glutamic acid and Neuronal Ceroid-Lipofuscinoses

glutamic acid has been researched along with Neuronal Ceroid-Lipofuscinoses in 13 studies

Research

Studies (13)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's3 (23.08)18.2507
2000's5 (38.46)29.6817
2010's4 (30.77)24.3611
2020's1 (7.69)2.80

Authors

AuthorsStudies
Baker, EH; Dang Do, AN; Farmer, CA; Porter, FD; Soldatos, AG; Thurm, AE1
Kielian, T; Xiong, J1
Bosch, M; Boska, MD; Burkovetskaya, M; Karpuk, N; Kielian, T; Suzumura, A; Takeuchi, H; Xiong, J1
Cooper, JD; Griffin, JL; Mitchison, HM; Mortishire-Smith, RJ; Pearce, DA; Pears, MR; Salek, RM1
Afzalov, R; Khiroug, L; Kolikova, J; Lehesjoki, AE; Surin, A1
Chattopadhyay, S; Curran, TM; McCall, K; Mooney, RA; Pearce, DA1
Autti, T; Bathen, TF; Gribbestad, IS; Häkkinen, AM; Haltia, MJ; Paetau, A; Polvikoski, T; Puranen, J; Santavuori, P; Sitter, B; Sonnewald, U; Tyynelä, J1
Cooper, JD; Griffin, JL; Mitchison, HM; Mortishire-Smith, RJ; Pearce, DA; Pears, MR1
Hachiya, Y; Hayashi, M; Kumada, S; Kurata, K; Tsuchiya, K; Uchiyama, A1
Brown, WT; Ju, W; Kaczmarski, AL; Kaczmarski, W; Liu, B; Mclendon, L; Sklower Brooks, SS; Wisniewski, KE; Xu, WM; Xu, WW; Zhong, N1
Blair, PS; Katz, ML; Savill, JD; Siakotos, AN1
Grodd, W; Klose, U; Nägele, T; Schwab, A; Seeger, U; Seitz, D1
Brooks, AI; Chattopadhyay, S; Cooper, JD; Curran, TM; Ito, M; Pearce, DA; Powers, JM1

Other Studies

13 other study(ies) available for glutamic acid and Neuronal Ceroid-Lipofuscinoses

ArticleYear
Brain proton MR spectroscopy measurements in CLN3 disease.
    Molecular genetics and metabolism, 2023, Volume: 139, Issue:1

    Topics: Adolescent; Adult; Brain; Child; gamma-Aminobutyric Acid; Glutamic Acid; Glutamine; Humans; Magnetic Resonance Spectroscopy; Membrane Glycoproteins; Molecular Chaperones; Neuronal Ceroid-Lipofuscinoses; Prospective Studies; Protons; Young Adult

2023
Microglia in juvenile neuronal ceroid lipofuscinosis are primed toward a pro-inflammatory phenotype.
    Journal of neurochemistry, 2013, Volume: 127, Issue:2

    Topics: Animals; Bone Marrow Cells; Caspase 1; Cells, Cultured; Chemokines; Cytokines; Electron Spin Resonance Spectroscopy; Enzyme-Linked Immunosorbent Assay; Glutamic Acid; Humans; Inflammation; Macrophages; Membrane Glycoproteins; Mice; Mice, Inbred C57BL; Mice, Knockout; Microglia; Microscopy, Confocal; Molecular Chaperones; Neuronal Ceroid-Lipofuscinoses; Phenotype; Primary Cell Culture

2013
Evidence for aberrant astrocyte hemichannel activity in Juvenile Neuronal Ceroid Lipofuscinosis (JNCL).
    PloS one, 2014, Volume: 9, Issue:4

    Topics: Animals; Astrocytes; Biomarkers; Brain; Ceroid; Connexins; Female; Gap Junctions; Glutamic Acid; Homeostasis; Lysosomes; Male; Membrane Glycoproteins; Membrane Transport Proteins; Mice; Mice, Knockout; Molecular Chaperones; Mutation; Neuronal Ceroid-Lipofuscinoses

2014
A metabolomic comparison of mouse models of the Neuronal Ceroid Lipofuscinoses.
    Journal of biomolecular NMR, 2011, Volume: 49, Issue:3-4

    Topics: Animals; Cerebellum; Cerebral Cortex; Disease Models, Animal; Glutamic Acid; Glutamine; Magnetic Resonance Spectroscopy; Mice; Neuronal Ceroid-Lipofuscinoses; Neurons; Pigments, Biological

2011
Deficient mitochondrial Ca(2+) buffering in the Cln8(mnd) mouse model of neuronal ceroid lipofuscinosis.
    Cell calcium, 2011, Volume: 50, Issue:6

    Topics: Animals; Calcium; Cells, Cultured; Disease Models, Animal; Endoplasmic Reticulum; Fura-2; Glutamic Acid; Hippocampus; Homeostasis; Interneurons; Membrane Proteins; Mice; Microscopy, Fluorescence; Mitochondria; Neuronal Ceroid-Lipofuscinoses; Patch-Clamp Techniques; Sarcoplasmic Reticulum Calcium-Transporting ATPases

