glutamine and Acidemia Propionic

glutamine has been researched along with Acidemia Propionic in 5 studies

Research

Studies (5)

Timeframe	Studies, this research(%)	All Research%
pre-1990	0 (0.00)	18.7374
1990's	0 (0.00)	18.2507
2000's	1 (20.00)	29.6817
2010's	3 (60.00)	24.3611
2020's	1 (20.00)	2.80

Authors

Authors	Studies
Arrieta, F; Belanger-Quintana, A; Del Valle, M; Fernandez-Felix, BM; Garcia, F; Martinez-Pardo, M; Ruiz-Sala, P; Stanescu, S	1
Bailey, C; Cantor, NL; Ernst, SL; Gappmaier, E; Longo, N; Pasquali, M; Price, LB	1
Ah Mew, N; Daikhin, Y; McCarter, R; Nissim, I; Tuchman, M; Yudkoff, M	1
Karall, D; Sass, JO; Scholl-Bürgi, S; Zschocke, J	1
Al-Hassnan, ZN; Boyadjiev, SA; Braverman, NE; Geraghty, MT; Hamosh, A; Praphanphoj, V; Thomas, GH	1

Reviews

1 review(s) available for glutamine and Acidemia Propionic

Article	Year
Amino acid metabolism in patients with propionic acidaemia. Journal of inherited metabolic disease, 2012, Volume: 35, Issue:1 Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Ammonia; Citric Acid Cycle; Diet; Glutamine; Glycine; Humans; Isoleucine; Lysine; Methylmalonyl-CoA Decarboxylase; Models, Biological; Propionic Acidemia; Urea; Valine	2012

Trials

2 trial(s) available for glutamine and Acidemia Propionic

Article	Year
Anaplerotic therapy in propionic acidemia. Molecular genetics and metabolism, 2017, Volume: 122, Issue:1-2 Topics: Amino Acids; Ammonia; Carbon-Carbon Ligases; Child; Child, Preschool; Citrates; Citric Acid; Citric Acid Cycle; Dietary Supplements; Female; Glutamine; Humans; Lactic Acid; Male; Ornithine; Propionic Acidemia; Treatment Outcome	2017
N-carbamylglutamate augments ureagenesis and reduces ammonia and glutamine in propionic acidemia. Pediatrics, 2010, Volume: 126, Issue:1 Topics: Administration, Oral; Adolescent; Ammonia; Blood Chemical Analysis; Child; Child, Preschool; Confidence Intervals; Dose-Response Relationship, Drug; Drug Administration Schedule; Female; Follow-Up Studies; Glutamates; Glutamine; Humans; Infant; Male; Probability; Propionic Acidemia; Prospective Studies; Risk Assessment; Treatment Outcome; Urea	2010

Article

Year

Anaplerotic therapy in propionic acidemia.

Molecular genetics and metabolism, 2017, Volume: 122, Issue:1-2

Topics: Amino Acids; Ammonia; Carbon-Carbon Ligases; Child; Child, Preschool; Citrates; Citric Acid; Citric Acid Cycle; Dietary Supplements; Female; Glutamine; Humans; Lactic Acid; Male; Ornithine; Propionic Acidemia; Treatment Outcome

2017

N-carbamylglutamate augments ureagenesis and reduces ammonia and glutamine in propionic acidemia.

Pediatrics, 2010, Volume: 126, Issue:1

Topics: Administration, Oral; Adolescent; Ammonia; Blood Chemical Analysis; Child; Child, Preschool; Confidence Intervals; Dose-Response Relationship, Drug; Drug Administration Schedule; Female; Follow-Up Studies; Glutamates; Glutamine; Humans; Infant; Male; Probability; Propionic Acidemia; Prospective Studies; Risk Assessment; Treatment Outcome; Urea

2010

Other Studies

2 other study(ies) available for glutamine and Acidemia Propionic

Article	Year
Interorgan amino acid interchange in propionic acidemia: the missing key to understanding its physiopathology. Amino acids, 2022, Volume: 54, Issue:5 Topics: Alanine; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Glutamine; Humans; Hyperammonemia; Ketosis; Propionic Acidemia; Urea	2022
The relationship of plasma glutamine to ammonium and of glycine to acid-base balance in propionic acidaemia. Journal of inherited metabolic disease, 2003, Volume: 26, Issue:1 Topics: Acid-Base Equilibrium; Amino Acid Metabolism, Inborn Errors; Bicarbonates; Biomarkers; Diet, Protein-Restricted; Disease Progression; Follow-Up Studies; Glutamine; Glycine; Humans; Propionates; Propionic Acidemia; Quaternary Ammonium Compounds	2003

Article

Year

Interorgan amino acid interchange in propionic acidemia: the missing key to understanding its physiopathology.

Amino acids, 2022, Volume: 54, Issue:5

Topics: Alanine; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Glutamine; Humans; Hyperammonemia; Ketosis; Propionic Acidemia; Urea

2022

The relationship of plasma glutamine to ammonium and of glycine to acid-base balance in propionic acidaemia.

Journal of inherited metabolic disease, 2003, Volume: 26, Issue:1

Topics: Acid-Base Equilibrium; Amino Acid Metabolism, Inborn Errors; Bicarbonates; Biomarkers; Diet, Protein-Restricted; Disease Progression; Follow-Up Studies; Glutamine; Glycine; Humans; Propionates; Propionic Acidemia; Quaternary Ammonium Compounds

2003