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glucagon and Glycogen Storage Disease Type I

glucagon has been researched along with Glycogen Storage Disease Type I in 40 studies

Research

Studies (40)

TimeframeStudies, this research(%)All Research%
pre-199036 (90.00)18.7374
1990's2 (5.00)18.2507
2000's2 (5.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
BULGARELLI, R1
GRASSI, A; TORCIGLIANI, A1
LOWE, CU; SARCIONE, EJ; SOKAL, JE2
KOMROWER, G1
Hackl, SI; Hasty, AH; Hutton, JC; McGuinness, OP; O'Brien, RM; Oeser, JK; Paradee, W; Powell, DR; Sarkar, S; Wang, Y; Yang, C1
Nuki, G; Parker, J1
Bashan, N; Coleman, RA; Moses, S; Mushlin, P; Shipp, E; Slonim, AE1
Fujita, T; Itakura, M; Koide, Y; Kugai, N; Yamamura, H; Yamashita, K; Yamashita, N1
Sanders, K1
Dunger, DB; Holder, AT; Leonard, JV; Okae, J; Preece, MA1
Brandt, IK; Powell, RC; Wentworth, SM1
Burchell, A; Hawkins, RA; Kamath, KR; Scott, HM1
Chioléro, R; Gillet, M; Koestinger, A; Mosimann, F; Tappy, L1
Applegarth, DA; Davidson, AG; Kirby, L; Rigg, JM; Tze, WJ; Wong, LT1
Burr, IM; Greene, HL; Lacy, WW; Slonim, AE; Terry, A2
Chalmers, RA; Ryman, BE; Watts, RW1
Ellefson, RD; Go, VL; Nelson, RA; Service, FJ; Veneziale, CM1
Arashima, S; Matsuda, I; Mitsuyama, T; Nagai, B; Ohkubo, I; Oka, Y1
Kogut, MD; Roe, TF1
Burr, IM; Claus, TH; Greene, HL; Hefferan, P; Moran, JR; Slonim, AE; Terry, AB; Wilson, FA1
Inui, K; Ishida, M; Kodama, H; Okada, S; Seino, Y; Yabuuchi, H; Yutaka, T1
Burr, IM; Greene, HL; O'Neill, JA; Slonim, AE1
Bartolozzi, G; Bernini, G; Marianelli, L; Nassi, P1
Aynsley-Green, A; Bartlett, K; Collins, JE; Leonard, JV1
Allam, CK; Bitar, JG; Wakid, NW1
Cohen, JL; Faller, J; Fox, IH; Vinik, A1
Loridan, L; Senior, B2
Dykes, JR; Spencer-Peet, J1
Bierich, JR; Rager, K; Schönberg, D1
Crockford, PM; Porte, D; Williams, RH; Wood, FC1
Fernandes, J; Huijing, F; van de Kamer, JH1
Spellberg, MA1
François, R; Moreau, P; Picaud, JJ; Pinçon, JA; Poncet, J; Ruitton-Ugliengo, A1
Matschke, I; Neubaur, J; Willms, B; Wolf, H1
Masarone, M; Pessina, S1
Rossi, E; Zuppinger, K1

Other Studies

40 other study(ies) available for glucagon and Glycogen Storage Disease Type I

ArticleYear
[More research on the effects of glucagon on carbohydrate metabolism in Gierke's disease].
    Minerva pediatrica, 1956, Aug-11, Volume: 8, Issue:31-32

    Topics: Carbohydrate Metabolism; Carbohydrates; Glucagon; Glycogen Storage Disease; Glycogen Storage Disease Type I; Humans

1956
[Galactose, glucagon, BZ 55 and thyroid in hepatic glycogenosis (Gierke's disease)].
    Minerva pediatrica, 1960, Aug-25, Volume: 12

    Topics: Carbutamide; Galactose; Glucagon; Glycogen Storage Disease; Glycogen Storage Disease Type I; Hormones; Humans; Thyroid Gland

1960
Liver glycogen disease (von Gierke's disease).
    Archives of internal medicine, 1962, Volume: 109

    Topics: Glucagon; Glycogen Storage Disease; Glycogen Storage Disease Type I; Humans; Liver Glycogen

