fucose and Fucosidosis

fucose has been researched along with Fucosidosis in 5 studies

Research

Studies (5)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's3 (60.00)18.2507
2000's1 (20.00)29.6817
2010's1 (20.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Beck, HC; D'Hooge, R; Damme, M; Dierks, T; Hermans-Borgmeyer, I; Lübke, T; Lüllmann-Rauch, R; Stroobants, S; Wolf, H1
Mononen, I; Noronkoski, T1
Yamaguchi, S1
Anson, DS; Bielicki, J; Fuller, M; Hopwood, JJ; Muller, V1
Alonso, C; Cache, P; Michalski, JC; Montreuil, J; Strecker, G; Wieruszeski, JM1

Reviews

1 review(s) available for fucose and Fucosidosis

ArticleYear
[Fucosidosis].
    Ryoikibetsu shokogun shirizu, 1998, Issue:19 Pt 2

    Topics: alpha-L-Fucosidase; Diagnosis, Differential; Fucose; Fucosidosis; Humans; Prognosis

1998

Other Studies

4 other study(ies) available for fucose and Fucosidosis

ArticleYear
A mouse model for fucosidosis recapitulates storage pathology and neurological features of the milder form of the human disease.
    Disease models & mechanisms, 2016, 09-01, Volume: 9, Issue:9

    Topics: alpha-L-Fucosidase; Animals; Behavior, Animal; Brain; Disease Models, Animal; Enzyme Activation; Fucose; Fucosidosis; G(M2) Ganglioside; Glycoconjugates; Glycoproteins; Humans; Inflammation; Lysosomes; Mice, Inbred C57BL; Organ Specificity; Proteolysis; Purkinje Cells; Viscera

2016
Influence of L-fucose attached alpha 1-->6 to the asparagine-linked N-acetylglucosamine on the hydrolysis of the N-glycosidic linkage by human glycosylasparaginase.
    Glycobiology, 1997, Volume: 7, Issue:2

    Topics: Acetylglucosamine; alpha-L-Fucosidase; Aspartylglucosylaminase; Fucose; Fucosidosis; Glycosides; Humans; Recombinant Proteins; Species Specificity; Substrate Specificity

1997
Recombinant canine alpha-l-fucosidase: expression, purification, and characterization.
    Molecular genetics and metabolism, 2000, Volume: 69, Issue:1

    Topics: alpha-L-Fucosidase; Ammonium Chloride; Animals; Base Sequence; Brain; Carbohydrate Metabolism; Cells, Cultured; Cricetinae; Culture Media, Conditioned; Disease Models, Animal; Dogs; Endocytosis; Fibroblasts; Fucose; Fucosidosis; Genetic Vectors; Hexosamines; Humans; Hydrogen-Ion Concentration; Kinetics; Molecular Weight; Receptor, IGF Type 2; Recombinant Proteins

2000
Characterization and 400-MHz 1H-NMR analysis of urinary fucosyl glycoasparagines in fucosidosis.
    European journal of biochemistry, 1991, Oct-15, Volume: 201, Issue:2

    Topics: Carbohydrate Sequence; Chromatography, High Pressure Liquid; Fucose; Fucosidosis; Glycopeptides; Humans; Magnetic Resonance Spectroscopy; Methylation; Molecular Sequence Data

1991