fibrinogen has been researched along with Orphan Diseases in 17 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 3 (17.65) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 3 (17.65) | 29.6817 |
2010's | 6 (35.29) | 24.3611 |
2020's | 5 (29.41) | 2.80 |
Authors | Studies |
---|---|
Djambas Khayat, C; Knaub, S; Kruzhkova, I; Lohade, SD; Peyvandi, F; Solomon, C; Zekavat, OR | 1 |
Azarkeivan, A; Baghaipour, MR; Jazebi, M; Menegatti, M; Moazezi, S; Mohsenian, S; Palla, R; Peyvandi, F; Seidizadeh, O | 1 |
Shapiro, A | 1 |
Brunclíkova, M; Dobrotova, M; Grendar, M; Kolkova, Z; Kubisz, P; Lasabova, Z; Loderer, D; Simurda, T; Skornova, I; Stasko, J; Zolkova, J | 1 |
Cao, L; Huang, X | 1 |
Boyle, MA; Breen, CM; McCallion, N; Riazat, MI | 1 |
Ali, S; Ghosh, K; Kulkarni, BP; Mota, L; Nair, SB; Shanbhag, S; Shetty, SD; Vijapurkar, M | 1 |
Amir, AZ; Avitzur, Y; Cattral, M; Cutz, E; De Angelis, M; Fecteau, A; Ghanekar, A; Grant, D; Jones, N; Kamath, B; Ling, SC; Nalli, N; Naqvi, A; Ng, V; Weitzman, S | 1 |
Biswas, A; Davoli, M; Detarsio, G; Gupta, S; Ivaškevičius, V; Oldenburg, J; Pérez, S; Quartara, A; Raviola, M; Rühl, H | 1 |
Menegatti, M; Peyvandi, F | 1 |
Acharya, SS; Dimichele, DM | 1 |
Ruiz-Sáez, A | 1 |
SOULIER, JP | 1 |
CALDER, A; VERNINO, RA | 1 |
LOEB, J | 1 |
Dolan, G; Garipidou, V; Hill, M; Lefkou, E; Perifanis, V; Rizopoulou, D; Tziomalos, K; Vakalopoulou, S; Zafiriadou, E | 1 |
Alexopoulou, E; Delis, S; Dourakis, S; Hatzimichail, K; Kelekis, A; Kelekis, D; Letsou, D; Malagari, K; Sissopoulos, A | 1 |
4 review(s) available for fibrinogen and Orphan Diseases
Article | Year |
---|---|
The use of prophylaxis in the treatment of rare bleeding disorders.
Topics: Blood Coagulation Disorders; Female; Fibrinogen; Hemorrhagic Disorders; Humans; Pregnancy; Prospective Studies; Rare Diseases | 2020 |
Molecular pathology of rare bleeding disorders (RBDs) in India: a systematic review.
Topics: Blood Coagulation Disorders; Blood Coagulation Factors; Databases, Genetic; Fibrinogen; Humans; India; Mutation; Pathology, Molecular; Rare Diseases | 2014 |
Treatment of rare factor deficiencies in 2016.
Topics: Blood Coagulation Factors; Blood Component Transfusion; Coagulation Protein Disorders; Factor VIII; Fibrinogen; Humans; Plasma; Rare Diseases | 2016 |
Rare inherited disorders of fibrinogen.
Topics: Adult; Afibrinogenemia; Blood Coagulation; Coagulants; Factor VIII; Female; Fibrinogen; Genotype; Hemorrhage; Humans; Infant, Newborn; Iran; Italy; Male; MEDLINE; Mutation; North America; Phenotype; Pregnancy; Pregnancy Complications, Hematologic; Prenatal Diagnosis; Rare Diseases | 2008 |
13 other study(ies) available for fibrinogen and Orphan Diseases
Article | Year |
---|---|
Analysis of fibrinogen concentrate pharmacokinetics and dosing for bleeds and surgery in adults, adolescents, and children with congenital afibrinogenaemia and hypofibrinogenaemia.
Topics: Adolescent; Adult; Afibrinogenemia; Child; Clinical Trials, Phase II as Topic; Clinical Trials, Phase III as Topic; Fibrinogen; Hemorrhage; Hemostatics; Humans; Prospective Studies; Rare Diseases; Young Adult | 2022 |
Diagnostic utility of bleeding assessment tools in congenital fibrinogen deficiencies.