1962
GLYCOGENOSIS.
    Developmental medicine and child neurology, 1964, Volume: 6

    Topics: Acidosis; Drug Therapy; Glucagon; Glycogen Storage Disease; Glycogen Storage Disease Type I; Humans; Hypoglycemia; Infant; Thyroxine

1964
Deletion of the gene encoding the ubiquitously expressed glucose-6-phosphatase catalytic subunit-related protein (UGRP)/glucose-6-phosphatase catalytic subunit-beta results in lowered plasma cholesterol and elevated glucagon.
    The Journal of biological chemistry, 2006, Dec-29, Volume: 281, Issue:52

    Topics: Animals; Catalytic Domain; Cholesterol; Down-Regulation; Female; Gene Deletion; Gene Expression Regulation; Glucagon; Glucose; Glucose-6-Phosphatase; Glycogen Storage Disease Type I; Homeostasis; Isoenzymes; Male; Mice; Mice, Inbred C57BL; Mice, Knockout; Protein Subunits; Proteins; Secretoglobins; Up-Regulation

2006
Clinical and enzymological studies in a child with type I glycogen storage disease associated with partial deficiency of hepatic glucose-6-phosphatase.
    Advances in experimental medicine and biology, 1980, Volume: 122A

    Topics: Blood Glucose; Erythrocytes; Female; Follow-Up Studies; Galactose; Glucagon; Glucose-6-Phosphatase; Glucosidases; Glycogen Debranching Enzyme System; Glycogen Storage Disease Type I; Humans; Hypoxanthine Phosphoribosyltransferase; Infant; Kinetics; Liver; Liver Glycogen; Phosphoribosyl Pyrophosphate

1980
Amino acid disturbances in type III glycogenosis: differences from type I glycogenosis.
    Metabolism: clinical and experimental, 1983, Volume: 32, Issue:1

    Topics: Adolescent; Adult; Amino Acids; Blood Glucose; Child; Child, Preschool; Diagnosis, Differential; Female; Glucagon; Glycogen Storage Disease; Glycogen Storage Disease Type I; Glycogen Storage Disease Type III; Humans; Insulin; Lactates; Lactic Acid; Male; Middle Aged

1983
A case of glycogen storage disease type I associated with an incomplete type of Fanconi syndrome; the protective role of lysosomal alpha 1,4-glucosidase and insulin deficiency against hypoglycemia.
    Hormone and metabolic research = Hormon- und Stoffwechselforschung = Hormones et metabolisme, 1984, Volume: 16 Suppl 1

    Topics: alpha-Glucosidases; Biopsy; Epinephrine; Fanconi Syndrome; Fructose; Glucagon; Glucosidases; Glycogen Storage Disease Type I; Humans; Hydrocortisone; Hypoglycemia; Insulin; Liver; Lysosomes; Male; Maltose; Middle Aged

1984
A teenager with a hepatic filling defect.
    Hospital practice (Office ed.), 1984, Volume: 19, Issue:7

    Topics: Adolescent; Diagnosis, Differential; Female; Glucagon; Glycogen Storage Disease Type I; Glycogen Storage Disease Type III; Humans; Liver; Tomography, X-Ray Computed

1984
Growth and endocrine changes in the hepatic glycogenoses.
    European journal of pediatrics, 1982, Volume: 138, Issue:3

    Topics: Adolescent; Blood Glucose; Body Height; Child; Female; Glucagon; Glycogen Storage Disease; Glycogen Storage Disease Type I; Glycogen Storage Disease Type III; Growth; Growth Hormone; Humans; Hydrocortisone; Infant; Insulin; Male; Somatomedins

1982
Endogenous glucose production in Type I glycogen storage disease.
    Metabolism: clinical and experimental, 1981, Volume: 30, Issue:5

    Topics: Adult; Blood Glucose; Ethanol; Fasting; Female; Fructose; Glucagon; Glycogen Storage Disease Type I; Humans; Hydrocortisone; Kinetics; Lactates; Lactic Acid; Male

1981
Multiple transport protein defects in a patient with glycogen storage disease type 1: GSD 1b/1c beta.
    Journal of inherited metabolic disease, 1995, Volume: 18, Issue:5

