glutamine and Electron Transport Chain Deficiencies, Mitochondrial

glutamine has been researched along with Electron Transport Chain Deficiencies, Mitochondrial in 5 studies

Research

Studies (5)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's1 (20.00)29.6817
2010's3 (60.00)24.3611
2020's1 (20.00)2.80

Authors

AuthorsStudies
Bornstein, R; Johnson, SC; Morgan, P; Mulholland, MT; Sedensky, M1
Alberti, JM; Baloh, RH; Biris, N; Dorn, GW; Franco, A; Gavathiotis, E; Janetka, JW; Kitsis, RN; Knight, WC; Krezel, AM; Mochly-Rosen, D; Rocha, AG; Rumsey, JM; Townsend, RR; Zacharioudakis, E1
Contreras, L; de la Villa, P; Du, J; Hurley, JB; Ramirez, L; Satrústegui, J1
Anglin, RE; Mazurek, MF; Noseworthy, MD; Rosebush, PI; Tarnopolsky, M1
Hodges, SD; Snyder, FF1

Reviews

1 review(s) available for glutamine and Electron Transport Chain Deficiencies, Mitochondrial

ArticleYear
Glutamine metabolism in diseases associated with mitochondrial dysfunction.
    Molecular and cellular neurosciences, 2023, Volume: 126

    Topics: Animals; Glutamine; MELAS Syndrome; Mitochondria; Mitochondrial Diseases; Neurodegenerative Diseases

2023

Other Studies

4 other study(ies) available for glutamine and Electron Transport Chain Deficiencies, Mitochondrial

ArticleYear
MFN2 agonists reverse mitochondrial defects in preclinical models of Charcot-Marie-Tooth disease type 2A.
    Science (New York, N.Y.), 2018, 04-20, Volume: 360, Issue:6386

    Topics: Amino Acid Substitution; Animals; Arginine; Axons; Charcot-Marie-Tooth Disease; Disease Models, Animal; Drug Design; Glutamine; GTP Phosphohydrolases; Humans; Methionine; Mice; Mice, Inbred C57BL; Mitochondria; Mitochondrial Diseases; Mitochondrial Proteins; Oligopeptides; Phosphorylation; Protein Kinases; Sciatic Nerve; Small Molecule Libraries; Threonine

2018
Deficient glucose and glutamine metabolism in
    Molecular vision, 2016, Volume: 22

    Topics: Aggrecans; Amino Acid Transport Systems, Acidic; Animals; Antiporters; Dark Adaptation; Electroretinography; Glucose; Glutamine; Hereditary Central Nervous System Demyelinating Diseases; Mice; Mice, Inbred C57BL; Mice, Knockout; Mitochondria; Mitochondrial Diseases; Mitochondrial Membrane Transport Proteins; Photic Stimulation; Psychomotor Disorders; Retina; Retinal Bipolar Cells; Synaptic Transmission; Vision Disorders

2016
Psychiatric symptoms correlate with metabolic indices in the hippocampus and cingulate in patients with mitochondrial disorders.
    Translational psychiatry, 2012, Nov-13, Volume: 2

    Topics: Adult; Aged; Anxiety; Aspartic Acid; Case-Control Studies; Caudate Nucleus; Creatine; Female; Glutamic Acid; Glutamine; Glycerylphosphorylcholine; Gyrus Cinguli; Hippocampus; Humans; Inositol; Magnetic Resonance Spectroscopy; Male; Middle Aged; Mitochondrial Diseases; Psychiatric Status Rating Scales

2012
Mitochondrial function dependent proliferation assay for the diagnosis of mitochondrial disorders in human fibroblasts.
    Nucleosides, nucleotides & nucleic acids, 2004, Volume: 23, Issue:8-9

    Topics: Biopsy; Cell Biology; Cell Proliferation; Cells, Cultured; Culture Media; Fibroblasts; Glutamine; Humans; Inosine; Mitochondria; Mitochondrial Diseases; Oxygen; Pentoses

2004