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gamma-aminobutyric acid and Adult-Onset Dystonias

gamma-aminobutyric acid has been researched along with Adult-Onset Dystonias in 11 studies

gamma-Aminobutyric Acid: The most common inhibitory neurotransmitter in the central nervous system.
gamma-aminobutyric acid : A gamma-amino acid that is butanoic acid with the amino substituent located at C-4.

Research Excerpts

ExcerptRelevanceReference
"A four-year retrospective, observational study analysed the use of gabapentin for severe dystonia in children at the Evelina London Children's Hospital."7.83Gabapentin can significantly improve dystonia severity and quality of life in children. ( Gimeno, H; Kaminska, M; Lin, JP; Liow, NY; Lumsden, DE; Marianczak, J; Tomlin, S, 2016)
"Gabapentin may significantly ameliorate dystonia severity and improve activities of daily living and quality of life in children with severe dystonia."7.83Gabapentin can significantly improve dystonia severity and quality of life in children. ( Gimeno, H; Kaminska, M; Lin, JP; Liow, NY; Lumsden, DE; Marianczak, J; Tomlin, S, 2016)
"Gabapentin has been used in the management of neuropathic pain, epilepsy and occasionally movement disorders."5.43Gabapentin can significantly improve dystonia severity and quality of life in children. ( Gimeno, H; Kaminska, M; Lin, JP; Liow, NY; Lumsden, DE; Marianczak, J; Tomlin, S, 2016)
"Gabapentin may significantly ameliorate dystonia severity and improve activities of daily living and quality of life in children with severe dystonia."5.43Gabapentin can significantly improve dystonia severity and quality of life in children. ( Gimeno, H; Kaminska, M; Lin, JP; Liow, NY; Lumsden, DE; Marianczak, J; Tomlin, S, 2016)
"A four-year retrospective, observational study analysed the use of gabapentin for severe dystonia in children at the Evelina London Children's Hospital."3.83Gabapentin can significantly improve dystonia severity and quality of life in children. ( Gimeno, H; Kaminska, M; Lin, JP; Liow, NY; Lumsden, DE; Marianczak, J; Tomlin, S, 2016)
"Gabapentin may significantly ameliorate dystonia severity and improve activities of daily living and quality of life in children with severe dystonia."3.83Gabapentin can significantly improve dystonia severity and quality of life in children. ( Gimeno, H; Kaminska, M; Lin, JP; Liow, NY; Lumsden, DE; Marianczak, J; Tomlin, S, 2016)
"Patients with task-specific dystonia (writer's cramp) have impaired cortical inhibition likely arising from striatal dysfunction."2.70Impaired brain GABA in focal dystonia. ( Hallett, M; Levy, LM, 2002)
"Despite recent advances in tremor and dystonia classification, it remains difficult to discriminate essential tremor from dystonic tremor as they are similar in appearance and no biomarker exists."1.72Multimodal imaging of essential tremor and dystonic tremor. ( Bédard, P; Cho, HJ; Hallett, M; Horovitz, SG; Panyakaew, P, 2022)
"We characterized, in 37 writer's cramp (WC) patients and 14 healthy volunteers (HV), the buildup of motor representations contralateral ("intended") and ispsilateral ("unintended") to the movement to be produced and the excitability changes in left primary motor cortex during the early reaction time (RT) of a pre-cued reaching movement to pick up a pen with either hand to write."1.48Severity of Writer's Cramp is Related to Faulty Motor Preparation. ( James, P; Kishore, A; Krishnan, S; Meunier, S; Popa, T; Robert, S, 2018)
"Gabapentin has been used in the management of neuropathic pain, epilepsy and occasionally movement disorders."1.43Gabapentin can significantly improve dystonia severity and quality of life in children. ( Gimeno, H; Kaminska, M; Lin, JP; Liow, NY; Lumsden, DE; Marianczak, J; Tomlin, S, 2016)
"Gabapentin may significantly ameliorate dystonia severity and improve activities of daily living and quality of life in children with severe dystonia."1.43Gabapentin can significantly improve dystonia severity and quality of life in children. ( Gimeno, H; Kaminska, M; Lin, JP; Liow, NY; Lumsden, DE; Marianczak, J; Tomlin, S, 2016)
"We describe a patient with primary writer's cramp that was completely improved by drinking a small amount of alcohol."1.38Alcohol-responsive writer's cramp. ( An, JY; Kim, JS; Lim, SC; Yoon Kang, S, 2012)
"Writer's cramp is a rare movement disorder of unknown etiology, in which a cramp is elicited primarily or exclusively with writing."1.38Alcohol-responsive writer's cramp. ( An, JY; Kim, JS; Lim, SC; Yoon Kang, S, 2012)

Research

Studies (11)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's5 (45.45)29.6817
2010's5 (45.45)24.3611
2020's1 (9.09)2.80

