glutamic acid has been researched along with Neuronal Ceroid-Lipofuscinoses in 13 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 3 (23.08) | 18.2507 |
2000's | 5 (38.46) | 29.6817 |
2010's | 4 (30.77) | 24.3611 |
2020's | 1 (7.69) | 2.80 |
Authors | Studies |
---|---|
Baker, EH; Dang Do, AN; Farmer, CA; Porter, FD; Soldatos, AG; Thurm, AE | 1 |
Kielian, T; Xiong, J | 1 |
Bosch, M; Boska, MD; Burkovetskaya, M; Karpuk, N; Kielian, T; Suzumura, A; Takeuchi, H; Xiong, J | 1 |
Cooper, JD; Griffin, JL; Mitchison, HM; Mortishire-Smith, RJ; Pearce, DA; Pears, MR; Salek, RM | 1 |
Afzalov, R; Khiroug, L; Kolikova, J; Lehesjoki, AE; Surin, A | 1 |
Chattopadhyay, S; Curran, TM; McCall, K; Mooney, RA; Pearce, DA | 1 |
Autti, T; Bathen, TF; Gribbestad, IS; Häkkinen, AM; Haltia, MJ; Paetau, A; Polvikoski, T; Puranen, J; Santavuori, P; Sitter, B; Sonnewald, U; Tyynelä, J | 1 |
Cooper, JD; Griffin, JL; Mitchison, HM; Mortishire-Smith, RJ; Pearce, DA; Pears, MR | 1 |
Hachiya, Y; Hayashi, M; Kumada, S; Kurata, K; Tsuchiya, K; Uchiyama, A | 1 |
Brown, WT; Ju, W; Kaczmarski, AL; Kaczmarski, W; Liu, B; Mclendon, L; Sklower Brooks, SS; Wisniewski, KE; Xu, WM; Xu, WW; Zhong, N | 1 |
Blair, PS; Katz, ML; Savill, JD; Siakotos, AN | 1 |
Grodd, W; Klose, U; Nägele, T; Schwab, A; Seeger, U; Seitz, D | 1 |
Brooks, AI; Chattopadhyay, S; Cooper, JD; Curran, TM; Ito, M; Pearce, DA; Powers, JM | 1 |
13 other study(ies) available for glutamic acid and Neuronal Ceroid-Lipofuscinoses
Article | Year |
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Brain proton MR spectroscopy measurements in CLN3 disease.
Topics: Adolescent; Adult; Brain; Child; gamma-Aminobutyric Acid; Glutamic Acid; Glutamine; Humans; Magnetic Resonance Spectroscopy; Membrane Glycoproteins; Molecular Chaperones; Neuronal Ceroid-Lipofuscinoses; Prospective Studies; Protons; Young Adult | 2023 |
Microglia in juvenile neuronal ceroid lipofuscinosis are primed toward a pro-inflammatory phenotype.
Topics: Animals; Bone Marrow Cells; Caspase 1; Cells, Cultured; Chemokines; Cytokines; Electron Spin Resonance Spectroscopy; Enzyme-Linked Immunosorbent Assay; Glutamic Acid; Humans; Inflammation; Macrophages; Membrane Glycoproteins; Mice; Mice, Inbred C57BL; Mice, Knockout; Microglia; Microscopy, Confocal; Molecular Chaperones; Neuronal Ceroid-Lipofuscinoses; Phenotype; Primary Cell Culture | 2013 |
Evidence for aberrant astrocyte hemichannel activity in Juvenile Neuronal Ceroid Lipofuscinosis (JNCL).
Topics: Animals; Astrocytes; Biomarkers; Brain; Ceroid; Connexins; Female; Gap Junctions; Glutamic Acid; Homeostasis; Lysosomes; Male; Membrane Glycoproteins; Membrane Transport Proteins; Mice; Mice, Knockout; Molecular Chaperones; Mutation; Neuronal Ceroid-Lipofuscinoses | 2014 |
A metabolomic comparison of mouse models of the Neuronal Ceroid Lipofuscinoses.
Topics: Animals; Cerebellum; Cerebral Cortex; Disease Models, Animal; Glutamic Acid; Glutamine; Magnetic Resonance Spectroscopy; Mice; Neuronal Ceroid-Lipofuscinoses; Neurons; Pigments, Biological | 2011 |
Deficient mitochondrial Ca(2+) buffering in the Cln8(mnd) mouse model of neuronal ceroid lipofuscinosis.
