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glycerophosphoinositol 4,5-bisphosphate and Long QT Syndrome

glycerophosphoinositol 4,5-bisphosphate has been researched along with Long QT Syndrome in 9 studies

Research

Studies (9)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's2 (22.22)29.6817
2010's7 (77.78)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Abderemane-Ali, F; Amarouch, MY; Baró, I; Brasseur, R; Coyan, FC; Loussouarn, G; Marionneau, C; Mérot, J; Mordel, J; Nicolas, CS; Piron, J; Steenman, M; Thomas, A1
Attali, B; Ben-Tal Cohen, I; Dessauer, C; Dvir, M; Haitin, Y; Hirsch, JA; Kass, R; Pongs, O; Sachyani, D; Strulovich, R1
Sanders, CR; Taylor, KC1
Attali, B; Buki, T; Cui, M; Dvir, M; Haitin, Y; Hirsch, JA; Lebel, G; Logothetis, DE; Marom, M; Peretz, A; Tobelaim, WS1
Baró, I; Loussouarn, G1
Cui, J; Guan, M; Li, Y; Shi, J; Virgin-Downey, B; Wu, D; Zaydman, MA1
Gao, Z; Lan, X; Li, M; Xu, H; Zheng, Y; Zhou, P; Zhu, X1
Baró, I; Dahimene, S; Escande, D; Loussouarn, G; Mérot, J; Park, KH; Piron, J1
Baró, I; Choveau, F; Loussouarn, G; Mérot, J; Peroz, D; Rodriguez, N1

Reviews

3 review(s) available for glycerophosphoinositol 4,5-bisphosphate and Long QT Syndrome

ArticleYear
Regulation of KCNQ/Kv7 family voltage-gated K
    Biochimica et biophysica acta. Biomembranes, 2017, Volume: 1859, Issue:4

    Topics: Amino Acid Sequence; Binding Sites; Cell Membrane; Epilepsy, Benign Neonatal; Fatty Acids, Unsaturated; Hearing Loss, Bilateral; Humans; Hydrophobic and Hydrophilic Interactions; KCNQ1 Potassium Channel; Long QT Syndrome; Membrane Lipids; Models, Molecular; Phosphatidylinositol 4,5-Diphosphate; Protein Binding; Protein Isoforms; Protein Structure, Secondary

2017
Neural modulation of ion channels in cardiac arrhythmias: clinical implications and future investigations.
    Heart rhythm, 2010, Volume: 7, Issue:6

    Topics: Arrhythmias, Cardiac; Caveolin 3; Computer Simulation; Cyclic AMP; Death, Sudden, Cardiac; Humans; Induced Pluripotent Stem Cells; Ion Channels; Long QT Syndrome; Neurotransmitter Agents; Phosphatidylinositol 4,5-Diphosphate; Signal Transduction

2010
Kv7.1 (KCNQ1) properties and channelopathies.
    The Journal of physiology, 2008, Apr-01, Volume: 586, Issue:7

    Topics: Atrial Fibrillation; Humans; KCNQ1 Potassium Channel; Long QT Syndrome; Mutation; Myocytes, Cardiac; Patch-Clamp Techniques; Phosphatidylinositol 4,5-Diphosphate

2008

Other Studies

6 other study(ies) available for glycerophosphoinositol 4,5-bisphosphate and Long QT Syndrome

ArticleYear
A long QT mutation substitutes cholesterol for phosphatidylinositol-4,5-bisphosphate in KCNQ1 channel regulation.
    PloS one, 2014, Volume: 9, Issue:3

    Topics: Animals; Arrhythmias, Cardiac; Brugada Syndrome; Cardiac Conduction System Disease; Cell Line; Chlorocebus aethiops; Cholesterol; COS Cells; Heart Conduction System; KCNQ1 Potassium Channel; Long QT Syndrome; Magnesium; Mutation; Phosphatidylinositol 4,5-Diphosphate

2014
Long QT mutations at the interface between KCNQ1 helix C and KCNE1 disrupt I(KS) regulation by PKA and PIP₂.
    Journal of cell science, 2014, Sep-15, Volume: 127, Issue:Pt 18

    Topics: A Kinase Anchor Proteins; Animals; CHO Cells; Cricetinae; Cricetulus; Cyclic AMP; Cyclic AMP-Dependent Protein Kinases; Cytoskeletal Proteins; Humans; KCNQ1 Potassium Channel; Long QT Syndrome; Mutation, Missense; Phosphatidylinositol 4,5-Diphosphate; Phosphorylation; Potassium Channels, Voltage-Gated; Protein Binding; Protein Structure, Secondary

2014
Competition of calcified calmodulin N lobe and PIP2 to an LQT mutation site in Kv7.1 channel.
    Proceedings of the National Academy of Sciences of the United States of America, 2017, 01-31, Volume: 114, Issue:5

    Topics: Animals; Binding Sites; Binding, Competitive; Calcium Signaling; Calmodulin; CHO Cells; Cricetinae; Cricetulus; Humans; Immobilized Proteins; Long QT Syndrome; Models, Molecular; Molecular Docking Simulation; Molecular Dynamics Simulation; Mutation; Phosphatidylinositol 4,5-Diphosphate; Point Mutation; Potassium; Potassium Channels, Voltage-Gated; Protein Conformation; Protein Domains; Recombinant Proteins; Shaker Superfamily of Potassium Channels; Spectrometry, Fluorescence

2017
KCNE1 enhances phosphatidylinositol 4,5-bisphosphate (PIP2) sensitivity of IKs to modulate channel activity.
    Proceedings of the National Academy of Sciences of the United States of America, 2011, May-31, Volume: 108, Issue:22

    Topics: Amino Acid Sequence; Animals; Humans; Ions; KCNQ1 Potassium Channel; Lipids; Long QT Syndrome; Molecular Sequence Data; Mutation; Patch-Clamp Techniques; Phosphatidylinositol 4,5-Diphosphate; Potassium Channels; Potassium Channels, Voltage-Gated; Protein Structure, Tertiary; Sequence Homology, Amino Acid; Xenopus laevis; Xenopus Proteins

2011
Hexachlorophene is a potent KCNQ1/KCNE1 potassium channel activator which rescues LQTs mutants.
    PloS one, 2012, Volume: 7, Issue:12

    Topics: Action Potentials; Animals; Cell Line; CHO Cells; Cricetinae; Heart; Hexachlorophene; KCNQ1 Potassium Channel; Long QT Syndrome; Mutation; Myocytes, Cardiac; Phosphatidylinositol 4,5-Diphosphate

2012
Impaired KCNQ1-KCNE1 and phosphatidylinositol-4,5-bisphosphate interaction underlies the long QT syndrome.
    Circulation research, 2005, Apr-15, Volume: 96, Issue:7

    Topics: Animals; COS Cells; Ethyl Methanesulfonate; Humans; KCNQ Potassium Channels; KCNQ1 Potassium Channel; Long QT Syndrome; Magnesium; Mutation; Phosphatidylinositol 4,5-Diphosphate; Potassium Channels, Voltage-Gated

2005