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glutaconyl-coenzyme a and Amino Acid Metabolism Disorders, Inborn

glutaconyl-coenzyme a has been researched along with Amino Acid Metabolism Disorders, Inborn in 2 studies

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's2 (100.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Lehnert, W1
Sass, JO1
Mack, M1
Schniegler-Mattox, U1
Peters, V1
Hoffmann, GF1
Liesert, M1
Buckel, W1
Zschocke, J1

Other Studies

2 other studies available for glutaconyl-coenzyme a and Amino Acid Metabolism Disorders, Inborn

ArticleYear
Glutaconyl-CoA is the main toxic agent in glutaryl-CoA dehydrogenase deficiency (glutaric aciduria type I).
    Medical hypotheses, 2005, Volume: 65, Issue:2

    Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Animals; Brain; Cysteine; Glutaryl-CoA Dehydr

2005
Biochemical characterization of human 3-methylglutaconyl-CoA hydratase and its role in leucine metabolism.
    The FEBS journal, 2006, Volume: 273, Issue:9

    Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Cloning, Molecular; Escheric

2006