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galactose and Alpers Diffuse Degeneration of Cerebral Gray Matter with Hepatic Cirrhosis

galactose has been researched along with Alpers Diffuse Degeneration of Cerebral Gray Matter with Hepatic Cirrhosis in 19 studies

Research

Studies (19)

TimeframeStudies, this research(%)All Research%
pre-199019 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Hansson, HA; Olsson, Y; Sourander, P; Svennerholm, L1
Andrews, JM; Cancilla, PA; Grippo, J; Menkes, JH1
Anzil, AP; Blinzinger, K; Dorn, G; Mehraein, P; Neuhäuser, G1
Brady, RO2
Bischoff, A; Herschkowitz, N; Meier, C1
Markey, JP; Satter, M; Wenger, DA1
Fletcher, TF; Kurtz, HJ1
Crome, L; Patrick, AD; Wilson, J; Young, E1
Miyatake, T; Suzuki, K1
Dawson, G; Desnick, RJ; Desnick, SJ; Suzuki, K; Suzuki, Y1
Suzuki, K1
Fletcher, TF; Kurtz, HJ; Stadlan, EM1
Epstein, CJ; Schneider, EL; Suzuki, K1
Eto, Y; Suzuki, K2
Bond, PR; Gerstl, B; Hayman, RB; Malamud, N1
Cabrera, M; Ledeen, R; Salsman, K1
Duncan, C; Menkes, JH; Moossy, J1

Other Studies

19 other study(ies) available for galactose and Alpers Diffuse Degeneration of Cerebral Gray Matter with Hepatic Cirrhosis

ArticleYear
Experimental studies on the pathogenesis of leucodystrophies. II. The effect of sphingolipids on various cell types in cultures from the nervous system.
    Acta neuropathologica, 1966, Jun-01, Volume: 6, Issue:3

    Topics: Animals; Brain; Cerebellum; Cerebrosides; Culture Techniques; Diffuse Cerebral Sclerosis of Schilder; Galactose; Glucose; Humans; Microscopy, Phase-Contrast; Nerve Tissue; Rats; Retina; Spleen; Staining and Labeling; Sulfates

1966
Globoid cell leukodystrophy (Krabbe's disease): morphological and biochemical studies.
    Neurology, 1971, Volume: 21, Issue:4

    Topics: Autopsy; Biopsy; Brain; Carbon Isotopes; Centrifugation, Density Gradient; Cerebrosides; Cholesterol; Chromatography, Thin Layer; Demyelinating Diseases; Diffuse Cerebral Sclerosis of Schilder; Female; Frontal Lobe; Galactose; Gangliosides; Glycolipids; Humans; Inclusion Bodies; Infant; Lipid Metabolism; Male; Microscopy, Electron; Microsomes; Mitochondria; Phospholipids

1971
Cytoplasmic inclusions in a child affected with Krabbe's disease (globoid leucodystrophy) and in the rabbit injected with galactocerebrosides.
    Journal of neuropathology and experimental neurology, 1972, Volume: 31, Issue:2

    Topics: Animals; Bone Marrow; Brain; Cerebral Cortex; Cerebral Ventricles; Cerebrosides; Diffuse Cerebral Sclerosis of Schilder; Female; Galactose; Humans; Hydrocephalus; Inclusion Bodies; Infant; Microscopy, Phase-Contrast; Rabbits

1972
The adnormal biochemistry of inherited disorders of lipid metabolism.
    Federation proceedings, 1973, Volume: 32, Issue:6

    Topics: Brain; Ceramides; Cerebrosides; Diffuse Cerebral Sclerosis of Schilder; Female; Fibroblasts; Galactose; Galactosidases; Gaucher Disease; Glucose; Glycolipids; Glycoside Hydrolases; Hexosaminidases; Humans; Intestines; Kidney; Leukocytes; Lipid Metabolism, Inborn Errors; Lipidoses; Liver; Male; Muscles; Niemann-Pick Diseases; Phosphoric Diester Hydrolases; Sphingomyelins; Spleen; Sulfoglycosphingolipids; Syndrome

1973
Morphological and biochemical observations in the Jimpy spinal cord.
    Acta neuropathologica, 1974, Apr-30, Volume: 27, Issue:4

    Topics: Age Factors; Animals; Axons; Cell Count; Cell Nucleus; Cerebrosides; Dendrites; Diffuse Cerebral Sclerosis of Schilder; Galactose; Humans; Inclusion Bodies; Mice; Mice, Inbred C57BL; Mutation; Myelin Sheath; Nerve Fibers, Myelinated; Neuroglia; Rodent Diseases; Sex Chromosomes; Spinal Cord; Spinal Cord Diseases

1974
Deficiency of monogalactosyl diglycerid beta-B-galactosidase activity in krabbe's disease.
    Biochemical and biophysical research communications, 1973, Jul-17, Volume: 53, Issue:2

    Topics: Brain; Cells, Cultured; Cerebrosides; Diffuse Cerebral Sclerosis of Schilder; Fibroblasts; Galactose; Galactosidases; Glucosidases; Glycerides; Humans; Infant; Liver; Skin; Sphingolipids; Sphingosine; Tritium

1973
Animal model: globoid cell leukodystrophy in the dog.
    The American journal of pathology, 1972, Volume: 66, Issue:2

