Page last updated: 2024-08-25

glutaconic acid and Brain Diseases, Metabolic, Familial

glutaconic acid has been researched along with Brain Diseases, Metabolic, Familial in 2 studies

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's2 (100.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Christensen, E; Kristensen, AS; Lund, AM; Lund, TM; Schousboe, A1
Bührer, C; Gerstner, B; Gratopp, A; Marcinkowski, M; Obladen, M; Sifringer, M1

Other Studies

2 other study(ies) available for glutaconic acid and Brain Diseases, Metabolic, Familial

ArticleYear
On the neurotoxicity of glutaric, 3-hydroxyglutaric, and trans-glutaconic acids in glutaric acidemia type 1.
    Journal of neuroscience research, 2004, Jul-01, Volume: 77, Issue:1

    Topics: Animals; Brain Diseases, Metabolic, Inborn; Cell Death; Cells, Cultured; Cerebral Cortex; Corpus Striatum; Fetus; Glutarates; Glutaryl-CoA Dehydrogenase; Membrane Potentials; Mice; Nerve Degeneration; Neurons; Neurotoxins; Oocytes; Oxidoreductases Acting on CH-CH Group Donors; Rats; Receptors, N-Methyl-D-Aspartate; Xenopus

2004
Glutaric acid and its metabolites cause apoptosis in immature oligodendrocytes: a novel mechanism of white matter degeneration in glutaryl-CoA dehydrogenase deficiency.
    Pediatric research, 2005, Volume: 57, Issue:6

    Topics: Amino Acid Chloromethyl Ketones; Animals; Apoptosis; Base Sequence; Brain Diseases, Metabolic, Inborn; Caspase Inhibitors; Cell Differentiation; Cell Line; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Nerve Degeneration; Oligodendroglia; Oxidoreductases Acting on CH-CH Group Donors; Rats; Receptors, Glutamate; RNA, Messenger

2005