galactose has been researched along with Sphingolipid Storage Diseases in 9 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 8 (88.89) | 18.7374 |
1990's | 1 (11.11) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Gajewski, A; Kolodny, EH; Raghavan, SA | 1 |
Brady, RO; Cornblath, M; Fishman, PH; Maclaren, NK; Max, SR; Tallman, JF | 1 |
Suzuki, K; Tanaka, H | 1 |
Berra, B; Brunngraber, EG; Davis, LG; Javaid, JI | 1 |
Beyreiss, K | 1 |
Debuch, H; Gielen, W; Kannan, R; Kerènyi, L | 1 |
Calatroni, A; Tira, ME | 1 |
Embil, JA; Ripley, BA; Spence, MW; Tibbles, JA | 1 |
Kaback, MM; Miller, K; Percy, AK; Sonneborn, M | 1 |
2 review(s) available for galactose and Sphingolipid Storage Diseases
Article | Year |
---|---|
Glycoprotein catabolism in brain tissue in the lysosomal enzyme deficiency diseases.
Topics: Adolescent; Binding Sites; Brain; Child; Concanavalin A; Fucose; Galactose; Gangliosidoses; Gaucher Disease; Glycoproteins; Hexosamines; Humans; Infant, Newborn; Leukodystrophy, Globoid Cell; Leukodystrophy, Metachromatic; Lipidoses; Lysosomes; Mannose; Middle Aged; Protein Binding; Sialic Acids; Sphingolipidoses | 1976 |
[Clinical and pathobiochemical findings in genetic diseases of carbohydrate and lipid metabolism].
Topics: Carbohydrate Metabolism, Inborn Errors; Fructose; Galactose; Glycogen Storage Disease; Humans; Hyperlipoproteinemias; Lipid Metabolism, Inborn Errors; Sphingolipidoses | 1992 |
7 other study(ies) available for galactose and Sphingolipid Storage Diseases
Article | Year |
---|---|
GM1-ganglioside beta-galactosidase in leukocytes and cultured fibroblasts.
Topics: Adult; Animals; Cattle; G(M1) Ganglioside; Galactose; Galactosidases; Gangliosides; Gangliosidoses; Humans; Leukocytes; Skin; Sphingolipidoses; Taurocholic Acid | 1977 |
Deficient Ganglioside Biosynthesis: a novel human sphingolipidosis.
Topics: Brain; Carbon Radioisotopes; Galactose; Gangliosides; Hexosyltransferases; Humans; Infant, Newborn; Liver; Male; Neuraminidase; Sphingolipidoses; Transferases | 1975 |
Lactosylceramide beta-galactosidase in human sphingolipidoses. Evidence for two genetically distinct enzymes.
Topics: Brain; Buffers; Cerebrosides; Coumarins; Galactose; Galactosidases; Humans; Lactose; Leukodystrophy, Globoid Cell; Liver; Molecular Biology; Oleic Acids; Sodium Chloride; Sphingolipidoses; Taurocholic Acid | 1975 |
[A sphingolipidosis with the accumulation of neutral glycosphingolipids, AO2(GM3) and A1(GM2)-ganglioside (author's transl)].
Topics: Brain; Ceramides; Cerebellum; Cerebral Cortex; Child; Fatty Acids; Galactose; Gangliosides; Glucose; Glycolipids; Hexoses; Humans; Lipidoses; Palmitic Acids; Parietal Lobe; Pons; Putamen; Sphingolipidoses; Sphingolipids; Stearic Acids; Thalamus | 1974 |
Isolation of acidic glycopeptides from urine by means of anion-exchange resins. Application to some cases of glycosphingolipidosis or mucolipidosis.
Topics: Amino Acids; Chromatography, Ion Exchange; Galactosamine; Glucosamine; Glycopeptides; Hexoses; Humans; Male; Sialic Acids; Sphingolipidoses | 1976 |
A new variant of Sandhoff's disease.
Topics: Appendix; Aspartate Aminotransferases; Cholesterol; Developmental Disabilities; Fibroblasts; Ganglia; Gangliosides; Hexosaminidases; Hexoses; Humans; Isoenzymes; L-Lactate Dehydrogenase; Leukocytes; Liver; Male; Neuraminic Acids; Phospholipids; Seizures; Sphingolipidoses; Syndrome; Temperature; Uronic Acids | 1974 |
Confirmatory studies in the prenatal diagnosis of sphingolipidoses.
Topics: Abortion, Induced; Amniocentesis; Brain Chemistry; Female; Fetus; Galactosidases; Gangliosides; Hexosaminidases; Hexoses; Humans; Isoenzymes; Kidney; Lipid Metabolism, Inborn Errors; Lipidoses; Liver; Neuraminic Acids; Phenols; Pregnancy; Sphingolipidoses; Sphingolipids; Sulfoglycosphingolipids | 1973 |