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etomoxir and Lipid Metabolism, Inborn Error

etomoxir has been researched along with Lipid Metabolism, Inborn Error in 4 studies

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's2 (50.00)18.2507
2000's0 (0.00)29.6817
2010's1 (25.00)24.3611
2020's1 (25.00)2.80

Authors

AuthorsStudies
Baartscheer, A; Bezzina, CR; Bleeker, JC; Coronel, R; Ferdinandusse, S; Guan, K; Houtkooper, RH; IJlst, L; Knottnerus, SJG; Li, W; Luo, X; Mengarelli, I; Portero, VM; Ulbricht, Y; Verkerk, AO; Visser, G; Wanders, RJA; Wijburg, FA; Wüst, RCI1
Acquaviva, C; Benoist, JF; Chevalier, S; Dumas, JF; Gouache, E; Labarthe, F; Lefort, B; Servais, S; Tardieu, M; Vianey-Saban, C1
Brivet, M; Divry, P; Mathieu, M; Nada, M; Roe, C; Vianey-Saban, C; Zabot, MT1
Bastin, J; Djouadi, F; Gonzalez, FJ; Kelly, DP; Pitchford, C; Saffitz, JE; Weinheimer, CJ1

Other Studies

4 other study(ies) available for etomoxir and Lipid Metabolism, Inborn Error

ArticleYear
Electrophysiological Abnormalities in VLCAD Deficient hiPSC-Cardiomyocytes Can Be Improved by Lowering Accumulation of Fatty Acid Oxidation Intermediates.
    International journal of molecular sciences, 2020, Apr-08, Volume: 21, Issue:7

    Topics: Action Potentials; Acyl-CoA Dehydrogenase, Long-Chain; Arrhythmias, Cardiac; Cardiac Electrophysiology; Congenital Bone Marrow Failure Syndromes; Epoxy Compounds; Fatty Acids; Humans; Induced Pluripotent Stem Cells; Lipid Metabolism, Inborn Errors; Mitochondria; Mitochondrial Diseases; Muscular Diseases; Myocytes, Cardiac; Oxidation-Reduction; Resveratrol

2020
Pharmacological inhibition of carnitine palmitoyltransferase 1 restores mitochondrial oxidative phosphorylation in human trifunctional protein deficient fibroblasts.
    Biochimica et biophysica acta. Molecular basis of disease, 2017, Volume: 1863, Issue:6

    Topics: Cardiomyopathies; Carnitine O-Palmitoyltransferase; Epoxy Compounds; Female; Fibroblasts; Humans; Infant; Infant, Newborn; Lipid Metabolism, Inborn Errors; Male; Mitochondria; Mitochondrial Myopathies; Mitochondrial Trifunctional Protein; Nervous System Diseases; Oxidative Phosphorylation; Rhabdomyolysis

2017
Mitochondrial very-long-chain acyl-coenzyme A dehydrogenase deficiency: clinical characteristics and diagnostic considerations in 30 patients.
    Clinica chimica acta; international journal of clinical chemistry, 1998, Jan-12, Volume: 269, Issue:1

    Topics: Acyl-CoA Dehydrogenase, Long-Chain; Carnitine O-Palmitoyltransferase; Cells, Cultured; Enzyme Inhibitors; Epoxy Compounds; Fatty Acids; Female; Humans; Lipid Metabolism, Inborn Errors; Mitochondria; Oxidation-Reduction; Palmitic Acid; Pregnancy; Prenatal Diagnosis; Skin

1998
A gender-related defect in lipid metabolism and glucose homeostasis in peroxisome proliferator- activated receptor alpha- deficient mice.
    The Journal of clinical investigation, 1998, Sep-15, Volume: 102, Issue:6

    Topics: Animals; Carbohydrate Metabolism, Inborn Errors; Carnitine O-Palmitoyltransferase; Epoxy Compounds; Estradiol; Fatty Acids; Feedback; Female; Glucose; Glycogen; Hypoglycemia; Lipid Metabolism, Inborn Errors; Liver; Male; Mice; Mice, Inbred C57BL; Mitochondria; Myocardium; Oxidation-Reduction; Receptors, Cytoplasmic and Nuclear; Sex Factors; Transcription Factors

1998