fatty acids in X-linked adrenoleukodystrophy fibroblasts by inhibiting fatty acid elongation.
Topics: Acetyltransferases; Adrenoleukodystrophy; Animals; ATP Binding Cassette Transporter, Subfamily D, Member 1; ATP-Binding Cassette Transporters; Bezafibrate; Cells, Cultured; Enzyme Inhibitors; Fatty Acid Elongases; Fatty Acids; Humans; Hypolipidemic Agents; Male; Mice; Mice, Transgenic; Microsomes, Liver; Oxidation-Reduction; Peroxisome Proliferator-Activated Receptors; Recombinant Proteins | 2012 |
Free radical release in C6 glial cells enriched in hexacosanoic acid: implication for X-linked adrenoleukodystrophy pathogenesis.
Topics: Adrenoleukodystrophy; Animals; Cell Line; Cytokines; Fatty Acids; Free Radicals; Humans; Microscopy, Electron, Scanning; Microscopy, Fluorescence; Neuroglia; Nitrates; Nitrites; Rats | 2004 |
Follow-up of 89 asymptomatic patients with adrenoleukodystrophy treated with Lorenzo's oil.
Topics: Adrenoleukodystrophy; Biomarkers; Brain; Child; Child, Preschool; Dietary Fats, Unsaturated; Drug Combinations; Erucic Acids; Fatty Acids; Follow-Up Studies; Humans; Magnetic Resonance Imaging; Male; Risk Factors; Treatment Outcome; Triolein | 2005 |
Hexacosanoic and docosanoic acids plasma levels in patients with cerebral childhood and asymptomatic X-linked adrenoleukodystrophy: Lorenzo's oil effect.
Topics: Adrenoleukodystrophy; Child; Diet; Drug Combinations; Erucic Acids; Fatty Acids; Female; Humans; Hyperkinesis; Learning Disabilities; Male; Seizures; Triolein | 2008 |
RNAi-mediated silencing of ABCD3 gene expression in rat C6 glial cells: a model system to study PMP70 function.
Topics: Adrenoleukodystrophy; Animals; ATP-Binding Cassette Transporters; Cell Line, Tumor; Central Nervous System; Down-Regulation; Fatty Acids; Gene Silencing; Lipid Peroxidation; Membrane Potential, Mitochondrial; Models, Biological; Myelin Sheath; Neuroglia; Oxidative Stress; Rats; RNA Interference; RNA, Messenger; RNA, Small Interfering | 2008 |
Early oxidative damage underlying neurodegeneration in X-adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Animals; Catalase; Chemokine CCL22; Chromans; Fatty Acids; Fibroblasts; Humans; In Vitro Techniques; Lysine; Malondialdehyde; Membrane Potential, Mitochondrial; Mice; Mice, Inbred C57BL; Motor Neurons; Oxidation-Reduction; Oxidative Stress; Spinal Cord; Superoxide Dismutase | 2008 |
Plasma and skin fibroblast C26 fatty acids in infantile Refsum's disease.
Topics: Adrenoleukodystrophy; Child, Preschool; Fatty Acids; Female; Fibroblasts; Humans; Infant; Male; Phytanic Acid; Refsum Disease; Skin | 1984 |
The design of a diet restricted in saturated very long-chain fatty acids: therapeutic application in adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Adult; Dietary Fats; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Food Analysis; Fruit; Humans; Male; Vegetables | 1984 |
The cerebrohepatorenal (Zellweger) syndrome. Increased levels and impaired degradation of very-long-chain fatty acids and their use in prenatal diagnosis.
Topics: Abnormalities, Multiple; Adrenoleukodystrophy; Amniocentesis; Brain Diseases; Diagnosis, Differential; Fatty Acids; Fatty Acids, Monounsaturated; Fatty Acids, Unsaturated; Female; Fibroblasts; Humans; Kidney Diseases, Cystic; Liver Diseases; Male; Microbodies; Pregnancy; Prenatal Diagnosis; Syndrome | 1984 |
Biochemical evidence for clinically diagnosed adrenoleucodystrophy in two brothers.
Topics: Adrenoleukodystrophy; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Erythrocytes; Fatty Acids; Fibroblasts; Humans; Male; Occipital Lobe; Skin | 1984 |
Plasma phospholipid fatty acids in X-linked adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Child; Fatty Acids; Fatty Acids, Unsaturated; Genetic Linkage; Humans; Linoleic Acid; Linoleic Acids; Male; Oleic Acid; Oleic Acids; Phospholipids; Sphingomyelins; X Chromosome | 1996 |
Testosterone metabolites in patients reduce the levels of very long chain fatty acids accumulated in X-adrenoleukodystrophic fibroblasts.
Topics: Adrenoleukodystrophy; Child; Dihydrotestosterone; Fatty Acids; Fibroblasts; Humans; Skin; Testosterone | 2000 |
Central nervous system malformations and white matter changes in pseudo-neonatal adrenoleukodystrophy.
Topics: Acyl-CoA Oxidase; Adrenoleukodystrophy; Brain; Fatty Acids; Female; Humans; Infant; Liver; Magnetic Resonance Imaging; Microbodies; Microscopy, Electron; Oxidoreductases | 1990 |
Adrenomyeloneuropathy presenting as Addison's disease in childhood.