    Topics: Antiporters; Blood Glucose; Galactose; Glucagon; Glycogen Storage Disease Type I; Humans; Infant; Kinetics; Male; Microsomes, Liver; Monosaccharide Transport Proteins; Phosphotransferases

1995
Effect of liver transplantation on hepatic glucose metabolism in a patient with type I glycogen storage disease.
    Transplantation, 2000, May-27, Volume: 69, Issue:10

    Topics: Adolescent; Blood Glucose; Carbon Isotopes; Deuterium; Female; Glucagon; Gluconeogenesis; Glucose; Glycerol; Glycogen; Glycogen Storage Disease Type I; Humans; Insulin; Kinetics; Liver Transplantation; Reference Values

2000
Glycogen storage disease type I: effect of continuous nocturnal nasogastric feeding.
    Monographs in human genetics, 1978, Volume: 9

    Topics: Child; Enteral Nutrition; Food, Formulated; Galactose; Glucagon; Glucose; Glucose Tolerance Test; Glycogen Storage Disease Type I; Humans; Infant; Male; Time Factors

1978
Amino acid and hormonal response to long-term nocturnal nasogastric feeding therapy of glycogen storage disease type I (GSD-I).
    Monographs in human genetics, 1978, Volume: 9

    Topics: Adolescent; Amino Acids; Blood Glucose; Child; Child, Preschool; Enteral Nutrition; Female; Glucagon; Glucose; Glucose Tolerance Test; Glycogen Storage Disease Type I; Growth Hormone; Humans; Insulin; Male; Time Factors

1978
Studies on a patient with in vivo evidence of type I glycogenosis and normal enzyme activities in vitro.
    Acta paediatrica Scandinavica, 1978, Volume: 67, Issue:2

    Topics: Fructose-Bisphosphatase; Galactose; Glucagon; Glucose Tolerance Test; Glucose-6-Phosphatase; Glucosyltransferases; Glycogen Debranching Enzyme System; Glycogen Storage Disease Type I; Humans; Infant; Ketoglutaric Acids; Liver; Liver Glycogen; Male; Phosphorylases

1978
Combined deficiency of glucose-6-phosphatase and fructose-1, 6-diphosphatase. Studies of glucagon secretion and fuel utilization.
    The American journal of medicine, 1978, Volume: 64, Issue:4

    Topics: Adult; Basal Metabolism; Dietary Carbohydrates; Energy Metabolism; Female; Fructose-1,6-Diphosphatase Deficiency; Glucagon; Gluconeogenesis; Glycogen Storage Disease Type I; Humans; Ketone Bodies; Liver

1978
Glucose-6-phosphatase activity in liver and blood platelets of two patients with glycogen storage disease type I.
    Clinica chimica acta; international journal of clinical chemistry, 1978, Aug-01, Volume: 87, Issue:3

    Topics: Alanine; Blood Glucose; Blood Platelets; Child, Preschool; Female; Galactose; Glucagon; Glucose-6-Phosphatase; Glycerophosphates; Glycogen Storage Disease Type I; Humans; Liver; Liver Glycogen

1978
The pathogenesis of hyperuricemia in glycogen storage disease, type I.
    Pediatric research, 1977, Volume: 11, Issue:5

    Topics: Adolescent; Adult; Child; Child, Preschool; Female; Fructose; Glucagon; Glycogen Storage Disease Type I; Humans; Male; Phosphates; Uric Acid

1977
ATP depletion, a possible role in the pathogenesis of hyperuricemia in glycogen storage disease type I.
    The Journal of clinical investigation, 1978, Volume: 62, Issue:2

    Topics: Adenosine Triphosphate; Adolescent; Adult; Animals; Child; Child, Preschool; Glucagon; Glycogen Storage Disease Type I; Humans; Infant; Liver; Rats; Uric Acid

1978
Nocturnal intragastric therapy in type I glycogen storage disease: effect on hormonal and amino acid metabolism.
    Metabolism: clinical and experimental, 1979, Volume: 28, Issue:7

    Topics: Adolescent; Amino Acids; Blood Chemical Analysis; Blood Glucose; Child; Child, Preschool; Dietary Proteins; Eating; Female; Glucagon; Glucose Tolerance Test; Glycogen Storage Disease Type I; Humans; Infant; Insulin; Male; Time Factors