    Topics: Animals; Brain; Cerebrosides; Child; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Disease Models, Animal; Dogs; Galactose; Galactosidases; Glycoside Hydrolases; Humans; Lipidoses; Macrophages

1972
Galactocerebrosidase deficiency in globoid cell leucodystrophy of late onset.
    Archives of disease in childhood, 1972, Volume: 47, Issue:253

    Topics: Cerebrosides; Child; Child, Preschool; Diffuse Cerebral Sclerosis of Schilder; Female; Galactose; Glycoside Hydrolases; Humans; Male; Tritium

1972
Globoid cell leukodystrophy: additional deficiency of psychosine galactosidase.
    Biochemical and biophysical research communications, 1972, Aug-07, Volume: 48, Issue:3

    Topics: Brain; Diffuse Cerebral Sclerosis of Schilder; Galactose; Glycoside Hydrolases; Humans; Kidney; Liver; Sphingolipids

1972
Urinary screening of globoid-cell leukodystrophy.
    The New England journal of medicine, 1971, Jul-22, Volume: 285, Issue:4

    Topics: Cerebrosides; Diffuse Cerebral Sclerosis of Schilder; Galactose; Glycolipids; Glycoside Hydrolases; Humans; Infant; Male; Sphingolipids

1971
Renal cerebroside in globoid cell leukodystrophy (Krabbe's disease).
    Lipids, 1971, Volume: 6, Issue:6

    Topics: Cerebrosides; Child, Preschool; Chromatography, Gas; Diffuse Cerebral Sclerosis of Schilder; Galactose; Galactosidases; Glucose; Humans; Infant; Kidney; Lipids; Water

1971
Experimental Wallerian degeneration in peripheral nerves of dogs with globoid cell leukodystrophy.
    Journal of neuropathology and experimental neurology, 1971, Volume: 30, Issue:4

    Topics: Animals; Cerebrosides; Diffuse Cerebral Sclerosis of Schilder; Dogs; Female; Galactose; Macrophages; Male; Nerve Degeneration; Phagocytosis; Schwann Cells; Ulnar Nerve

1971
In utero diagnosis of globoid cell leukodystrophy (Krabb's disease).
    Biochemical and biophysical research communications, 1971, Dec-03, Volume: 45, Issue:5

    Topics: Abortion, Induced; Amniocentesis; Amniotic Fluid; Brain; Cells, Cultured; Cerebrosides; Diffuse Cerebral Sclerosis of Schilder; Female; Fetal Diseases; Galactose; Galactosidases; Gestational Age; Humans; Liver; Pregnancy

1971
Globoid cell leukodystrophy (Krabbe's disease): isolation of myelin with normal glycolipid composition.
    Journal of lipid research, 1970, Volume: 11, Issue:5

    Topics: Brain Chemistry; Centrifugation, Density Gradient; Cerebrosides; Cholesterol; Chromatography, Thin Layer; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Galactose; Glycolipids; Humans; Infant; Lipids; Male; Microscopy, Electron; Myelin Sheath; Phospholipids; Sulfuric Acids

1970
Brain sphingoglycolipids in Krabbe's globoid cell leucodystrophy.
    Journal of neurochemistry, 1971, Volume: 18, Issue:3

    Topics: Autopsy; Brain Chemistry; Carbohydrates; Cerebrosides; Chromatography; Chromatography, Paper; Chromatography, Thin Layer; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Galactose; Gangliosides; Glucose; Glycolipids; Hexoses; Humans; Infant; Lipids; Male; Nervous System; Sphingolipids

1971
Morphological and neurochemical study of Pelizaeus-Merzbacher disease.
    Journal of neurology, neurosurgery, and psychiatry, 1965, Volume: 28, Issue:6

    Topics: Adolescent; Brain; Brain Chemistry; Diffuse Cerebral Sclerosis of Schilder; Galactose; Humans; Lipids; Male; Proteins; Water

1965
Metabolic disorders of sphingolipid metabolism in man.
    Chemistry and physics of lipids, 1970, Volume: 5, Issue:1

    Topics: Amino Alcohols; Carbon Isotopes; Cerebrosides; Diffuse Cerebral Sclerosis of Schilder; Esterases; Fatty Acids; Gangliosides; Gaucher Disease; Glycols; Hexoses; Humans; Lipid Metabolism; Lipidoses; Niemann-Pick Diseases; Sphingomyelins; Sulfuric Acids

1970
Gangliosides in subacute sclerosing leukoencephalitis: isolation and fatty acid composition of nine fractions.
    Journal of lipid research, 1968, Volume: 9, Issue:1

    Topics: Brain Chemistry; Child; Chromatography; Chromatography, Gas; Chromatography, Paper; Chromatography, Thin Layer; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Gangliosides; Hexosamines; Hexoses; Humans; Male; Oleic Acids; Palmitic Acids; Stearic Acids

1968
Molecular composition of the major glycolipids in globoid cell leukodystrophy.
    Neurology, 1966, Volume: 16, Issue:6

    Topics: Brain Chemistry; Cerebral Cortex; Cerebrosides; Chromatography, Thin Layer; Demyelinating Diseases; Diffuse Cerebral Sclerosis of Schilder; Fatty Acids; Female; Glycolipids; Hexoses; Humans; Infant; Lipid Metabolism, Inborn Errors; Sulfates

1966