Page last updated: 2024-08-23

heme and Hemoglobinopathies

heme has been researched along with Hemoglobinopathies in 31 studies

Research

Studies (31)

Timeframe	Studies, this research(%)	All Research%
pre-1990	25 (80.65)	18.7374
1990's	4 (12.90)	18.2507
2000's	0 (0.00)	29.6817
2010's	2 (6.45)	24.3611
2020's	0 (0.00)	2.80

Authors

Authors	Studies
Chen, JJ; Zhang, S	1
Arnaud, L; Bieker, JJ; Higgs, DR; Patrinos, GP; Perkins, A; Philipsen, S; Xu, X	1
Atamna, H; Ginsburg, H	1
Rachmilewitz, EA; Shinar, E	1
Anderson, KE; Kappas, A; Peterson, CM; Sassa, S	1
Kolski, GB; Miller, DR	1
Martelo, OJ	1
Harano, K; Harano, T; Kushida, Y; Nishinarita, M; Ueda, S; Yoshii, A	1
Kitagawa, T; Nagai, M; Yoneyama, Y	1
Felice, AE; Huisman, TH; Kutlar, A; Lutcher, CL; McKie, VC; Reese, AL; Webber, BB; Wilson, JB	1
Espinós Pérez, D	1
Hseih, JW; Tanaka, KR; Zerez, CR	1
Sears, DA	1
Piddington, SK; White, JM	1
Lehmann, H	1
Bannerman, RM; Glass, U; Kreimer-Birnbaum, M; Rusnak, PA	1
Lorkin, PA	1
Harari, E; Rachmilewitz, EA	1
Albahary, C	1
Labie, D; Wajcman, H	1
Weatherall, DJ	1
Ruckpaul, K	1
Fairbanks, VF	1
Dacie, JV; White, JM	1
Perkins, RP	1
Sebahoun, G	1
Popović, K	1
Belkhodja, O; Labie, D; Wajcman, H	1
Carrell, RW; Owen, MC	1
Mainzer, K	1
Heller, P	1

