heme has been researched along with Amino Acid Metabolism Disorders, Inborn in 11 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 1 (9.09) | 18.7374 |
| 1990's | 6 (54.55) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 1 (9.09) | 24.3611 |
| 2020's | 3 (27.27) | 2.80 |
| Authors | Studies |
|---|---|
| Bender, D; Cirak, S; Daimagüler, HS; Gehling, T; Kaczmarek, AT; Kohl, JB; Koy, A; Liebau, MC; Santamaria-Araujo, JA; Schwarz, G | 1 |
| Langendonk, JG; Neeleman, RA; Williams, M; Wilson, JHP | 1 |
| Bender, D; Burlina, AB; Kaczmarek, AT; Kuester, S; Schwarz, G | 1 |
| Arjune, S; Belaidi, AA; Krizowski, S; Röper, J; Schwarz, G; Trifunovic, A | 1 |
| Kappas, A; Sassa, S | 1 |
| Beri, R; Chandra, R | 1 |
| Boynton, SB; Carter, BE; Connor, E; Fowler, B; Roth, KS; Wyss, PA | 1 |
| Bloomer, JR; Freese, D; Glock, M; Pascual-Leone, A; Payne, W; Rank, JM; Sharp, H | 1 |
| Halvorsen, S; Kvittingen, EA; Steen-Johnsen, J; Søvik, O | 1 |
| Carter, BE; Moses, LC; Roth, KS; Spencer, PD | 1 |
| Bain, MD; Bingham, P; Chalmers, RA; Jones, M; Purkiss, P; Stacey, TE | 1 |
1 review(s) available for heme and Amino Acid Metabolism Disorders, Inborn
| Article | Year |
|---|---|
Chemistry and biology of heme. Effect of metal salts, organometals, and metalloporphyrins on heme synthesis and catabolism, with special reference to clinical implications and interactions with cytochrome P-450.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Catalysis; Cytochrome P-450 Enzyme System; Drug Interactions; Heme; Humans; Hyperbilirubinemia; Infant, Newborn; Lead Poisoning; Leukemia, Erythroblastic, Acute; Metalloporphyrins; Metals; Organometallic Compounds; Tyrosine | 1993 |
1 trial(s) available for heme and Amino Acid Metabolism Disorders, Inborn
| Article | Year |
|---|---|
Hematin therapy for the neurologic crisis of tyrosinemia.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Aminolevulinic Acid; Heme; Hemin; Heptanoates; Humans; Infant; Liver Transplantation; Male; Tyrosine | 1991 |
9 other study(ies) available for heme and Amino Acid Metabolism Disorders, Inborn
| Article | Year |
|---|---|
A defect in molybdenum cofactor binding causes an attenuated form of sulfite oxidase deficiency.
Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Coenzymes; Heme; Humans; Metalloproteins; Molybdenum Cofactors; Pteridines; Sulfite Oxidase; Sulfites | 2022 |
Heme as an initial treatment for severe decompensation in tyrosinemia type 1.
Topics: Amino Acid Metabolism, Inborn Errors; Canada; Consensus; Heme; Humans; Tyrosinemias | 2020 |
Oxygen and nitrite reduction by heme-deficient sulphite oxidase in a patient with mild sulphite oxidase deficiency.
Topics: Amino Acid Metabolism, Inborn Errors; Catalytic Domain; Coenzymes; Electron Transport; Heme; Humans; Infant; Mitochondria; Molybdenum; Nitrites; Oxidation-Reduction; Oxidoreductases Acting on Sulfur Group Donors; Oxygen; Sulfite Oxidase | 2020 |
Oxygen reactivity of mammalian sulfite oxidase provides a concept for the treatment of sulfite oxidase deficiency.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Enzyme Replacement Therapy; Enzyme Stability; HEK293 Cells; Heme; Humans; Hydrogen Peroxide; Mice; Oxidoreductases Acting on Sulfur Group Donors; Oxygen; Oxygen Consumption; Polyethylene Glycols; Sulfite Oxidase | 2015 |
Hereditary tyrosinemia and the heme biosynthetic pathway. Profound inhibition of delta-aminolevulinic acid dehydratase activity by succinylacetone.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Cattle; Chick Embryo; Erythrocytes; Heme; Heptanoates; Heptanoic Acids; Humans; In Vitro Techniques; Liver; Mice; Mice, Inbred BALB C; Porphobilinogen Synthase; Species Specificity; Tyrosine | 1983 |
Renal heme metabolism in hereditary tyrosinemia: use of succinylacetone in rat renal tubules.
Topics: Amino Acid Metabolism, Inborn Errors; Animals; Cytochrome P-450 Enzyme System; Cytosol; Ferrochelatase; Heme; Heme Oxygenase (Decyclizing); Heptanoates; Kidney Cortex; Kidney Tubules; Male; Models, Biological; Porphyrins; Rats; Rats, Inbred Strains; Tyrosine | 1991 |
Hereditary tyrosinemia of chronic course without rickets and renal tubular dysfunction.
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Amino Acids; Child; Child, Preschool; Chronic Kidney Disease-Mineral and Bone Disorder; Female; Heme; Heptanoates; Humans; Hydrolases; Male; Porphobilinogen Synthase; Thrombocytopenia; Tyrosine | 1990 |
On rat renal aminolevulinate transport and metabolism in experimental Fanconi syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Aminolevulinic Acid; Animals; Biological Transport, Active; Fanconi Syndrome; Heme; Heptanoates; In Vitro Techniques; Kidney Tubules; Male; Maleates; Microvilli; Porphobilinogen Synthase; Rats; Rats, Inbred Strains; Tyrosine | 1990 |
Dietary treatment eliminates succinylacetone from the urine of a patient with tyrosinaemia type 1.
Topics: Amino Acid Metabolism, Inborn Errors; Female; Heme; Heptanoates; Heptanoic Acids; Humans; Infant; Methionine; Phenylalanine; Tyrosine | 1990 |