glutamic acid and Leigh Disease

glutamic acid has been researched along with Leigh Disease in 4 studies

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's1 (25.00)29.6817
2010's1 (25.00)24.3611
2020's2 (50.00)2.80

Authors

AuthorsStudies
Bitto, A; Bornstein, R; Johnson, SC; Kaeberlein, M; Kayser, EB; Morgan, PG; Pan, A; Park, KY; Raftery, D; Sedensky, MM; Stokes, J; Sun, G1
Coetzer, J; Lindeque, JZ; Louw, R; Terburgh, K; van der Westhuizen, FH1
Kayser, EB; Morgan, PG; Sedensky, MM1
Bénit, P; Chol, M; Chretien, D; Lebon, S; Munnich, A; Rötig, A; Rustin, P1

Other Studies

4 other study(ies) available for glutamic acid and Leigh Disease

ArticleYear
Regional metabolic signatures in the Ndufs4(KO) mouse brain implicate defective glutamate/α-ketoglutarate metabolism in mitochondrial disease.
    Molecular genetics and metabolism, 2020, Volume: 130, Issue:2

    Topics: Animals; Brain; Disease Models, Animal; Electron Transport Complex I; Female; Glutamic Acid; Ketoglutaric Acids; Leigh Disease; Male; Metabolome; Mice; Mice, Inbred C57BL; Mice, Knockout; Mitochondrial Diseases; TOR Serine-Threonine Kinases

2020
Aberrant BCAA and glutamate metabolism linked to regional neurodegeneration in a mouse model of Leigh syndrome.
    Biochimica et biophysica acta. Molecular basis of disease, 2021, 05-01, Volume: 1867, Issue:5

    Topics: Amino Acids, Branched-Chain; Animals; Disease Models, Animal; Electron Transport Complex I; Glutamic Acid; Leigh Disease; Male; Metabolome; Mice; Mice, Knockout; Neurodegenerative Diseases; Oxidative Phosphorylation

2021
Region-Specific Defects of Respiratory Capacities in the Ndufs4(KO) Mouse Brain.
    PloS one, 2016, Volume: 11, Issue:1

    Topics: Animals; Brain Stem; Cell Respiration; Cerebellum; Disease Models, Animal; Electron Transport Complex I; Gene Expression; Glutamic Acid; Glycolysis; Humans; Ketoglutaric Acids; Leigh Disease; Malates; Mice; Mitochondria; Olfactory Bulb; Organ Specificity; Oxidative Phosphorylation; Presynaptic Terminals; Pyruvic Acid; Reactive Oxygen Species; Synaptosomes

2016
Assay of mitochondrial respiratory chain complex I in human lymphocytes and cultured skin fibroblasts.
    Biochemical and biophysical research communications, 2003, Jan-31, Volume: 301, Issue:1

    Topics: Cells, Cultured; Electron Transport Complex I; Fibroblasts; Glutamic Acid; Humans; Leigh Disease; Lymphocytes; Malates; Male; Mitochondria; NADH, NADPH Oxidoreductases; Oxygen; Polarography; Rotenone; Skin; Uncoupling Agents

2003