Topics: Addison Disease; Adolescent; Adrenoleukodystrophy; Adult; Brain; Child; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Genetic Linkage; Humans; Infant; Magnetic Resonance Imaging; Male; Sex Factors | 1990 |
Beta-oxidation of very-long-chain fatty acids and their coenzyme A derivatives by human skin fibroblasts.
Topics: Abnormalities, Multiple; Acyl Coenzyme A; Adenosine Triphosphate; Adrenoleukodystrophy; Cell Line; Fatty Acids; Fibroblasts; Humans; Kinetics; Magnesium; NAD; Oxidation-Reduction; Refsum Disease; Skin; X Chromosome | 1987 |
A new dietary therapy for adrenoleukodystrophy: biochemical and preliminary clinical results in 36 patients.
Topics: Adrenoleukodystrophy; Dietary Fats; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Heterozygote; Humans; Infant, Newborn; Male; Neural Conduction; Oleic Acid; Oleic Acids; Refsum Disease | 1987 |
Impaired ability of peroxisomes to activate very-long-chain fatty acids in X-linked adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Humans; Male; Microbodies | 1988 |
Adrenoleukodystrophy: dietary oleic acid lowers hexacosanoate levels.
Topics: Adrenoleukodystrophy; Dietary Fats; Diffuse Cerebral Sclerosis of Schilder; Erythrocytes; Fatty Acids; Female; Heterozygote; Humans; Male; Oleic Acid; Oleic Acids; Peripheral Nervous System Diseases | 1987 |
Hexacosanoate contents in Japanese common foods.
Topics: Adrenoleukodystrophy; Fatty Acids; Food Analysis; Gas Chromatography-Mass Spectrometry; Japan | 1988 |
[Two adult cases of adrenoleukodystrophy with clinical features of striatonigral degeneration--a probable variant of adrenoleukodystrophy].
Topics: Adrenoleukodystrophy; Aged; Corpus Striatum; Diagnosis, Differential; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Humans; Magnetic Resonance Imaging; Male; Middle Aged; Sphingomyelins; Substantia Nigra | 1988 |
Carrier detection for adrenoleukodystrophy by high-performance liquid chromatography.
Topics: Adrenoleukodystrophy; Chromatography, High Pressure Liquid; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Genetic Carrier Screening; Humans; Lipids; Skin | 1988 |
Direct demonstration that the deficient oxidation of very long chain fatty acids in X-linked adrenoleukodystrophy is due to an impaired ability of peroxisomes to activate very long chain fatty acids.
Topics: Adrenoleukodystrophy; Catalase; Cell Fractionation; Cells, Cultured; Centrifugation, Density Gradient; Diffuse Cerebral Sclerosis of Schilder; Fatty Acid Synthases; Fatty Acids; Humans; Microbodies; Microsomes; Mitochondria; Skin | 1988 |
Adrenoleukodystrophy. Report of an autopsy case with adrenoleukomyeloneuropathy.
Topics: Adrenoleukodystrophy; Adult; Autopsy; Cerebrosides; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Histocytochemistry; Humans; Immunoenzyme Techniques; Male; Microscopy, Electron; Spinal Cord; Sulfoglycosphingolipids | 1986 |
Electronmicroscopic study on biopsied rectal mucosa in adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Child; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Humans; Male; Microscopy, Electron; Mucous Membrane; Rectum | 1987 |
First trimester prenatal diagnosis of adrenoleukodystrophy by determination of very long chain fatty acid levels and by linkage analysis to a DNA probe.
Topics: Adrenoleukodystrophy; Cells, Cultured; Chorionic Villi; Chromosome Mapping; Diffuse Cerebral Sclerosis of Schilder; DNA; Fatty Acids; Female; Genetic Linkage; Genetic Markers; Humans; Male; Pedigree; Pregnancy; Pregnancy Trimester, First; Prenatal Diagnosis; X Chromosome | 1985 |
Adrenoleukodystrophy: oleic acid lowers fibroblast saturated C22-26 fatty acids.
Topics: Adrenoleukodystrophy; Animals; Cattle; Cell Line; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Fibroblasts; Humans; In Vitro Techniques; Male; Oleic Acid; Oleic Acids; Skin | 1986 |
Adrenoleukodystrophy without adrenal insufficiency and its magnetic resonance imaging.
Topics: Adolescent; Adrenoleukodystrophy; Brain; Chemical Phenomena; Chemistry; Child; Diffuse Cerebral Sclerosis of Schilder; Erythrocyte Membrane; Fatty Acids; Humans; Magnetic Resonance Spectroscopy; Male; Membrane Proteins; Sphingomyelins | 1985 |
Very long-chain fatty acids in neutral lipids and glycerophospholipids of adrenoleukodystrophy-cultured skin fibroblasts.
Topics: Adrenoleukodystrophy; Carrier State; Cells, Cultured; Cholesterol Esters; Chromatography, High Pressure Liquid; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Humans; Phospholipids; Skin; Triglycerides | 1985 |
Metabolism of [17,18-3H2]hexacosanoic acid and [15,16-3H2]lignoceric acid in cultured skin fibroblasts from patients with adrenoleukodystrophy (ALD) and adrenomyeloneuropathy (AMN).
Topics: Adrenoleukodystrophy; Cells, Cultured; Centrifugation, Density Gradient; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Fibroblasts; Humans; Skin; Solubility | 1985 |