2011
Altered amino acid levels in sera of a mouse model for juvenile neuronal ceroid lipofuscinoses.
    Clinica chimica acta; international journal of clinical chemistry, 2003, Volume: 332, Issue:1-2

    Topics: Amino Acids; Animals; Brain Chemistry; Creatine Kinase; Disease Models, Animal; Glutamate Decarboxylase; Glutamic Acid; Mice; Mice, Knockout; Neuronal Ceroid-Lipofuscinoses; Time Factors; Transaminases

2003
High-resolution magic angle spinning and 1H magnetic resonance spectroscopy reveal significantly altered neuronal metabolite profiles in CLN1 but not in CLN3.
    Journal of neuroscience research, 2004, Sep-01, Volume: 77, Issue:5

    Topics: Adolescent; Adult; Analysis of Variance; Aspartic Acid; Brain; Brain Chemistry; Child; Child, Preschool; Choline; Creatine; Female; gamma-Aminobutyric Acid; Glutamic Acid; Glutamine; Humans; Inositol; Magnetic Resonance Spectroscopy; Male; Membrane Glycoproteins; Membrane Proteins; Molecular Chaperones; Neuronal Ceroid-Lipofuscinoses; Neurons; Thiolester Hydrolases

2004
High resolution 1H NMR-based metabolomics indicates a neurotransmitter cycling deficit in cerebral tissue from a mouse model of Batten disease.
    The Journal of biological chemistry, 2005, Dec-30, Volume: 280, Issue:52

    Topics: Aging; Animals; Aspartic Acid; Brain; Cerebellum; Cerebral Cortex; Creatine; Disease Models, Animal; gamma-Aminobutyric Acid; Glutamic Acid; Glutamine; Humans; Inositol; Magnetic Resonance Spectroscopy; Membrane Glycoproteins; Mice; Mice, Knockout; Models, Biological; Molecular Chaperones; Neuronal Ceroid-Lipofuscinoses; Neurotransmitter Agents; Phenotype; Spectrophotometry; Time Factors

2005
Mechanisms of neurodegeneration in neuronal ceroid-lipofuscinoses.
    Acta neuropathologica, 2006, Volume: 111, Issue:2

    Topics: Adolescent; Adult; Apoptosis; Calcium-Binding Proteins; Child; Excitatory Amino Acid Transporter 1; Excitatory Amino Acid Transporter 2; Female; Glutamate Plasma Membrane Transport Proteins; Glutamic Acid; Humans; Male; Nerve Degeneration; Neuroglia; Neuronal Ceroid-Lipofuscinoses; Neurotoxins; Oxidative Stress

2006
Molecular screening of Batten disease: identification of a missense mutation (E295K) in the CLN3 gene.
    Human genetics, 1998, Volume: 102, Issue:1

    Topics: Alternative Splicing; Amino Acid Sequence; Amino Acid Substitution; Animals; Dogs; Gene Deletion; Genetic Testing; Glutamic Acid; Humans; Lysine; Membrane Glycoproteins; Mice; Molecular Chaperones; Molecular Sequence Data; Neuronal Ceroid-Lipofuscinoses; Point Mutation; Polymerase Chain Reaction; Polymorphism, Genetic; Proteins

1998
Altered mitochondrial function in canine ceroid-lipofuscinosis.
    Neurochemical research, 1998, Volume: 23, Issue:7

    Topics: Adenosine Diphosphate; Adenosine Triphosphate; Animals; Disease Models, Animal; Dogs; Glutamic Acid; Malates; Microscopy, Electron; Mitochondria, Liver; Neuronal Ceroid-Lipofuscinoses; Oxygen Consumption; Succinic Acid

1998
MR imaging and localized proton MR spectroscopy in late infantile neuronal ceroid lipofuscinosis.
    AJNR. American journal of neuroradiology, 1998, Volume: 19, Issue:7

    Topics: Aspartic Acid; Brain; Brain Diseases; Case-Control Studies; Cerebellum; Cerebral Ventricles; Child; Child, Preschool; Choline; Creatine; Diagnosis, Differential; Female; Glutamic Acid; Glutamine; Humans; Inositol; Lactates; Magnetic Resonance Imaging; Magnetic Resonance Spectroscopy; Male; Mitochondrial Encephalomyopathies; Neuronal Ceroid-Lipofuscinoses; Peroxisomal Disorders; Thalamus

1998
An autoantibody inhibitory to glutamic acid decarboxylase in the neurodegenerative disorder Batten disease.
    Human molecular genetics, 2002, Jun-01, Volume: 11, Issue:12

    Topics: Adult; Animals; Autoantibodies; Blotting, Western; Cerebellum; Cerebral Cortex; Gene Expression Regulation; Glutamate Decarboxylase; Glutamic Acid; Humans; Male; Membrane Glycoproteins; Mice; Molecular Chaperones; Neuronal Ceroid-Lipofuscinoses; Proteins

2002