Authors

AuthorsStudies
Bédard, P3
Panyakaew, P3
Cho, HJ3
Hallett, M5
Horovitz, SG4
Kishore, A1
Popa, T1
James, P1
Krishnan, S1
Robert, S1
Meunier, S1
Tronnier, VM1
Domingo, A1
Moll, CK1
Rasche, D1
Mohr, C1
Rosales, R1
Capetian, P1
Jamora, RD1
Lee, LV1
Münchau, A1
Diesta, CC1
Tadic, V1
Klein, C1
Brüggemann, N1
Moser, A1
Liow, NY1
Gimeno, H1
Lumsden, DE1
Marianczak, J1
Kaminska, M1
Tomlin, S1
Lin, JP1
Sciamanna, G1
Bonsi, P1
Tassone, A1
Cuomo, D1
Tscherter, A1
Viscomi, MT1
Martella, G1
Sharma, N1
Bernardi, G1
Standaert, DG1
Pisani, A1
Herath, P1
Gallea, C1
van der Veen, JW1
Lim, SC1
Kim, JS1
An, JY1
Yoon Kang, S1
Hess, CW1
Saunders-Pullman, R1
Hanajima, R1
Nomura, Y1
Segawa, M1
Ugawa, Y1
Leuzzi, V1
Di Sabato, ML1
Deodato, F1
Rizzo, C1
Boenzi, S1
Carducci, C1
Malaspina, P1
Liberanome, C1
Dionisi-Vici, C1
Levy, LM1

Reviews

1 review available for gamma-aminobutyric acid and Adult-Onset Dystonias

ArticleYear
Movement disorders and alcohol misuse.
    Addiction biology, 2006, Volume: 11, Issue:2

    Topics: Adjuvants, Anesthesia; Alcohol Drinking; Brain; Comorbidity; Dystonic Disorders; Essential Tremor; E

2006

Trials

1 trial available for gamma-aminobutyric acid and Adult-Onset Dystonias

ArticleYear
Impaired brain GABA in focal dystonia.
    Annals of neurology, 2002, Volume: 51, Issue:1

    Topics: Adult; Corpus Striatum; Dystonic Disorders; Functional Laterality; gamma-Aminobutyric Acid; Humans;

2002

Other Studies

9 other studies available for gamma-aminobutyric acid and Adult-Onset Dystonias

ArticleYear
Multimodal imaging of essential tremor and dystonic tremor.
    NeuroImage. Clinical, 2022, Volume: 36

    Topics: Case-Control Studies; Cross-Sectional Studies; Diffusion Tensor Imaging; Dystonia; Dystonic Disorder

2022
Multimodal imaging of essential tremor and dystonic tremor.
    NeuroImage. Clinical, 2022, Volume: 36

    Topics: Case-Control Studies; Cross-Sectional Studies; Diffusion Tensor Imaging; Dystonia; Dystonic Disorder

2022
Multimodal imaging of essential tremor and dystonic tremor.
    NeuroImage. Clinical, 2022, Volume: 36

    Topics: Case-Control Studies; Cross-Sectional Studies; Diffusion Tensor Imaging; Dystonia; Dystonic Disorder

2022
Multimodal imaging of essential tremor and dystonic tremor.
    NeuroImage. Clinical, 2022, Volume: 36

    Topics: Case-Control Studies; Cross-Sectional Studies; Diffusion Tensor Imaging; Dystonia; Dystonic Disorder

2022
Severity of Writer's Cramp is Related to Faulty Motor Preparation.
    Cerebral cortex (New York, N.Y. : 1991), 2018, 10-01, Volume: 28, Issue:10

    Topics: Adult; Anticipation, Psychological; Cues; Dystonic Disorders; Electromyography; Female; Functional L

2018
Biochemical mechanisms of pallidal deep brain stimulation in X-linked dystonia parkinsonism.
    Parkinsonism & related disorders, 2015, Volume: 21, Issue:8

    Topics: Adult; Deep Brain Stimulation; Dystonic Disorders; Female; gamma-Aminobutyric Acid; Genetic Diseases

2015
Gabapentin can significantly improve dystonia severity and quality of life in children.
    European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society, 2016, Volume: 20, Issue:1

    Topics: Activities of Daily Living; Adolescent; Amines; Child; Cyclohexanecarboxylic Acids; Disability Evalu

2016
Impaired striatal D2 receptor function leads to enhanced GABA transmission in a mouse model of DYT1 dystonia.
    Neurobiology of disease, 2009, Volume: 34, Issue:1

    Topics: Analysis of Variance; Animals; Disease Models, Animal; Dystonic Disorders; Excitatory Postsynaptic P

2009
In vivo neurochemistry of primary focal hand dystonia: a magnetic resonance spectroscopic neurometabolite profiling study at 3T.
    Movement disorders : official journal of the Movement Disorder Society, 2010, Dec-15, Volume: 25, Issue:16

    Topics: Adult; Aged; Basal Ganglia; Botulinum Toxins, Type A; Cerebral Cortex; Dystonic Disorders; gamma-Ami

2010
Alcohol-responsive writer's cramp.
    Internal medicine (Tokyo, Japan), 2012, Volume: 51, Issue:1

    Topics: Adult; Alcohol Drinking; Brain; Dystonic Disorders; Electromyography; Ethanol; Female; gamma-Aminobu

2012
Intracortical inhibition of the motor cortex in Segawa disease (DYT5).
    Neurology, 2007, Mar-27, Volume: 68, Issue:13

    Topics: Adult; Basal Ganglia; Biopterins; Brain Diseases, Metabolic; Diagnosis, Differential; Dopamine; Dopa

2007
Vigabatrin improves paroxysmal dystonia in succinic semialdehyde dehydrogenase deficiency.
    Neurology, 2007, Apr-17, Volume: 68, Issue:16

    Topics: Adolescent; Brain; Brain Diseases, Metabolic; Dystonic Disorders; Epilepsy; Extremities; GABA Agents

2007