Reviews

10 review(s) available for heme and Hemoglobinopathies

Article	Year
Heme-regulated eIF2α kinase in erythropoiesis and hemoglobinopathies. Blood, 2019, 11-14, Volume: 134, Issue:20 Topics: Activating Transcription Factor 4; Anemia, Iron-Deficiency; Animals; eIF-2 Kinase; Erythropoiesis; Heme; Hemoglobinopathies; Humans; Mechanistic Target of Rapamycin Complex 1; Signal Transduction	2019
Krüppeling erythropoiesis: an unexpected broad spectrum of human red blood cell disorders due to KLF1 variants. Blood, 2016, Apr-14, Volume: 127, Issue:15 Topics: Anemia, Hemolytic; Animals; beta-Globins; Blood Group Antigens; Erythrocytes; Erythropoiesis; Exome; Gene Deletion; Gene Expression Regulation; Genetic Variation; Heme; Hemoglobinopathies; Humans; Hydrops Fetalis; Iron; Kruppel-Like Transcription Factors; Mice; Phenotype; Protein Structure, Tertiary; Pyruvate Kinase; Sequence Analysis, DNA	2016
Haemoglobinopathies and red cell membrane function. Bailliere's clinical haematology, 1993, Volume: 6, Issue:2 Topics: Erythrocyte Membrane; Heme; Hemoglobinopathies; Humans; Iron; Oxidation-Reduction; Oxyhemoglobins; Porphyrins; Protein Denaturation; Thalassemia	1993
Diseases of disordered hemoglobin degradation. Advances in internal medicine, 1975, Volume: 20 Topics: Amino Acids; Anemia, Hemolytic; Animals; Bile; Bile Pigments; Bilirubin; Chemical Phenomena; Chemistry; Heinz Bodies; Heme; Hemoglobinopathies; Hemoglobins; Hemolysis; Humans; Mixed Function Oxygenases; Mutation; Rats; Thalassemia	1975
Fetal and embryonic haemoglobins. Journal of medical genetics, 1973, Volume: 10, Issue:1 Topics: Amino Acid Sequence; Anemia; Animals; Chromosome Aberrations; Chromosome Disorders; Disease Models, Animal; Female; Fetal Hemoglobin; Genes; Genotype; Goats; Heme; Hemoglobinopathies; Hemoglobins, Abnormal; Humans; Immunoglobulin Fragments; Male; Mutation; Oxygen; Pregnancy; Sheep	1973
Lead and hemopoiesis. The mechanism and consequences of the erythropathy of occupational lead poisoning. The American journal of medicine, 1972, Volume: 52, Issue:3 Topics: Anemia; Bone Marrow Diseases; Cell Membrane; Cell Survival; Child; Edetic Acid; Erythrocytes; Erythrocytes, Abnormal; Erythropoiesis; Hematologic Diseases; Hematopoiesis; Heme; Hemoglobinopathies; Humans; Iron; Lead; Lead Poisoning; Mitochondria; Occupational Diseases; Osmotic Fragility; Penicillamine; Porphyrias; Porphyrins; Reticulocytes	1972
The control of haemoglobin synthesis. Proceedings of the Royal Society of Medicine, 1967, Volume: 60, Issue:10 Topics: Adult; Amino Acid Sequence; Black People; Cytoplasm; Genetic Code; Globins; Heme; Hemoglobinopathies; Hemoglobins; Hemoglobins, Abnormal; Humans; Molecular Biology; RNA, Messenger; RNA, Transfer; Thalassemia	1967
[Structure-function relations of abnormal hemoglobins. II]. Das Deutsche Gesundheitswesen, 1969, Jan-23, Volume: 24, Issue:4 Topics: Amino Acids; Carboxypeptidases; Chemistry Techniques, Analytical; Heme; Hemoglobinopathies; Hemoglobins; Hemoglobins, Abnormal; Humans; Methemoglobin; Models, Biological; Mutation; Myoglobin; Oxygen; Protein Binding	1969
Introduction to discussion of Heinz body anemias--unstable hemoglobinopathies. Experimental eye research, 1971, Volume: 11, Issue:3 Topics: Adenosine Triphosphate; Anemia, Hemolytic, Congenital; Chemical Precipitation; Disulfides; Erythrocytes; Genes, Dominant; Genetic Code; Globins; Glucose; Glutathione; Heinz Bodies; Heme; Hemoglobinopathies; Hemoglobins, Abnormal; Hemolysis; Humans; Mutation; Oxygen; Protein Denaturation; Splenectomy; Structure-Activity Relationship; Sulfonamides	1971
The unstable hemoglobins--molecular and clinical features. Progress in hematology, 1971, Volume: 7, Issue:0 Topics: Anemia, Hemolytic, Congenital; Blood Protein Electrophoresis; Cell Survival; Chromium Radioisotopes; Erythrocytes; Globins; Glucose; Heinz Bodies; Heme; Hemoglobinopathies; Hemoglobins; Hemoglobins, Abnormal; Hexosephosphates; Humans; Oxidation-Reduction; Protein Conformation; Protein Denaturation; Splenectomy	1971