Topics: Afibrinogenemia; Blood Coagulation Disorders; Fibrinogen; Hemorrhage; Humans; Iran; Rare Diseases | 2023 |
Comparison of clinical phenotype with genetic and laboratory results in 31 patients with congenital dysfibrinogenemia in northern Slovakia.
Topics: Adolescent; Adult; Afibrinogenemia; Asymptomatic Diseases; Child; Child, Preschool; Cross-Sectional Studies; Female; Fibrinogen; Genotype; Hemorrhage; Humans; Male; Middle Aged; Phenotype; Point Mutation; Rare Diseases; Slovakia; Young Adult | 2020 |
Rare severe hypofibrinogenemia induced by tissue plasminogen activator in stroke patients: Case report.
Topics: Afibrinogenemia; Aged; Aged, 80 and over; Biomarkers; Female; Fibrinogen; Fibrinolytic Agents; Humans; Male; Rare Diseases; Severity of Illness Index; Stroke; Thrombolytic Therapy; Tissue Plasminogen Activator | 2021 |
Congenital hypofibrinogenaemia: a presymptomatic detection of an extremely rare bleeding disorder in preterm twins.
Topics: Afibrinogenemia; Continuous Positive Airway Pressure; Diagnosis, Differential; Female; Fibrinogen; Hemorrhage; Humans; Infant, Low Birth Weight; Infant, Newborn; Infant, Premature, Diseases; Infusions, Intravenous; Ireland; Menorrhagia; Pregnancy; Pregnancy, Twin; Premature Birth; Pulmonary Surfactants; Rare Diseases; Respiratory Distress Syndrome, Newborn; Treatment Outcome; Twins, Monozygotic | 2017 |
Liver transplantation for children with acute liver failure associated with secondary hemophagocytic lymphohistiocytosis.
Topics: Adolescent; Biopsy; Child; Child, Preschool; Cross-Sectional Studies; Disease Progression; Female; Ferritins; Fibrinogen; Graft Rejection; Humans; Immunosuppression Therapy; Immunosuppressive Agents; Infant; Liver; Liver Failure, Acute; Liver Transplantation; Lymphohistiocytosis, Hemophagocytic; Male; Rare Diseases; Recurrence; Retrospective Studies; Survival Rate; Time-to-Treatment; Treatment Outcome; Triglycerides | 2016 |
A novel missense mutation in the FGB gene (p.Gly302Arg) leading to afibrinogenemia. Predicted structure and function consequences.
Topics: Adult; Afibrinogenemia; Base Sequence; Codon, Nonsense; Diagnosis, Differential; Fibrinogen; Genetic Predisposition to Disease; Genetic Testing; Hemorrhage; Humans; Male; Molecular Sequence Data; Rare Diseases; Structure-Activity Relationship | 2016 |
Thrombosis in rare bleeding disorders.
Topics: Blood Coagulation Disorders, Inherited; Factor VII Deficiency; Factor XI Deficiency; Fibrinogen; Hemorrhage; Hemorrhagic Disorders; Humans; Rare Diseases; Thrombosis | 2012 |
[Separation of fibrinogen and of antihemophilic factor A. II. With the aid of bentonite].
Topics: Aluminum Silicates; Bentonite; Blood Coagulation; Factor VIII; Fibrinogen; Humans; Prothrombin; Rare Diseases; Retinal Degeneration | 1959 |
Afibrinogenemia occurring in premature separation of the placenta; with a case report.
Topics: Afibrinogenemia; Female; Fibrinogen; Placenta; Pregnancy; Rare Diseases; Retinal Degeneration; Retinal Detachment | 1955 |
[Separation of fibrinogen and of antihemophilic factor A. I. With the aid of kaolin].
Topics: Blood Coagulation; Factor VIII; Fibrinogen; Humans; Kaolin; Rare Diseases; Retinal Degeneration | 1959 |
Management of acute bleeding in a patient with congenital afibrinogenaemia.
Topics: Adult; Afibrinogenemia; Blood Coagulation Disorders; Fibrinogen; Hemorrhage; Humans; Male; Rare Diseases | 2006 |
Transarterial embolization of giant liver hemangiomas associated with Kasabach-Merritt syndrome: a case report.
Topics: Aged; Blood Coagulation Disorders; Embolization, Therapeutic; Female; Fibrinogen; Follow-Up Studies; Hemangioma; Hematocrit; Hepatic Artery; Humans; Liver Neoplasms; Microspheres; Middle Aged; Platelet Count; Rare Diseases; Syndrome; Tomography, X-Ray Computed; Treatment Outcome | 2007 |