1979
Insulin and glucagon secretion in hepatic glycogenoses.
    Acta paediatrica Scandinavica, 1979, Volume: 68, Issue:5

    Topics: Blood Glucose; C-Peptide; Child; Child, Preschool; Female; Glucagon; Glucose Tolerance Test; Glycogen Storage Disease; Glycogen Storage Disease Type I; Glycogen Storage Disease Type III; Humans; Infant; Insulin; Insulin Secretion; Male

1979
Continuous nocturnal intragastric feeding for management of type 1 glycogen-storage disease.
    The New England journal of medicine, 1976, Feb-19, Volume: 294, Issue:8

    Topics: Adolescent; Aspartate Aminotransferases; Blood Glucose; Child; Cholesterol; Clofibrate; Eating; Enteral Nutrition; Female; Glucagon; Glucose; Glycogen Storage Disease Type I; Growth Hormone; Humans; Hypoglycemia; Insulin; Lactates; Time Factors; Triglycerides; Uric Acid

1976
[Type I glycogenosis. Description of 2 cases with hyperuricemia].
    Minerva pediatrica, 1975, Jun-23, Volume: 27, Issue:22

    Topics: Biopsy; Child; Galactose; Glucagon; Glucose Tolerance Test; Glycogen Storage Disease Type I; Gout; Humans; Lactates; Lipids; Liver; Liver Glycogen; Male; Pyruvates; Uric Acid

1975
Glucose production rates in type 1 glycogen storage disease.
    Journal of inherited metabolic disease, 1990, Volume: 13, Issue:2

    Topics: Adolescent; Adult; Alanine; Blood Glucose; Female; Glucagon; Glucose; Glycogen Storage Disease Type I; Humans; Infusions, Intravenous; Injections, Intravenous; Lactates; Lactic Acid; Male

1990
Glycogen storage disease type I: laboratory data and diagnosis.
    Clinical chemistry, 1987, Volume: 33, Issue:11

    Topics: Adult; Alanine Transaminase; Aspartate Aminotransferases; Child, Preschool; Cholesterol; Female; Glucagon; Glucose-6-Phosphatase; Glycogen Storage Disease Type I; Humans; Infant; Infant, Newborn; Male; Triglycerides; Uric Acid

1987
Hyperuricemia in glycogen storage disease type I. Contributions by hypoglycemia and hyperglucagonemia to increased urate production.
    The Journal of clinical investigation, 1985, Volume: 75, Issue:1

    Topics: Adenosine Triphosphate; Adolescent; Adult; Female; Glucagon; Glucose; Glycogen Storage Disease Type I; Humans; Hypoglycemia; Infusions, Parenteral; Somatostatin; Uric Acid

1985
Functional differentiation of glycogenoses of the liver with respect to the use of glycerol.
    The New England journal of medicine, 1968, Oct-31, Volume: 279, Issue:18

    Topics: Biopsy; Blood Glucose; Diagnosis, Differential; Epinephrine; Fatty Acids, Nonesterified; Glucagon; Glucose Tolerance Test; Glucose-6-Phosphatase; Glucosidases; Glucosyltransferases; Glycerol; Glycogen Storage Disease; Glycogen Storage Disease Type I; Humans; Injections, Intravenous; Insulin; Lactates

1968
Studies of liver glycogenoses, with particular reference to the metabolism of intravenously administered glycerol.
    The New England journal of medicine, 1968, Oct-31, Volume: 279, Issue:18

    Topics: Adolescent; Adult; Blood Glucose; Child; Child, Preschool; Epinephrine; Female; Glucagon; Glucose-6-Phosphatase; Glucosidases; Glucosyltransferases; Glycerol; Glycogen; Glycogen Storage Disease; Glycogen Storage Disease Type I; Humans; Injections, Intravenous; Lactates; Liver; Liver Glycogen; Male; Muscles

1968
Hepatic glycogen synthetase deficiency. Further studies on a family.
    Archives of disease in childhood, 1972, Volume: 47, Issue:254