Other Studies

21 other study(ies) available for heme and Hemoglobinopathies

Article	Year
Heme degradation in the presence of glutathione. A proposed mechanism to account for the high levels of non-heme iron found in the membranes of hemoglobinopathic red blood cells. The Journal of biological chemistry, 1995, Oct-20, Volume: 270, Issue:42 Topics: Deferoxamine; Erythrocyte Membrane; Glutathione; Heme; Hemoglobinopathies; Humans; Hydrogen Peroxide; Iron; Pentose Phosphate Pathway	1995
Increased erythrocyte uroporphyrinogen-l-synthetase, delta-aminolevulinic acid dehydratase and protoporphyrin in hemolytic anemias. The American journal of medicine, 1977, Volume: 63, Issue:3 Topics: Ammonia-Lyases; Anemia, Hemolytic; Anemia, Sickle Cell; Erythrocyte Count; Erythrocytes; Heme; Hemoglobinopathies; Hemolysis; Humans; Hydro-Lyases; Hydroxymethylbilane Synthase; Porphobilinogen Synthase; Porphyrins; Protoporphyrins; Reticulocytes; Thalassemia	1977
Heme synthesis in hereditary hemolytic anemias: decreased delta-aminolevulinic acid synthetase in hemoglobin Köln disease. Pediatric research, 1976, Volume: 10, Issue:7 Topics: 5-Aminolevulinate Synthetase; Adult; Anemia, Hemolytic, Congenital; Anemia, Sickle Cell; Erythrocytes; Heme; Hemoglobinopathies; Hemoglobins, Abnormal; Humans; Infant; Infant, Newborn; Porphobilinogen Synthase; Pyruvate Kinase; Thalassemia	1976
Hb Isehara (or Hb Redondo) [beta 92 (F8) His----Asn]: an unstable variant with a proximal histidine substitution at the heme contact. Hemoglobin, 1991, Volume: 15, Issue:4 Topics: Amino Acid Sequence; Anemia, Hemolytic, Congenital; Base Sequence; Female; Globins; Heme; Hemoglobinopathies; Hemoglobins, Abnormal; Humans; Middle Aged; Molecular Sequence Data	1991
Molecular pathology of hemoglobin M Saskatoon disease. Biomedica biochimica acta, 1990, Volume: 49, Issue:2-3 Topics: Ferrous Compounds; Heme; Hemoglobin M; Hemoglobinopathies; Hemoglobins, Abnormal; Humans; Methemoglobin; Spectrum Analysis, Raman	1990
Hb Evans or alpha 262(E11)Val----Met beta 2; an unstable hemoglobin causing a mild hemolytic anemia. Hemoglobin, 1989, Volume: 13, Issue:6 Topics: Adult; Amino Acid Sequence; Anemia, Hemolytic; Base Sequence; Binding Sites; Child, Preschool; DNA Mutational Analysis; Female; Genes; Globins; Heme; Hemoglobinopathies; Hemoglobins, Abnormal; Humans; Molecular Sequence Data; Protein Conformation	1989
[Hemoglobinopathies and oxygen transport]. Bulletin de l'Academie nationale de medecine, 1989, Volume: 173, Issue:3 Topics: Adult; Amino Acids; Female; Heme; Hemoglobinopathies; Hemoglobins; Humans; Male; Middle Aged; Oxygen	1989
Inhibition of red blood cell enzymes by hemin: a mechanism for hemolysis in hemoglobinopathies. Transactions of the Association of American Physicians, 1987, Volume: 100 Topics: Enzyme Inhibitors; Enzymes; Erythrocytes; Glycolysis; Heme; Hemoglobinopathies; Hemolysis; Humans; Kinetics; Pentose Phosphate Pathway; Reference Values	1987
Plasma heme-binding in patients with hemolytic disorders. The Journal of laboratory and clinical medicine, 1968, Volume: 71, Issue:3 Topics: Adult; Beta-Globulins; Blood Protein Electrophoresis; Blood Proteins; Female; Haptoglobins; Hematologic Diseases; Heme; Hemoglobinopathies; Hemolysis; Humans; Immunoelectrophoresis; Male; Middle Aged; Protein Binding; Serum Albumin	1968
The effect of lead on total globin and alpha- and beta-chain synthesis; in vitro and in vivo. British journal of haematology, 1974, Volume: 27, Issue:3 Topics: Adult; Anemia, Hemolytic, Autoimmune; Anemia, Hypochromic; Depression, Chemical; Female; Globins; Heme; Hemoglobinopathies; Hemoglobins; Humans; In Vitro Techniques; Lead; Leucine; Male; Puromycin; Radioisotopes; Reticulocytes; Tritium	1974
