Page last updated: 2024-09-04

glucagon and Congenital Hyperinsulinism

glucagon has been researched along with Congenital Hyperinsulinism in 16 studies

Research

Studies (16)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's3 (18.75)29.6817
2010's11 (68.75)24.3611
2020's2 (12.50)2.80

Authors

AuthorsStudies
Choi, IY; Heo, YH; Kim, HH; Kim, JK; Lee, JS; Lee, SH; Shin, SH1
Adzick, NS; Bhatti, TR; Boodhansingh, KE; Chen, P; De León, DD; Doliba, NM; Juliana, CA; Li, C; Li, M; Lu, M; Stanley, CA; Yuan, Y1
Dionisi-Vici, C; Maiorana, A1
Banerjee, I; Cosgrove, KE; Dunne, MJ; Nicholson, J; Salomon-Estebanez, M; Shah, P1
Moran, MM; Neylon, OM; Nightingale, M; O'Connell, MA; Pellicano, A1
Gannon, H; Hussain, K; Ponmani, C; Senniappan, S1
Edwards, TM; Spatz, DL1
Gilbert, C; Güemes, M; Hinchey, L; Hussain, K; Morgan, K; Shah, P; Silvera, S1
Bhowmick, SK; Narayanaswamy, V; Rettig, KR1
Ellard, S; Flanagan, SE; Gilbert, C; Hussain, K; Kapoor, RR; Moyo, Y; Padidela, R1
Empting, S; Holl, R; Ludwig, A; Marquard, J; Meissner, T; Mohnike, K; Ziegenhorn, K1
Brusgaard, K; Christesen, HT; Hussain, K1
Calabria, AC; De León, DD; Gallagher, PR; Li, C; Stanley, CA1
Krans, HM1
Aynsley-Green, A; Hussain, K; Stanley, CA1
Blankenstein, O; Grimberg, A; Hardy, OT; Mohnike, K; Pfuetzner, A; Pötzsch, S; Schober, E; Steiner, S; van Waarde, WM1

Reviews

4 review(s) available for glucagon and Congenital Hyperinsulinism

ArticleYear
Hyperinsulinemic hypoglycemia: clinical, molecular and therapeutical novelties.
    Journal of inherited metabolic disease, 2017, Volume: 40, Issue:4

    Topics: Adenosine Triphosphate; Animals; Child; Child, Preschool; Congenital Hyperinsulinism; Diet, Ketogenic; Galactose; Glucagon; Humans; Hypoglycemia; Infant; Insulin; Insulin Secretion; Insulin-Secreting Cells; Mice; Nervous System Diseases; Peptide Fragments; Potassium Channels; Receptor, Insulin; Sirolimus; Somatostatin; Treatment Outcome

2017
Therapies and outcomes of congenital hyperinsulinism-induced hypoglycaemia.
    Diabetic medicine : a journal of the British Diabetic Association, 2019, Volume: 36, Issue:1

    Topics: Antihypertensive Agents; Congenital Hyperinsulinism; Diazoxide; Gastrointestinal Agents; Glucagon; Humans; Hypoglycemia; Pancreatectomy; Potassium Channels, Inwardly Rectifying; Precision Medicine; Sulfonylurea Receptors; Treatment Outcome

2019
Congenital hyperinsulinism: exclusive human milk and breastfeeding.
    Advances in neonatal care : official journal of the National Association of Neonatal Nurses, 2014, Volume: 14, Issue:4

    Topics: Breast Feeding; Congenital Hyperinsulinism; Diazoxide; Female; Fluid Therapy; Food, Fortified; Gastrointestinal Agents; Glucagon; Glucose; Humans; Hypoglycemia; Infant, Newborn; Milk, Human; Octreotide; Pancreatectomy; Sweetening Agents

2014
Medications used in the treatment of hypoglycemia due to congenital hyperinsulinism of infancy (HI).
    Pediatric endocrinology reviews : PER, 2004, Volume: 2 Suppl 1

    Topics: Congenital Hyperinsulinism; Diazoxide; Gastrointestinal Agents; Glucagon; Humans; Hypoglycemia; Infant; Nifedipine; Octreotide; Vasodilator Agents

2004

Trials

2 trial(s) available for glucagon and Congenital Hyperinsulinism

ArticleYear
GLP-1 receptor antagonist exendin-(9-39) elevates fasting blood glucose levels in congenital hyperinsulinism owing to inactivating mutations in the ATP-sensitive K+ channel.
    Diabetes, 2012, Volume: 61, Issue:10

    Topics: Adolescent; Adult; Blood Glucose; Congenital Hyperinsulinism; Cross-Over Studies; Female; Glucagon; Glucagon-Like Peptide 1; Glucagon-Like Peptide-1 Receptor; Humans; Infant, Newborn; Insulin; Insulin Secretion; Islets of Langerhans; KATP Channels; Male; Mutation; Peptide Fragments; Pilot Projects; Receptors, Glucagon