    Topics: Adolescent; Blood Glucose; Child; Child, Preschool; Diagnosis, Differential; Fasting; Female; Galactose; Glucagon; Glucose; Glucose Tolerance Test; Glucosyltransferases; Glycogen; Glycogen Storage Disease Type I; Hexosaminidases; Humans; Hydrocortisone; Hypoglycemia; Infant; Insulin; Liver; Male; Metabolism, Inborn Errors

1972
[Diagnosis of glycogenosis].
    Padiatrie und Padologie, 1973, Volume: 8, Issue:1

    Topics: Diagnosis, Differential; Galactose; Glucagon; Glucose; Glucose Tolerance Test; Glucosidases; Glycogen Storage Disease; Glycogen Storage Disease Type I; Humans; Infant; Liver Diseases; Male

1973
Endocrinological findings in patients with glycogenosis.
    Acta endocrinologica. Supplementum, 1973, Volume: 173

    Topics: Blood Glucose; Fatty Acids, Nonesterified; Galactose; Glucagon; Glucosidases; Glycogen Storage Disease; Glycogen Storage Disease Type I; Growth Hormone; Humans; Hydrocortisone; Insulin

1973
Effect of glucagon on serum insulin, plasma glucose and free fatty acids in man.
    Metabolism: clinical and experimental, 1966, Volume: 15, Issue:2

    Topics: Blood; Blood Glucose; Fatty Acids; Glucagon; Glycogen Storage Disease Type I; Humans; Insulin

1966
A screening method for liver glycogen diseases.
    Archives of disease in childhood, 1969, Volume: 44, Issue:235

    Topics: Adolescent; Biological Assay; Child; Child, Preschool; Clinical Enzyme Tests; Female; Fructose; Galactose; Glucagon; Glucose Tolerance Test; Glucosyltransferases; Glycogen Storage Disease; Glycogen Storage Disease Type I; Humans; Infant; Liver Diseases; Liver Function Tests; Male; Mass Screening

1969
Treatment of glycogen storage disease (Von Gierke's disease).
    The American journal of gastroenterology, 1969, Volume: 52, Issue:1

    Topics: Adolescent; Adult; Child, Preschool; Female; Genes, Recessive; Glucagon; Glycogen Storage Disease Type I; Humans; Hypoglycemia; Male; Prognosis; Testosterone

1969
[Method of action of zinc glucagon in treatment of glycogenosis].
    Pediatrie, 1968, Volume: 23, Issue:6

    Topics: Consanguinity; Female; Glucagon; Glycogen Storage Disease; Glycogen Storage Disease Type I; Humans; Infant; Male; Zinc

1968
[Metabolism studies in children and young adults with glycogenoses].
    Monatsschrift fur Kinderheilkunde, 1969, Volume: 117, Issue:4

    Topics: Adolescent; Adult; Child; Fatty Acids; Glucagon; Glucosidases; Glucosyltransferases; Glycogen Storage Disease; Glycogen Storage Disease Type I; Humans; Ketone Bodies; Liver Glycogen; Male; Uric Acid

1969
[Case of type I glycogenosis. Considerations on its treatment with glucagon].
    Minerva pediatrica, 1970, Sep-15, Volume: 22, Issue:37

    Topics: Child; Female; Glucagon; Glycogen Storage Disease; Glycogen Storage Disease Type I; Humans; Liver

1970
Metabolic studies in liver glycogen disease with special reference to lactate metabolism.
    Helvetica medica acta, 1970, Volume: 35, Issue:5

    Topics: Acidosis; Adolescent; Adult; Blood Glucose; Child; Child, Preschool; Ethanol; Fatty Acids; Female; Glucagon; Gluconeogenesis; Glucose; Glucosidases; Glycogen Storage Disease; Glycogen Storage Disease Type I; Growth Hormone; Humans; Hydrocortisone; Lactates; Male; Pyruvates

1970
Hepatic glycogenolysis induced by glucagon in a patient with type I liver glycogen disease.
    Biochemical medicine, 1970, Volume: 3, Issue:4

    Topics: Blood Glucose; Carbon Isotopes; Child, Preschool; Fasting; Female; Glucagon; Glucose; Glycogen Storage Disease; Glycogen Storage Disease Type I; Humans; Kinetics; Lactates; Liver; Liver Glycogen; Metabolism

1970