glycine has been researched along with Acidemia Propionic in 3 studies
Excerpt | Relevance | Reference |
---|---|---|
"Propionic Acidemia (PA) is a rare metabolic disorder caused by the defect in enzyme (propionyl-coenzyme A (CoA) carboxylase) leading to the abnormal accumulation of metabolites of branched-chain amino acid catabolism in blood and urine." | 4.12 | A Rare Case of Propionic Acidemia in a Six Months Female Child. ( Aamir, M; Bibi, A; Chaudhry, N; Haroon, ZH; Irum, S; Rehman, A, 2022) |
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 1 (33.33) | 29.6817 |
2010's | 1 (33.33) | 24.3611 |
2020's | 1 (33.33) | 2.80 |
Authors | Studies |
---|---|
Irum, S | 1 |
Rehman, A | 1 |
Aamir, M | 1 |
Haroon, ZH | 1 |
Chaudhry, N | 1 |
Bibi, A | 1 |
Scholl-Bürgi, S | 1 |
Sass, JO | 1 |
Zschocke, J | 1 |
Karall, D | 1 |
Al-Hassnan, ZN | 1 |
Boyadjiev, SA | 1 |
Praphanphoj, V | 1 |
Hamosh, A | 1 |
Braverman, NE | 1 |
Thomas, GH | 1 |
Geraghty, MT | 1 |
1 review available for glycine and Acidemia Propionic
Article | Year |
---|---|
Amino acid metabolism in patients with propionic acidaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Ammonia; Citric Acid Cycle; Diet; | 2012 |
2 other studies available for glycine and Acidemia Propionic
Article | Year |
---|---|
A Rare Case of Propionic Acidemia in a Six Months Female Child.
Topics: Amino Acids, Branched-Chain; Butyric Acid; Citrates; Coenzyme A; Female; Glycine; Humans; Infant; Ke | 2022 |
The relationship of plasma glutamine to ammonium and of glycine to acid-base balance in propionic acidaemia.
Topics: Acid-Base Equilibrium; Amino Acid Metabolism, Inborn Errors; Bicarbonates; Biomarkers; Diet, Protein | 2003 |