Page last updated: 2024-10-18

glycocyamine and Muscle Disorders

glycocyamine has been researched along with Muscle Disorders in 8 studies

glycocyamine: RN given refers to parent cpd; structure
guanidinoacetate : A monocarboxylic acid anion that is the conjugate base of guanidinoacetic acid, obtained by deprotonation of the carboxy group.
guanidinoacetic acid : The N-amidino derivative of glycine.

Research Excerpts

ExcerptRelevanceReference
"Treatment with creatine monohydrate (100-800 mg/kg/day) resulted in almost complete restoration of brain creatine levels and significant improvement of myopathy."1.42Arginine:glycine amidinotransferase (AGAT) deficiency: Clinical features and long term outcomes in 16 patients diagnosed worldwide. ( Apatean, D; Battini, R; DeBrosse, S; Dessoffy, K; Dowling, MD; Edvardson, S; Eichler, F; Johnston, K; Koeller, DM; Nouioua, S; Stockler-Ipsiroglu, S; Tazir, M; Verma, A; Wierenga, AM; Wierenga, KJ; Wong, LJ; Zhang, V, 2015)

Research

Studies (8)

TimeframeStudies, this research(%)All Research%
pre-19903 (37.50)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's3 (37.50)24.3611
2020's2 (25.00)2.80

Authors

AuthorsStudies
Balestrino, M1
Adriano, E1
Neu, A1
Hornig, S1
Sasani, A1
Isbrandt, D1
Gerloff, C1
Tsikas, D1
Schwedhelm, E1
Choe, CU1
Córdova-Noboa, HA2
Oviedo-Rondón, EO2
Sarsour, AH2
Barnes, J2
Sapcota, D1
López, D1
Gross, L1
Rademacher-Heilshorn, M2
Braun, U2
Ferzola, P1
Stockler-Ipsiroglu, S1
Apatean, D1
Battini, R1
DeBrosse, S1
Dessoffy, K1
Edvardson, S1
Eichler, F1
Johnston, K1
Koeller, DM1
Nouioua, S1
Tazir, M1
Verma, A1
Dowling, MD1
Wierenga, KJ1
Wierenga, AM1
Zhang, V1
Wong, LJ1
CUMINGS, JN1
ALDES, JH1
Afting, EG1
Bernhardt, W1
Janzen, RW1
Röthig, HJ1

Other Studies

8 other studies available for glycocyamine and Muscle Disorders

ArticleYear
Presence of guanidinoacetate may compensate creatine absence and account for less statin-induced muscle damage in GAMT-deficient compared to AGAT-deficient mice.
    Amino acids, 2020, Volume: 52, Issue:4

    Topics: Amidinotransferases; Amino Acid Metabolism, Inborn Errors; Animals; Creatine; Developmental Disabili

2020
Creatine, guanidinoacetate and homoarginine in statin-induced myopathy.
    Amino acids, 2020, Volume: 52, Issue:6-7

    Topics: Amidinotransferases; Amino Acid Metabolism, Inborn Errors; Animals; Creatine; Developmental Disabili

2020
Effect of guanidinoacetic acid supplementation on live performance, meat quality, pectoral myopathies and blood parameters of male broilers fed corn-based diets with or without poultry by-products.
    Poultry science, 2018, Jul-01, Volume: 97, Issue:7

    Topics: Animal Feed; Animal Nutritional Physiological Phenomena; Animals; Blood Chemical Analysis; Chickens;

2018
Performance, meat quality, and pectoral myopathies of broilers fed either corn or sorghum based diets supplemented with guanidinoacetic acid.
    Poultry science, 2018, Jul-01, Volume: 97, Issue:7

    Topics: Animal Feed; Animal Nutritional Physiological Phenomena; Animals; Chickens; Diet; Dietary Supplement

2018
Arginine:glycine amidinotransferase (AGAT) deficiency: Clinical features and long term outcomes in 16 patients diagnosed worldwide.
    Molecular genetics and metabolism, 2015, Volume: 116, Issue:4

    Topics: Adolescent; Amidinotransferases; Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Crea

2015
Creatine and guanidoacetic acid metabolism in muscle disease.
    Brain : a journal of neurology, 1953, Volume: 76, Issue:2

    Topics: Acetates; Blood; Creatine; Disease; Glycine; Muscles; Muscular Diseases; Urine

1953
Glycocyamine betaine as an adjunct in the treatment of neuromuscular disease patients.
    The Journal of the Arkansas Medical Society, 1957, Volume: 54, Issue:5

    Topics: Amidines; Betaine; Choline; Disease; Glycine; Humans; Muscles; Muscular Diseases; Neuromuscular Dise

1957
Quantitative importance of non-skeletal-muscle N tau-methylhistidine and creatine in human urine.
    The Biochemical journal, 1981, Nov-15, Volume: 200, Issue:2

    Topics: Creatine; Creatinine; Glycine; Histidine; Humans; Male; Methylhistidines; Middle Aged; Muscles; Musc

1981