Page last updated: 2024-08-17

galactose and Classic Globoid Cell Leukodystrophy

galactose has been researched along with Classic Globoid Cell Leukodystrophy in 15 studies

Research

Studies (15)

Timeframe	Studies, this research(%)	All Research%
pre-1990	12 (80.00)	18.7374
1990's	1 (6.67)	18.2507
2000's	0 (0.00)	29.6817
2010's	2 (13.33)	24.3611
2020's	0 (0.00)	2.80

Authors

Authors	Studies
Suzuki, Y	1
Alvares, E; Cardile, V; Costantino-Ceccarini, E; Mazzone, D; Pannuzzo, G; Perciavalle, V	1
Suzuki, K; Tanaka, H	1
Berra, B; Brunngraber, EG; Davis, LG; Javaid, JI	1
Costantino-Ceccarini, E; Fletcher, TF; Suzuki, K	1
Inui, K; Midorikawa, M; Nishimoto, J; Okada, S; Taniike, M; Tsukamoto, H; Yabuuchi, H	1
Brady, RO; Gal, AE; Quirk, JM; Tokoro, T; Weis, AL	1
Brady, RO	1
Aguilar, V; Aro, A; Berra, B; Brunngraber, EG; Zambotti, V	1
Clark, C; McKelvey, H; Sattler, M; Wenger, DA	1
Wenger, DA	1
Hiatt, W; Sattler, M; Wenger, DA	1
Miyatake, T; Suzuki, K	1
Berra, B; Brunngraber, EG; Zambotti, V	1
NORMAN, RM; OPPENHEIMER, DR; TINGEY, AH	1

Reviews

4 review(s) available for galactose and Classic Globoid Cell Leukodystrophy

Article	Year
[The world of galactose and glucose: pathogenesis and therapy of lysosomal diseases]. No to hattatsu = Brain and development, 2014, Volume: 46, Issue:2 Topics: Administration, Oral; Animals; Fabry Disease; Galactose; Galactosidases; Gangliosidosis, GM1; Glucose; Glucosidases; Humans; Leukodystrophy, Globoid Cell; Lysosomal Storage Diseases; Molecular Chaperones; Molecular Targeted Therapy; Pathology, Molecular; Proteostasis Deficiencies	2014
Glycoprotein catabolism in brain tissue in the lysosomal enzyme deficiency diseases. Advances in experimental medicine and biology, 1976, Volume: 68 Topics: Adolescent; Binding Sites; Brain; Child; Concanavalin A; Fucose; Galactose; Gangliosidoses; Gaucher Disease; Glycoproteins; Hexosamines; Humans; Infant, Newborn; Leukodystrophy, Globoid Cell; Leukodystrophy, Metachromatic; Lipidoses; Lysosomes; Mannose; Middle Aged; Protein Binding; Sialic Acids; Sphingolipidoses	1976
Disorders of lipid metabolism. Biochemical Society symposium, 1972, Issue:35 Topics: Adult; Animals; Bone Marrow; Cell Line; Ceramides; Child; Fabry Disease; Fucose; Galactose; Gangliosides; Gaucher Disease; Genetic Variation; Glycolipids; Glycoside Hydrolases; Humans; Leukemia, Myeloid; Leukodystrophy, Globoid Cell; Leukodystrophy, Metachromatic; Lipid Metabolism, Inborn Errors; Lipidoses; Mice; Niemann-Pick Diseases; Sulfoglycosphingolipids	1972
Additional deficiency of psychosine galactosidase in globoid cell leukodystrophy: an implication to enzyme replacement therapy. Birth defects original article series, 1973, Volume: 9, Issue:2 Topics: Animals; Brain; Carbon Radioisotopes; Cerebrosides; Chemical Phenomena; Chemistry; Galactose; Galactosidases; Kidney; Leukodystrophy, Globoid Cell; Liver; Rats	1973

Other Studies

11 other study(ies) available for galactose and Classic Globoid Cell Leukodystrophy

