Page last updated: 2024-08-24

halofuginone and Becker Muscular Dystrophy

halofuginone has been researched along with Becker Muscular Dystrophy in 7 studies

Research

Studies (7)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's2 (28.57)29.6817
2010's4 (57.14)24.3611
2020's1 (14.29)2.80

Authors

AuthorsStudies
Evans, P; Genin, O; Halevy, O; Mordechay, S; Pines, M; Smullen, S1
Evans, P; Genin, O; Halevy, O; Mordechay, S; Pines, M; Wellner, G1
Barzilai-Tutsch, H; Bodanovsky, A; Genin, O; Guttman, N; Halevy, O; Levy, O; Pines, M1
Angelini, C; Genin, O; Halevy, O; Levi, O; Pines, M1
Barzilai-Tutsch, H; Bodanovsky, A; Halevy, O; Maimon, H; Pines, M1
Anderson, JE; Halevy, O; Huebner, KD; Jassal, DS; Pines, M1
McLoon, LK1

Other Studies

7 other study(ies) available for halofuginone and Becker Muscular Dystrophy

ArticleYear
Differential Effects of Halofuginone Enantiomers on Muscle Fibrosis and Histopathology in Duchenne Muscular Dystrophy.
    International journal of molecular sciences, 2021, Jun-30, Volume: 22, Issue:13

    Topics: Animals; Disease Models, Animal; Fibrosis; Male; Mice; Mice, Inbred mdx; Muscle, Skeletal; Muscular Dystrophy, Duchenne; Piperidines; Quinazolinones

2021
Hydroxy group requirement for halofuginone-dependent inhibition of muscle fibrosis and improvement of histopathology in the mdx mouse model for Duchenne muscular dystrophy.
    Histology and histopathology, 2019, Volume: 34, Issue:7

    Topics: Animals; Disease Models, Animal; Fibrillar Collagens; Fibrosis; Humans; Male; Mice; Mice, Inbred C57BL; Mice, Inbred mdx; Muscle Fibers, Skeletal; Muscle, Skeletal; Muscular Dystrophy, Duchenne; Phosphorylation; Piperidines; Quinazolinones; Signal Transduction; Smad3 Protein; Utrophin

2019
Halofuginone improves muscle-cell survival in muscular dystrophies.
    Biochimica et biophysica acta, 2014, Volume: 1843, Issue:7

    Topics: Actins; Animals; Apoptosis; bcl-2 Homologous Antagonist-Killer Protein; bcl-2-Associated X Protein; Cell Survival; Diaphragm; Disease Models, Animal; Extracellular Signal-Regulated MAP Kinases; Gene Expression Regulation; Humans; Macrophages; Mice; Mice, Inbred mdx; Mixed Function Oxygenases; Muscular Dystrophy, Duchenne; Myoblasts; Myofibrils; PAX7 Transcription Factor; Phosphatidylinositol 3-Kinases; Piperidines; Primary Cell Culture; Quinazolinones; Signal Transduction

2014
Inhibition of muscle fibrosis results in increases in both utrophin levels and the number of revertant myofibers in Duchenne muscular dystrophy.
    Oncotarget, 2015, Sep-15, Volume: 6, Issue:27

    Topics: Animals; Biopsy; Child; Child, Preschool; Collagen; Collagen Type I; Gene Expression Regulation; Humans; Immunohistochemistry; Male; Mice; Mice, Inbred C57BL; Mice, Inbred mdx; Muscle Fibers, Skeletal; Muscle, Skeletal; Muscular Dystrophy, Duchenne; Piperidines; Quadriceps Muscle; Quinazolinones; Utrophin

2015
Halofuginone promotes satellite cell activation and survival in muscular dystrophies.
    Biochimica et biophysica acta, 2016, Volume: 1862, Issue:1

    Topics: Animals; Apoptosis; Cell Cycle; Cell Survival; Male; MAP Kinase Signaling System; Mice; Mice, Inbred C57BL; Muscle Fibers, Skeletal; Muscular Dystrophies, Limb-Girdle; Muscular Dystrophy, Duchenne; Phosphatidylinositol 3-Kinases; Piperidines; Proto-Oncogene Proteins c-akt; Quinazolinones; Satellite Cells, Skeletal Muscle; Signal Transduction

2016
Functional resolution of fibrosis in mdx mouse dystrophic heart and skeletal muscle by halofuginone.
    American journal of physiology. Heart and circulatory physiology, 2008, Volume: 294, Issue:4

    Topics: Actins; Age Factors; Animals; Cell Proliferation; Collagen Type I; Collagen Type III; Diaphragm; Disease Models, Animal; Fibrosis; Heart; Hepatocyte Growth Factor; Mice; Mice, Inbred mdx; Muscle Strength; Muscle, Skeletal; Muscular Dystrophy, Duchenne; Myocardium; Physical Endurance; Piperidines; Protein Synthesis Inhibitors; Quadriceps Muscle; Quinazolinones; Respiratory Mechanics; Running; Time Factors; Ventricular Function, Left

2008
Focusing on fibrosis: halofuginone-induced functional improvement in the mdx mouse model of Duchenne muscular dystrophy.
    American journal of physiology. Heart and circulatory physiology, 2008, Volume: 294, Issue:4

    Topics: Age Factors; Animals; Collagen Type I; Collagen Type III; Disease Models, Animal; Fibrosis; Heart; Mice; Mice, Inbred mdx; Muscle Strength; Muscle, Skeletal; Muscular Dystrophy, Duchenne; Myocardium; Physical Endurance; Piperidines; Protein Synthesis Inhibitors; Quinazolinones; Respiratory Mechanics; Time Factors; Ventricular Function, Left

2008