glutamic acid and Brain Diseases, Metabolic, Familial

glutamic acid has been researched along with Brain Diseases, Metabolic, Familial in 7 studies

Research

Studies (7)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's7 (100.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Aldred, S; Fitzgerald, M; Moore, KM; Waring, RH1
Brusque, AM; Frizzo, ME; Junqueira, D; Porciúncula, LO; Rotta, LN; Souza, DO; Wajner, M; Wannmacher, CM; Wyse, AT1
Levy, HL1
Brinco, F; Vasques, V; Viegas, CM; Wajner, M1
Brusilow, WS1
Cheng, KC; Connor, JR; Goodman, SI; Housman, C; Jacobs, RE; LaNoue, K; Lazovic, J; O'Callaghan, JP; Simpson, I; Woontner, M; Zinnanti, WJ1
Ahlemeyer, B; de Mello, CF; de Souza, FR; Fighera, MR; Hoffmann, GF; Kölker, S; Krieglstein, J; Mayatepek, E; Wajner, M1

Reviews

1 review(s) available for glutamic acid and Brain Diseases, Metabolic, Familial

ArticleYear
Is Huntington's a glutamine storage disease?
    The Neuroscientist : a review journal bringing neurobiology, neurology and psychiatry, 2006, Volume: 12, Issue:4

    Topics: Animals; Biological Evolution; Brain; Brain Diseases, Metabolic, Inborn; Glutamic Acid; Glutamine; Humans; Huntingtin Protein; Huntington Disease; Nerve Tissue Proteins; Nuclear Proteins; Peptides

2006

Other Studies

6 other study(ies) available for glutamic acid and Brain Diseases, Metabolic, Familial

ArticleYear
Plasma amino acid levels in children with autism and their families.
    Journal of autism and developmental disorders, 2003, Volume: 33, Issue:1

    Topics: Adolescent; Alanine; Amino Acids; Asparagine; Asperger Syndrome; Autistic Disorder; Brain Diseases, Metabolic, Inborn; Child; Child, Preschool; Family; Female; Glutamic Acid; Glutamine; Humans; Lysine; Male; Phenylalanine; Tyrosine

2003
In vitro effects of D-2-hydroxyglutaric acid on glutamate binding, uptake and release in cerebral cortex of rats.
    Journal of the neurological sciences, 2004, Feb-15, Volume: 217, Issue:2

    Topics: Animals; Binding Sites; Brain Diseases, Metabolic, Inborn; Cerebral Cortex; Disease Models, Animal; Glutamic Acid; Glutarates; L-Lactate Dehydrogenase; Male; Neurotoxins; Presynaptic Terminals; Rats; Rats, Wistar; Receptors, N-Methyl-D-Aspartate; Synaptic Transmission; Synaptosomes

2004
Metabolic disorders in the center of genetic medicine.
    The New England journal of medicine, 2005, Nov-03, Volume: 353, Issue:18

    Topics: Amino Acid Metabolism, Inborn Errors; Brain; Brain Diseases, Metabolic, Inborn; Glutamate-Ammonia Ligase; Glutamic Acid; Glutamine; Homocystinuria; Humans; Hyperhomocysteinemia; Infant, Newborn; Mutation; Phenylketonurias

2005
Creatine prevents behavioral alterations caused by methylmalonic acid administration into the hippocampus of rats in the open field task.
    Journal of the neurological sciences, 2006, May-15, Volume: 244, Issue:1-2

    Topics: Animals; Avoidance Learning; Brain Diseases, Metabolic, Inborn; Creatine; Disease Models, Animal; Energy Metabolism; Excitatory Amino Acid Antagonists; Exploratory Behavior; Glutamic Acid; Habituation, Psychophysiologic; Hippocampus; Male; Memory; Memory Disorders; Methylmalonic Acid; Neuropsychological Tests; Psychomotor Disorders; Rats; Rats, Wistar; Receptors, N-Methyl-D-Aspartate; Succinic Acid; Synaptic Transmission

2006
Mechanism of age-dependent susceptibility and novel treatment strategy in glutaric acidemia type I.
    The Journal of clinical investigation, 2007, Volume: 117, Issue:11

    Topics: Aging; Amino Acid Metabolism, Inborn Errors; Animals; Brain Diseases, Metabolic, Inborn; Child; Diet; Disease Models, Animal; gamma-Aminobutyric Acid; Genetic Predisposition to Disease; Glucose; Glutamic Acid; Glutarates; Glutaryl-CoA Dehydrogenase; Homoarginine; Humans; Lysine; Mice; Mice, Knockout; Mitochondria; Neurons; Nuclear Magnetic Resonance, Biomolecular; Tryptophan

2007
Intrastriatal administration of 3-hydroxyglutaric acid induces convulsions and striatal lesions in rats.
    Brain research, 2001, Oct-19, Volume: 916, Issue:1-2

    Topics: Acyl Coenzyme A; Animals; Brain Diseases, Metabolic, Inborn; Excitatory Amino Acid Antagonists; GABA Agonists; GABA-A Receptor Agonists; Glutamic Acid; Glutarates; Male; Neostriatum; Neurotoxins; Rats; Rats, Wistar; Receptors, AMPA; Receptors, GABA-A; Receptors, N-Methyl-D-Aspartate; Seizures

2001