glycine has been researched along with Hyperammonemia in 12 studies
Hyperammonemia: Elevated level of AMMONIA in the blood. It is a sign of defective CATABOLISM of AMINO ACIDS or ammonia to UREA.
Excerpt | Relevance | Reference |
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"Hyperornithinemia, hyperammonemia, and homocitrullinuria (HHH) syndrome is caused by mutations in the SLC25A15 (ORNT1) gene encoding the mitochondrial ornithine transporter, but the mechanism of pathogenesis of the encephalopathy, spastic paraparesis and hepatopathy remains undetermined." | 7.72 | Hyperornithinemia, hyperammonemia, and homocitrullinuria syndrome with evidence of mitochondrial dysfunction due to a novel SLC25A15 (ORNT1) gene mutation in a Palestinian family. ( Abu-Libdeh, B; Gutman, A; Kanazawa, N; Korman, SH; Tsujino, S, 2004) |
"Hyperammonemia is a common finding in children with methylmalonic acidemia." | 3.83 | A neuronal disruption in redox homeostasis elicited by ammonia alters the glycine/glutamate (GABA) cycle and contributes to MMA-induced excitability. ( Braga, DV; da Silva, AM; da Silva, LR; da Silveira Junior, ME; de Oliveira Ferreira, AP; Della-Pace, ID; Dobrachinski, F; Fighera, MR; Furian, AF; Gabbi, P; Grisólia, AB; Marchesan, S; Oliveira, MS; Ribeiro, LR; Rodrigues, FS; Royes, LF; Soares, FA, 2016) |
"Hyperornithinemia, hyperammonemia, and homocitrullinuria (HHH) syndrome is caused by mutations in the SLC25A15 (ORNT1) gene encoding the mitochondrial ornithine transporter, but the mechanism of pathogenesis of the encephalopathy, spastic paraparesis and hepatopathy remains undetermined." | 3.72 | Hyperornithinemia, hyperammonemia, and homocitrullinuria syndrome with evidence of mitochondrial dysfunction due to a novel SLC25A15 (ORNT1) gene mutation in a Palestinian family. ( Abu-Libdeh, B; Gutman, A; Kanazawa, N; Korman, SH; Tsujino, S, 2004) |
"Sivelestat was given for the complication of ARDS." | 1.42 | Elevation of pivaloylcarnitine by sivelestat sodium in two children. ( Bo, R; Hasegawa, Y; Ishige, N; Kobayashi, H; Nakamura, M; Takahashi, T; Yamada, K; Yamaguchi, S, 2015) |
"Glycine is an important ammoniagenic amino acid, which is increased in acute liver failure (ALF)." | 1.40 | L-Ornithine phenylacetate reduces ammonia in pigs with acute liver failure through phenylacetylglycine formation: a novel ammonia-lowering pathway. ( Fuskevåg, OM; Jalan, R; Kristiansen, RG; Mæhre, H; Revhaug, A; Rose, CF; Ytrebø, LM, 2014) |
"The encephalopathy and seizures were ascribed to accumulation of toxic metabolites of glycine, especially ammonia (serum level -1261 mcmol/L)." | 1.37 | Postprostatectomy seizures: A case report. ( Bichu, P; Misra, M; Phadke, G; Sangha, H, 2011) |
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 1 (8.33) | 18.2507 |
2000's | 4 (33.33) | 29.6817 |
2010's | 7 (58.33) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Auray-Blais, C | 1 |
Maranda, B | 1 |
Lavoie, P | 1 |
Kristiansen, RG | 2 |
Rose, CF | 2 |
Fuskevåg, OM | 1 |
Mæhre, H | 1 |
Revhaug, A | 1 |
Jalan, R | 1 |
Ytrebø, LM | 2 |
Yamada, K | 1 |
Kobayashi, H | 1 |
Bo, R | 1 |
Takahashi, T | 1 |
Hasegawa, Y | 1 |
Nakamura, M | 1 |
Ishige, N | 1 |
Yamaguchi, S | 1 |
Cabrera-Pastor, A | 1 |
Taoro-Gonzalez, L | 1 |
Felipo, V | 3 |
Royes, LF | 1 |
Gabbi, P | 1 |
Ribeiro, LR | 1 |
Della-Pace, ID | 1 |
Rodrigues, FS | 1 |
de Oliveira Ferreira, AP | 1 |
da Silveira Junior, ME | 1 |
da Silva, LR | 1 |
Grisólia, AB | 1 |
Braga, DV | 1 |
Dobrachinski, F | 1 |
da Silva, AM | 1 |
Soares, FA | 1 |
Marchesan, S | 1 |
Furian, AF | 1 |
Oliveira, MS | 1 |
Fighera, MR | 1 |
Poo, JL | 1 |
Cervera, E | 1 |
de Hoyos, A | 1 |
Gil, S | 1 |
Cadena, M | 1 |
Uribe, M | 1 |
Bichu, P | 1 |
Phadke, G | 1 |
Sangha, H | 1 |
Misra, M | 1 |
Canales, JJ | 1 |
Elayadi, A | 1 |
Errami, M | 1 |
Llansola, M | 1 |
Cauli, O | 2 |
Korman, SH | 1 |
Kanazawa, N | 1 |
Abu-Libdeh, B | 1 |
Gutman, A | 1 |
Tsujino, S | 1 |
Mlili, N | 1 |
Rodrigo, R | 1 |
Bhakta, P | 1 |
Goel, A | 1 |
Acharjee, P | 1 |
Biswas, BK | 1 |
2 reviews available for glycine and Hyperammonemia
Article | Year |
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Glycine and hyperammonemia: potential target for the treatment of hepatic encephalopathy.