Topics: Animals; Calcium; Cells, Cultured; Disease Models, Animal; Endoplasmic Reticulum; Fura-2; Glutamic Acid; Hippocampus; Homeostasis; Interneurons; Membrane Proteins; Mice; Microscopy, Fluorescence; Mitochondria; Neuronal Ceroid-Lipofuscinoses; Patch-Clamp Techniques; Sarcoplasmic Reticulum Calcium-Transporting ATPases | 2011 |
Altered amino acid levels in sera of a mouse model for juvenile neuronal ceroid lipofuscinoses.
Topics: Amino Acids; Animals; Brain Chemistry; Creatine Kinase; Disease Models, Animal; Glutamate Decarboxylase; Glutamic Acid; Mice; Mice, Knockout; Neuronal Ceroid-Lipofuscinoses; Time Factors; Transaminases | 2003 |
High-resolution magic angle spinning and 1H magnetic resonance spectroscopy reveal significantly altered neuronal metabolite profiles in CLN1 but not in CLN3.
Topics: Adolescent; Adult; Analysis of Variance; Aspartic Acid; Brain; Brain Chemistry; Child; Child, Preschool; Choline; Creatine; Female; gamma-Aminobutyric Acid; Glutamic Acid; Glutamine; Humans; Inositol; Magnetic Resonance Spectroscopy; Male; Membrane Glycoproteins; Membrane Proteins; Molecular Chaperones; Neuronal Ceroid-Lipofuscinoses; Neurons; Thiolester Hydrolases | 2004 |
High resolution 1H NMR-based metabolomics indicates a neurotransmitter cycling deficit in cerebral tissue from a mouse model of Batten disease.
Topics: Aging; Animals; Aspartic Acid; Brain; Cerebellum; Cerebral Cortex; Creatine; Disease Models, Animal; gamma-Aminobutyric Acid; Glutamic Acid; Glutamine; Humans; Inositol; Magnetic Resonance Spectroscopy; Membrane Glycoproteins; Mice; Mice, Knockout; Models, Biological; Molecular Chaperones; Neuronal Ceroid-Lipofuscinoses; Neurotransmitter Agents; Phenotype; Spectrophotometry; Time Factors | 2005 |
Mechanisms of neurodegeneration in neuronal ceroid-lipofuscinoses.
Topics: Adolescent; Adult; Apoptosis; Calcium-Binding Proteins; Child; Excitatory Amino Acid Transporter 1; Excitatory Amino Acid Transporter 2; Female; Glutamate Plasma Membrane Transport Proteins; Glutamic Acid; Humans; Male; Nerve Degeneration; Neuroglia; Neuronal Ceroid-Lipofuscinoses; Neurotoxins; Oxidative Stress | 2006 |
Molecular screening of Batten disease: identification of a missense mutation (E295K) in the CLN3 gene.
Topics: Alternative Splicing; Amino Acid Sequence; Amino Acid Substitution; Animals; Dogs; Gene Deletion; Genetic Testing; Glutamic Acid; Humans; Lysine; Membrane Glycoproteins; Mice; Molecular Chaperones; Molecular Sequence Data; Neuronal Ceroid-Lipofuscinoses; Point Mutation; Polymerase Chain Reaction; Polymorphism, Genetic; Proteins | 1998 |
Altered mitochondrial function in canine ceroid-lipofuscinosis.
Topics: Adenosine Diphosphate; Adenosine Triphosphate; Animals; Disease Models, Animal; Dogs; Glutamic Acid; Malates; Microscopy, Electron; Mitochondria, Liver; Neuronal Ceroid-Lipofuscinoses; Oxygen Consumption; Succinic Acid | 1998 |
MR imaging and localized proton MR spectroscopy in late infantile neuronal ceroid lipofuscinosis.
Topics: Aspartic Acid; Brain; Brain Diseases; Case-Control Studies; Cerebellum; Cerebral Ventricles; Child; Child, Preschool; Choline; Creatine; Diagnosis, Differential; Female; Glutamic Acid; Glutamine; Humans; Inositol; Lactates; Magnetic Resonance Imaging; Magnetic Resonance Spectroscopy; Male; Mitochondrial Encephalomyopathies; Neuronal Ceroid-Lipofuscinoses; Peroxisomal Disorders; Thalamus | 1998 |
An autoantibody inhibitory to glutamic acid decarboxylase in the neurodegenerative disorder Batten disease.
Topics: Adult; Animals; Autoantibodies; Blotting, Western; Cerebellum; Cerebral Cortex; Gene Expression Regulation; Glutamate Decarboxylase; Glutamic Acid; Humans; Male; Membrane Glycoproteins; Mice; Molecular Chaperones; Neuronal Ceroid-Lipofuscinoses; Proteins | 2002 |