glycocyamine has been researched along with Aprosodia in 6 studies
glycocyamine: RN given refers to parent cpd; structure
guanidinoacetate : A monocarboxylic acid anion that is the conjugate base of guanidinoacetic acid, obtained by deprotonation of the carboxy group.
guanidinoacetic acid : The N-amidino derivative of glycine.
Excerpt | Relevance | Reference |
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" AGAT patients might benefit from oral GAA due to upgraded bioavailability and convenient utilization of the compound, while possible drawbacks (e." | 2.61 | Benefits and drawbacks of guanidinoacetic acid as a possible treatment to replenish cerebral creatine in AGAT deficiency. ( Ostojic, SM, 2019) |
"Treatment with creatine monohydrate (100-800 mg/kg/day) resulted in almost complete restoration of brain creatine levels and significant improvement of myopathy." | 1.42 | Arginine:glycine amidinotransferase (AGAT) deficiency: Clinical features and long term outcomes in 16 patients diagnosed worldwide. ( Apatean, D; Battini, R; DeBrosse, S; Dessoffy, K; Dowling, MD; Edvardson, S; Eichler, F; Johnston, K; Koeller, DM; Nouioua, S; Stockler-Ipsiroglu, S; Tazir, M; Verma, A; Wierenga, AM; Wierenga, KJ; Wong, LJ; Zhang, V, 2015) |
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 1 (16.67) | 29.6817 |
2010's | 3 (50.00) | 24.3611 |
2020's | 2 (33.33) | 2.80 |
Authors | Studies |
---|---|
Balestrino, M | 1 |
Adriano, E | 1 |
Neu, A | 1 |
Hornig, S | 1 |
Sasani, A | 1 |
Isbrandt, D | 1 |
Gerloff, C | 1 |
Tsikas, D | 1 |
Schwedhelm, E | 1 |
Choe, CU | 1 |
Ostojic, SM | 1 |
Nouioua, S | 2 |
Cheillan, D | 1 |
Zaouidi, S | 1 |
Salomons, GS | 1 |
Amedjout, N | 1 |
Kessaci, F | 1 |
Boulahdour, N | 1 |
Hamadouche, T | 1 |
Tazir, M | 2 |
Stockler-Ipsiroglu, S | 1 |
Apatean, D | 1 |
Battini, R | 1 |
DeBrosse, S | 1 |
Dessoffy, K | 1 |
Edvardson, S | 1 |
Eichler, F | 1 |
Johnston, K | 1 |
Koeller, DM | 1 |
Verma, A | 1 |
Dowling, MD | 1 |
Wierenga, KJ | 1 |
Wierenga, AM | 1 |
Zhang, V | 1 |
Wong, LJ | 1 |
Braissant, O | 1 |
Henry, H | 1 |
2 reviews available for glycocyamine and Aprosodia
Article | Year |
---|---|
Benefits and drawbacks of guanidinoacetic acid as a possible treatment to replenish cerebral creatine in AGAT deficiency.
Topics: Amidinotransferases; Amino Acid Metabolism, Inborn Errors; Clinical Trials as Topic; Creatine; Devel | 2019 |
AGAT, GAMT and SLC6A8 distribution in the central nervous system, in relation to creatine deficiency syndromes: a review.
Topics: Amidinotransferases; Amino Acid Metabolism, Inborn Errors; Animals; Brain; Creatine; Developmental D | 2008 |
4 other studies available for glycocyamine and Aprosodia
Article | Year |
---|---|
Presence of guanidinoacetate may compensate creatine absence and account for less statin-induced muscle damage in GAMT-deficient compared to AGAT-deficient mice.
Topics: Amidinotransferases; Amino Acid Metabolism, Inborn Errors; Animals; Creatine; Developmental Disabili | 2020 |
Creatine, guanidinoacetate and homoarginine in statin-induced myopathy.
Topics: Amidinotransferases; Amino Acid Metabolism, Inborn Errors; Animals; Creatine; Developmental Disabili | 2020 |
Creatine deficiency syndrome. A treatable myopathy due to arginine-glycine amidinotransferase (AGAT) deficiency.
Topics: Amidinotransferases; Amino Acid Metabolism, Inborn Errors; Brain; Child; Creatine; Developmental Dis | 2013 |
Arginine:glycine amidinotransferase (AGAT) deficiency: Clinical features and long term outcomes in 16 patients diagnosed worldwide.
Topics: Adolescent; Amidinotransferases; Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Crea | 2015 |