Topics: Animals; Drug Delivery Systems; Glycine; Hepatic Encephalopathy; Humans; Hyperammonemia; Ornithine; | 2016 |
[Rationale for the use of sodium benzoate in clinical hepatology].
Topics: Acetates; Adult; Animals; Child; Clinical Trials as Topic; Drug Evaluation, Preclinical; Glycine; He | 1990 |
10 other studies available for glycine and Hyperammonemia
Article | Year |
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High-throughput tandem mass spectrometry multiplex analysis for newborn urinary screening of creatine synthesis and transport disorders, Triple H syndrome and OTC deficiency.
Topics: Biomarkers; Creatine; Creatinine; Filtration; Glycine; Humans; Hyperammonemia; Infant, Newborn; Orni | 2014 |
L-Ornithine phenylacetate reduces ammonia in pigs with acute liver failure through phenylacetylglycine formation: a novel ammonia-lowering pathway.
Topics: Ammonia; Animals; Biomarkers; Brain; Disease Models, Animal; Female; Glycine; Hyperammonemia; Kidney | 2014 |
Elevation of pivaloylcarnitine by sivelestat sodium in two children.
Topics: Amino Acid Metabolism, Inborn Errors; Cardiomyopathies; Carnitine; Child, Preschool; Chromatography, | 2015 |
Hyperammonemia alters glycinergic neurotransmission and modulation of the glutamate-nitric oxide-cGMP pathway by extracellular glycine in cerebellum in vivo.
Topics: Animals; Cerebellum; Cyclic GMP; Dose-Response Relationship, Drug; Extracellular Fluid; Glutamic Aci | 2016 |
A neuronal disruption in redox homeostasis elicited by ammonia alters the glycine/glutamate (GABA) cycle and contributes to MMA-induced excitability.
Topics: Ammonia; Animals; Cerebral Cortex; Cytokines; Electroencephalography; Glutamic Acid; Glycine; Homeos | 2016 |
Postprostatectomy seizures: A case report.
Topics: Aged; Glycine; Humans; Hyperammonemia; Hyponatremia; Male; Prostatectomy; Renal Dialysis; Seizures | 2011 |
Chronic hyperammonemia alters motor and neurochemical responses to activation of group I metabotropic glutamate receptors in the nucleus accumbens in rats in vivo.
Topics: Animals; Chromones; Chronic Disease; Dopamine; Excitatory Amino Acid Agonists; Excitatory Amino Acid | 2003 |
Hyperornithinemia, hyperammonemia, and homocitrullinuria syndrome with evidence of mitochondrial dysfunction due to a novel SLC25A15 (ORNT1) gene mutation in a Palestinian family.
Topics: Adolescent; Alanine; Amino Acid Metabolism, Inborn Errors; Amino Acid Transport Systems, Basic; Arab | 2004 |
Hyperammonaemia alters the mechanisms by which metabotropic glutamate receptors in nucleus accumbens modulate motor function.
Topics: Animals; Disease Models, Animal; Excitatory Amino Acid Agonists; Glycine; Hyperammonemia; Male; Micr | 2007 |
Propofol for the management of glycine-mediated excitatory symptoms of TURP syndrome.
Topics: Aged; Akathisia, Drug-Induced; Glycine; Glycine Agents; Humans; Hyperammonemia; Hypnotics and Sedati | 2008 |