Article	Year
A galactose-free diet enriched in soy isoflavones and antioxidants results in delayed onset of symptoms of Krabbe disease in twitcher mice. Molecular genetics and metabolism, 2010, Volume: 100, Issue:3 Topics: Animals; Antioxidants; Apoptosis; Cell Survival; Cells, Cultured; Disease Models, Animal; Female; Galactose; Glutathione; Humans; Isoflavones; Leukodystrophy, Globoid Cell; Male; Mice; Mice, Inbred C57BL; Mice, Neurologic Mutants; Oligodendroglia; Psychosine; Ubiquinone; Xanthophylls	2010
Lactosylceramide beta-galactosidase in human sphingolipidoses. Evidence for two genetically distinct enzymes. The Journal of biological chemistry, 1975, Mar-25, Volume: 250, Issue:6 Topics: Brain; Buffers; Cerebrosides; Coumarins; Galactose; Galactosidases; Humans; Lactose; Leukodystrophy, Globoid Cell; Liver; Molecular Biology; Oleic Acids; Sodium Chloride; Sphingolipidoses; Taurocholic Acid	1975
Glycolipid metabolism in the canine form of globoid cell leukodystrophy. Advances in experimental medicine and biology, 1976, Volume: 68 Topics: Animals; Brain; Cerebral Cortex; Disease Models, Animal; Dogs; Galactose; Galactosylceramidase; Galactosyltransferases; Glucosyltransferases; Glycolipids; Leukodystrophy, Globoid Cell	1976
Study of pathogenesis in twitcher mouse, an enzymatically authentic model of Krabbe's disease. Journal of the neurological sciences, 1990, Volume: 100, Issue:1-2 Topics: Age Factors; Animals; Ceramides; Disease Models, Animal; Galactose; Galactosylceramidase; Galactosylceramides; Galactosyltransferases; Ganglioside Galactosyltransferase; Leukodystrophy, Globoid Cell; Mice; Mice, Neurologic Mutants; Myelin Sheath; Organ Culture Techniques; Psychosine; Sciatic Nerve; Sphingosine; Spinal Cord	1990
Animal and cellular models of sphingolipid storage disorders of humans. Chemistry and physics of lipids, 1986, Dec-15, Volume: 42, Issue:1-3 Topics: Animals; Brain; Cerebrosides; Disease Models, Animal; Galactose; Galactosylceramidase; Galactosylceramides; Gaucher Disease; Glucosylceramides; Humans; Intestine, Small; Leukodystrophy, Globoid Cell; Rats; Rats, Inbred Strains	1986
Gangliosides, glycoproteins, and glycosaminoglycans in Krabbe's disease. Clinica chimica acta; international journal of clinical chemistry, 1973, Aug-30, Volume: 47, Issue:2 Topics: Brain; Brain Chemistry; Child, Preschool; Chromatography, Thin Layer; Fucose; Galactose; Gangliosides; Glycoproteins; Glycosaminoglycans; Hexosamines; Humans; Kidney; Leukodystrophy, Globoid Cell; Liver; Mannose; Neuraminic Acids	1973
An improved method for the identification of patients and carriers of Krabbe's disease. Clinica chimica acta; international journal of clinical chemistry, 1974, Oct-30, Volume: 56, Issue:2 Topics: Amniotic Fluid; Ceramides; Cerebrosides; Female; Fibroblasts; Galactose; Galactosidases; Humans; Lactose; Leukocytes; Leukodystrophy, Globoid Cell; Male; Oleic Acids; Pregnancy; Prenatal Diagnosis; Taurocholic Acid; Tritium	1974
Studies on galactosyl ceramide and lactosyl ceramide beta-galactosidase. Chemistry and physics of lipids, 1974, Volume: 13, Issue:4 Topics: Brain; Ceramides; Cerebrosides; Death, Sudden; Galactose; Galactosidases; Glycosides; Hot Temperature; Humans; Infant; Kinetics; Lactose; Leukodystrophy, Globoid Cell; Lipid Metabolism, Inborn Errors	1974
Globoid cell leukodystrophy: deficiency of lactosyl ceramide beta-galactosidase. Proceedings of the National Academy of Sciences of the United States of America, 1974, Volume: 71, Issue:3 Topics: Adult; Brain; Ceramides; Female; Galactose; Galactosidases; Gangliosides; Humans; Infant; Lactose; Leukodystrophy, Globoid Cell; Leukodystrophy, Metachromatic; Lipidoses; Liver; Male; Niemann-Pick Diseases; Skin; Spleen; Syndrome	1974
Brain glycoproteins in GM1-gangliosidosis: isolation and carbohydrate composition of glycopeptides. FEBS letters, 1973, Aug-15, Volume: 34, Issue:2 Topics: Brain; Brain Chemistry; Carbohydrate Metabolism, Inborn Errors; Child; Child, Preschool; Female; Fucose; Galactose; Gangliosides; Glycopeptides; Glycoproteins; Hexosamines; Humans; Infant; Leukodystrophy, Globoid Cell; Mannose; Neuraminic Acids	1973
Histological and chemical findings in Krabbe's leucodystrophy. Journal of neurology, neurosurgery, and psychiatry, 1961, Volume: 24 Topics: Brain; Central Nervous System Diseases; Hexoses; Humans; Leukodystrophy, Globoid Cell; Lipid Metabolism; Lipids	1961