Page last updated: 2024-08-17

galactose and Ganglioside Storage Diseases

galactose has been researched along with Ganglioside Storage Diseases in 7 studies

Research

Studies (7)

TimeframeStudies, this research(%)All Research%
pre-19903 (42.86)18.7374
1990's3 (42.86)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's1 (14.29)2.80

Authors

AuthorsStudies
Li, L; Liu, LL1
Brescia, MR; French, SA; Harbour, MJ; Kaneski, CR; Miller, SP1
Ariga, T; Bermudez, AJ; Freischutz, B; Tokuda, A; Yu, RK1
Gajewski, A; Kolodny, EH; Raghavan, SA1
Ng Kin Kin, NM; Wolfe, LS1
Berra, B; Brunngraber, EG; Davis, LG; Javaid, JI1
Ahern-Rindell, AJ; Murnane, RD; Prieur, DJ; Wright, RW1

Reviews

1 review(s) available for galactose and Ganglioside Storage Diseases

ArticleYear
Glycoprotein catabolism in brain tissue in the lysosomal enzyme deficiency diseases.
    Advances in experimental medicine and biology, 1976, Volume: 68

    Topics: Adolescent; Binding Sites; Brain; Child; Concanavalin A; Fucose; Galactose; Gangliosidoses; Gaucher Disease; Glycoproteins; Hexosamines; Humans; Infant, Newborn; Leukodystrophy, Globoid Cell; Leukodystrophy, Metachromatic; Lipidoses; Lysosomes; Mannose; Middle Aged; Protein Binding; Sialic Acids; Sphingolipidoses

1976

Other Studies

6 other study(ies) available for galactose and Ganglioside Storage Diseases

ArticleYear
[A case of GM1 gangliosidoses].
    [Zhonghua yan ke za zhi] Chinese journal of ophthalmology, 2022, Oct-11, Volume: 58, Issue:10

    Topics: G(M1) Ganglioside; Galactose; Gangliosidoses; Glucosides; Humans; Mutation

2022
Hydrolysis of a novel lysosomotropic enzyme substrate for beta-galactosidase within intact cells.
    Journal of lipid research, 1994, Volume: 35, Issue:8

    Topics: beta-Galactosidase; Cell Line; Enzyme Activation; Fibroblasts; Fluorescent Dyes; Galactose; Gangliosidoses; Humans; Lysosomes; Microscopy, Fluorescence; Substrate Specificity

1994
Unusual gangliosidosis in emu (Dromaius novaehollandiae).
    Journal of neurochemistry, 1997, Volume: 68, Issue:5

    Topics: Animals; Antigens, CD; Bird Diseases; Birds; Brain; Galactose; Galactosylceramides; Gangliosides; Gangliosidoses; Glucose; Glycolipids; Lactosylceramides; Lipid Metabolism; Liver; N-Acetylneuraminic Acid; Nerve Tissue Proteins; Sulfoglycosphingolipids

1997
GM1-ganglioside beta-galactosidase in leukocytes and cultured fibroblasts.
    Clinica chimica acta; international journal of clinical chemistry, 1977, Nov-15, Volume: 81, Issue:1

    Topics: Adult; Animals; Cattle; G(M1) Ganglioside; Galactose; Galactosidases; Gangliosides; Gangliosidoses; Humans; Leukocytes; Skin; Sphingolipidoses; Taurocholic Acid

1977
Storage and excretion of oligosaccharides and glycopeptides in the gangliosidoses.
    Advances in experimental medicine and biology, 1976, Volume: 68

    Topics: Galactose; Gangliosidoses; Glucosamine; Glycopeptides; Humans; Infant; Lipidoses; Liver; Mannose; Molecular Conformation; Molecular Weight; Oligosaccharides

1976
Prenatal lesions in an ovine fetus with GM1 gangliosidosis.
    American journal of medical genetics, 1991, Apr-01, Volume: 39, Issue:1

    Topics: Acetylgalactosamine; Animals; beta-Galactosidase; Embryo Transfer; Female; Fetus; G(M1) Ganglioside; Galactose; Gangliosidoses; Heterozygote; Lysosomes; N-Acetylneuraminic Acid; Pregnancy; Prenatal Diagnosis; Sheep; Sheep Diseases; Sialic Acids

1991