2012
Long-term non-surgical therapy of severe persistent congenital hyperinsulinism with glucagon.
    Hormone research, 2008, Volume: 70, Issue:1

    Topics: Blood Glucose; Brain Diseases, Metabolic; Congenital Hyperinsulinism; Female; Gastrointestinal Agents; Glucagon; Glycogen; Humans; Hypoglycemia; Infant, Newborn; Male; Octreotide; Pancreatectomy; Retrospective Studies

2008

Other Studies

10 other study(ies) available for glucagon and Congenital Hyperinsulinism

ArticleYear
A novel glucagon analog with an extended half-life, HM15136, normalizes glucose levels in rodent models of congenital hyperinsulinism.
    Scientific reports, 2022, 10-06, Volume: 12, Issue:1

    Topics: Animals; Blood Glucose; Congenital Hyperinsulinism; Glucagon; Half-Life; Humans; Hyperinsulinism; Immunoglobulin Fc Fragments; Insulin; Mice; Polyethylene Glycols; Rats; Receptors, Glucagon; Rodentia

2022
Phenotypic Characterization of Congenital Hyperinsulinism Due to Novel Activating Glucokinase Mutations.
    Diabetes, 2023, Dec-01, Volume: 72, Issue:12

    Topics: Child; Congenital Hyperinsulinism; Glucagon; Glucokinase; Glucose; Humans; Hyperinsulinism; Mutation; Phenotype

2023
Successful subcutaneous glucagon use for persistent hypoglycaemia in congenital hyperinsulinism.
    Journal of pediatric endocrinology & metabolism : JPEM, 2013, Volume: 26, Issue:11-12

    Topics: Congenital Hyperinsulinism; Glucagon; Humans; Hypoglycemia; Infant, Newborn; Male; Pancreas; Pancreatectomy

2013
Paradoxical hypoglycaemia associated with diazoxide therapy for hyperinsulinaemic hypoglycaemia.
    Hormone research in paediatrics, 2013, Volume: 80, Issue:2

    Topics: Congenital Hyperinsulinism; Diazoxide; Female; Glucagon; Glucose; Humans; Hypoglycemia; Infant; Octreotide; Sulfonylurea Receptors

2013
Assessment of Nifedipine Therapy in Hyperinsulinemic Hypoglycemia due to Mutations in the ABCC8 Gene.
    The Journal of clinical endocrinology and metabolism, 2017, Mar-01, Volume: 102, Issue:3

    Topics: Calcium Channel Blockers; Child, Preschool; Cohort Studies; Congenital Hyperinsulinism; Diazoxide; Drug Therapy, Combination; Female; Gastrointestinal Agents; Glucagon; Humans; Infant; Male; Nifedipine; Octreotide; Prospective Studies; Starch; Sulfonylurea Receptors; Treatment Outcome

2017
A lethargic neonate and an infant with seizure.
    Clinical pediatrics, 2010, Volume: 49, Issue:4

    Topics: Blood Glucose; Congenital Hyperinsulinism; Diazoxide; Glucagon; Glucose; Humans; Hypoglycemia; Infant; Infant, Newborn; Lethargy; Male; Physical Examination; Respiratory Distress Syndrome, Newborn; Seizures; Vasodilator Agents

2010
Focal congenital hyperinsulinism in a patient with septo-optic dysplasia.
    Nature reviews. Endocrinology, 2010, Volume: 6, Issue:11

    Topics: 3-Hydroxybutyric Acid; Blood Glucose; C-Peptide; Congenital Hyperinsulinism; Glucagon; Glucose; Humans; Hydrocortisone; Hypopituitarism; Infant; Insulin; Loss of Heterozygosity; Male; Pancreas; Pituitary Hormones; Septo-Optic Dysplasia

2010
Glucose metabolism and neurological outcome in congenital hyperinsulinism.
    Seminars in pediatric surgery, 2011, Volume: 20, Issue:1

    Topics: Adolescent; Case-Control Studies; Child; Child, Preschool; Congenital Hyperinsulinism; Developmental Disabilities; Diabetes Mellitus; Female; Gastrointestinal Agents; Germany; Glucagon; Humans; Infant; Infant, Newborn; Language Development Disorders; Male; Octreotide; Pancreatectomy; Prospective Studies; Psychomotor Disorders; Treatment Outcome

2011
Recurrent spontaneous hypoglycaemia causes loss of neurogenic and neuroglycopaenic signs in infants with congenital hyperinsulinism.
    Clinical endocrinology, 2012, Volume: 76, Issue:4

    Topics: Blood Glucose; Congenital Hyperinsulinism; Epinephrine; Fasting; Female; Glucagon; Glucose Clamp Technique; Humans; Hypoglycemia; Infant; Insulin; Male; Norepinephrine

2012
[Congenital hyperinsulinism in 15 infants, 1981-1999; experiences and new insights].
    Nederlands tijdschrift voor geneeskunde, 2004, Mar-13, Volume: 148, Issue:11

    Topics: Congenital Hyperinsulinism; Erythema; Glucagon; Humans; Infant, Newborn

2004