Some aspects of the haemoglobinopathies. Transactions of the Royal Society of Tropical Medicine and Hygiene, 1974, Volume: 68, Issue:2 Topics: Amino Acid Sequence; Anemia, Sickle Cell; Fetal Hemoglobin; Genetic Variation; Heme; Hemoglobinometry; Hemoglobinopathies; Hemoglobins, Abnormal; Heterozygote; Humans; Imino Acids; Molecular Conformation; Mutation; Structure-Activity Relationship; Thalassemia	1974
Urinary pyrrole pigments in thalassemia and unstable hemoglobin diseases. Annals of the New York Academy of Sciences, 1974, Volume: 232, Issue:0 Topics: Blood Transfusion; Chromatography; Esters; Heme; Hemoglobinopathies; Pyrroles; Splenectomy; Thalassemia	1974
Intermediate hemichrome formation after oxidation of three unstable hemoglobins (Freiburg, Riverdale-Bronx and Köln). Hamatologie und Bluttransfusion, 1972, Volume: 10 Topics: Chromatography, DEAE-Cellulose; Erythrocytes; Heinz Bodies; Heme; Hemoglobinopathies; Hemoglobins, Abnormal; Hemolysis; Methemoglobin; Microscopy, Phase-Contrast; Oxidation-Reduction; Protein Denaturation; Spectrophotometry	1972
[Unstable hemoglobins]. Biochimie, 1972, Volume: 54, Issue:5 Topics: Amino Acid Sequence; Binding Sites; Globins; Heme; Hemoglobinopathies; Hemoglobins; Hemoglobins, Abnormal; Humans; Oxygen; Oxyhemoglobins; Protein Conformation; Structure-Activity Relationship	1972
Inherited disorders of hemoglobin synthesis and pregnancy. American journal of obstetrics and gynecology, 1971, Volume: 111, Issue:1 Topics: Abortion, Induced; Abortion, Therapeutic; Adult; Anemia, Sickle Cell; Cesarean Section; Female; Fetal Death; Fetal Hemoglobin; Hematopoiesis; Hematuria; Heme; Hemoglobin C Disease; Hemoglobinopathies; Hemoglobins; Humans; Infant, Newborn; Infertility, Female; Kidney Diseases; Lung Diseases; Maternal-Fetal Exchange; Obstetric Labor, Premature; Pre-Eclampsia; Pregnancy; Pregnancy Complications, Cardiovascular; Pregnancy Complications, Hematologic; Splenomegaly; Thalassemia; Uterine Hemorrhage	1971
[Chemical and genetic aspects of hemoglobinosynthesis]. Marseille medical, 1971, Volume: 108, Issue:9 Topics: Chemical Phenomena; Chemistry; Genes; Genes, Regulator; Globins; Heme; Hemoglobinopathies; Hemoglobins; Humans; Thalassemia	1971
[Erythrocyte diseases caused by disordered synthesis of heme]. Medicinski pregled, 1971, Volume: 24, Issue:9 Topics: Anemia, Sideroblastic; Heme; Hemoglobinopathies; Humans; Porphyrins	1971
[Niort hemoglobin: a new unstable hemoglobin]. Bulletin de la Societe de chimie biologique, 1970, Volume: 52, Issue:11 Topics: Chromatography, Gel; Electrophoresis; Heme; Hemoglobinopathies; Hemoglobins, Abnormal; Methods; Oxygen; Spectrophotometry	1970
A new approach to haemoglobin variant identification. Haemoglobin Christchurch beta-71 (E15) phenylalanine leads to serine. Biochimica et biophysica acta, 1971, Jun-29, Volume: 236, Issue:3 Topics: Adolescent; Amino Acid Sequence; Amino Acids; Anemia, Hemolytic; Anemia, Pernicious; Autoradiography; Carbon Isotopes; Chromatography, Thin Layer; Drug Stability; Electrophoresis; Erythrocytes; Female; Heme; Hemoglobinopathies; Hemoglobins; Hemoglobins, Abnormal; Hemolysis; Humans; Methods; New Zealand; Peptides; Phenylalanine; Serine	1971
[Significance of disorders of hemoglobin synthesis for the clinical practice]. Die Medizinische Welt, 1967, Dec-16, Volume: 50 Topics: Anemia, Macrocytic; Anemia, Sickle Cell; Deferoxamine; Erythrocyte Aging; Erythropoiesis; Hematologic Diseases; Heme; Hemoglobinopathies; Hemoglobins; Hemoglobins, Abnormal; Humans; Methemoglobinemia; Mitochondria; Peptide Biosynthesis	1967
Hemoglobin M--an early chapter in the saga of molecular pathology. Annals of internal medicine, 1969, Volume: 70, Issue:5 Topics: Heme; Hemoglobinopathies; Hemoglobins, Abnormal; Humans; Methemoglobin; Methemoglobinemia; Molecular Biology	1969